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, M 2010

Filip II - Skopje


2003-2009

Filip II - Skopje

DEFINICIJA
Zaboluvawa na KVS -disembriogeneza na srcevite
strukturi vo razli~en period na gestacijata
*Pediatrics, 2006
INCIDENCA (0,7- 1,7%)
*Europian journal Epidemiology, 2006

Korekcija na VSM = maksimalna informacija za


anatomskata/hemodinamskata sostojba, minimalno travmatski
metod
Od site kongenitalni malformacii, VSM imaat >>>
efekt vo novorodene~kata smrtnost
Filip II - Skopje

Filip II - Skopje

-

*
*
*A
*
*

*
T
A
. , 2007
*
Filip II - Skopje

30.0
9.0
7.5
7.2
6.2
5.6
5.2
4.8
3.9

T
6000

N = 7000

4637 (72.6%)

5000
4000
3000
883(19.1%)
2000
1000

304(5.0%)

182(3.0%)

18(0.3%)

0
CA
BG

Va
lvu

lar
s

urg
e

Ao
rti
cs
ry

urg
e

Filip II - Skopje

ry

Co
ng
.h e
art

Tu
mo
dis
.

rs

(e, 64 M, )

..
, ,
stand
by

Filip II - Skopje

ASD

Ao

M VSD

T/PAPVD

E + dg.

SV

.Fallot . ()

. VSD

M VSD

Filip II - Skopje

64 M

*
* 3-D

M
T -
vs >7

, ECG > 7

64 M

TGV
oAo

M
TF
Filip II - Skopje

-64MT

GV
Filip II - Skopje

-64 MT

PDA


Fallot
Filip II - Skopje

-64MT

II

Sy Scimitar-PAPVD
Filip II - Skopje

Filip II - Skopje


(2003-2009)

PDA; 35; 24%

PS; 39; 26%

CoAo; 7;
5%
VSD; 5; 3%

ASD II; 60; 41%

CAV &
Fallot; 2;
1%

Filip II - Skopje

N=148

Filip II - Skopje

Filip II - Skopje

Amplatz septal ocluder, n= 60


(7%)


,
< 1%,
7-8%
( follow up)

Filip II - Skopje

ASD
3 mm
(TTE v.s )
10-30mm ASD
4
-
204 hours
TEE

ASA 10mg/kgTT/ 6

75mg/24h-
3
Filip II - Skopje

n=39*
7%
,
PG >50mmHg (
CO)
BVP < RVSP PG
(PR)


()



* 2 TF

Filip II - Skopje

Filip II - Skopje


SPG 44
9mmHg
(14)





-
PR < 1 .

Filip II - Skopje

;
n=35
(9 ) %


,

(d < 2.5 mm)





(5%-10%)
Filip II - Skopje

-
33/35 . ,

(1 )
(23) Amplatzer
12
28 4 h

-

. -
(OR in stand by)
3

Filip II - Skopje

VSD- Amplatz perimembraneous ocluder


(5)

5-45
21 VSD

A-V loop

ECG AV
Amplatz perimembraneous ocluder
8-14mm

Filip II - Skopje

, n=7

, 6


PG 30 5 mmHg
Filip II - Skopje

-
55

PAH, DM II, , ,

O, 2005 ()
May, 2007 ,
( )

3
A 2007,
VSD occluder,
8 mm
Filip II - Skopje

Sy Eissenmanager
I - o: 07.12.2001
E PAH
(PA syst/med 110/65)
MReg.+3, TReg +4,VSD, 42mm
: A banding, MKR, TKR
PA- 29mm, PA syst/med 68/43

01/2005 , AV
18.02/2005 PM
18.08.2007 Amplatzer
device VSD
Th: ACE inh, , ,
OAT

Follow up 8 godini

II- o 05.11.2004
Eo: MReg.+4 (/
), TReg.+3
.A syst/med 110/60, LAP 30
:MVR, TKR, patch
VSD
. PA syst/med 60/23

Filip II - Skopje



TTE, TEE (3D), 64

Filip II - Skopje


T

, (in utero)


/
-

Filip II - Skopje


VSD, 60/64 . ASD
, 33/35 .
PG .
> 40%
96% . ,
18 8 .
(
),
,
M ,

Filip II - Skopje

2003
Filip II - Skopje

Filip II - Skopje

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