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MKB v1 Part1 PDF
MKB v1 Part1 PDF
1 ( 1)
International
ICD - 10
Statistical
Classification
of Diseases and
Related Health
Problems
Tenth Revision
Volume 1
1 ( 1)
-
-
,
.
2003
1*
-
,
, -
2
3
* 1 - -
. IXIII, XIV
XXI, ,
, .
,
; 10
: 1 ;
2 ; 3
1. I. : 10
(NLM Classification: WB 15)
ISBN 92 4 154419 8 (v. 1) ISBN 9548541122 (. 1)
ISBN 92 4 154420 1 (v. 2) ISBN 9548541130 (. 2)
ISBN 92 4 154421 X (v. 3) ISBN 9548541149 (. 3)
World Health Organization, 1992
, 2003
2 .
, , -
, , .
.
:
: .
........................................................................................................ 1
................................................................................................... 5
.................................. 7
............................................................. 30
,
I ..................................... 119
II ............................................................................... 204
III ,
, .............. 289
IV ,
............................... 313
V ........................................ 359
VI ......................................................... 453
VII .............................................. 499
VIII .................................... 533
IX .................................. 547
X .................................................... 597
XI ........................................ 636
XII ....................................... 691
XIII -
.............................................................. 726
10 -
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Australian Institute of Health
GPO Box 570
Canberra ACT 2601,
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Office of Population Censuses and Surveys
St. Catherines House
Kingsway 10
London WC2B 6JP
England
National Center for Health Statistics
6525 Belcrest Road
Hyattsville, MD 20782
United States of America
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Peking Union Medical College Hospital
Chinese Academy of Medical Sciences
Beijing 100730
China ( )
INSERM
44 Chemin de Ronde
F-78110 Le Vsinet
France ( )
Department of Social Medicine
University Hospital
S-751 85 Uppsala
Sweden ( )
Faculdade de Sade Publica/Universidade de So Paulo
Avenida Dr Arnaldo 715,
0255 So Paulo, SP
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Centro Venezolano de Clasificatin de Enfermedades
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28
1. , 1975 ., . 1.
, , 1977, . iii - xxiv.
2. Report of the Expert Committee on the Internatioinal Classification of
Diseases - 10th Revision: First Meeting. Geneva, World Health Organiza-
tion, 1984 (unpublished document DES/EC/ICD-10/84.34).
3. Report of the Expert Committee on the Internatioinal Classification of
Diseases - 10th Revision: Second Meeting. Geneva, World Health Organi-
zation, 1987 (unpublished document WHO/DES/EC/ICD-10/83.38).
4. Report of the Preparatory Meeting on ICD-10. Geneva, World Health Or-
ganization, 1983 (unpublished document DES/ICD-10/83.19).
5. Lay reporting of health information. Geneva, World Health Organization,
1978.
6. International Conference on Health Statistics for the Year 2000. Budapest,
Statistical Publishing House, 1984.
7. Report of the Consultation on Primary Care Classification. Geneva,
World Health Organization, 1985 (unpublished document DES/PHC/
85.7).
8. International Classification of Impairments, Disabilities, and Handicaps.
Geneva, World Health Organization, 1980.
9. WHO Official Records, No. 233, 1976, p. 18.
10. International Classification of Procedures in Medicine. Geneva, World
Health Organization, 1978.
29
I
(0099)
(0009)
00
01
02
03
04
05
06
07
08
09
(1519)
15 , -
16 , -
17
18
19
(2028)
20
21
22
23
24
25
26
27
28 ,
30
(3049)
30 [ Hansen]
31 ,
32
33
34
35
36
37
38
39
40
41
42
43
44
46
48 ,
49
, (5064)
50
51
52
53
54
55 ()
56 ,
57
58 ,
59
60 [herpes simplex]
63 , , -
64 , ,
, (6569)
65
66
31
67 []
68
69 ,
, (7074)
70 , Chlamydia psittaci
71
74 ,
(7579)
75
77 [ ]
78 -
79
(8089)
80
81
82
83 ,
84 ,
85 ,
86 ,
87
88 , -
89 ,
,
(9099)
90 [ ]
91 , -
92 ,
93 , , -
94 , ,
95
96
98 ,
99 ,
32
, -
(0009)
00 - [herpes simplex]
01 [varicella]
02 Herpes zoster
03
04 ,
05
06 [ ]
07
08 ,
,
09 ,
,
(1519)
15
16
17
18
19 ,
, [HIV]
(2024)
20 ,
[HIV],
21 ,
[HIV],
22 ,
[HIV],
23 ,
[HIV],
24 ,
[HIV],
(2534)
25
26
27
30
33
33 ,
34
(3549)
35
36
37
38
39
40
41
42
43
44
45
46
47
48 ,
49 ,
(5064)
50 , Plasmodium falciparum
51 , Plasmodium vivax
52 , Plasmodium malariae
53
54 ,
55
56
57 Chagas
58
59
60 ,
64 ,
(6583)
65 []
66
67
68
69
34
70
71 ,
72
73
74
75
76
77
78
79
80
81 ,
82 ,
83
, (8589)
85
86
87
88
89 ,
(9094)
90
91
92
94 -
, (9597)
95 , -
96 , -
97 , -
(99)
99
35
II
(C00D48)
(C00C97)
, -
(C00C14)
C00
C01
C02
C03
C04
C05
C06
C07
C08
C09
C10
C11
C12
C13
C14
,
(C15C26)
C15
C16
C17
C18
C19
C20
C21
C22 -
36
C23
C24
C25
C26
(C30C39)
C30
C31
C32
C33
C34
C37
C38 ,
C39
(C40C41)
C40
C41
(C43C44)
C43
C44
-
(C45C49)
C45
C46 Kaposi
C47 -
37
C48 -
C49
(C50)
C50
(C51C58)
C51
C52
C53
C54
C55 -
C56
C57
C58
(C60C63)
C60
C61
C62
C63
(C64C68)
C64 ,
C65
C66
C67
C68
, -
(6972)
C69
C70
38
C71
C72 , -
-
(7375)
C73
C74
C75
, -
(7680)
C76
C77 -
C78
C79
C80
, -
(8196)
C81 Hodgkin []
C82 []
C83
C84 -
C85
C88
C90 -
C91 []
C92 []
C93
C94
C95
C96 -
,
39
() -
(97)
C97 ()
in situ (D00D09)
D00 in situ ,
D01 in situ -
D02 in situ
D03 in situ
D04 in situ
D05 in situ
D06 in situ
D07 in situ
D09 in situ
(D10D36)
D10 ,
D11 -
D12 , ,
D13 -
D14 -
D15 -
D16 -
D17
D18
D19
D20 -
D21
D22
40
D23
D24
D25
D26
D27
D28 -
D29
D30
D31 -
D32
D33
D34
D35 -
D36 -
(D37D48)
D37 -
D38
,
D39
D40
D41 -
D42
D43
D44 -
D45
D46
41
D47
,
D48 -
III
,
,
(D50D89)
, (D50D53)
D50
D51 12-
D52
D53 ,
(D55D59)
D55 ,
D56
D57 -
D58
D59
(D60D64)
D60 () [-
]
D61
D62
D63* ,
D64
,
(D65D69)
D65 [ -
]
D66 VIII
D67 IX
D68
42
D69
(D70D77)
D70
D71 - -
D72
D73
D74
D75
D76 , -
D77* -
,
, (D80D89)
D80
D81
D82 ,
D83
D84
D86
D89 , -
IV
,
(0090)
(E00E07)
00
01 , ,
02 ,
03
04
05 []
43
06
07
(1014)
10
11
12 ,
13
14 ,
(1516)
15
16
(2035)
20
21 -
22
23
24 Cushing
25
26
27
28
29
30 ,
31
32
34
35* , -
(4046)
40
41
42
43 - ,
44 -
44
45 , -
46 - ,
(5064)
50
51
52 []
53
54
55 D
56
58
59
60
61
63
64
(6568)
65
66
67
68
(7090)
70
71
72
73
74
75 -
76
77
78 -
79
80
45
83
84
85
86 []
87 - --
88
89 , -
,
90*
,
V
(F00F99)
, ,
(F00F09)
F00* Alzheimer
F01
F02* ,
F03 ,
F04 ,
F05 , -
F06 , -
F07 , -
,
F09 , -
,
(F10F19)
F10 , -
46
F11 , -
F12 , -
F13 , -
F14 , -
F15 , -
( )
F16 , -
F17 , -
F18 , -
F19 , -
, (F20F29)
F20
F21
F22
F23
F24
F25
F28
F29 ,
[ ] (F30F39)
F30
F31
F32
F33
F34 [ -
]
F38 []
F39 [],
47
,
(F40F48)
F40
F41
F42 -
F43
F44 []
F45
F48
,
(F50F59)
F50
F51
F52 , -
F53 , -
,
F54 , -
,
F55 ,
F59 ,
,
(F60F69)
F60
F61
F62 , -
F63
F64
F65
F66 , -
F68 -
F69 , -
48
(F70F79)
F70
F71
F72
F73
F78
F79 ,
(F80F89)
F80
F81
F82 -
F83
F84
F88
F89 ,
, -
(F90F98)
F90
F91
F92
F93 ,
F94 ,
F95
F98 , -
(F99)
F99
49
VI
(G00G99)
(G00G09)
G00 ,
G01* ,
G02* , -
G03 ,
G04 ,
G05* , , -
G06
G07* -
,
G08
G09 -
,
(G10G13)
G10 Huntington
G11
G12
G13* ,
,
(G20G26)
G20 Parkinson
G21
G22* ,
G23
G24
G25
G26* ,
50
(G30G32)
G30
G31 , -
G32* -
,
(G35G37)
G35
G36
G37 -
(G40G47)
G40
G41
G43
G44
G45 []
G46*
G47
,
(G50G59)
G50
G51
G52
G53* , -
G54
G55* , -
G56
G57
G58
G59* ,
51
(G60G64)
G60
G61
G62
G63* ,
G64
- (G70G73)
G70 Myasthenia gravis - -
G71
G72
G73* - -
,
(G80G83)
G80
G81
G82
G83
(G90G99)
G90 []
G91
G92
G93
G94* , -
G95
G96
G97 ,
G98 , -
G99* , -
52
VII
(0059)
, (0006)
00
01
02
03* ,
04
05
06* , -
(1013)
10
11
13* ,
, , (1522)
15
16
17
18
19* , -
20
21
22* , -
(2528)
25
26
27
28* , -
53
(3036)
30
31
32* , -
33
34
35
36* ,
(4042)
40
42* ,
(4345)
43
44
45* -
,
(4648)
46
47 [2-]
48* [2-]
,
,
, (4952)
49
50
51
52
(5354)
53
54
(5559)
55
57
54
58* , -
59 -
VIII
(6095)
(6062)
60
61
62* , -
(6575)
65
66
67* , -
68 []
69 []
70
71
72
73
74
75*
,
(8083)
80
81
82* ,
83
55
(9095)
90 , (-
)
91
92
93 ,
94* , -
95
,
IX
(I00I99)
(I00I02)
I00
I01
I02
(I05I09)
I05
I06
I07
I08
I09
(I10I15)
I10 []
I11
I12 [ ]
I13
I15
(I20I25)
I20
I21
I22
56
I23
I24
I25
(I26I28)
I26
I27
I28
(I30I52)
I30
I31
I32* ,
I33
I34
I35
I36
I37
I38
I39* ,
I40
I41* ,
I42
I43* ,
I44
I45
I46
I47
I48
I49
I50
I51
I52* , -
(I60I69)
I60
I61
57
I62
I63
I64 ,
I65 , -
I66 , -
I67
I68* , -
I69
, (I70I79)
I70
I71
I72
I73
I74
I77
I78
I79* , -
,
, , -
(I80I89)
I80
I81
I82
I83
I84
I85
I86
I87
I88
I89
58
(I95I99)
I95
I97 ,
I98* ,
I99
X
(J00J99)
(J00J06)
J00 []
J01
J02
J03
J04
J05 []
J06
(J10J18)
J10 ,
J11 ,
J12 ,
J13 , Streptococcus pneumoniae
J14 , Haemophilus influenzae
J15 ,
J16 , , -
J17* ,
J18
59
(J20J22)
J20
J21
J22 ,
(J30J39)
J30
J31 ,
J32
J33
J34
J35
J36
J37
J38 , -
J39
(J40J47)
J40 ,
J41 -
J42 ,
J43
J44
J45
J46 [status asthmaticus]
J47
, (J60J70)
J60
J61 , -
J62 , ,
J63 ,
J64 ,
J65 ,
J66 ,
60
J67 ,
J68 ,
, ,
J69 ,
J70 ,
, -
(J80J84)
J80 [] -
J81
J82 ,
J84
(J85J86)
J85
J86
(J90J94)
J90 ,
J91* ,
J92
J93
J94
(J95J99)
J95 , -
J96 ,
J98
J99* ,
61
XI
(0093)
, (0014)
00
01
02
03
04
05
06
07 [ -
]
08
09 ,
10
11
12
13
14
, (2031)
20
21
22
23* , -
25
26
27
28
29
30
31
(3538)
35
36
62
37 ,
38
(4046)
40
41
42
43
44
45
46 ,
(5052)
50 Chron [ ]
51
52
(5563)
55
56
57
58
59
60
61
62
63
(6567)
65
66
67* , -
(7077)
70
71
72 ,
73 ,
74
63
75
76
77* , -
,
(8087)
80 []
81
82
83
85
86
87* , -
,
(9093)
90
91
,
92
93* ,
XII
(L00L99)
(L00L08)
L00
L01
L02 ,
L03
L04
L05
L08
64
(L10L14)
L10
L11
L12
L13
L14* ,
(L20L30)
L20
L21
L22
L23
L24 [irritant]
L25 ,
L26
L27
L28
L29
L30
(L40L45)
L40
L41
L42
L43
L44
L45* , -
(L50L54)
L50
L51 Erythema multiforme
L52 Erythema nodosum
L53
L54* ,
65
,
(L55L59)
L55
L56 , -
L57 ,
L58
L59 ,
(L60L75)
L60
L62* ,
L63
L64
L65
L66
L67
L68
L70
L71
L72
L73
L74
L75
(L80L99)
L80
L81
L82
L83 Acanthosis nigricans
L84
L85
L86* ,
L87
L88
L89
L90
L91
66
L92
L93
L94
L95 ,
L97 ,
L98 , -
L99* ,
XIII
-
(0099)
(0025)
(0003)
00
01*
,
02
03* , -
(0514)
05
06
07*
08 []
09* [] ,
10
11
12
13
14* ,
67
(1519)
15
16 [ ]
17 [ ]
18 -
19
(2025)
20
21
22
23
24
25 ,
(3036)
30
31
32 lupus erithematodes
33
34
35
36* ,
(4054)
(4043)
40
41
42
43
(4549)
45
46
47
48
49* ,
68
(5054)
50
51
53 ,
54
(6079)
(6063)
60
61
62
63* ,
(6568)
65
66
67
68*
,
(7079)
70 , , -
71
72
73* , -
75
76 ,
77
79 ,
(8094)
(8085)
80
81
82* ,
83
69
84
85
(8690)
86
87
88 Paget [ ]
89
90* ,
(9194)
91
92
93
94
-
(9599)
95 -
96 -
,
99 ,
XIV
-
(N00N99)
(N00N08)
N00
N01
N02
N03
N04
N05 ,
N06
N07 ,
N08* ,
70
(N10N16)
N10
N11
N12 , -
N13
N14 ,
N15
N16* ,
(N17N19)
N17
N18
N19 ,
(N20N23)
N20
N21
N22* , -
N23 ,
(N25N29)
N25 , -
N26 ,
N27
N28 ,
N29* , -
(N30N39)
N30
N31 , -
N32
71
N33* ,
N34
N35
N36
N37* ,
N39
(N40N51)
