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VACTER SYNDROME
VACTERL ASSOCIATION

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314557224 -
021597232 -
, '- 2012

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4 :
2,145 :"
38 :
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: 25 . -.

Term Newborn
Small For Gestitation Age
Esophagial Arthresia
Upper Limb Deformitis
Susp. VACTER Syndrome.

G10P4E- 8 ml\hour
LIPOFUNDIN 20% I.V- 1.3 ml\hour
DORMICUM I.V-0.2 ml\hour
FENTANYL I.V-0.1 ml\hour
. 2

:
95% -Sat.
117 -Pulse
on skin 36.9-Temp.

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5-" .
-,
.

:
NA-131
K-5.3
CA.-1.18
GLUCOSSE-78
Hct-58
Ph-7.43
Po2-48
PCo2-45

Hc03-29/9


:
ventilation mode -SIMV TUBE
PEEP- 5
IT SET-2
PIP SET-20
PRESSURE SUPPORT-100
Fi02-32
PIP measured- 19
:
Thoracic Drein
Umblical vein catheter
Single umblical Arthery
:
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:
UVC

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Vacterl syndrome

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(klippel feli syndrome and goldenhar syndrome:
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18
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VACTERL

V - Vertebral anomalies
A - Anal atresia
C - Cardiovascular anomalies
T - Tracheoesophageal fistula
E - Esophageal atresia
R - Renal (Kidney) and/or radial anomalies
L - Limb defects

V - Vertebral anomalies
,
. 70 -
.

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A - Anal atresia

55
.

.

C - Cardiovascular anomalies
75 ,
.VSD, TOF

.

T - Tracheoesophageal fistula
- ,
70- .
,
.
33- 15
.

E - Esophageal atresia
70
.

R - Renal
(Kidney) and/or radial anomalies
50 30
( 2
) ,
,
.

.

L - Limb defects
70 .
, ,
, .
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Solomon, D. (2011). Vacterl/vater association.
Orphanet Journal of rare diseases, 6(56), 317. doi: 10.1186/1750-1172-6-56
http://www.cincinnatichildrens.org/health/v/
vacterl/
http://rarediseases.about.com/od/raredisease
sv/a/vacterl.htm

!!!

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