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T.C.

FIRAT NVERSTES
MHENDSLK FAKLTES
BYOMHENDSLK BLM
BTRME DEV

KONU
TRKYEDEK KAN HASTALIKLARI

HAZIRLAYAN
AYEGL ELK
10205007

DANIMAN
PROF.DR.MER MUNZUROLU

ELAZI,2014

NDEKLER
Sayfa
EKL VE TABLOLAR
TEEKKR...iiY
Y1.GR...........................................................................................................................1
1.1.Kann Grevleri.......................................................................................................1
1.1.1.Tama:.............................................................................................................1
1.1.2.Dzenleme:.......................................................................................................2
1.1.3 Koruma:............................................................................................................2
2. KANIN YAPISI ve FZYOLOJS................................................................................3
2.1.Plazma.....................................................................................................................3
2.2.ekilli elemanlar......................................................................................................3
2.2.1.Alyuvarlar (Eritrositler)....................................................................................4
2.2.2.Lkositler (Akyuvarlar)....................................................................................5
2.2.3.Lenfositler.........................................................................................................7
3.KAN HCRELERNN YAPIMI..................................................................................8
4.KAN HASTALIKLARI...............................................................................................10
4.1.Kan Hastalklarnda Genel Tehis Yntemleri......................................................10
4.1.1.Hematolojik testler:........................................................................................10
4.2.Trkiyedeki Kan Hastalklar...............................................................................11
4.2.1. Anemi ve eitleri.........................................................................................11
4.2.1.a.Demir Eksiklii Anemisi (Hipokrom Mikrositer Anemi)............................14
4.2.1.b.Hemolitik Anemi.........................................................................................15
4.2.1.c.Pernisiyz Anemi (Megablastik Anemi)......................................................17
4.2.1.d.Aplastik anemi.............................................................................................18
4.2.1.e.Orak Hcreli Anemi (Sickle Cell Anemi)....................................................19
4.2.2.Talasemi (Akdeniz Anemisi)..........................................................................21
4.2.2.a.Talasemi minr (talasemi taycl):........................................................21
4.2.2.b.Talasemi intermedia:...................................................................................22
4.2.2.c. Talasemi major:...........................................................................................22
4.2.3.Phtlama Bozukluklar.................................................................................23
4.2.3.1.Hemofili.......................................................................................................24
4.2.3.2.Trombositopeniler.......................................................................................26
4.2.4.Polisitemia Vera (Vaquez Hastal)...............................................................30
4.2.5. Lsemi...........................................................................................................31
4.2.5.a. Akut Myeloid Lsemi (AML)....................................................................32
4.2.5.b. Akut Lenfoblastik Lsemi (ALL)...............................................................33
4.2.5.c. Kronik Myeloid Lsemi (KML).................................................................34

5.2.5. Lenfoma.........................................................................................................35
4.2.5.a Hodgkin Hastal........................................................................................35
4.2.5.b Hodgking D Lenfoma (HDL Non-Hodgkin Lenfoma, NHL).................36
5.KAYNAKLAR.............................................................................................................39

EKL VE TABLOLAR
Sayfa
ekil 1.Anemide eritrositler......................................................................................................11

ekil 2.Hipoknomik Anemide eritrositler...................................................................................15


ekil 3.Orak Hcreli Anemide orak eklinde eritrositler..........................................................21
ekil 4.Yaa gre AML insidans..............................................................................................32
Tablo.1.Anemi iin maksimum dzeydeki Hb e Hemotokrit deeri........................................12
Tablo.2.Kanda bulunan phtlama faktrleri............................................................................24
Tablo.3.Trombositopenilerin fizyopatolojik snflamas...........................................................27

TEEKKR
Bu alma srasnda katklarn, desteklerini ve ilgisini esirgemeyen deerli Prof.Dr.mer
MUNZUROLU hocama teekkr bir bor bilirim. Benden maddi ve manevi desteklerini
esirgemeyen aileme sonsuz teekkrler.

ii

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