N40
N41
N42
N43
N44
N45
N46
N47 ,
N48
N49 , -
N50
N51* , -
(N60N64)
N60
N61
N62
N63 ,
N64
(N70N77)
N70
N71 ,
N72
N73
N74* -
,
N75
N76
72
N77* , -
(N80N98)
N80
N81
N82
N83 , -
N84
N85 , -
N86
N87
N88
N89
N90
N91 ,
N92 ,
N93
N94 ,
N95
N96
N97
N98 ,
- (N99)
N99 -
,
73
XV
,
(0099)
, (0008)
00 []
01
02
03
04
05
06 ,
07
08 , -
, -
, (1016)
10 , , -
11
12 -
13 -
14 -
15
16 ,
,
(2029)
20
21
22
23 -
24
25
74
26 ,
28
29
,
-
(3048)
30
31 ,
32 -
33 -
34 -
35 -
36 -
40
41
42
43
44
45 [abruptio placentae]
46 ,
47
48
(6075)
60
61
62
63
64 -
65
66
75
67 , -
,
68 , [-
]
69 -
70
71
72
73
74 -
75 , -
(8084)
80
81 - -
82
83
84
, (8592)
85
86
87
88
89
90 ,
91 ,
92 , -
, (9599)
95
96 ,
42 , -
97
76
98 ,
, , -
99 , , -
,
XVI
,
(P00P96)
, ,
(P00P04)
P00 ,
P01 -
P02 ,
,
P03
P04 -
,
, -
(P05P08)
P05
P07 ,
,
P08 ,
(P10P15)
P10 ,
P11
P12
77
P13
P14
P15
- ,
(P20P29)
P20
P21
P22
P23
P24
P25 ,
P26 ,
P27 , -
P28 ,
P29 - , -
, (P35P39)
P35
P36
P37
P38
P39 , -
(P50P61)
P50
P51
P52 -
P53
P54
P55
P56 ,
P57
78
P58 ,
P59
P60 -
P61
-
, (P70P74)
P70 ,
P71
P72
P74 -
(P75P78)
P75*
P76
P77
P78 -
, ,
(P80P83)
P80
P81
P83 ,
, (P90P96)
P90
P91
P92 ,
P93 , -
,
P94
P95
P96 ,
79
XVII
[ ],
(Q00Q99)
[ ]
(Q00Q07)
Q00
Q01
Q02
Q03
Q04 [ ]
Q05 Spina bifida
Q06 [ ]
Q07 [ ]
[ ] , ,
(Q10Q18)
Q10 [ ] ,
Q11 ,
Q12 [ ]
Q13 [ ]
Q14 [ ]
Q15 [ ]
Q16 [ ] , -
Q17 [ ]
Q18 [ ] -
[ ] -
(Q20Q28)
Q20 [ ] -
80
Q21 [ ] -
Q22 [ ]
Q23 [ ] -
Q24 [ ]
Q25 [ ]
Q26 [ ]
Q27 [ ] -
Q28 [ ]
[ ]
(Q30Q34)
Q30 [ ]
Q31 [ ]
Q32 [ ] -
Q33 [ ]
Q34 [ ] -
[ ] (Q35Q37)
Q35 [ ]
Q36 [ ]
Q37 [ -
]
[ ]
(Q38Q45)
Q38 [ ] , -
Q39 [ ]
Q40 [ ]
Q41 ,
Q42 ,
Q43 [ ]
81
Q44 [ ] ,
Q45 [ ] -
[ ]
(Q50Q56)
Q50 [ ] , -
Q51 [ ] -
Q52 [ ]
Q53
Q54
Q55 [ ]
Q56
[ ]
Q60Q64)
Q60
Q61
Q62
Q63 [ ]
Q64 [ ] -
[ ] -
(Q65Q79)
Q65
Q66
Q67 - , , -
Q68 -
Q69
Q70
Q71
Q72
82
Q73
Q74 [ ]
()
Q75 [ ]
Q76 [ ]
Q77 -
Q78
Q79 [ ] --
,
[ ] (Q80Q89)
Q80
Q81 Epidermolysis bullosa
Q82 [ ]
Q83 [ ]
Q84 [ ]
Q85 ,
Q86 [ ], -
, -
Q87 [
],
Q89 [ ], -
, (Q90Q99)
Q90 Down
Q91 Edward Patau
Q92 , -
Q93 ,
Q95 -
,
Q96 Turner
Q97 , -
83
Q98 , -
Q99 ,
XVIII
, ,
,
(R00R99)
, - -
(R00R09)
R00
R01
R02 ,
R03 -
R04
R05
R06
R07
R09 , --
,
(R10R19)
R10
R11
R12
R13
R14
R15
R16 ,
R17
R18
R19 , -
84
,
(R20R23)
R20
R21
R22 ,
R23
, -
(R25R29)
R25
R26
R27
R29 , -
-
,
(R30R39)
R30 ,
R31
R32 ,
R33
R34
R35
R36
R39 , -
, , -
, (R40R46)
R40 ,
R41 ,
R42
R43
R44 ,
R45 , -
85
R46 , -
, (R47R49)
R47 ,
R48
,
R49
(R50R69)
R50
R51
R52 ,
R53
R54
R55 []
R56 ,
R57 ,
R58 ,
R59
R60 ,
R61
R62
R63 , -
R64
R68
R69
, ,
(R70R79)
R70 -
[]
R71
R72 ,
R73
R74
R75 -
[HIV]
86
R76 , -
R77
R78 ,
R79
, , -
(R80R82)
R80
R81
R82 , -
, ,
,
(R83R89)
R83 ,
R84 ,
R85 ,
R86 ,
R87 ,
R89 ,
,
, -
, -
(R90R94)
R90 , -
-
R91 , -
R92 , -
87
R93 , -
-
R94 , -
(R95R99)
R95
R96
R98
R99
XIX
,
(S00T98)
(S00S09)
S00
S01
S02
S03 , -
S04
S05
S06
S07
S08
S09
(S10S19)
S10
S11
S12
S13 , -
S14
S15
88
S16
S17
S18
S19
(S20S29)
S20
S21
S22 (), -
S23 , -
S24
S25
S26
S27
S28
S29
, , -
(S30S39)
S30 ,
S31 ,
S32
S33 , -
S34 -
,
S35 ,
S36
S37
S38 , -
S39 ,
(S40S49)
S40
S41
S42
89
S43 , -
S44
S45 -
S46
S47
S48
S49
(S50S59)
S50
S51
S52
S53 , -
S54
S55
S56
S57
S58
S59
(S60S69)
S60
S61
S62
S63 , -
S64
S65
S66
S67
S68
S69
(S70S79)
S70 -
90
S71
S72
S73 , -
S74
S75
S76 -
S77
S78
S79
(S80S89)
S80
S81
S82 , -
S83 , -
S84
S85
S86
S87
S88
S89
(S90S99)
S90
S91
S92
S93 , -
S94
S95
S96
S97
S98
91
S99
, (0007)
00 ,
01 ,
02 ,
03 , , -
04 ,
05 , -
06 , , -
07 ,
, -
(0814)
08
09 -
10
11
12
13
14
(1519)
15
16
17
18
19 -
(2032)
,
(2025)
20
21
92
22
,
23
24
,
25 -
(2628)
26 , -
27
28
-
(2932)
29
30
31 , -
32 , -
(3335)
33
34
35 , , -
, -
(3650)
36
37
38 , -
,
39 , -
40 []
93
41
42 , , -
43 , -
44 , -
45 , , -
,
46 , -
-
47 , -
48 ,
49 ,
, , -
,
50 -
,
,
(5165)
51
52
53
54
55
56
57
58
59 ,
60
61 ,
62 ,
63
94
64 -
65
(6678)
66
67
68
69
70
71
73 [-
]
74
75
78 ,
(79)
79 ,
, -
(8088)
80 , , -
81 ,
82 , -
,
83 , - ,
84 ,
,
85 , ,
86
87 ,
88
,
95
, -
(9098)
90
91
92
93
94 , ,
95 ,
96 ,
97 ,
98 -
XX
(V01Y98)
(V01V99)
, (V01V09)
V01 ,
V02 ,
V03 , , -
V04 , -
V05 , -
V06 , -
V09 ,
96
, (V10V19)
V10 , -
V11 ,
V12 ,
V13 , , -
V14 , -
V15 , -
V16 ,
V17 , -
V18 ,
V19 ,
, (V20V29)
V20 ,
V21 ,
V22 ,
V23 , ,
V24 , -
V25 , -
V26 ,
V27 ,
V28 ,
97
V29 , -
, , -
(V30V39)
V30 ,
-
V31 ,
V32 ,
V33 ,
, -
V34 ,
-
V35 ,
-
V36 ,
V37 ,
-
V38 ,
V39 ,
,
(V40V49)
V40 , -
V41 , -
98
V42 ,
V43 , -
,
V44 , -
V45 , -
-
V46 , -
V47 , -
V48 , -
V49 ,
,
(V50V59)
V50 ,
-
V51 ,
V52 ,
V53 ,
, -
V54 ,
-
V55 ,
-
99
V56 ,
V57 ,
-
V58 ,
V59 ,
,
(V60V69)
V60 ,
V61 ,
V62 ,
V63 ,
,
V64 ,
-
V65 ,
-
V66 ,
-
V67 ,
V68 ,
V69 ,
100
, -
(V70V79)
V70 , -
V71 , -
V72 , -
V73 , -
, -
V74 , -
V75 , -
V76 , -
V77 , -
V78 ,
V79 , -
, (V80V89)
V80 , -
,
V81 ,
V82 ,
V83 , ,
, -
V84 , ,
,
101
V85 , ,
, -
V86 , -
, -
, , -
V87 ,
V88 ,
V89 -
(V90V94)
V90 -
V91
V92 ,
,
V93 , -
V94
(V95V97)
V95 ,
,
V96 ,
, ,
V97
(V98V99)
V98
V99 ,
102
(W00X59)
(W00W19)
W00 ,
W01 ,
W02 , ,
-
W03
W04
W05 ,
W06 ,
W07 ,
W08 ,
W09 ,
W10
W11
W12
W13 ()
W14
W15 ( )
W16 , ,
W17
W18
W19 ,
(W20W49)
W20 ,
W21
W22
W23 , ,
W24 , -
W25
W26 ,
W27
103
W28
W29 -
W30
W31
W32
W33 , -
W34
W35 ,
W36 ,
W37 , ,
W38 , -
W39
W40
W41
W42
W43
W44
W45
W49
(W50W64)
W50 , , , ,
W51
W52 ,
W53
W54
W55
W56
W57 -
W58
W59
W60 -
104
W64
(W65W74)
W65
W66
W67
W68
W69
W70
W73
W74 ,
(W75W84)
W75
W76
W77
W78
W79 , -
W80 ,
W81
W83
W84 ,
, , -
-
(W85W99)
W85 ,
W86 ,
W87 ,
W88
W89
W90
W91 ,
W92
W93
105
W94 -
W99 -
, (0009)
00 () -
01 ()
02
03 -
04
05 ()
06 -
08 , -
09 ,
() (1019)
10 , , -
11
12
13
14
15
16 ,
17 ,
18
19 -
(2029)
20
21
22
106
23 ,
24 () -
25
26
27
28
29
(3039)
30
31
32
33
34
35
36 ,
37
38
39
(4049)
40 ,
41 , -
, , , -
42 -
[],
43 -
,
44 -
,
45
46 ,
47 -
107
48
49 -
, (5057)
50
51
52
53
54
57 ,
(5859)
58
59
(6084)
60 -
,
61 ,
, , -
,
62 -
[],
63
,
64
,
65
66 -
67 -
68
69
70 , -
71
72
108
73 ,
74
75 -
76 ,
77 , -
78
79
80
81
82
83
84
(85Y09)
85 ,
86
87
88
89
90 -
91 ,
92
93
94 , -
95
96
97 ,
98 ,
109
99
Y00
Y01
Y02
Y03
Y04
Y05
Y06
Y07
Y08
Y09
(Y10Y34)
Y10 , -
,
Y11 , , -
, , -
,
Y12 [-
], , -
Y13 , -
, -
Y14
, ,
Y15 ,
Y16 , -
, -
Y17 -
,
Y18 , -
Y19 -
,
Y20 , ,
Y21 ,
110
Y22 , -
Y23 , -
,
Y24 -
,
Y25 ,
Y26 , ,
Y27 , , -
Y28 ,
Y29 ,
Y30 , , -
Y31 , ,
Y32 , -
Y33 ,
Y34
(Y35Y36)
Y35
Y36
(Y40Y84)
, , -
(Y40Y59)
Y40
Y41
Y42 , -
Y43
Y44 ,
Y45 , -
Y46
111
Y47 , []
Y48
Y49 ,
Y50 , , -
Y51 , -
Y52 , - -
Y53 , -
Y54 , ,
Y55 ,
Y56 ,
, , , -
Y57
Y58
Y59
-
(Y60Y69)
Y60 , ,
Y61
Y62 -
Y63 -
Y64
Y65 -
Y66
Y69
,
112
, ,
(Y70Y82)
Y70 ,
Y71
- ,
Y72 , ,
Y73 ,
,
Y74 -
,
Y75 , ,
Y76 , -
,
Y77 , ,
Y78 , -
Y79 , -
Y80 ,
Y81 , -
,
Y82 ,
, -
, -
(Y83Y84)
Y83 ,
,
-
Y84 ,
,
113
(Y85Y89)
Y85
Y86
Y87 , -
[],
Y88
Y89
, -
, (Y90Y98)
Y90 , -
Y91 , -
Y95
Y96 ,
Y97 ,
Y98 ,
XXI
,
(Z00Z99)
, -
(Z00Z13)
Z00 ,
Z01 ,
Z02
Z03
Z04
Z08 -
114
Z09 ,
Z10
Z11 -
Z12 -
Z13 -
, -
(Z20Z29)
Z20 -
Z21 ,
[HIV]
Z22
Z23
Z24
Z25
Z26 -
Z27 -
Z28
Z29
, , -
(Z30Z39)
Z30
Z31
Z32
Z33 ,
Z34
Z35 , -
115
Z36 [-
]
Z37
Z38
Z39
,
-
(Z40Z54)
Z40
Z41 ,
Z42
Z43
Z44
Z45
Z46
Z47
Z48
Z49 ,
Z50 , -
Z51
Z52
Z53 , -
Z54
, -
(Z55Z65)
Z55 ,
Z56 ,
Z57
Z58 ,
Z59 , -
Z60 ,
Z61 , -
Z62 ,
116
Z63 , , -
Z64 , -
Z65 ,
, -
(Z70Z76)
Z70 ,
Z71 ,
,
Z72 ,
Z73 ,
Z74 , , -
Z75 , -
Z76 , -
, -
,
(Z80Z99)
Z80
Z81 -
Z82 , -
,
Z83
Z84
Z85
Z86
Z87 -
Z88 , -
Z89
117
Z90 ,
Z91 , -
Z92
Z93 ,
Z94
Z95
Z96
Z97
Z98
Z99
,
118
I
(0099)
: ,
:
(Z22.)
,
, -
, ( -
, -
[HIV]) (O98.)
, -
( ,
,
,
[HIV]) (3539)
(J00J22)
:
0009
1519
2028
A3049
5064 ,
6569 ,
7074 ,
7579
8089
9099 , -
0009 , -
1519
119
2024 ,
[HIV]
2534
3549
5064
6583
8589 ,
9094
9597 ,
99
(0009)
00
00.0 , 01, -
cholerae
00.1 , 01, -
eltor
-
00.9 ,
01
01.0
, Salmonella typhi
01.1
01.2
01.3
01.4 ,
, Salmonella paratyphi
120
02
: ( ), -
Salmonella , -
S. typhi S. paratyphi
02.0
02.1
02.2
(-):
(01.3*)
(G01*)
(90.2*)
(J17.0*)
(N16.0*)
02.8
02.9 ,
03
03.0 , Shigella dysenteriae
[ Shiga-Kruse]
03.1 , Shigella flexneri
03.2 , Shigella boydii
03.3 , Shigella sonnei
D
03.8
03.9 ,
121
04
: (05.)
(18.3)
04.0 , Es-
cherichia coli
04.1 , Es-
cherichia coli
04.2 , Es-
cherichia coli
04.3 ,
Escherichia coli
04.4 , Escheri-
chia coli
, Escherichia coli
04.5 , Campylobacter
04.6 , Yersinia enterocolitica
: (28.2)
04.7 , Clostridium difficile
04.8
04.9 ,
05
: , Escherichia coli
(04.004.4)
(32.)
-
(02.)
(6162)
05.0
122
05.1
, Clostri-
dium botulinum
05.2 , Clostridium
perfringens [Clostridium welchii]
Pig-bel
05.3 , Vibrio pa-
rahaemolyticus
A05.4 , Bacillus
cereus
05.8 -
05.9 ,
06
: , Entamoeba histoly-
tica
: (07.)
06.0
06.1
06.2
06.3
06.4
06.5 (J99.8*)
( )
06.6 (G07*)
( )(
)
123
06.7
06.8
:
(N51.2*)
06.9 ,
07
07.0
07.1 []
07.2
07.3
, Isospora belli Isospora hominis
07.8
07.9 ,
,
(-):
08
: -
(J10.8, J11.8)
08.0
124
08.1 , Nor-
walk
Small round structured virus enteritis
08.2
08.3
08.4 ,
(-):
08.5
09
. , , -
09, ,
,
52.9.
[]
: , ,
(00
08)
(52.9)
(P78.3)
125
(1519)
: , Mycobacterium tuberculosis
Mycobacterium bovis
: (P37.0)
, (J65)
(90.)
(J65)
15 ,
15.0 , -
-
(-):
15.1 ,
, 15.0,
15.2 , -
, 15.0, -
15.3 , -
, 15.0, ,
126
15.4 ,
:
: (15.7)
15.5 , , -
:
15.6 ,
: -
,
(15.7)
15.7 , -
15.8 , -
:
15.9 -
, -
127
16 ,
16.0
(-):
16.1
, 16.0,
16.2 -
(-)
( -
-
)
16.3 ,
:
(
)
:
, (16.7)
128
16.4 , ,
:
(
)
16.5 , -
(
:
)
: (16.7)
16.7 ,
(-):
16.8 , -
-
(
:
)
16.9
,
129
17
17.0 (G01*)
( )(
)
17.1 (G07*)
17.8 -
(G07*)
(G07*)
(-):
(G07*)
(G05.0*)
(G05.0*)
(G63.0*)
17.9 ,
(G99.8*)
18
18.0
:
(01.1*)
(M01.1*)
(M49.0*)
(-):
(M01.1*)
(H75.0*)
(M90.0*)
(M90.0*)
(M90.0*)
(M68.0*)
(M68.0*)
130
18.1 -
:
(N33.0*)
(N74.0*)
(N29.1*)
(N51.*)
(N29.1*)
(N74.1*)
18.2
: :
(15.4, 16.3)
(18.3)
(15.4, 16.3)
18.3 , -
:
(93.0*)
()() (K93.0*)
:
(93.0*)
(K67.3*)
18.4
,
:
:
(H03.1*)
: (L93.)
(M32.)
131
18.5
:
(H32.0*)
(H19.0*)
(H19.2*)
(H22.0*)
() ()
(H19.2*)
: , (A18.4)
18.6
(67.0*)
: (A18.0)
18.7 (E35.1*)
Addison
18.8
:
(I39.8*)
(I41.0*)
(K23.0*)
(I32.0*)
(E35.0*)
(I68.1*)
19
: :
19.0 -
19.1 -
19.2 -
19.8
19.9
132
(2028)
20
: , Yersinia pestis
20.0
20.1 -
20.2
20.3
20.7
20.8
20.9 ,
21
:
, Francisella tula-
rensis
21.0 -
21.1 -
21.2
21.3
21.7
21.8
21.9 ,
133
22
: , Bacillus anthrcis
22.0
(-):
22.1
22.2 -
22.7
22.8
(G01*)
22.9 ,
23
: :
23.0 , Brucella melitensis
23.1 , Brucella abortus
23.2 , Brucella suis
23.3 , Brucella canis
A23.8
23.9 ,
24
24.0
, Pseudomonas mallei
134
24.1
:
24.2
24.3
24.4 ,
, Pseudomonas pseudomallei
Whitmore
25
25.0
25.1
25.9 ,
26
26.0
26.7 , Erysipelothrix
26.8
26.9 ,
27
27.0 -
, Leptospira interrogans, -
icterohaemorrhagiae
27.8
27.9 ,
135
28 ,
28.0
28.1
28.2
: , Yersinia enterocolitica
(04.6)
(20.)
28.8 , -
28.9 ,
(3049)
30 [ Hansen]
: , Mycobacterium lep-
rae
: (92)
30.0
I
30.1
30.2
30.3
30.4
BL
30.5
LL
136
30.8
30.9 ,
31 ,
: (30.)
