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Sieu Am Mot So Benh TBS Thuong Gap - GS. Loi
Sieu Am Mot So Benh TBS Thuong Gap - GS. Loi
bm sinh thng gp
Bs. Don Li
B mn Tim mch
Vin Tim mch
Thng lin nh
Thng lin nh
Bnh sinh:
1. Shunt T - P do c l TLN v Pnt > P np
. Tng gnh th tch NP v TP
. Tng lu lng qua tiu tun hon.
--> Cc tiu ng mch phi co phn x
--> Ri lon chuyn ho
2. Thnh cc tiu M phi dy v x (Pulmonary vascular disease)
. Tng sc cn c nh tiu tun hon
. i chiu shunt: phi-tri
. Suy tim phi, tr tun hon ngoi bin
(hi chng Eisenmenger)
Thng lin nh
Thng lin nh
Thng lin nh
Dc tm trng gim
Mt sng a
ng van gia tm thu
- TMP lc ch
- TMP lc ch
TLN
TLN
Siu m cn m
Siu m cn m
TLN - nh gi mc bnh
+ Kch thc l thng
< 10 mm
10 - 20 mm
> 20 mm
p lc ng mch phi
AL tb = 4V .t.tr2 + 10
Bnh thng: < 20 mmHg
AL t.tr = 4V c.t.tr2 + 10
Bnh thng: < 15 mmHg
AL tt
= 3 AL tb - 2 AL t.tr
Thng lin nh
Cc bnh phi hp:
. Nhiu l TLN
. HoHL: van dy, vng, sa van
. TMP lc ch
. Hp MP
tng lu lng
. HHL (Lutembacher)
...
Thng lin nh
Cc du hiu trc tip:
1. L TLN trn 2D
2. Shunt trn Doppler mu
3.
--------
xung
4. Ra bt cn m
5. Bt cn m sang nh tri
Thng lin nh
Cc du hiu gin tip:
1. Gin: NP, TP, MP
2. VLT di ng nghch thng
3. Van MP dng tng p
4. Vn tc dng MP ln - Gradient lu lng
5. Qp > Qc
6. Tng p lc MP: HoBL, HoP
Thng lin nh
Thng lin nh
Thng lin nh
Thng lin nh
Vena contracta
TLT - nh gi mc bnh
+ V tr l thng
+
+ Vena contracta
+ Tng gnh cc bung tim
+ Tng p lc MP: HoBL ?, HoP, qua Shunt
+ Qp/Qc
TLT - nh gi mc bnh
TLT
shunt nh
shunt ln
Vena contracta
< 3 mm
> 5 mm
Cc bung tim
khng gin
gin
AL mp
bnh thng
tng
Qp/Qc
< 1,3
> 1,3
Nhiu l TLT
H ch
Cn ng M
Hp MP
T chng Fallot
Thng sn nh tht
o gc cc M ln
Cn ng ng mch
Cn ng ng mch
Cn ng ng mch
Cn ng ng mch
Cn ng ng mch
+ Kch thc ng, hnh dng ng ?
+ Gin NT, TT
+ Chc nng tm thu TT
+ p lc MP: HoBL, shunt qua M
+ Qc/Qp
Cn ng ng mch
Cn ng ng mch
Cn ng ng mch
Cn ng ng mch
Chn on phn bit
+ D ng mch vnh
Cn ng ng mch
Chn on phn bit
+ D ng mch vnh vo MP
Cn ng ng mch
Chn on phn bit
+ D ng mch vnh vo MP
Cn ng ng mch
Chn on phn bit
+ D ng mch vnh
Cn ng ng mch
Chn on phn bit
+ D ng mch vnh
+ V phnh xoang Valsalva
+ D ch ph
+ D ng - tnh mch phi
Hp ng ra tht phi
Cc thit
Cc thit
Cc thit
Hp ng ra tht phi
Hp di van MP
- Tht phi hai bung
- Hp phu
Hp vng van MP
Hp van MP
Hp trn van MP
- Hp thn
- Hp nhnh
Hp ng ra tht phi
Hp di van MP
- Hp phu
Hp phu
Hp phu
Hp phu
Hp van MP
Hp van MP
Hp van MP
Hp phu v van MP
Hp trn van MP
Hp trn van MP
T chng Fallot
T chng Fallot
nh gi p lc t.thu MP
ALttTP - ALttNP = 4 VHoBL2
chuyn v phng trnh:
ALttTP = 4 VHoBL2 + ALttNP
nh gi p lc t.thu MP
5 mmHg
ALttNP:
10 mmHg
15 mmHg
30-40
40-70
> 70
nh gi p lc t.trng MP
ALttrMP - ALttrTP = 4 V2
Chuyn v
ALttrMP = 4 V2 + ALttrNP
Cho ALttrNP = ALttrTP = 10 mmHg
ALttrMP = 4 V2 + 10 (mmHg)
nh gi p lc tr.bnh MP
ALtbMP = 4 V2 + 10 (mmHg)