Professional Documents
Culture Documents
VACTER SYNDROME
VACTERL ASSOCIATION
-
:
314557224 -
021597232 -
, '- 2012
:
:..-.
4 :
2,145 :"
38 :
: .
:
: .1
: 25, ,4 .3 - .
: 25 . -.
Term Newborn
Small For Gestitation Age
Esophagial Arthresia
Upper Limb Deformitis
Susp. VACTER Syndrome.
G10P4E- 8 ml\hour
LIPOFUNDIN 20% I.V- 1.3 ml\hour
DORMICUM I.V-0.2 ml\hour
FENTANYL I.V-0.1 ml\hour
. 2
:
95% -Sat.
117 -Pulse
on skin 36.9-Temp.
:
- .
5-" .
-,
.
:
NA-131
K-5.3
CA.-1.18
GLUCOSSE-78
Hct-58
Ph-7.43
Po2-48
PCo2-45
Hc03-29/9
:
ventilation mode -SIMV TUBE
PEEP- 5
IT SET-2
PIP SET-20
PRESSURE SUPPORT-100
Fi02-32
PIP measured- 19
:
Thoracic Drein
Umblical vein catheter
Single umblical Arthery
:
.
:
UVC
- 4.
:
- 4.
.
" .
, .
" .
.
" .
Vacterl syndrome
.
,
.
.
(klippel feli syndrome and goldenhar syndrome:
", ) .
18
,
.
.
.
, ,
, ,
.
VACTERL
V - Vertebral anomalies
A - Anal atresia
C - Cardiovascular anomalies
T - Tracheoesophageal fistula
E - Esophageal atresia
R - Renal (Kidney) and/or radial anomalies
L - Limb defects
V - Vertebral anomalies
,
. 70 -
.
.
A - Anal atresia
55
.
.
C - Cardiovascular anomalies
75 ,
.VSD, TOF
.
T - Tracheoesophageal fistula
- ,
70- .
,
.
33- 15
.
E - Esophageal atresia
70
.
R - Renal
(Kidney) and/or radial anomalies
50 30
( 2
) ,
,
.
.
L - Limb defects
70 .
, ,
, .
"
,
.
.
3
.
.
.
.
,
.
Solomon, D. (2011). Vacterl/vater association.
Orphanet Journal of rare diseases, 6(56), 317. doi: 10.1186/1750-1172-6-56
http://www.cincinnatichildrens.org/health/v/
vacterl/
http://rarediseases.about.com/od/raredisease
sv/a/vacterl.htm
!!!