(1519)
31.0 , Mycobac-
terium
, Mycobacterium:
avium
intracellulare [Battey bacillus]
kansasii
31.1 , Mycobacterium
Buruli
, Mycobacterium:
marinum
ulcerans
31.8 , Mycobacterium
31.9 , Mycobacterium, -
32
:
: ()
(P37.2)
32.0
32.1
:
(G01*)
(G05.0*)
32.7
137
32.8
:
(I68.1*)
(I39.8*)
-
32.9 ,
33
34
35
: ():
(33)
(34)
36
36.0
36.1
36.2
36.3
: (L08.1)
36.8
:
(H13.1*)
(I41.0*)
(G63.0*)
36.9 ,
138
37
37.0 , Bordetella pertussis
37.1 , Bordetella parapertussis
37.8 , Borde-
tella
37.9 ,
38
: (J02.0)
39
39.0 (G01*)
39.1 Weterhouse-Friderichsen (E35.1*)
39.2
39.3
39.4 ,
39.5
:
(I52.0*)
(I39.8*)
(I41.0*)
(I32.0*)
39.8
:
(M01.0*)
(H13.1*)
(G05.0*)
(H48.1*)
(M03.0*)
139
39.9 ,
40
: (75.3)
:
,
(0307, 08.0)
(88.0)
, -
(80.2)
(36.036.1)
(81.4)
(85)
40.0 ,
40.1 ,
40.2 , D
40.3 , Streptococcus pneu-
moniae
40.8
40.9 ,
140
41
: (49.9)
(75.3)
:
, -
(0307, 08.0)
(88.0)
, -
(80.2)
( )():
(42.7)
(22.7)
(37.7)
Erysipelothrix (26.7)
(28.2)
(54.8)
- (00.7)
(32.7)
(39.239.4)
(36.)
(81.4)
(85)
(40.)
(21.7)
:
(24.1)
(20.7)
(48.3)
41.0 , Staphyloccocus aureus
41.1 , -
, -
41.2 , -
41.3 , Haemophilus influen-
zae
141
41.4 ,
: (48.0)
41.5 , -
, -
41.8
41.9 ,
42
: (47.1)
42.0
42.1
42.2
42.7
42.8
42.9 ,
43
43.0
43.1
43.8
43.9 ,
44
44.0
Oroya
44.1
44.8
142
44.9 ,
46
: -
(86.8)
48 ,
: (47.1)
48.0
(-) Clostridium:
48.1
48.2 [
Pontiac]
48.3
: (R57.8)
(41.9)
48.4
, Haemophilus aegyptius
48.8
49
: -
, (95
96)
,
(74.9)
(39.9)
,
(79.9)
,
(69.9)
143
49.0 ,
49.1 ,
49.2 , Haemophilus influen-
zae,
49.3 , , -
49.8 -
49.9 ,
,
(5064)
: ,
[HIV] (2024)
(N34.1)
Reiter (02.3)
A50
50.0
,
():
(-):
144
50.1
, , -
-
50.2 ,
,
50.3
(H19.2*)
, (H58.8*)
: Hutchinson (50.5)
50.4 [ -
]
(-):
(-):
(G05.0*)
(G01*)
(G63.0*)
-
.
: Hutchinson (50.5)
145
50.5 -
, --
-
Clutton (M03.1*)
Hutchinson-(-):
(-) (-):
(I98.*)
:
(M03.1*)
(M90.2*)
50.6
, , -
--
-
50.7 ,
-
50.9 ,
51
51.0
51.1
51.2
51.3
(-):
(L99.8*)
(L99.8*)
146
51.4
(-)(-) (-)(-):
(N74.2*)
(H22.0*)
(G01*)
(M63.0*)
, (H58.8*)
(M90.1*)
51.5
(), ,
--
- -
51.9 ,
52
52.0 -
- (I98.0*)
(-):
(I79.0*)
(I39.1*)
(I79.1*)
(I68.1*)
(I39.8*)
(I41.0*)
(I32.0*)
(I39.3*)
52.1
Charcot (M14.6*)
(-) (-):
(H94.0*)
(G05.0*)
(G01*)
(H48.0*)
(G63.0*)
(H48.1*)
(G22*)
147
52.2
52.3 ,
()
()
52.7
(N08.0*)
() ,
52.052.3
(-)(-) (-)(-):
(M73.1*)
(H32.0*)
(H19.0*)
(N74.2*)
(L99.8*)
, (H58.8*)
(K67.2*)
() ( ):
(M90.2*)
(K77.0*)
(J99.8*)
(M63.0*)
(M68.0*)
52.8
(), ,
--
, -
52.9 ,
53
53.0 ,
148
53.9 ,
, Treponema pallidum
()
: -
(50.2)
54
54.0 -
- -
:
: :
- (54.1)
(54.1)
54.1 -
-
54.2
-
(-):
(N51.1*)
(N74.3*)
(N51.1*)
(N51.0*)
: (A54.8)
54.3
:
(H13.1*)
(H22.0*)
149
54.4 - -
:
(M01.3*)
(M73.0*)
(M90.2*)
(M68.0*)
(M68.0*)
54.5
54.6
54.8
(-)(-):
(G07*)
(I39.8*)
(G01*)
(I41.0*)
(I32.0*)
(K67.1*)
(J17.0*)
: (A54.2)
54.9 ,
55 ()
Durand-Nicolas-Favre
150
56 ,
: , , -
Chlamydia trachomatis
: (-):
(55)
(-):
(39.1)
(23.1)
, 74.
56.0 -
-
:
56.1
-
(-):
(N51.1*)
(N74.4*)
(N51.1*)
56.2 - ,
56.3
56.4
56.8 ,
57
151
58 ,
59
: (07.8)
59.0
()
(N51.0*) Trichmonas (vaginalis)
59.8
59.9 ,
60 -
[herpes simplex]
60.0 -
-
:
(N77.1N77.1*)
(N51.*)
60.1 -
60.9 - , -
63 ,
,
: (08.1)
(D26.0)
63.0 ()
63.8 ,
152
64 ,
,
,
(6569)
: (27.)
(5053)
65
Bejel
Njovera
66
: bouba
()
pian
66.0
,
,
66.1 --
153
66.2
- -
() () ()
() ()
66.3
() ()
66.4
()
66.5
66.6
() ()
()
()
66.7
66.8
, , -
66.9 ,
67 []
67.0
()
[]
()
154
67.1
[]
67.2
- (I98.1*)
:
[]
67.3
[]
67.9 ,
68
:
: (69.2)
68.0
, Borrelia recurrentis
68.1
, Borrelia, -
Borrelia recurrentis
68.9 ,
69 ,
69.0
155
69.1 Vincent
():
- Vincent:
69.2
, Borrelia burg-
dorferi
69.8
69.9 ,
,
(7074)
70 ,
Chlamydia psittaci
71
: (94.0)
71.0
71.1
()
:
71.9 ,
156
74 ,
: (J16.0)
(-) (-):
(39.1)
(23.1)
, -
(5556)
74.0 (13.1*)
74.8
(K67.0*)
74.9 ,
(7579)
75
: , Ehrlichia sennetsu
(79.8)
75.0 ,
Rickettsia prowazekii
()
()
75.1 [ Brill]
Brill-Zinsser
75.2 , Rickettsia typhi
( )
75.3 , Rickettsia tsutsugamushi
()
(Tsutsugamushi)
157
75.9 ,
()
77
[ ]
77.0 , Rickettsia
rickettsii
Sao Paulo
77.1 , Rickettsia
conorii
77.2 , Rickettsia
siberica
77.3 , Rickettsia aus-
tralis
77.8
77.9 ,
78 -
, Coxiella burnetti
158
79
79.0
79.1 ,
Rickettsia akari
Kew Garden
79.8
, Ehrlichia sennetsu
79.9 ,
,
(8089)
: :
(91)
(94.1)
80
80.0 ,
80.1 ,
80.2 ,
80.3 ,
80.4
80.9 ,
159
81
: prion
81.0 Creutzfeldt-Jakob
81.1
Dawson-
Van Bogaert
81.2
81.8
81.9 -
,
Prion
82
82.0
82.1
82.9 ,
83 ,
: , -
: (92.2)
83.0
83.1
83.2
83.3 St Louis
160
83.4
, Kunjin-
83.5
La Crosse
83.6 , Rocio-
83.8 ,
83.9 , ,
84 ,
:
84.0 [ -
- ]
84.1
84.8
Louping
, Powassan-
84.9 ,
85 ,
: :
,
,
:
(G93.3)
, :
- [herpes simplex] (00.4)
- (05.0)
(26.2)
(80.)
- (02.0)
(87.2)
161
85.0 (G05.1*)
85.1 (G05.1*)
85.2 , , -
85.8
Economo-Cruchet
86 ,
:
87
: , :
- [herpes simplex] (00.3)
- (05.1)
(26.1)
(80.)
- (02.1)
87.0 (G02.0*)
87.1 (G02.0*)
87.2
87.8
87.9 ,
162
88
,
: :
(86)
(87.9)
88.0 [
]
88.1
88.8
89
,
,
(9099)
90 [ ]
: , dengue-
(91)
91 ,
dengue-
92 ,
: (33.1)
163
92.0 , Chikungunya-
Chikungunya
92.1 Onyong-nyong
92.2
(-) (-):
,
92.3 -
92.4 - [ ]
92.8 , -
92.9 , ,
93 ,
,
93.0 , -
93.1
93.2
93.8 , -
, Piry-
,
[ ]
94 ,
,
164
95
95.0
95.1
95.9 ,
96
96.0 Junin
96.1 Machupo
96.2 Lassa
96.8
96.9 ,
98 ,
: chikungunya (92.0)
dengue (91)
98.0 (
-)
98.1 Omsk
98.2 Kyasanur
98.3 Marburg
98.4 Ebola
165
98.5
:
, Hantaan-
98.8
99 ,
,
(0009)
00 - [herpes simplex]
: - (60.)
- (35.2)
-- (27.0)
(08.5)
00.0
00.1 -
:
:
() - 2
166
00.2 - -
-
00.3 - (G02.0*)
00.4 - (G05.1*)
-
00.5 -
-:
(H13.1*)
(H03.1*)
(H22.0*)
(H22.0*)
(H19.1*)
(H19.1*)
(H22.0*)
00.7 -
-
00.8 -
-(-):
(77.0*)
00.9 - ,
01 [varicella]
01.0 (G02.0*)
01.1 (G05.1*)
01.2 (J17.1*)
01.8
01.9
167
02 [herpes zoster]
:
zona
02.0 (G05.1*)
02.1 (G02.0*)
02.2 -
(-):
(G53.0*)
(G63.0*)
(G53.0*)
02.3
:
(H03.1*)
(H13.1*)
(H22.0*)
(H22.0*)
(H19.2*)
(H19.2*)
(H19.0*)
02.7
02.8
02.9
03 1
04 ,
1
1980 .
,
.
168
05
: morbilli
: (81.1)
05.0 , (G05.1*)
05.1 , (G02.0*)
05.2 , (J17.1*)
05.3 , (H67.1*)
05.4
05.8
(H19.2*)
05.9
06 [ ]
: (35.0)
06.0
:
(G05.1*)
(G02.0*)
(G05.1*)
06.8
(-):
(01.4*)
(J17.1*)
06.9
169
07
:
: () (63.0)
:
(D41.4)
(D26.0)
(D14.1)
08 ,
,
: , -
(93.8)
08.0
[ ]
: , -
(04)
08.1
08.2 ( )
08.3 ( )
08.4
08.5
170
08.8 , -
Tana-
Yaba-
09 ,
,
:
(1519)
: (25.1)
- [herpes simplex] (00.8)
(94.2)
15
15.0
15.9
() ()
16
16.0 - ()
16.1 - ()
16.2 -
171
16.9
()()
17
17.0 -() -
17.1
17.2
17.8
, ()(),
18
18.0 -
18.1 -
18.2
18.8
18.9 ,
19 ,
19.0
19.9
172
,
[HIV]
(2024)
: 2023 -
, -
-
.
: , -
[HIV] (Z21)
20 ,
[HIV],
: HIV (23.0)
20.0 , HIV, -
, HIV,
20.1 , HIV,
20.2 , HIV, -
-
20.3 , HIV,
20.4 , HIV, -
20.5 , HIV,
20.6 , HIV, -
, Pneumocystis carinii
173
20.7 , HIV, -
20.8 , HIV,
20.9 , HIV, -
, HIV, ,
21 ,
[HIV],
21.0 , HIV, Kaposi-
21.1 , HIV, Burkitt-
21.2 , HIV,
21.3 , HIV,
, -
21.7 , HIV, -
21.8 , HIV,
21.9 , HIV, -
174
22 ,
[HIV],
22.0 , HIV, -
HIV
22.1 , HIV,
22.2 , HIV,
, HIV, -
[ ]
22.7 , HIV, -
,
:
. 2.
23 ,
[HIV],
23.0 HIV-
23.1 , HIV, (-
)
23.2 , HIV, -
, -
23.8 , HIV,
175
24 ,
[HIV],
[]
- []
(2534)
25
: (35.1)
(27.1)
25.0 (J17.1*)
25.1 (K77.0*)
25.2 (K87.1*)
25.8
25.9 ,
26
: :
26.0 (N51.1*)
26.1 (G02.0*)
26.2 (G05.1*)
26.3 (K87.1*)
176
26.8
(-):
(M01.5*)
(I41.1*)
(N08.0*)
(G63.0*)
26.9 ,
:
27
:
Pfeiffer
27.0 --
, Epstein-Barr
27.1
27.8
27.9 ,
30
: , :
[herpes simplex] (00.5)
(02.3)
30.0 ,
(H19.2*)
30.1 , (H13.1*)
30.2
177
30.3
() (H13.1*)
, :
- 24
- 70
()()
30.8 (H13.1*)
Newcastle
30.9 ,
33 ,
33.0
Bornholm
33.1 Ross River
Ross River
33.2
33.3 , -
33.8
34
: (25.9)
- [herpes simplex]
(00.9)
(33.3)
, -
(97.)
34.0 ,
178
34.1 ,
34.2 ,
34.3 ,
34.4 ,
34.8 -
34.9 ,
(3549)
: ,
(J67.)
(G84.0)
35
:
, Epidermophy-
ton, Microsporum Trichophyton
, -
36.
35.0
35.1
179
35.2
35.3
35.4
35.5
35.6
35.8
:
35.9 ,
36
36.0
:
36.1
36.2
36.3
36.8
36.9 ,
180
37
:
: (37.5)
37.0
37.1
37.2
:
: (L22)
37.3 (N77.1*)
37.4
:
(N51.2*)
(N37.0*)
37.5 (G02.1*)
37.6 (I39.8*)
37.7
37.8
:
37.9 ,
38
38.0
38.1
181
38.2 ,
38.3
38.4 (G02.1*)
38.7
38.8
38.9 ,
39
39.0 , His-
toplasma capsulatum
39.1 ,
Histoplasma capsulatum
39.2 ,
39.3
39.4 ,
39.5 , Histoplasma duboisii
39.9 ,
40
: (41.)
(48.0)
40.0
40.1
40.2 ,
40.3
182
40.7
40.8
40.9 ,
41
:
Lutz
41.0
41.7
41.8
41.9 ,
42
42.0 (J99.8*)
42.1
42.7
42.8
42.9 ,
43
43.0
43.1
43.2
43.8
43.9 ,
183
44
:
44.0
44.1
44.2
44.7
44.8
44.9 ,
45
45.0
45.1
(G02.1*)
45.2
45.3
45.7
45.8
45.9 ,
46
46.0
46.1
46.2
46.3
46.4
184
46.5 ,
46.8
46.9 ,
47
47.0
,
47.1
47.9 ,
48 ,
48.0
Lobo
48.1
48.2
, Pseudallescheria boydii
: (47.0)
48.3
48.4
48.7
, ,
,
-
. -
,
.
185
48.8
49 ,
(5064)
: (06.)
(07.)
50 , Plasmodium
falciparum
: , -
Plasmodium falciparum -
50.0 , Plasmodium falciparum
50.8
, Plasmodium falciparum
,
Plasmodium falciparum,
50.9 , Plasmodium falciparum,
51 , Plasmodium
vivax
: , -
Plasmodium vivax
, Plasmodium
falciparum
: , Plasmodium falciparum
(50.)
186
52 , Plasmodium
malaria
: , -
Plasmodium malariae
, Plasmodium falciparum
Plasmodium vivax
: Plasmodium:
falciparum (50.)
vivax (51.)
52.0 , Plasmodium malaria
52.8 , Plasmodium malariae
52.9 , Plasmodium malariae
, Plasmodium malariae,
53
53.0 , Plasmodium ovale
: Plasmodium:
falciparum (50.)
malariae (52.)
vivax (51.)
187
53.1 ,
: Plasmodium:
falciparum (50.)
malariae (52.)
ovale (53.)
vivax (51.)
53.8 , -
54 ,
55
55.0
-
--
55.1
55.2 -
55.9 ,
56
56.0
, Trypanosoma brucei gambiense
-
56.1
-
, Tripanosoma brucei rhodesiense
56.9 ,
, -
188
57 Chagas
:
, Trypanosoma cruzi
57.0 Chagas
(I41.2*, I98.1*)
Chagas :
, (I98.1*)
(I41.2*)
57.1 Chagas
Chagas
57.2 Chagas () -
(I41.2*, I98.1*)
Chagas () ():
, (I98.1*)
(I41.2*)
, -
Chagas
57.3 Chagas () -
57.4 Chagas () -
57.5 Chagas ()
58
: , Toxoplasma gondii
: (37.1)
58.0
(H32.0*)
58.1 (K77.0*)
58.2 (G05.2*)
189
58.3 (J17.3*)
58.8
:
(I41.2*)
(M63.1*)
58.9 ,
59
, Pneumocystis carinii
60 ,
: (07.2)
(07.3)
(A07.8)
60.0
60.1
, Acanthamoeba (H13.1*)
, Acanthamoeba (H19.2*)
60.2
(G05.2*)
60.8
64 ,
(6583)
65 []
:
65.0 , Schistosoma
haematobium [ ]
190
66
66.0
, :
Opisthorchis (felineus)(viverrini)
66.1
, -
, Clonorchis sinensis
,
66.2
, Dicrocoelium dendriticum
,
66.3
, Fasciola:
gigantica
hepatica
indica
,
191
66.4
, Paragonimus
,
66.5
, Fasciolopsis buski
66.8 ,
66.9 ,
67
: []
67.0 , chino-
coccus granulosus
67.1 , Echino-
coccus granulosus
67.2 , Echinococcus
granulosus
67.3 -
, Echinococcus granulosus
67.4 , Echinococcus granulosus,
67.5 , Echino-
coccus multilocularis
67.6 -
, Echinococcus multilocu-
laris
192
68
: (69.)
