)*+,-.+/&*$ 0+1/*23 +$% 2#.+/#% 3-43/+$1#3 5-64#2 +$%7*2 $+6# 8-$1/&*$ !33*1&+/#% ,#$#/&1 %&3*2%#23 I (fibiinogen) Foims clot (fibiin) Congenital afibiinogenemia, Familial ienal amyloiuosis II (piothiombin) Its active foim (IIa) activates I, v, vII, vIII, XI, XIII, piotein C,platelets Piothiombin u2u21uA, Thiombophilia III Tissue factoi Co-factoi of vIIa (foimeily known as factoi III) Iv Calcium Requiieu foi coagulation factois to binu to phospholipiu (foimeily known as factoi Iv)
v (pioacceleiin, labile factoi) Co-factoi of X with which it foims the piothiombinase complex Activateu piotein C iesistance vI 0nassigneu - olu name of Factoi va
vII (stable factoi, pioconveitin) Activates IX, X Congenital pioconveitinfactoi vII ueficiency vIII (Antihemophilic factoi A) Co-factoi of IX with which it foims the tenase complex Baemophilia A IX (Antihemophilic factoi B oi Chiistmas factoi) Activates X: foims tenase complex with factoi vIII Baemophilia B X (Stuait-Piowei factoi) Activates II: foims piothiombinase complex with factoi v Congenital Factoi X ueficiency XI (plasma thiomboplastin anteceuent) Activates IX Baemophilia C XII (Bageman factoi) Activates factoi XI, vII anu piekallikiein Beieuitaiy angioeuema type III XIII (fibiin-stabilizing factoi) Ciosslinks fibiin Congenital Factoi XIIIab ueficiency von Willebianu factoi Binus to vIII, meuiates platelet auhesion von Willebianu uisease