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Dini Rachmawati, drg, SpKGA.

Dentinogenesis Imperfecta
Inheritable dentinal defect during the
histodifferentiation stage of the tooth
A defect of predentin matrix amorphic,
disorganized, atubular circumpulpal dentin.

Dentinogenesis imperfecta divided into:

1. Shield type 1
Primary teeth tend to be more severely affected
than permanent teeth.
Periapical radiolucencies: bulbous crowns,
obliteration of pulp chambers, and root fracture
are evident.
An amber translucent tooth color is common.
Occur with osteogenesis imperfecta.

2. Shield type 2
Known as hereditary opalescent dentin
Both primary and permanent dentitions are
equally affected
Characteristics previously described for type 1
are the same.

3. Shields type 3
Involves teeth with a shell-like appearence and
multiple pulp exposures
It has occured exclusively in a triracial isolated
group in Maryland known as the Brandywine

Dentin Dysplasia
Involving the circumpulpal dentin and root
roothless teeth is an alternative descriptive
The teeth may be clinically normal but root
formation is abnormal to varying degrees.
Under microscope the coronal dentine is
normal but the root dentine is not, with masses
of abnormal dentine obliterating the pulp

Shields classification 1973
1. Shields type 1
normal primary and permanent crown
morphology with an amber translucency.
The roots tend to be short and sharply
Absent pulp chamber.

2. Shields type
Involves amber-colored primary teeth closely
resembling dentinogenesis imperfecta types 1
and 2
Permanent teeth appear normal, but
radiographically they demonstrate thistle-tubeshaped pulp chambers with multiple pup

Regional Odontodysplasia
Odontodysplasia is a condition representing a
localized arrest in tooth development thought to
result from a regional vascular developmental
Teeth have thin layers of poorly calcified enamel
and dentin with large, diffusely calcified pulp
chambers and shortened poorly defined roots.

The teeth have a ghost-like radiographic

appearance with shortened roots and shell-like
crowns and are dysmorphic in overall
No conclusive etiologic factor or inheritance
pattern has been identified that can explain
the reported cases.