68.0 , Taenia solium
()
68.1 , Taenia saginata
()
, Taenia saginata
68.9 ,
69
: ,
Taenia solium
69.0
69.1
69.8
69.9 ,
70
70.0
, Diphyllobothrium (latum)(pacificum)
( )
()
: (70.1)
193
70.1
, :
Sparganum (mansoni)(proliferum)
Spirometra larva
71 ,
71.0
()
()
71.1
()
71.8
71.9 ,
, ,
72
, Dracunculus medinensis
73
, Onchocerca volvulus
74
: (73)
()
(J82)
74.0 , Wuchereria bancrofti
:
194
75
, Trichinella species
76
:
76.0
, Ancylostoma species
76.1
, Necator americanus
76.8
76.9 ,
77
:
77.0
195
77.8
77.9 ,
78
: (81.2)
78.0
78.1
78.7
78.9 ,
79
80
()
81 ,
: , Para-
strongylus cantonensis (83.2)
81.0
, Anisakis
81.1
, Capillaria philippinensis
: (83.8)
81.2
81.3
, Parastrongylus costa-
ricensis
196
81.4
,
65.081.3 81.8
81.8
, :
Oesophagostomum []
Ternidens diminutus []
82 ,
82.0 ,
82.9 ,
83
: :
(81.1)
(81.1)
83.0 ,
[
Larva migrans]
83.1
83.2 a, Parastron-
gylus cantonensis
(G05.2*)
: (81.3)
83.3
83.4 (88.3)
: (88.3)
83.8
197
83.9 ,
: (82.0)
(8589)
85
85.0 , Pediculus humanus
capitis
85.1 , Pediculus humanus
corporis
85.2 ,
85.3
, :
Phthirius pubis
85.4
, -
85.085.3
86
,
87
: ,
198
87.0
87.1
87.2
87.3
87.4
87.8
87.9 ,
88
88.0
, :
Demodex species
Dermanyssus gallina
Liponyssoides sanguineus
: (86)
88.1 [ ]
88.2
88.3
: (83.4)
88.8
, Vandellia cirrhosa
199
88.9 ,
()
89 ,
(9094)
:
, 0089,
.
, , -
,
- , , -
.
, -
, . 2.
90
90.0
90.1 --
90.2 -
90.8 -
90.9
91
200
92
94
94.0
94.1
94.2
94.8
94.9
,
(9597)
: -
.
,
, -
.
95
,
95.0 , -
95.1 , -
95.2 D ,
95.3 Streptococcus pneumonia ,
201
95.4 , -
95.5 ,
95.6 Staphylococcus aureus ,
95.7 , -
95.8 ,
96
,
96.0 Mycoplasma pneumoniae [M. pneumoniae] -
,
Pleuro-pneumonia-like-organism [PPLO]
B96.1 Klebsiella pneumonia [K. pneumonia] -
,
96.2 Escherichia coli [E. coli] ,
96.3 Haemophilus influenzae [H. influenzae] -
,
96.4 Proteus (mirabilis)(morganii) -
,
96.5 Pseudomonas (aeruginosa)(mallei)(pseudomallei) -
,
96.6 Bacillus fragilis [B. fragilis] -
,
96.7 Clostridium perfringens [C. perfringens] -
,
96.8
,
202
97
,
97.0 , -
97.1 , -
-
97.2 , -
97.3 , -
97.4 -
,
97.5 ,
97.6 , -
97.7 , -
97.8 ,
(99)
99
203
II
(00D48)
:
0075 , -
,
, ()
0014 , -
1526 -
3039
4041
4344
4549 -
50
5158 -
6063 -
6468
6972 , -
7375
7680 , -
8196 , -
,
204
97 (-
)
D00D09 in situ
D10D36
D37D48
( . 280)
1. , , -
7680 -
,
, ,
.
.
2.
,
. -
-
, IV.
, ,
, 74,
27.5; , Cushing,
D35.2, 24.0.
3.
()
: , -
; ; ,
; ( );
; ;
.
- ,
, -
. -
.
II -
, , .
205
.
. 616643,
1, 2, ,
.
(),
, -
. 6 : -
;
( , , .. , in
situ, , -
); -
, -
.
4. II
-
.8 ( 5). ,
,
.7.
5. , -
.8
(, -
)
0075 -
().
,
. -
, -
,
, -
.8 (,
),
. ,
16.0 (), -
,
02.8. ,
, ,
206
02.1,
. ,
, -
( ).
, ,
(, 67.) -
,
.
,
, -
.
:
02.8 ,
08.8 ,
14.8 , ,
-
21.8 , , -
24.8 ,
26.8 ,
39.8 , -
-
41.8 ,
49.8 ,
-
57.8 , -
63.8 , -
68.8 ,
207
72.8 -
,
,
26.8 ( , -
).
6.
,
, (25.9).
7. -
, ,
,
.
3
. -
II -
, -
.
8.
()
II
, . -
,
- , -
II (0077, 80).
[ (), -
, in situ ].
( -
, , -
)
-
.
208
(0097)
,
(0014)
00
: (43.0, 44.0)
00.0
:
[vermilion border]
00.1
:
00.2 ,
00.3 ,
:
()
00.4 ,
:
209
00.5 , ,
, :
00.6
00.8 ,
[ 5 . 206]
00.9 ,
01
02
02.0
- ,
: (01)
02.1
02.2
- ,
02.3 - ,
02.4
: (09.9)
210
02.8 ,
[ 5 . 206]
,
-
0102.4
02.9 ,
03
:
:
(41.041.1)
03.0
03.1
03.9 ,
04
04.0
-
04.1
04.8 ,
[ 5 . 206]
04.9 ,
05
05.0
211
05.1
:
(11.3)
05.2 ()
05.8 ,
[ 5 . 206]
05.9 ,
06
06.0
06.1
() ()()
() ()()
06.2
06.8 ,
-
[ 5 . 206]
06.9 ,
,
07
()
212
08
:
,
(06.9)
(07)
08.0 ()
08.1 ()
08.8 ,
-
[ 5 . 206]
-
,
0708.1
08.9 ,
()
09
()
: (02.4)
(11.1)
09.0
09.1 () ()
09.8 ,
[ 5 . 206]
213
09.9 ,
:
10
()
: (09.)
10.0
10.1
,
- (-)
: () (32.1)
10.2
10.3
10.4
[ ]
10.8 ,
[ 5 . 206]
10.9 ,
11
()
11.0
11.1
214
11.2
Rosenmuller
11.3
()() -
:
()
11.8 ,
[ 5 . 206]
11.9 ,
12
13
: (12)
13.0
13.1 , -
:
()
: , -
(32.1)
13.2
215
13.8 ,
[ 5 . 206]
13.9 ,
14
,
: (06.9)
14.0 ,
14.2 Waldeyer ()
14.8 ,
,
[ 5 . 206]
,
, -
0014.2
216
(1526)
15
: -
:
.0.2
.3.5
,
,
,
, -
.
15.0
15.1
15.2
15.3
15.4
15.5
15.8 ,
[ 5 . 206]
15.9 ,
217
16
16.0
16.1
16.2
16.3
16.4
16.5 ,
, 16.116.4
16.6 ,
, 16.016.4
16.8 ,
[ 5 . 206]
16.9 ,
17
17.0 ()
17.1
17.2
: - (18.0)
17.3 Meckel
218
17.8 ,
[ 5 . 206]
17.9 ,
C18
()
18.0
-
18.1
18.2
18.3
18.4
18.5
18.6
18.7
()
: (19)
18.8 ,
[ 5 . 206]
18.9 ,
19
()
20
()
219
21
21.0 ,
: (-):
(43.5, 44.5)
(43.5, 44.5)
(43.5, 44.5)
21.1
21.2
21.8 ,
,
[ 5 . 206]
,
, -
2021.2
22
: (24.9)
(78.7)
22.0 ,
22.1
22.2
22.3
Kupffer
220
22.4
22.7
22.9 , -
23
24
: (22.1)
24.0
24.1 Vater
24.8 ,
[ 5 . 206]
,
,
22.024.1
24.9 -
,
25
25.0
25.1
221
25.2
25.3
25.4
25.7
25.8 ,
[ 5 . 206]
25.9 , -
26
: (48.)
26.0 ,
26.1
: Hodgkin (81.)
(8285)
26.8 ,
-
[ 5 . 206]
-
,
1526.1
: (16.0)
26.9 -
222
(3039)
:
: (45.)
30
30.0
()
: (41.0)
(76.0)
(72.2)
(11.3)
(43.3, 44.3)
30.1
: () (43.2, 44.2)
() (41.0)
(49.0)
() (43.2, 44.2)
31
31.0
( Highmore) ()
31.1
223
31.2
31.3
31.8 ,
[ 5 . 206]
31.9 , -
32
32.0
()
()
32.1
,
( )
()
: (10.1)
:
(13.1)
(13.1)
(13.1)
32.2
32.3
32.8 ,
[ 5 . 206]
32.9 , -
224
33
34
34.0
( )
34.1 ,
34.2 ,
34.3 ,
34.8 ,
[ 5 . 206]
34.9 ,
37
38
,
: (45.)
38.0
: (49.3)
38.1
38.2
38.3 ,
38.4
225
38.8 ,
,
[ 5 . 206]
39
: (76.1)
(76.1)
39.0 ,
39.8 ,
[ 5 . 206]
,
3039.0
39.9
(4041)
: (96.7)
(49.)
40
40.0 ()
226
40.1
40.2
40.3
40.8 ,
-
[ 5 . 206]
40.9 , -
41
: (40.)
:
(49.0)
(32.3)
(40.)
(30.0)
41.0
() ()
: , -
:
(31.0)
(03.0)
() (41.1)
41.1 ()
: , -
:
(03.9)
(03.1)
(41.0)
227
41.2
: (41.4)
41.3 ,
41.4 ,
41.8 ,
-
[ 5 . 206]
-
, -
4041.4
41.9
,
(4344)
43
: 872879 -
/3
:
(5152, 60., 63.)
43.0
: (00.000.2)
43.1 ,
43.2
43.3
228
43.4 -
43.5
:
: (21.0)
43.6 , -
43.7 , -
43.8 ,
[ 5 . 206]
43.9 ,
()
44
: :
: Kaposi (46.)
(43.)
(5152, 60.,
63.)
44.0
:
(00.)
229
44.1 , -
: (49.0)
44.2
: (49.0)
44.3
44.4
44.5
:
: (21.0)
44.6 ,
44.7 , -
44.8 ,
[ 5 . 206]
44.9 , -
(4549)
45
: 905
/3
230
45.0
:
(38.4)
45.1
()()
: -
(48.)
45.2
: -
(38.0)
45.7
45.9 ,
46 Kaposi
: 9140
/3
46.0 Kaposi
46.1 Kaposi
46.2 Kaposi ()
46.3 Kaposi
46.7 Kaposi
46.8 Kaposi
46.9 Kaposi,
47
:
231
47.0 ,
: (69.6)
47.1 ,
47.2 ,
47.3
47.4
47.5
47.6 -
,
47.8 ,
-
[ 5 . 206]
47.9 ,
48
: Kaposi (46.1)
(45.)
48.0
48.1
:
48.2 ,
232
48.8 ,
-
[ 5 . 206]
49
:
,
( )
: :
(4041)
(32.3)
(30.0)
(50.)
Kaposi (46.)
(45.)
(47.)
(48.)
(48.0)
49.0 ,
:
: (69.6)
49.1 ,
49.2 ,
233
49.3
: (50.)
(38.0)
(38.138.3)
(37)
49.4
49.5
49.6 , -
49.8 ,
[ 5 . 206]
, -
4749.6
49.9 , -
234
(50)
50
:
: (43.544.5)
50.0
50.1
50.2
50.3
50.4
50.5
50.6
50.8 ,
[ 5 . 206]
50.9 ,
235
(5158)
:
51
51.0 ()
51.1
51.2
51.8 ,
[ 5 . 206]
51.9 ,
52
()
53
()
53.0
53.1
53.8 ,
[ 5 . 206]
53.9 ,
236
54
54.0
54.1
54.2
54.3 ()
54.8 ,
[ 5 . 206]
54.9 ,
55
56
57
57.0
57.1
57.2
57.3
57.4 ,
57.7
237
57.8 ,
[ 5 . 206]
,
5157.7, 58
-
-
57.9 ,
-
58
: () (D39.2)
:
(O01.9)
(D39.2)
(D39.2)
(6063)
:
60
60.0
60.1
60.2
238
60.8 ,
[ 5 . 206]
60.9 ,
61
62
62.0
[ ]
[ ]
62.1
62.9 , -
63
63.0
63.1
63.2
63.7
( )
239
63.8 ,
[ 5 . 206]
,
6063.7
63.9 ,
-
(6468)
64
,
: :
(65)
(65)
65
66
: (67.6)
67
67.0
240
67.1
67.2
67.3
67.4
67.5
67.6 ()
67.7
67.8 ,
[ 5 . 206]
67.9 ,
68
: - :
(57.9)
(63.9)
68.0
: (67.5)
68.1
68.8 ,
[ 5 . 206]
,
6468.1
68.9 -
,
241
,
(6972)
69
: (49.0)
(43.1, 44.1)
(72.3)
69.0
69.1
69.2
69.3
69.4
69.5
69.6
: (41.0)
69.8 ,
-
[ 5 . 206]
69.9 ,
242
70
()
70.0
70.1
70.9 , -
71
: (72.272.5)
(69.6)
71.0 , ()
()
(Corpus callosum)
()
71.1
71.2
71.3
71.4
71.5
: (71.7)
71.6
71.7
()
71.8 ,
[ 5 . 206]
71.9 ,
243
72
,
: (70.)
-
(47.)
72.0
72.1 ( )
72.2 ()
72.3
72.4
72.5
72.8 ,
[ 5 . 206]
,
-
7072.5
72.9 ,
244
(7375)
73
74
74.0 ()
74.1
74.9 ,
75
: (74.)
(25.4)
(56)
(62.)
(37)
(73)
75.0
75.1
75.2
75.3 ()
75.4
75.5
245
75.8 , -
:
,
.
75.9
,
,
(7680)
76
: ():
:
(57.9)
(63.9)
, -
(8196)
(80)
76.0 ,
76.1
76.2
246
76.3
, , :
()
()
76.4
76.5
76.7
76.8 ,
-
[ 5 . 206]
77
:
, (8188,
96.)
77.0 ,
77.1
77.2
77.3 -
77.4
77.5
77.8
77.9 ,
247
78
78.0
78.1 -
78.2 -
78.3
78.4 -
78.5 -
78.6 -
78.7 -
78.8
79
79.0 -
79.1 -
,
248
79.2 -
79.3 -
79.4
79.5
79.6 -
79.7 -
79.8
80
:
() ()
249
,
(8196)
: , 8285 -
, ,
-
. , -
,
, ;
-
.
: 959994
/3
:
(77.)
81 Hodgkin
: 965966 -
/3
81.0
-
81.1
81.2
81.3
81.7 Hodgkin
81.9 Hodgkin,
250
82 []
:
969
/3
82.0 ,
82.1 , -
,
82.2 ,
82.7
82.9 ,
83
: 9593, 9595, 967
968 -
/3
83.0 ()
83.1 ()
83.2 , ()
83.3 ()
83.4 ()
83.5 ()
83.6 ()
83.7 Burkitt
83.8
83.9 ,
251
84 -
: 970
/3
84.0 Mycosis fungoides
84.1 Sezary
84.2 -
84.3
Lennert
84.4 -
84.5 -
: -
-
, -
.
85
: 95909592, 9594,
971 -
/3
85.0
85.1 - ,
: -
-
, -
.
85.7
:
252
85.9 ,
88
: 976
/3
88.0 Waldenstrom
88.1 -
88.2 -
Franklin
88.3
88.7 -
88.9 , -
90
: 973, 9830
/3
90.0
Kahler
: (90.2)
90.1
90.2 ,
253
C91
: 982, 99409941
/3
91.0
: -
(91.1)
91.1
91.2
91.3
91.4
91.5 -
91.7
91.9 ,
92
: :
986988, 9930
/3
92.0
: -
(92.1)
92.1
92.2
92.3
92.4
92.5
254
92.7
92.9 ,
93
:
989
/3
93.0
: -
(93.1)
93.1
93.2
93.7
93.9 ,
94
: 984, 9850, 9900,
9910, 99319932
/3
: (91.4)
(90.1)
94.0
Di Guglielmo
94.1
Heilmeyer-Schner
94.2
:
()
()
94.3
94.4
255
94.5
94.7
95
: 980
/3
95.0
: -
(95.1)
95.1
95.2
95.7
95.9 ,
96
,
: 972, 974 -
/3
96.0 Letterer-Siwe
:
96.1
256
96.2
(-):
: (94.3)
() (Q82.2)
96.3
96.7
,
96.9 , -
,
()
(97)
97
()
:
-
, 2.
257
in situ
(D00D09)
: in situ -
. , -
(CIN) , -
(CIN III) -
, in situ.
.
-
III -
; I II
, .
: Bowen
-
/2
Queyrat
D00 in situ ,
: in situ (D03.)
D00.0 ,
:
,
: , -
(D02.0)
:
(D02.0)
(D02.0)
(D03.0, D04.0)
D00.1
D00.2
258
D01 in situ
: in situ (D03.)
D01.0
: (D01.1)
D01.1
D01.2
D01.3
: :
(D03.5, D04.5)
(D03.5, D04.5)
(D03.5, D04.5)
D01.4
: Vater (D01.5)
D01.5 ,
Vater
D01.7
D01.9 ,
D02 in situ
: in situ (D03.)
