9.

,
,

(
)

( )

(
)

10%
, 50%

, ,

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, (
)

(.
)

(
)

(.

) -

(.

)

( 50)

(
)



(Autosomal dominant cerebellar ataxia - ADCA):

(ADCA-I) - (SCA1,
2, 3, 4)

(ADCA-II), SCA7

ADCA - III): SCA5, SCA6

Friedreich-

Friedreich-

9
GAA

Friedreich-

(pes cavus; 50%)

Pes cavus

Friedreich-

2/3

1-15 .

je

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,

(SCA)

25

SCA1 -1
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SCA 6

(1
5000 )

,
, 2

20

(
)

DDT

()

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von Hippel
Lindau-

(
)

(),

2
-

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,

 (cerebellitis)

,

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ADHD

- --

(
)

,
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,

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