D02.0
,
( )
: :
(D00.0)
, (D00.0)
(D00.0)
D02.1
D02.2
259
D02.3
: () () (D03.2, D04.2)
:
(D09.7)
(D03.3, D04.3)
D02.4 ,
D03 in situ
: 872879 -
/2
D03.0 in situ
D03.1 in situ ,
D03.2 in situ
D03.3 in situ
D03.4 in situ
D03.5 in situ
:
()( )
D03.6 in situ ,
D03.7 in situ ,
D03.8 in situ
D03.9 in situ,
260
D04 in situ
: Queyrat () (D07.4)
in situ (D03.)
D04.0
: (D00.0)
D04.1 ,
D04.2
D04.3
D04.4
D04.5
:
: (D01.3)
(D07.)
D04.6 ,
D04.7 , -
D04.8
D04.9 ,
D05 in situ
: in situ
(D04.5)
in situ ()
(D03.5)
D05.0 in situ
D05.1 in situ
D05.7 in situ
261
D05.9 in situ ,
D06 in situ
:
[CIN], III ,
: in situ (D03.5)
(N87.2)
D06.0
D06.1
D06.7
D06.9 ,
D07 in situ
: in situ (D03.)
D07.0
D07.1
[VIN], III ,
: (N90.2)
D07.2
[VIN], III
,
: (N89.2)
D07.3
D07.4
Queyrat
D07.5
D07.6
262
D09 in situ
: in situ (D03.)
D09.0
D09.1
D09.2
: (D04.1)
D09.3
: (D01.7)
(D07.3)
(D07.6)
D09.7 in situ
D09.9 in situ,
(D10D36)
: -
/0
D10
,
D10.0
()( )()( )
: (D22.0, D23.0)
D10.1
[Tonsilla Lingualis]
D10.2
263
D10.3
: -
(D16.4, D16.5)
(D10.0)
(D10.6)
D10.4 ()
() ()
: (D10.1)
(D10.6)
:
(D10.5)
(D10.5)
D10.5
,
:
: :
(D14.1)
(D14.1)
D10.6
D10.7
D10.9 ,
D11
: -
, -
-
(D10.3)
264
D11.0
D11.7
:
D11.9 ,
D12
, ,
D12.0
D12.1
D12.2 ()
D12.3 ()
D12.4 ()
D12.5
D12.6 ,
()
D12.7
D12.8
D12.9
: :
(D22.5, D23.5)
(D22.5, D23.5)
(D22.5, D23.5)
265
D13
D13.0
D13.1
D13.2 ()
D13.3
D13.4
D13.5
D13.6
: (D13.7)
D13.7
D13.9 -
266
D14
D14.0 ,
: () (D22.2, D23.2)
:
(D16.4)
(D16.4)
(D21.0)
()() (D22.2, D23.2)
:
(D36.7)
(D22.3, D23.3)
(D33.3)
:
(J33.8)
() (H74.4)
() (J33.)
(D10.6)
D14.1
( )
: , (D10.5)
(J38.1)
D14.2
D14.3
D14.4 ,
D15
: (D19.)
D15.0
D15.1
: (D21.3)
267
D15.2
D15.7
D15.9 ,
D16
: :
(D21.0)
(D21.0)
(D14.1)
(D14.0)
(D21.)
D16.0
D16.1
D16.2
D16.3
D16.4
()
: (D16.5)
D16.5
D16.6
: (D16.8)
D16.7 ,
D16.8 ,
D16.9 ,
D17
: 885888 -
/0
268
D17.0 -
, -
D17.1 -
D17.2 -
D17.3 -
-
D17.4 -
D17.5 -
: (D17.7)
D17.6 -
D17.7 -
D17.9 -
,
D18
: 912917 -
/0
: (D22.)
D18.0
269
D18.1
D19
: 905
/0
D19.0
D19.1
D19.7
D19.9 ,
D20
: -
(D17.7)
(D19.)
D20.0
D20.1
270
D21
:
,
( )
: :
(D16.)
(D14.1)
(D14.0)
(D24)
(D18.0)
(D17.)
(D18.1)
-
(D36.1)
(D20.1)
(D20.0)
:
(D25.)
(), (D28.2)
(D18.)
D21.0 , -
:
: (D31.6)
D21.1 -
,
271
D21.2 -
,
D21.3
: (D15.1)
(D15.2)
(D15.0)
D21.4
D21.5
: :
(D25.)
(), (D28.2)
D21.6 , -
D21.9 ,
D22
: 872879 -
/0
:
D22.0
D22.1 , -
D22.2 -
272
D22.3
D22.4
D22.5
:
D22.6 , -
D22.7 , -
D22.9 ,
D23
: :
: -
(D17.0 D17.3)
(D22.)
D23.0
: (D10.0)
D23.1 , -
D23.2
D23.3
D23.4
273
D23.5
:
: (D12.9)
(D28 D29)
D23.6 ,
D23.7 , -
D23.9 ,
D24
:
: -
(N60.)
(D22.5, D23.5)
D25
:
889 -
/0
D25.0
D25.1
D25.2
D25.9 ,
274
D26
D26.0
D26.1
D26.7
D26.9 ,
D27
D28
:
D28.0
D28.1
D28.2
() ()
D28.7
D28.9 ,
D29
:
D29.0
275
D29.1
: ()
(N40)
:
(N40)
(N40)
(N40)
D29.2
D29.3
D29.4
D29.7
D29.9 ,
D30
D30.0
: :
(D30.1)
(D30.1)
D30.1
D30.2
: (D30.3)
D30.3
:
D30.4
: (D30.3)
D30.7
276
D30.9 ,
D31
: (D21.0)
(D33.3)
(D22.1, D23.1)
D31.0
D31.1
D31.2
D31.3
D31.4
D31.5
-
D31.6 ,
: (D16.4)
D31.9 ,
D32
()
D32.0
D32.1
D32.9 ,
277
D33
: (D18.0)
(D32.)
-
(D36.1)
(D31.6)
D33.0 ,
: (D33.1)
D33.1 ,
D33.2 ,
D33.3
D33.4
D33.7 -
D33.9 , -
()
D34
278
D35
: (D13.7)
(D27)
(D29.2)
(D15.0)
D35.0
D35.1
D35.2
D35.3
D35.4 ()
D35.5
D35.6
D35.7
D35.8
D35.9 ,
D36
D36.0
D36.1
: (D31.6)
D36.7
D36.9 ,
279
(D37D48)
: D37D48 -
, ..
-
. -
-
/1.
D37
D37.0 ,
:
: , -
(D38.0)
:
(D38.0)
(D38.0)
(D48.5)
D37.1
D37.2
D37.3
D37.4
D37.5
280
D37.6 ,
Vater
D37.7
:
: :
(D48.5)
(D48.5)
(D48.5)
D37.9 ,
D38
,
: (D48.7)
D38.0
,
( )
: :
(D37.0)
(D37.0)
(D37.0)
D38.1 ,
D38.2
D38.3
D38.4
281
D38.5
: ()() (D48.5)
:
(D48.7)
(D48.5)
D38.6 ,
D39
D39.0
D39.1
D39.2
()
: (O01.9)
D39.7
D39.9 ,
D40
D40.0
D40.1
D40.7
282
D40.9 ,
D41
D41.0
: (D41.1)
D41.1
D41.2
D41.3
D41.4
D41.7
D41.9 ,
D42
D42.0
D42.1
D42.9 ,
283
D43
: -
(D48.2)
D43.0 ,
: (D43.1)
D43.1 ,
D43.2 ,
D43.3
D43.4
D43.7 -
D43.9 ,
()
D44
: (D37.7)
(D39.1)
(D40.1)
(D38.4)
D44.0
284
D44.1
D44.2
D44.3
D44.4
D44.5 ()
D44.6
D44.7
D44.8
D44.9 ,
D45
9950 -
/1
D46
: 998
/1
D46.0 ,
D46.1
D46.2
D46.3
D46.4 ,
D46.7
D46.9 ,
()
285
D47
,
: 974, 976, 996
997 -
/1
D47.0 -
: () (Q82.2)
D47.1
( )
,
()
D47.2
D47.3 ()
D47.7
, -
D47.9 -
,
,
D48
: ( ) (Q85.0)
286
D48.0
: :
(D48.1)
(D38.0)
(D38.5)
(D48.1)
(D48.1)
D48.1
:
: :
(D48.0)
(D38.0)
(D38.5)
(D48.6)
D48.2
: (D48.7)
D48.3
D48.4
D48.5
:
: (D37.7)
(D39.7, D40.7)
(D37.0)
D48.6
()
: (D48.5)
287
D48.7
: (D48.1)
(D48.5)
D48.9 -
,
288
III
,
,
(D50D89)
: () (M35.9)
,
(P00P96)
,
(O00O99)
,
(Q00Q99)
, -
(E00E99)
, -
[HIV] (B20B24)
, -
(S00T98)
(C00D48)
, ,
, -
(R00R99)
:
D50D53 ,
D55D59
D60D64
D65D69 , -
D70D77
D80D89 ,
:
D63* ,
D77* -
,
289
,
(D50D53)
D50
: :
D50.0 , ,
()
()
: (D62)
,
(P61.3)
D50.1
Kelly-Paterson
Plummer-Vinson
D50.8
D50.9 ,
D51 B12-
: B12 (E53.8)
D51.0 B12- , -
:
Addison
Biermer
()
D51.1 B12- , -
B12
Immerslund (-Grasbeck)
290
D51.2 II
D51.3 B12- ,
D51.8 B12-
D51.9 B12- ,
D52
D52.0 ,
D52.1 , -
( XX).
D52.8
D52.9 ,
, ,
D53 ,
: , -
B12
D53.0 ,
: Lesch-Nyhan (E79.1)
D53.1 ,
: Di Guglielmo (C94.0)
D53.2
: (E54)
291
D53.8 ,
, :
: , -
, :
(E61.0)
(E61.5)
(E60)
D53.9 , ,
: (D64.9)
(D55D59)
D55 ,
: , -
(D59.2)
D55.0 , -6--
[G6PD]
G6PD-
D55.1 , -
, ( G6PD),
(HMP) -
, (), I
292
D55.2 ,
:
, (), II
-
-
D55.3 ,
D55.8 ,
D55.9 , , -
D56
D56.0
: ,
(P56.)
D56.1
Cooley
-
D56.2 -
D56.3
D56.4
[HPFH]
D56.8
D56.9 ,
( )
()()( )
293
D57 -
: (D58.)
- (D56.1)
D57.0 -
Hb-SS
D57.1 -
-(-):
D57.2 - -
:
Hb-SC
Hb-SD
Hb-SE
D57.3
Hb-S
S
D57.8 -
D58
D58.0
()
()
Minkowski-Chauffard
D58.1
()
()()
294
D58.2
Heinz
:
Hb-C
Hb-D
Hb-E
: (D75.0)
Hb-M (D74.0)
-
(D56.4)
(D75.1)
(D74.)
D58.8
D58.9 ,
D59
D59.0
( XX).
D59.1
( )( )
, -
:
:
()()
()()
: Evans (D69.3)
(P55.)
(D59.6)
295
D59.2 -
( XX).
D59.3 -
D59.4
:
-
( XX).
D59.5 [
Marchiafava-Micheli]
: (R82.3)
D59.6 ,
:
-
( XX).
: (R82.3)
D59.8
D59.9 ,
,
296
(D60D64)
D60 ()
[]
: ()( -
)( )
D60.0 () -
D60.1 () -
D60.8 ()
D60.9 () , -
D61
: (D70)
D61.0
() :
Blackfan-Diamond
Fanconi
D61.1
( XX).
D61.2 , -
-
( XX).
297
D61.3
D61.8
D61.9 ,
D62
: ,
(P61.3)
D63* , -
D63.0* (C00D48)
D63.8* , -
D64
: :
(D46.4)
(D46.2)
(D46.3)
(D46.1)
(D46.0)
D64.0
,
D64.1 ,
-
.
D64.2 ,
-
( XX).
298
D64.3
:
,
D64.4
()
: Blackfan-Diamond (D61.0)
Di Guglielmo (C94.0)
D64.8
D64.9 ,
,
(D65D69)
D65
[ ]
,
[DIC]
,
:
: ( ):
, -
(O00O07, O08.1)
(P60)
, -
(O45.0, O46.0, O67.0, O72.3)
299
D66 VIII
VIII ( )
:
: VIII
(D68.0)
D67 IX
Christmas
:
IX ()
o B
D68
: , :
, -
(O00O07, O08.1)
,
(O45.0, O46.0, O67.0, O72.3)
D68.0 von Willebrand
VIII
: ()
(D69.8)
VIII:
(D66)
(D66)
D68.1 XI
C
300
D68.2 -
:
AC
:
I []
II []
V []
VII []
X [Stuart-Prower]
XII [Hageman]
XIII []
()
Owren
D68.3 , -
:
-VIIIa
-IXa
-Xa
-XIa
-
( XX).
D68.4 -
, :
K
: K (P53)
D68.8
[SLE]
301
D68.9 ,
D69
:
(D89.0)
(D89.1)
()
(D47.3)
(D65)
(M31.1)
D69.0
:
Henoch(-Schonlein)
:
D69.1
Bernard-Soulier [ ]
Glanzmann
()()
: von Willebrand (D68.0)
D69.2
:
D69.3
Evans
302
D69.4
:
(Q87.2)
(P61.0)
Wiskott-Aldrich (D82.0)
D69.5
-
( XX).
D69.6 ,
D69.8
()
D69.9 ,
(D70D77)
D70
Kostmann
:
()
, , -
( XX).
: (P61.5)
303
D71
-
( )
D72
: (D75.8)
(D80D89)
(D70)
() (D46.9)
D72.0
( )( ) :
Alder
May-Hegglin
Pelger-Huet
:
:
: Chediak(-Steinbrinck)-Higashi
(E70.3)
D72.1
:
304
D72.8 -
:
()
()
D72.9 ,
D73
D73.0
,
: () (Q89.0)
D73.1
: :
(R16.1)
(Q89.0)
D73.2
D73.3
D73.4
D73.5
,
: (S36.0)
D73.8
D73.9 ,
305
D74
D74.0
NADH-
M [ Hb-M]
,
D74.8
( )
-
( XX).
D74.9 ,
D75
: (R59.)
(D89.2)
:
(I88.9)
(L04.)
(I88.1)
()() (I88.0)
D75.0
:
: (D58.1)
306
D75.1
:
:
: :
(P61.1)
vera (D45)
D75.2
: ()
(D47.3)
D75.8 -
D75.9 , -
D76 ,
: Letterer-Siwe (C96.0)
(C96.1)
:
(C96.1)
(C91.4)
(I89.8)
(C85.7)
(C96.0)
307
D76.0 Langerhans, -
Hand-Schuller-Christian
X ()
D76.1
,
Langerhans
D76.2
.
D76.3
()
D77* -
,
[] (B65.)
,
(D80D89)
:
, , -
[HIV]
: () (M35.9)
- -
(D71)
, -
[HIV] (B20B24)
308
D80
D80.0
( )
X- [Bruton] (
)
D80.1
B-, -
[CVAgamma]
D80.2 A [IgA]
D80.3 -
G [IgG]
D80.4 M [IgM]
D80.5 M [IgM]
D80.6 -
D80.7
D80.8
-
D80.9 -
,
D81
:
( ) (D80.0)
D81.0 -
309
D81.1 -
T- B-
D81.2 -
B-
D81.3 [ADA]
D81.4 Nezelof
D81.5 -- [PNP]
D81.6
I
D81.7
II
D81.8
-
D81.9 ,
D82 , -
: - [Louis-Bar] (G11.3)
D82.0 Wiskott-Aldrich
D82.1 Di George
:
D82.2
D82.3 -
, Epstein-Barr
X-
D82.4 E [IgE]
310
D82.8 , -
D82.9 , ,
D83
D83.0 -
B--
D83.1 -
T-
D83.2 -
B- T-
D83.8
D83.9 ,
D84
D84.0 -1 [LFA-1]
D84.1
C1 [C1-INH]
D84.8
D84.9 ,
D86
D86.0
D86.1
D86.2
D86.3
311
D86.8
(H22.1*)
-
(G53.2*)
(-):
(M14.8*)
(I41.8*)
(M63.3*)
[Heerfordt]
D86.9 ,
D89
,
: (R77.1)
(D47.2)
(T86.)
D89.0
D89.1
:
(-):
D89.2 ,
D89.8 ,
,
D89.9 , , -
312
IV
,
(E00E90)
: , ,
, II. -
(. E05.8, E07.0, E16E31, E34.),
-
, -
,
,
.
: ,
(O00O99)
, ,
, -
(R00R99)
-
, -
(P70P74)
:
E00E07
E10E14
E15E16 -
E20E35
E40E46
E50E64
E65E68
E70E90
313
:
E35* , -
E90*
,
(E00E07)
E00
: ,
, -
,
.
, -
-
.
.
(F70F79).
: - -
(E02)
E00.0 - ,
,
E00.1 - ,
:
E00.2 - ,
,
E00.9 - ,
-
314
,
E01 ,
,
: - (E00.)
- -
(E02)
E01.0 () , -
E01.1 () ,
,
E01.2 (), , -
E01.8 ,
,
E02 ,
E03
: ,
(E00E02)
(E89.0)
E03.0
() :
:
(P72.0)
315
E03.1
( )
:
E03.2 ,
-
( XX).
E03.3
E03.4 ()
:
(E03.1)
E03.5
E03.8
E03.9 ,
E04
: :
(03.0)
, (E00E02)
E04.0
:
()
E04.1
()()
()
316
,
E04.2
()
E04.8
E04.9 ,
()
E05 []
: -
(E06.2)
(P72.1)
E05.0
Graves
E05.1 -
E05.2
E05.3
E05.4 , (factitia)
E05.5
E05.8
-
( XX).
E05.9 ,
(I43.8*)
317
E06
: (O90.5)
E06.0
:
(B95B97).
E06.1
:
de Quervain
: (E06.3)
E06.2
: ((E06.3)
E06.3
Hashimoto
()
E06.4
( XX).
E06.5
:
:
Riedel
E06.9 ,
318
,
E07
E07.0
C-
E07.1
Pendred
:
(P72.0)
E07.8
-
E07.9 ,
319
(E10E14)
, -
,
( XX).
E10E14:
.0
:
.1
:
.2
(N08.3*)
(N08.3*)
Kimmelstiel-Wilson (N08.3*)
.3
:
(H28.0*)
(H36.0*)
.4
:
(G73.0*)
(G99.0*)
(G59.0*)
(G63.2*)
(G99.0*)
.5
:
(I79.2*)
320
,
.6
(M14.2*)
(M14.6*)
.7
.8
.9
E10
[ - ]
:
I
: ():
(E12.)
(P72.2)
,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(E89.1)
321
E11
[ - ]
: ()( )( -
):
II
: ():
(E12.)
(P70.2)
,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(E89.1)
E12 ,
[ - ]
: , -
:
: ,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(P70.2)
(E89.1)
322
,
E13
[ - ]
: ():
(E10.)
(E12.)
(P70.2)
(E11.)
,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(E89.1)
E14 ,
[ - ]
:
: ():
(E10.)
(E12.)
(P70.2)
(E11.)
,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(E89.1)
323
(E15E16)
E15
-
, ,
( XX).
E16
E16.0
( XX).
E16.1
:
-
E16.2 ,
E16.3
-
324
,
E16.4
ZollingerEllison
E16.8 -
:
-
E16.9 -
,
(E20E35)
: (N64.3)
(N62)
E20
: Di George (D82.1)
-
(E89.2)
(R29.0)
-
(P71.4)
E20.0
E20.1
E20.8
325
E20.9 ,
E21
: :
(M83.)
(E55.0)
E21.0
( von Reck-
linghausen)
E21.1 ,
:
(N25.8)
E21.2
:
(E83.5)
E21.3 ,
E21.4
E21.5 , -
E22
: Cushing (E24.)
Nelson (E24.1)
:
ACTH, Cushing
(E27.0)
ACTH (E24.0)
- TSH (E05.8)
326
,
E22.0
, (M14.5*)
: :
(E34.4)
(E34.4)
- -
(GHRH) (E16.8)
E22.1
, ,
( XX).
E22.2 -
E22.8
E22.9 ,
E23
: , -
: -
(E89.3)
327
E23.0
:
Kallmann
Lorain-Levi
( )
:
Sheehan
Simmonds
E23.1
( XX).
E23.2
: (N25.1)
E23.3 ,
: Prader-Willi (Q87.1)
Russell-Silver (Q87.1)
E23.6
E23.7 ,
328
,
24 Cushing
E24.0 Cushing
ACTH
E24.1 Nelson
E24.2 Cushing
-
(
XX).
E24.3 ACTH
E24.4 -Cushing
E24.8 Cushing
E24.9 Cushing,
E25
: ,
,
, -
-
:
-
:
-
-
( )
E25.0 ,
21-
329
E25.8
, ,
( XX).
E25.9 ,
E26
E26.0
Conn
, -
()
E26.1
E26.8
Bartter
E26.9 ,
E27
E27.0 -
ACTH, Cushing
: Cushing (E24.)
E27.1 -
Addison
: (E85.)
Addison (A18.7)
Waterhouse-Friderichsen (A39.1)
E27.2
330
,
E27.3 -
( XX).
E27.4 -
:
: [Addison-Schilder]
(E71.3)
Waterhouse-Friderichsen (39.1)
E27.5
E27.8
-
E27.9 ,
E28
: (E23.0)
-
(E89.4)
E28.0
, , -
( XX).
E28.1
, , -
( XX).
331
E28.2
Stein-Leventhal
E28.3
: (N95.1)
(Q99.1)
Turner (Q96.)
E28.8
E28.9 ,
E29
: (E34.5)
(N46)
(E23.0)
Klinefelter (Q98.0Q98.2,Q98.4)
(E89.5)
() (E34.5)
E29.0
E29.1
5-- ( )
, , -
( XX).
E29.8
E29.9 ,
332
,
E30 ,
E30.0
E30.1
: Albright (-McCune)(-Sternberg)
(Q78.1)
-
(E22.8)
(E25.0)
-
(E25.)
-
(E25.)
E30.8
30.9 ,
E31
: - [Louis-Bar] (G11.3)
[Steinert] (G71.1)
(E20.1)
E31.0
Schmidt
E31.1
: (D44.8)
E31.8 a a
E31.9 ,
E32
:
(D82.1)
(G70.0)
333
E32.0
E32.1
E32.8
E32.9 ,
E34
: (E20.1)
E34.0
: -
,
, .
E34.1 -
E34.2 , -
E34.3 ,
:
Laron
: (E34.8)
Russsell-Silver (Q87.1)
(D82.2)
:
(Q77.4)
(Q77.4)
( )
(E45)
(E23.0)
(N25.0)
334
,
E34.4
E34.5
Reifenstein
()
E34.8
E34.9 ,
:
35*
,
E35.0* ,
(A18.8)
E35.1* , -
(A18.7)
Waterhouse-Friderichsen () (A39.1)
E35.8* -
,
335
(E40E46)
: -
, -
. -
,
-
. , -
-
. -
, ,
.
-
, -
, -
3 -
;
2 3 -
; -
1 2
.
: (K90.)
(D50D53)
- (64.0)
(B22.2)
(T73.0)
E40
: (E42)
E41
: (E42)
336
,
E42
- [ E43]:
E43 -
,
[] , -
, -
- 3
( , -
). ,
3 -
.
E44 -
E44.0 -
,
, 2 3 -
( , ).
, -
- -
2 3 -
.
E44.1 -
,
, 1 2 -
( , ).
,
- 1
2 .
337
E45 ,
-
:
, -
E46 - ,
-
(E50E64)
: (D50D53)
E50 A
: A (E64.1)
E50.0 A -
E50.1 A Bitot
Bitot
E50.2
E50.3 A
E50.4 A
E50.5 A
E50.6 A -
338
,
E50.7 A
E50.8 A
A (L86*)
E50.9 A,
A
E51
: (E64.8)
E51.1 -
-:
(I98.8*)
E51.2 Wernicke
E51.8
E51.9 ,
E52 []
:
(-)
()
: (E64.8)
E53
B
: B (E64.8)
B12- (D51.)
E53.0
E53.1
B6
: -
(D64.3)
339
E53.8 B
:
B12
E53.9 B,
E54
C
: (D53.2)
C (E64.2)
E55 D
: (M83.)
o (M80M81)
(E64.3)
E55.0 ,
:
: :
(K90.0)
Crohn (K50.)
(E64.3)
(N25.0)
D- (E83.3)
E55.9 D,
D
E56
:
(E64.8)
E56.0 E
340
,
E56.1 K
: ,
K (D68.4)
K (P53)
E56.8
E56.9 ,
E58
: (E83.5)
(E64.8)
E59
Keshan
: (E64.8)
E60
E61
, ,
( XX).
:
(E83.)
,
(E00E02)
(E64.)
E61.0
E61.1
: (D50.)
E61.2
E61.3
E61.4
E61.5
341
E61.6
E61.7
E61.8 ,
E61.9 ,
E63
: (E86)
(R62.8)
(P92.)
(E64.)
E63.0 [EFA]
E63.1
E63.8 ,
E63.9 ,
(I43.2*)
E64
E64.0 -
: , -
(E45)
E64.1 A
E64.2 C
E64.3
E64.8
E64.9 ,
342
,
(E65E68)
E65
E66
: (E23.6)
:
(E88.2)
[ Dercum] (E88.2)
Prader-Willi (Q87.1)
E66.0 ,
E66.1
( XX).
E66.2 -
Pickwick
E66.8
E66.9 ,
E67
: (R63.2)
(E68)
E67.0 A
E67.1
E67.2 B6
343
E67.3 D
E67.8
E68
(E70E90)
: (E34.5)
(E25.0)
Ehlers-Danlos (Q79.6)
, -
(D55.)
Marfan (Q87.4)
5-a (E29.1)
E70 -
E70.0
E70.1
E70.2
344
,
E70.3
:
-
:
Chediak(-Steinbrinck)-Higashi
Cross
Hermansky-Pudlak
E70.8
:
E70.9 -
,
E71
E71.0
E71.1 -
-
E71.2
,
E71.3
[Addison-Schilder]
-
: Refsum (G60.1)
Schilder (G37.0)
Zellweger (Q87.8)
345
E72
: -
(R70R89)
:
(E70.)
(E71.0E71.2)
(E71.3)
(E79.)
(M10.)
E72.0 -
Fanconi(-de Toni)(-Debre)
Hartnup
Lowe
:
(E70.8)
E72.1 -
: II (D51.2)
E72.2
: (E72.4)
346
,
E72.3 -
E72.4
( I, II )
E72.5
( I, II)
E72.8 -
:
b-
g-
E27.9 , -
E73
E73.0
E73.1
E73.8
E73.9 ,
E74
: (E16.3)
(E10E14)
(E16.2)
(E76.0E76.3)
347
E74.0
:
Andersen
Cori
Forbes
Hers
McArdle
Pompe
Tauri
Von Gierke
E74.1
-1,6-
E74.2
E74.3 -
-
: (E73.)
E74.4 -
:
:
: (D55.)
E74.8 -
348
,
E74.9 , -
E75
: , I-III (E77.0E77.1)
Refsum (G60.1)
E75.0 GM2
:
Sandhoff
Tay-Sachs
GM2 :
E75.1
:
GM1
GM3
IV
E75.2
:
Fabry(-Anderson)
Gaucher
Krabbe
Niemann-Pick
Farber
: [Addison-Schilder]
(E71.3)
E75.3 ,
349
E75.4
:
Batten
Bielschowsky-Jansky
Kufs
Spielmeyer-Vogt
E75.5
[van Bogaert-Scherer-Epstein]
Wolman
E75.6 ,
E76
E76.0 , I
:
Hurler
Hurler-Scheie
Scheie
E76.1 , II
Hunter
E76.2
b-
, III, IV, VI, VII
:
Maroteaux-Lamy ()()
Morquio(-)()
Sanfilippo ( B)( C)( D)
E76.3 ,
E76.8 -
E76.9 -
,
350
,
E77
E77.0
II [I- ]
III [-Hurler ]
E77.1
[ I]
E77.8 -
E77.9 , -
E78
: (E75.0E75.3)
E78.0
Fredrickson, IIa
,
[LDL]
E78.1
Fredrickson, IV
, B
-
[VLDL]
351
E78.2
Fredrickson, IIb III
, C
-
Xanthoma tuberosum
: [van Bogaert-
Scherer-Epstein] (E75.5)
E78.3
Fredrickson, I V
, D
E78.4
E78.5 ,
E78.6
()
--
E78.8 -
E78.9 , -
352
,
E79
: (N20.0)
(D81.)
(M10.)
(D53.0)
(Q82.1)
E79.0 -
E79.1 Lesch-Nyhan
E79.8 -
E79.9 -
,
E80
:
E80.0
E80.1
E80.2
:
()
-
( XX).
E80.3
[Takahara]
353
E80.4 Gilbert
E80.5 Crigler-Najjar
E80.6
Dubin-Johnson
Rotor
E80.7 , -
E83
: -
(E58E61)
(E20E21)
D (E55.)
E83.0
Menkes ( ) ( -
)
Wilson
E83.1
: :
(D50.)
(D64.0D64.3)
E83.2
E83.3
D-:
: (M83.)
o (M80M81)
E83.4
354
,
E83.5
: (M11.1M11.2)
(E21.0E21.3)
E83.8
E83.9 ,
E84
:
E84.0
E84.1
(P75*)
E84.8
E84.9 ,
E85
: Alzheimer (G30.)
E85.0
E85.1
()
E85.2 ,
E85.3
E85.4
E85.8
E85.9 ,
355
E86
: (P74.1)
:
(R57.1)
(T81.1)
(T79.4)
E87
-
-
E87.0
[Na]
[Na]
E87.1
[Na]
: -
(E22.2)
E87.2
:
- ()
: (E10E14)
.1
E87.3
:
E87.4 - -
356
,
E87.5
[K]
[K]
E87.6
[K]
E87.7
: (R60.)
E87.8 - ,
E88
: X () (D76.0)
, -
,
( XX).
E88.0 ,
a-1-
:
(E78.)
(D47.2)
(D89.0)
Waldenstrom (C88.0)
E88.1 ,
: Whipple (K90.8)
E88.2 ,
:
[Dercum]
357
E88.8
Launois-Bensaude
E88.9 , -
E89 ,
,
E89.0
E89.1
E89.2
E89.3
E89.4
E89.5
E89.6 (-)
E89.8
E89.9
,
E90*
,
358
V
(F00F99)
:
: , ,
, -
(R00R99)
:
F00F09 , , -
F10F19 , -
F20F29 ,
F30F39 [ ]
F40F48 , -
F50F59 , -
F60F69
F70F79
F80F89
F90F98 , -
F99
:
F00* Alzheimer
F02* ,
359
, ,
(F00F09)
,
,
,
, .
( , ,
) ( -
,
).
[] (F00F03) ,
, ,
, ,
, , , , ,
. . -
, ,
-
.
Alzheimer, , -
.
.
F00* Alzheimer
(G30.)
-
. ,
, , -
.
360
F00.0* Alzheimer -
(G30.0)
Alzheimer, 65-
, -
.
Alzheimer, 2
,
F00.1* Alzheimer -
(G30.1)
Alzheimer, 65-
, 70 -,
.
Alzheimer, 1
,
F00.2* Alzheimer,
(G30.8)
F00.9* Alzheimer,
(G30.9)
F01
, -
, -
. ,
. .
:
F01.0
, . -
.
F01.1
, -
,
.
361
F01.2
, -
. -
, -
Alzheimer.
F01.3
F01.8
F01.9 ,
F02* ,
, ,
, Alzheimer -
. , -
.
F02.0* Pick (G31.0)
, , -
,
, , -
, , -
.
F02.1* Creutzfeldt-Jacob
(A81.0)
, -
,
.
, -
. , -
.
F02.2* Huntington (G10)
, -
. -
. -
. ,
10-15 .
Huntington
362
363
F03 ,
:
:
:
: -
(F05.1)
(R54)
F04 ,
-
.
.
,
, , . -
.
,
: :
(R41.3)
(R41.1)
(F44.0)
(R41.2)
:
(F10.6)
-
(F11F19 .6)
364
F05 ,
,
-
, , , , ,
-. -
, .
: :
()
: delirium tremens,
(F10.4)
F05.0 ,
F05.1
, , -
(F00F03).
F05.8 ,
F05.9 ,
F06 ,
,
, ,
, ,
,
.
: , :
(F05.)
, F00
F03
(F10
F19)
365
F06.0
, -
, ,
.
, -
. -
.
()
: (F10.5)
(F20.)
F06.1
() () -
, .
.
: (F20.2)
:
(R40.1)
(F44.2)
F06.2 [] -
, -
. -
. ,
, -
.
- -
: :
(F23.)
(F22.)
,
(F11F19 .5)
(F20.)
366
F06.3 [-
]
,
,
, , , -
( F30F38), -
.
: ,
(F30F39)
F06.4
, -
(F41.1), (F41.0)
, -
.
: , -
(F41.)
F06.5
, -
,
-
, ( F44.), -
.
: [ ],
(F44.)
F06.6 [] -
, -
, -
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[ - ]
F12. ,
[ - ]
F13. ,
[ - ]
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374
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381
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392
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395
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F45.1
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F45.9 ,
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F48.8
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411
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413
F52.3
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414
F53.0 , -
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F60.5
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423
F63.1 [-
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F64.2
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.
F65.3
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.
F65.4
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.
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.
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F65.6 -
.
- , -
.
F65.8
,
: ,
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.
F65.9 ,
427
F66
,
:
.
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,
. - ,
, ,
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.
F66.1 -
(-
, ) ,
-
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.
F66.2
(-
, )
.
F66.8
F66.9 , -
428
F68
F68.0 -
,
, ,
-
.
, (-
)
.
F68.1 -
, -
[ ]
, -
.
,
. -
.
Munchausen
: (L98.1)
, ( -
) (Z76.5)
F68.8 -
F69
,
429
(F70F79)
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-
, .. , , .
, ,
.
-
.
. -
-
.
.
, , -
.
.
F70F79 :
.0
.1 , -
.8
.9
,
, , ,
, .
430
F70
IQ ( ) -
50 69 (
9 12 ).
. -
-
.
:
F71
IQ 35 49 ( -
6 9 ).
, -
, -
.
.
:
F72
IQ 20 34 ( -
3 6 ).
-
.
:
F73
IQ 20 (
3 ). -
, , -
.
:
F78
F79 ,
: (-):
431
(F80F89)
, , : (1)
; (2)
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; (3) -
.
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,
.
F80
, -
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-
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-
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.
F80.0
,
, ,
.
:
: ( ):
(R47.0)
(R48.2)
(H90H91)
(F70F79)
432
:
(F80.1)
(F80.2)
F80.1
,
-
,
. -
, .
,
: [
Landau-Kleffner] (F80.3)
, -
(F80.2)
(R47.0)
(F94.0)
(F70F79)
(F84.)
F80.2
,
.
, -
.
,
Wernicke
: [
Landau-Kleffner] (F80.3)
(F84.0F84.1)
:
(R47.0)
(F80.1)
(F94.0)
,
(H90H91)
(F70F79)
433
F80.3 [ Lan-
dau-Kleffner]
, , -
, ,
, . -
-
. -
- , -
.
-
,
.
. - - -
.
: :
(R47.0)
(F84.0F84.1)
-
(F84.2F84.3)
F80.8
F80.9 , -
F81
,
. -
-
, -
.
434
F81.0
-
,
,
. -
,
, , -
.
, -
,
.
. -
.
: (R48.0)
(R48.0)
,
(F93.)
F81.1
, -
, -
.
, -
.
( -
)
: (R48.8)
:
(F81.0)
(Z55.8)
435
F81.2 -
,
-
.
, -
, - -
, , ,
.
(-)(-) :
Gertsmann
: (R48.8)
:
(F81.3)
(Z55.8)
F81.3
, -
, -
, -
. , -
F81.2 F81.0
F81.1.
: :
(F81.2)
(F81.0)
(F81.1)
F81.8
F81.9 ,
:
436
F82
, -
,
-
. -
, -
-
-
,
.
(-) :
:
(R26.)
(R27.0)
(F70F79)
F83
,
,
, -
. ,
. -
-
, . ,
, , -
: F80., F81. F82.
437
F84
,
,
, , -
.
.
-
.
F84.0
,
: () , -
() -
-
, ,
, .
, -
,
, (
) .
(-):
Kanner
: (F84.5)
F84.1
,
-
, ,
. , -
-
, ( -
, , -
, ), -
. -
-
.
438
-
(F70F79).
F84.2 Rett
, ,
-
-
, . -
7 24 .
, -
.
,
. -
, -
.
.
F84.3
,
-
. , -
, -
, .
;
, ; -
, , -
. -
,
.
Heller
, , -
.
: Rett (F84.2)
439
F84.4 ,
-
.
(IQ 34),
,
. -
( , IQ )
(
), . -
(
,
). -
, .
IQ
.
F84.5 Asperger
, -
-
, , ,
, . -
, . -
. -
. -
.
F84.8
F84.9 , -
F88
F89 -
,
440
,
(F90F98)
F90
, (-
),
, ,
,
, , , -
. -
. ,
-
, -
. -
,
.
. -
,
. -
.
: (F41.)
[ -
] (F30F39)
-
(F84.)
(F20.)
F90.0
: , -
(F90.1)
F90.1
,
F90.8
441
F90.9 ,
F91
,
, .
-
. - -
-
( ). -
,
.
,
: -
; ;
; , , -
, ; -
. ,
, ,
.
: [ -
] (F30F39)
(F84.)
(F20.)
, :
(F92.)
(F90.1)
F91.0 ,
, -
( ,
),
, , -
. -
F91., -
. /
.
442
F91.1
, -
( -
F91., , -
)
.
F91.2
,
( -
F91., ,
), , -
.
,
,
F91.3 -
, -
, -
, , -
- .
F91.. -
.
, - , -
,
, -
.
F91.8
F91.9 ,
443
F92
, -
,
, -
.
(F91.)
(F93.), -
(F40F48),
(F30F39).
F92.0
(F91.) (F32.), -
,
,
.
.
(F91.),
(F32.)
F92.8 -
(F91.)
, , -
, .
(F91.), :
(F93.)
(F40F48)
F92.9 ,
444
F93 ,
- ,
, . -
-
, -
(F40F48).
: ,
,
(F92.)
F93.0 ,
, -
-
.
, (), -
(
), -
.
: [ -
] (F30F39)
(F40F48)
-
(F93.1)
-
(F93.2)
F93.1 -
, ,
( )
, .
, ,
( ),
(F40F48).
:
(F41.1)
445
F93.2
, -
. -
, -
,
.
F93.3
( )
-
-
.
, -
, -
.
F93.8
:
(F64.2)
F93.9 ,
F94
,
, -
, -
, , (
) -
,
. , -
.
446
F94.0
, -
, -
, () .
, , ,
.
:
(F84.)
(F20.)
-
(F80.)
(F93.0)
F94.1 , -
,
-
, -
(-
, -
, , -
). -
, .
,
,
, .
: Asperger (F84.5)
,
(F94.2)
(T74.)
-
, -
(Z61.4Z61.6)
447
F94.2 , -
, -
, . -
, ,
-
,
. -
.
: Asperger (F84.5)
(F43.2)
(F90.)
,
(F94.1)
F94.8
F94.9 -
,
F95
,
. , , , -
( )
, .
, -
, -
. -
, ,
. -
, , . -
-
, . -
-
( ) (-
), ().
F95.0
, -
12 .
, .
448
F95.1 -
,
( -
), ( -
) .
F95.2
[ Tourette]
, -
, -
.
.
,
, ,
. -
, (-
).
F95.8
F95.9 ,
F98
,
, -
, .
,
,
,
.
: (R06.8)
-
(F64.2)
Kleine-Levin (G47.8)
- (F42.)
, -
(F51.)
449
F98.0
,
, -
, -
,
.
. -
-
.
()()
: (R32)
F98.1
, -
, , -
.
-
,
-
, -
.
- , -
(F93.) (F91.).
-
.
: (R15)
F98.2
, -
.
-
, , -
. ,
, (
).
450
:
(F50.)
(R63.3)
(P92.)
(F98.3)
F98.3
( ,
.).
- ( ), -
.
. - -
, -
F70F79 .
F98.4
, , , ( -
) ,
. -
, -
. , -
, : , , -
, ,
. : -
, ,
, . -
- -
(
).
, :
, -
.
/
: (R25.)
-
(G20G25)
(F98.8)
(F98.8)
, - -
(F00F95)
(F98.8)
(F95.)
(F63.3)
451
F98.5
, ,
, .
, -
, .
: (F95.)
(F98.6)
F98.6
, ,
, -
.
, -
.
: (F98.5)
(F95.)
F98.8 -
, -
,
F98.9 -
, , -
(F99)
F99
: (F06.9)
452
VI
(G00G99)
: ,
(0096)
(0099)
,
(0099)
,
(Q00Q99)
, -
(0090)
, -
(S00T98)
(00D48)
, ,
, -
(R00R99)
:
G00G09
G10G13 ,
G20G26
G30G32 -
G35G37
G40G47
G50G59 ,
G60G64
G70G73 -
G80G83
G90G99
453
:
G01* ,
G02* , -
G05* , , -
G07* -
,
G13* ,
, ,
G22* ,
G26* -
,
G32*
,
G46*
G53* , -
G55* ,
G59* ,
G63* ,
G73* -
,
G94* , -
G99* , -
454
(G00G09)
G00 ,
:
: :
(G04.2)
(G04.2)
G00.0
, Haemophilus influenzae
G00.1
G00.2
G00.3
G00.8 ,
:
Friedlander
Escherichia coli
Klebsiella
G00.9 ,
:
455
G01* ,
():
(22.8)
(54.8)
(27.)
(32.1)
(69.2)
(39.0)
(52.1)
(02.2)
:
(50.4)
(51.4)
(17.0)
(01.0)
: -
,
(G05.0*)
G02*
,
: -
, -
(G05.1G05.2*)
G02.0* ,
( ):
(87.1)
(87.0)
herpes simplex (B00.3)
(27.)
(05.1)
(26.1)
(06.0)
(01.0)
herpes zoster (B02.1)
456
G02.1*
():
(37.5)
(38.4)
(B45.1)
G02.8* -
,
:
(56.)
Chagas (57.4)
G03 ,
:
: (G04.)
(G04.)
G03.0
G03.1
G03.2 [Mollaret]
G03.8 , -
G03.9 ,
()
457
G04 ,
:
: (G93.3)
:
(G93.4)
(G31.2)
(G92)
(G35)
:
(G37.3)
(G37.4)
G04.0
-
( ).
G04.1
G04.2 ,
G04.8 ,
G04.9 , ,
()
G05* ,
,
: -
,
458
G05.0* , -
,
, ():
(32.1)
(39.8)
:
(50.4)
(52.1)
(17.8)
G05.1* ,
,
, ():
(85.1)
(25.8)
(85.0)
herpes simplex (B00.4)
(J10.8, J11.8)
(05.0)
(26.2)
(01.1)
(06.0)
herpes zoster (02.0)
G05.2* ,
,
, :
(56.)
Chagas ( ) (57.4)
,
(naegleria) (60.2)
(58.2)
(83.2)
G05.8* , ,
lupus (M32.1)
459
G06
(9597).
G06.0
():
[ ]
:
G06.1
() [ ]
:
G06.2 ,
G07*
,
:
(06.6)
(54.8)
(17.8)
(65.)
:
(17.8)
(17.1)
460
G08
(-):
: :
:
, -
(0007, 08.7)
,
(22.5, 87.3)
(I67.6)
-
(G95.1)
G09
: -
,
G00G08 ( -
,
*) ,
.
,
, -
, . -
-
, 2.
461
,
(G10G13)
G10 Huntington
Huntington
G11
:
(G60.)
(G80.)
(7090)
G11.0
G11.1
: 20- -
.
:
[ Hunt]
Friedreich (-)
-
G11.2
: 20- .
G11.3 -
- [ Louis-Bar]
: Cockayne (Q87.1)
(Q82.1)
G11.4
G11.8
462
G11.9 ,
(-) (-):
G12
G12.0 , I [Werd-
nig-Hoffman]
G12.1
[Fazio-Londe]
:
, II
, III [Kugelberg-Welander]
-
G12.2
:
:
G12.8 -
G12.9 ,
463
G13* ,
,
,
G13.0*
(0097)
[Denny-Brown] (00
D48)
G13.1* , -
,
(00D48)
G13.2* , -
(00.1, 03.)
G13.8* , -
, ,
(G20G26)
G20 Parkinson
Paralysis agitans
Parkinson:
(-)
(-)
G21
G21.0
( ).
464
G21.1 , -
( ).
G21.2 ,
( ).
G21.3
G21.8
G21.9 ,
G22* ,
(52.1)
G23
: (G90.3)
G23.0 Hallervorden-Spatz
G23.1 [Steele-
Richardson-Olszewski]
G23.2
G23.8 -
G23.9 , -
465
G24
:
: (G80.3)
G24.0 ,
( ).
G24.1
G24.2
G24.3
: (43.6)
G24.4
G24.5
G24.8
G24.9 ,
G25
G25.0
: (R25.1)
G25.1 ,
( ).
G25.2
466
G25.3
,
( ).
: (G51.4)
(G40.)
G25.4 ,
( ).
G25.5
: , (I02.0)
Huntington (G10)
(I02.)
Sydenham (I02.)
G25.6 ,
( ).
: de la Tourette (F95.2)
(F95.9)
G25.8 -
G25.9 , -
G26*
,
467
(G30G32)
G30
:
: :
, (G31.1)
(F03)
(R54)
G30.0
: 65-
.
G30.1
: 65-
.
G30.8
G30.9 ,
G31
,
: Reye (G93.7)
G31.0
Pick
G31.1 , -
: (G30.)
(R54)
468
G31.2 ,
:
:
[] ,
G31.8
[ Alpers]
[ Leigh]
G31.9 , -
G32*
,
G32.0*
,
12 (53.8)
G32.8* -
,
469
(G35G37)
G35
:
G36
: -
(G04.8)
G36.0 [ Devic]
: (H46)
G36.1
[ Hurst]
G36.8
G36.9 ,
G37
G37.0
Schilder
: [Addison-Schilder]
(71.3)
470
(G40G47)
G40
: Landau-Kleffner (F80.3)
(R56.8)
(G41.)
Todd (G83.8)
G40.0 () ()
--
-
-
471
G40.1 () () -
-
, -
G40.2 () () -
-
, -
, -
G40.3 -
(-):
()
[]
[grand mal]
:
-
[ , petit
mal]
:
-
472
G40.4 -
:
-
Lennox-Gastaut
West
G40.5
[Kozevnikof]
, :
( ).
G40.6 Grand mal ( [petit
mal] ),
G40.7 [petit mal], grand
mal,
G40.8
,
G40.9 ,
:
473
G41
G41.0 grand mal ( -
)
-
:
[Kozhevnikof] (G40.5)
G41.1 petit mal ( )
G41.2
G41.8
G41.9 ,
G43
: (R51)
G43.0 [ ]
G43.1 [ ]
:
:
G43.2
G43.3
G43.8
G43.9 ,
474
G44
: (G50.1)
(R51)
(G50.0)
G44.0
:
G44.1 ,
G44.2
G44.3
G44.4 , -
,
( ).
G44.8
G45
[]
: (91.0)
G45.0 -
G45.1 ()
G45.2 -
G45.3
475
G45.4
: (R41.3)
G45.8
G45.9 ,
G46*
(I60I67)
G46.0* (I66.0)
G46.1* (I66.1)
G46.2* (I66.2)
G46.3* (I60I67)
:
Benedikt
Claude
Foville
Millard-Gubler
Wallenberg
Weber
G46.4* (I60I67)
G46.5* (I60I67)
G46.6* (I60I67)
G46.7* (I60I67)
G46.8* -
(I60I67)
476
G47
: (F51.5)
(F51.)
(F51.4)
(F51.3)
G47.0
[]
G47.1 []
G47.2 -
G47.3
:
: Pickwick (66.2)
(28.3)
G47.4
G47.8
Kleine-Levin
G47.9 e ,
477
,
(G50G59)
: ,
-
(79.2)
(26.8)
(54.1)
G50
: 5-
G50.0
G50.1
G50.8
G50.9 ,
G51
: 7-
G51.0 Bell
G51.1 ganglion geniculi
: ganglion genicu-
li (02.2)
G51.2 Melkersson
Melkersson-Rosenthal
G51.3
G51.4
478
G51.8
G51.9 ,
G52
: :
(8-) (93.3)
(2-) (46, 47.0)
,
(49.049.2)
G52.0
1-
G52.1 n. glossopharingeus
9-
G52.2 n. vagus
(10-)
G52.3
12-
G52.7
G52.8
G52.9 , -
G53*
,
G53.0* herpes zoster(02.2)
(-):
ganglion geniculi
479
G53.1* -
, -
(0099)
G53.2* -
(D86.8)
G53.3* -
(00D48)
G53.8*
,
G54
:
-
(5051)
(79.2)
:
-
(54.1)
(47.)
G54.0
G54.1 -
G54.2 , -
G54.3 , -
G54.4 - , -
480
G54.5
Parsonage-Aldren-Turner
G54.6
G54.7
G54.8
G54.9 , -
G55*
,
G55.0*
(00D48)
G55.1*
(50
51)
G55.2*
(47.)
G55.3*
(4546, 48., 53
54)
G55.8*
,
G56
: -
-
G56.0
G56.1
481
G56.2
G56.3
G56.4
G56.8
G56.9 ,
G57
: -
-
G57.0
: :
(54.3)
(51.1)
G57.1
G57.2
G57.3 n. fibularis
()
G57.4 n. tibialis
G57.5
G57.6 n. plantaris
Morton
G57.8
G57.9 ,
G58
G58.0
482
G58.7
G58.8
G58.9 ,
G59* ,
G59.0* (1014 -
.4)
G59.8* , -
(G60G64)
: (79.2)
(79.2)
(26.8)
(54.1)
G60
G60.0
:
Charcot-Marie-Tooth
Djerine-Sottas
, I-IV
( )(-
)
Roussy-Levy
G60.1 Refsum
G60.2
483
G60.3
G60.8
Morvan
Nelaton
:
G60.9 , -
G61
G61.0 Guillain-Barr
(-)
G61.1
-
( ).
G61.8
G61.9 ,
G62
G62.0
( ).
G62.1
G62.2 ,
-
(
).
484
G62.8
( ).
G62.9 ,
G63* ,
G63.0* -
,
:
(36.8)
(27.)
(30.)
(69.2)
(26.8)
herpes zoster (B02.2)
(52.1)
(50.4)
(17.8)
G63.1* (00D48)
G63.2* (1014 -
.4)
G63.3*
(00
07, 1516, 2034, 7089)
G63.4* (40
64)
G63.5* -
(3035)
G63.6* - -
(0025, 4096)
485
G63.8* , -
(N18.8)
G64
-
(G70G73)
G70 Myasthenia gravis
-
: (05.1)
Myasthenia gravis (94.0)
G70.0 Myasthenia gravis
, -
( ).
G70.1 -
-
(
).
G70.2
G70.8 -
G70.9 - , -
486
G71
: arthrogryposis multiplex congenita (Q74.3)
(7090)
(60.)
G71.0
:
- , -
Duchenne Becker
[Becker]
-
[Emery-Dreifuss]
--
-
-
[Duchenne]
: :
(G71.2)
(G71.2)
G71.1
[Steinert]
:
:
[Thomsen]
[Becker]
[Isaacs]
, , -
( ).
487
G71.2
:
:
:
()
G71.3 , -
G71.8
G71.9 ,
G72
: arthrogryposis multiplex congenita (Q74.3)
(33.)
(62.2)
(60.)
(33.2)
G72.0
, , -
( ).
G72.1
G72.2 , -
-
(
).
488
G72.3
():
G72.4 ,
G72.8
G72.9 ,
G73* -
,
G73.0*
:
(1014 .4)
[] (05.)
G73.1* Eaton-Lambert (80)
G73.2*
(00D48)
G73.3* ,
G73.4* ,
G73.5*
:
(21.021.3)
(20.)
(05.)
489
G73.6* -
:
(74.0)
(75.)
G73.7* ,
:
(0506)
(34.8)
Sjogren (35.0)
lupus (32.1)
(G80G83)
G80
: Little
: (G11.4)
G80.0
()
G80.1
G80.2
G80.3
G80.4
G80.8
G80.9 ,
490
G81
: -
, -
() () -
,
,
,
.
-
,
.
: (G80.)
G81.0
G81.1
G81.9 ,
G82
: -
, -
, -
, -
, . -
-
-
, .
: (G80.)
G82.0
G82.1
G82.2 ,
()
G82.3
G82.4
G82.5 ,
491
G83
: -
, -
, -
, -
, . -
-
-
, .
: () (),
G80G82
G83.0
()
G83.1
G83.2
G83.3 ,
G83.4 cauda equina
, cauda
equina
: (G95.8)
G83.8
Todd ()
G83.9 ,
492
(G90G99)
G90
[]
: -
, (G31.2)
G90.0
,
G90.1 [Riley-Day]
G90.2 Horner
Bernard(-Horner)
G90.3
[Shy-Drager]
: (I95.1)
G90.8 []
G90.9 [] -
,
G91
:
: :
(Q03.)
(37.1)
G91.0
G91.1
G91.2
G91.3 ,
493
G91.8
G91.9 ,
G92
-
(
).
G93
G93.0
: -
(91.1)
(Q04.6)
G93.1 , -
: :
, -
(0007, 08.8)
,
(29.2, 74.3, 89.2)
(8088)
(21.9)
G93.2
: (I67.4)
G93.3 -
G93.4 ,
: :
(G31.2)
(G92)
494
G93.5
( )
:
(S06.2)
(S06.3)
G93.6
: :
(11.0)
(S06.1)
G93.7 Reye
( ).
G93.8
,
( ).
G93.9 ,
G94*
,
G94.0* -
, (0099)
G94.1* (00D48)
G94.2* ,
G94.8*
,
G95
: (G04.)
G95.0
495
G95.1
()(-
)
: ,
(G08)
G95.2 ,
G95.8
:
( ).
: :
(N31.9)
cauda equina
(G83.4)
- -
-
(N31.)
G95.9 ,
G96
G96.0
: (G97.0)
G96.1 , -
()()
496
G96.8
G96.9 , -
G97
,
G97.0
G97.1
G97.2 -
G97.8 -
G97.9
,
G98 ,
G99*
,
G99.0* -
(85.)
(1014
.4)
G99.1* []
, -
497
G99.2* ,
(47.0)
:
(50.0,
51.0)
(00D48)
(47.)
G99.8*
,
498
VII
(H0059)
: ,
(0096)
(0099)
,
(0099)
,
(Q00Q99)
, -
(0090)
, -
(S00T98)
(C00D48)
, ,
, -
(R00R99)
:
H00H06 ,
H10H13
H15H22 , ,
H25H28
H30H36
H40H42
H43H45
H46H48
H49H52 , -
,
H53H54
H55H59
:
H03* ,
H06* , -
499
H13* ,
H19* , -
H22* , -
H28* , -
H32* ,
H36* , -
H42* ,
H45* -
,
H48* -
,
H58* ,
,
(H00H06)
H00
H00.0
A
H00.1
H01
H01.0
: (H10.5)
500
H01.1
:
H01.8
H01.9 ,
H02
: (Q10.0Q10.3)
H02.0
H02.1
H02.2
H02.3
H02.4
H02.5 ,
: (G24.5)
() (F95.)
(G25.6)
H02.6
H02.7 -
H02.8
H02.9 ,
501
H03* ,
H03.0* , -
, Demodex (B88.0)
:
(B55.)
(B74.3)
(B73)
(B85.3)
H03.1* -
,
:
- [herpes simplex] (B00.5)
(30.)
(08.1)
(18.4)
(66.)
herpes zoster (B02.3)
H03.8* , -
(L01.0)
H04
: (Q10.4
Q10.6)
H04.0
H04.1
:
H04.2
502
H04.3 -
()
,
a
: (39.1)
H04.4
:
(-)
a
H04.5
:
()
H04.6
H04.8
H04.9 ,
H05
: (Q10.7)
H05.0
H05.1
503
H05.2
c ()
H05.3
H05.4
H05.5 ( )
H05.8
H05.9 ,
H06*
,
H06.0* , -
H06.1* , -
(67.)
(B87.2)
H06.2* -
(05.)
H06.3* , -
504
(H10H13)
H10
: (16.2)
H10.0
H10.1
H10.2
H10.3 ,
: (39.1)
H10.4
H10.5
H10.8
H10.9 ,
H11 k
: (16.2)
H11.0
: (11.8)
H11.1
:
H11.2
H11.3
505
H11.4
:
H11.8
H11.9 ,
H13*
,
H13.0* (B74.)
H13.1* ,
( ):
(60.1)
() (30.1)
(74.0)
(36.8)
(54.3)
() () (30.3)
- [herpes simplex] (B00.5)
(39.8)
Newcastle (30.8)
herpes zoster (B02.3)
H13.2* ,
H13.3* (L12.)
H13.8* ,
506
, ,
(H15H22)
H15
H15.0
H15.1
H15.8
( )
: (44.2)
H15.9 ,
H16
H16.0
:
:
Mooren
H16.1
:
()
()
507
H16.2
:
( )
H16.3
H16.4
()
()
H16.8
H16.9 ,
H17
H17.0 ()
H17.1
H17.8 () -
H17.9 ,
H18
H18.0
()
Kayser-Fleischer
Krukenberg
Staehli
, , -
( ).
H18.1
H18.2
508
H18.3
H18.4
: Mooren (H16.0)
H18.5
:
:
Fuchs
H18.6
H18.7
:
: (Q13.3
Q13.4)
H18.8
H18.9 ,
19*
,
H19.0* , -
(52.7)
(18.5)
herpes zoster (02.3)
509
H19.1* , -
herpes simplex (B00.5)
H19.2* -
,
(30.0)
() :
(60.1)
(05.8)
(50.3)
(18.5)
herpes zoster (02.3)
H19.3* , -
(M35.0)
H19.8* -
,
Down (Q90.)
20
H20.0
,
H20.1
H20.2 ,
H20.8
H20.9 ,
21
: (44.1)
H21.0
: (S05.1)
510
H21.1
H21.2
:
()
()()
H21.3 , -
, :
: (21.2)
H21.4
:
H21.5
()
:
: (Q13.2)
H21.8
H21.9 ,
511
22*
,
H22.0* , -
:
(54.3)
- [herpes simplex] (00.5)
() (51.4)
(18.5)
herpes zoster (B02.3)
H22.1* ,
:
(45)
(D86.8)
H22.8*
,
(2528)
25
:
(H40.1)
H25.0
:
()()
()
H25.1
brunescens
512
H25.2 ,
H25.8
H25.9 ,
26
: (Q12.0)
H26.0 ,
H26.1
-
( ).
H26.2
( )
H26.3 ,
, , -
( ).
H26.4
Soemmerring
H26.8
H26.9 ,
27
: (Q12.)
, -
(85.2)
(Z96.1)
H27.0
H27.1
513
H27.8
H27.9 ,
28*
,
H28.0* (1014
.3)
H28.1* -
,
, k
(20.)
(40
46)
H28.2* , -
(G71.1)
H28.8* , -
(3036)
30
H30.0
:
514
H30.1
:
: (H35.0)
H30.2
Pars planitis
H30.8
Harada
H30.9 ,
H31
H31.0
( )
()
H31.1
: (35.3)
H31.2
(-)(-
)()
: (72.4)
H31.3
:
515
H31.4
H31.8
H31.9 ,
32*
,
H32.0*
,
:
(52.7)
(58.0)
(18.5)
H32.8* ,
33
:
(35.7)
H33.0
H33.1
ora serrata
: (Q14.1)
(35.4)
H33.2
: (35.7)
516
H33.3
Operculum
:
(59.8)
-
(35.4)
H33.4
-
H33.5
34
: (G45.3)
H34.0
H34.1
H34.2
Hollenhorst
:
:
H34.8
:
H34.9 ,
517
35
H35.0 -
:
:
Coats
H35.1
H35.2
: -
(33.4)
H35.3
()
Kuhnt-Junius
()(-
)
, , -
( ).
518
H35.4
:
: (33.3)
H35.5
:
()()()
Stargardt
H35.6
H35.7 ,
H35.8
H35.9 ,
36* ,
H36.0* (1014
.3)
H36.8* , -
(I70.8)
- (D57.)
(75.)
519
(4042)
40
: (44.5)
(Q15.0)
(15.3)
H40.0
H40.1
()( ):
H40.2
()( ):
H40.3 ,
-
.
H40.4 ,
-
.
H40.5 ,
-
.
520
H40.6 ,
, , -
( ).
H40.8
H40.9 ,
42* ,
H42.0* ,
-
:
(85.)
Lowe (72.0 )
H42.8* , -
(73)
(4345)
43
H43.0
: -
(59.0)
H43.1
H43.2
H43.3
521
H43.8
:
: -
(33.4)
H43.9 ,
44
: ,
H44.0
H44.1
H44.2
H44.3
H44.4
H44.5
H44.6 ( )
:
522
H44.7 ( )
:
H44.8
H44.9 ,
45*
,
H45.0* ,
H45.1* ,
:
(69.1)
(73)
(83.0)
H45.8*
,
523
(4648)
46
(-):
,
:
(47.0)
[Devic] (G36.0)
47 [2-]
H47.0 , -
H47.1 ,
H47.2
H47.3
H47.4
H47.5
, nuclei geniculate -
H47.6
H47.7 ,
524
48* [2-]
,
H48.0* , -
(52.1)
H48.1* ,
:
(52.1)
(39.8)
(G35)
H48.8*
,
,
,
(4952)
: (55)
49
: :
(52.5)
(51.2)
(G23.1)
H49.0 3- [n. ocumotorius]
H49.1 4- [n. trochlearis]
H49.2 6- [n. abducent]
H49.3 ()
525
H49.4
H49.8
Kearns-Sayre
H49.9 ,
50
H50.0
()(), -
H50.1
()(), -
H50.2
H50.3
:
()()
H50.4
H50.5
H50.6
Brown
,
526
H50.8
Duane
H50.9 ,
51
H51.0
H51.1 [
]
H51.2
H51.8 -
H51.9 , -
52
H52.0
H52.1
: (44.2)
H52.2
H52.3
H52.4
H52.5
()()
H52.6
H52.7 ,
527
(5354)
53
H53.0 ,
, :
H53.1
: (R44.1)
H53.2
H53.3
H53.4
()()
:
()
Bjerrum
528
H53.5
: (H53.1)
H53.6
: (50.5)
H53.8
H53.9 ,
54
:
-.
: (G45.3)
H54.0
3, 4, 5
H54.1 ,
3, 4, 5
1 2
H54.2
1 2
H54.3
9
H54.4
3, 4 5
[ ]
H54.5
1 2
[ ]
529
H54.6
9 [-
]
H54.7 ,
9
: - -
,
, -
6-10 1972 .1
H54 1 2 ,
3, 4 5, -
9. -
, -
- 100, 50 -
,
3, 50 -
4, -
.
-
: :
6/18 6/60
1 3/10 (0.3) 1/10 (0.1)
20/70 20/200
6/60 3/60
2 1/10 (0.1) 1/20 (0.5)
20/200 20/400
3/60 1/60 (
1 )
3
1/20 (0.05) 1/50 (0.02)
20/400 5/300 (20/1200)
1/60 ( -
1 )
4
1/50 (0.02)
5/300
5
1
WHO Technical Report Series 518, 1973.
530
(5559)
55
:
57
H57.0
H57.1
H57.8
H57.9 ,
58*
,
H58.0* ,
Argil Robertson, (52.1)
H58.1* , -
531
H58.8*
,
,
:
(50.0)
(50.3)
() (51.4)
(52.7)
59
: :
(85.2)
, -
(T85.3)
(Z96.1)
H59.0
H59.8
-
H59.9 -
,
532
VIII
(6095)
: ,
(0096)
(0099)
,
(0099)
,
(Q00Q99)
, -
(0090)
, -
(S00T98)
(00D48)
, ,
, -
(R00R99)
:
6062
6575
8083
9095
:
62* ,
67* ,
75*
, .
82* , -
94* , -
533
(6062)
60
H60.0
H60.1
:
H60.2
H60.3
:
H60.4
()
H60.5 ,
:
H60.8
H60.9 ,
534
61
H61.0
:
H61.1
:
: ,
(95.1)
H61.2
H61.3
H61.8
H61.9 ,
62*
,
H62.0* , -
(46)
H62.1* ,
:
- [herpes simplex] (00.1)
herpes zoster (02.8)
535
H62.2*
:
(44.8)
(37.2)
(36.9)
H62.3*
,
H62.4* ,
(L01.)
H62.8* ,
(6575)
65
:
H65.0
H65.1
Otitis media, :
()()()
: (70.0)
titis media acuta (66.9)
H65.2
536
H65.3
otitis media:
: (74.1)
H65.4
:
()
H65.9 ,
:
()
66
:
H66.0
H66.1
[]
537
H66.2 -
- []
H66.3
H66.4 ,
H66.9 ,
Otitis media:
67*
,
H67.0* -
,
Otitis media :
(38)
(18.6)
H67.1* ,
Otitis media :
(J10J11)
(05.3)
H67.8* ,
68
H68.0
H68.1
538
69
H69.0
H69.8
H69.9 ,
70
H70.0
H70.1
H70.2
pars petrosa () ()
H70.8
H70.9 ,
71
: (60.4)
-
(90.5)
72
: :
: (S09.2)
H72.0
H72.1
pars flaccida
H72.2
539
H72.8 :
(-):
H72.9 ,
73
H73.0
: otitis media (H65H66)
H73.1
: otitis media (H65H66)
H73.8
H73.9 ,
74
H74.0
H74.1
: (65.3)
H74.2
H74.3
H74.4
H74.8 -
H74.9 , -
540
H75*
,
H75.0* ,
(18.0)
H75.8* -
,
(8083)
H80
:
H80.0 , , -
H80.1 , , -
H80.2 ,
, :
H80.8
H80.9 ,
H81
: :
(R42)
(88.0)
H81.0 Meniere
, , Meniere
541
H81.1
H81.2
H81.3
Lermoyez
:
H81.4
H81.8
H81.9 , -
H82* ,
H83
H83.0
H83.1
H83.2
H83.3
H83.8
H83.9 ,
542
(9095)
H90 ,
()
:
: , (91.3)
(91.9)
a :
(H91.9)
(83.3)
(91.0)
() (91.2)
H90.0 () -
H90.1 -
H90.2 ,
, ,
H90.3
H90.4 -
H90.5 ,
:
543
H90.6
H90.7
,
H90.8 ,
H91
: (93.2)
a ,
90.
(61.2)
a
(83.3)
(F44.6)
(93.0)
H91.0
( ).
H91.1
H91.2
H91.3 ,
H91.8
H91.9 ,
:
H92
H92.0
544
H92.1
:
(G96.0)
H92.2 ( )
: (
)
H93 ,
H93.0
: (91.1)
H93.1 ()
H93.2
: (R44.0)
H93.3
8-
H93.8
H93.9 ,
H94*
,
H94.0*
,
(52.1)
H94.8* ,
545
H95
,
H95.0 -
H95.1
H95.8
H95.9
,
546
IX
(I00I99)
: ,
(0096)
(0099)
,
(0099)
,
(Q00Q99)
, -
(0090)
, -
(S00T98)
(00D48)
, ,
, -
(R00R99)
(30
36)
-
(G45.)
:
I00I02
I05I09
I10I15
I20I25
I26I28 [ ]
I30I52
I60I69
I70I79 ,
I80I89 , , -
I95I99 -
547
:
I32* ,
I39* ,
I41* ,
I43* ,
I52* ,
I68* ,
I79* , -
,
I98* -
,
(I00I02)
I00
I01
:
(I05I09), -
,
. ,
-
,
2.
I01.0
, I00,
()
: , (I30.)
548
I01.1
, I00,
I01.2
, I00,
I01.8
, I00,
I01.9 ,
, I00,
:
,
,
I02
: Sydenham
:
(G25.5)
Huntington (G10)
I02.0
I01.
I02.9
549
(I05I09)
I05
: , I05.0
I05.2I05.9,
: , (I34.)
I05.0
() ()
I05.1
:
I05.2
I05.8
()
I05.9 ,
() ()
I06
: , (I35.)
I06.0
()
I06.1
:
550
I06.2
-
I06.8
I06.9 ,
()
I07
: , -
: , (I36.)
I07.0
() ()
I07.1
() ()
I07.2
I07.8
I07.9 ,
I08
: , -
: (I38)
-
(I09.1)
I08.0
, -
I08.1 -
551
I08.2
I08.3 , -
I08.8
I08.9 ,
I09
I09.0
: , (I51.4)
I09.1
:
()
()
: (I38)
I09.2
:
: , (I31.)
I09.8
I09.9 ,
:
: (05.3)
552
(I10I15)
: ,
(1011, 1316)
(I20I25)
(29.2)
(I27.0)
I10 []
()()()(-
)()()
: :
(I60I69)
(35.0)
I11
: I50., I51.4
I51.9,
I11.0 () -
I11.9 () -
553
I12
[ ]
: N18., N19.
N26.
I10
()(-
)
: (I15.)
I12.0
I12.9
I13
: I11. -
I12.
:
-
-
I13.0
()
I13.1
I13.2
() -
,
I13.9
,
554
I15
: :
(I60I69)
(35.0)
I15.0 -
I15.1 , -
I15.2 , -
I15.8
I15.9 ,
(I20I25)
:
, I21I25,
.
-
.
: (I10I15)
.
I20
I20.0
:
555
I20.1
:
Prinzmetal
I20.8
I20.9 ,
:
I21
: ,
4
(28 ) -
:
(I23.)
:
(I25.2)
4 ( 28 -
) (I25.8)
(I22.)
(I24.1)
I21.0 -
()():
( )
-
-
-
556
I21.1 -
()():
( )
-
-
I21.2
():
-
-
( )
()
-
-
-
I21.3 -
I21.4
I21.9 ,
()
I22
:
: -
4 ( 28 )
(I25.8)
I22.0
()():
( )
-
-
-
557
I22.1
()():
( )
-
-
I22.8
():
-
-
( )
()
-
-
-
I22.9 -
I23
: , :
(I21I22)
(I31., I51.)
I23.0
I23.1
I23.2
558
I23.3 -
-
: (I23.0)
I23.4 -
I23.5 -
I23.6 , -
I23.8
I24
: (I20.)
(29.4)
I24.0 , -
()():
: -
4 ( 28 )
(I25.8)
I24.1 Dressler
I24.8
:
559
I24.9 ,
: ()
(I25.9)
I25
: - (I51.6)
I25.0 - -
I25.1
(-) ((-)):
I25.2
,
,
I25.3
:
I25.4
,
: () (Q24.5)
I25.5
I25.6
I25.8
I21I22 I24.,
4
( 28 )
I25.9 ,
()
560
[
]
(I26I28)
I26
: (-) ()():
: :
, -
(0007, 08.2)
,
(88.)
I26.0 -
I26.9 -
I27
I27.0
() ()(-
)
I27.1
I27.8
I27.9 ,
-
[cor pulmonale] ()
561
I28
I28.0
I28.1
I28.8
I28.9 - ,
(I30I52)
I30
:
: () (I01.0)
I30.0
I30.1
:
(9597).
I30.8
I30.9 ,
562
I31
:
(I23.)
(I97.0)
(S26.)
, (I09.2)
I31.0
Accretio cordis
I31.1
Concretio cordis
I31.2 ,
I31.3 ()
I31.8
I31.9 ,
()
I32* ,
I32.0* , -
:
(54.8)
(39.5)
(52.0)
(18.8)
I32.1*
,
563
I32.8* ,
():
(32.1)
(32.1)
(N18.8)
I33
: (I01.1)
(I38)
I33.0
()():
(9597).
I33.9 ,
I34
: ():
(I05.9)
(I05.8)
(I05.0)
, :
(I08.0)
(I05.0)
(I05.)
564
I34.0 ()
():
,
I34.1 ()
: arfan (Q87.4)
I34.2 ()
I34.8
I34.9 , -
I35
: (I42.1)
,
(I08.0)
(I06.)
I35.0 ()
I35.1 ()
():
,
I35.2 ()
I35.8
I35.9 ,
I36
: (I07.)
(I07.)
I36.0 ()
565
I36.1 () -
():
,
I36.2 ()
I36.8
I36.9 ,
I37
: (I09.8)
I37.0
I37.1
:
,
I37.2
I37.8
I37.9 ,
I38
()
:
,
-
()
: (I42.4)
(I09.1)
566
I39*
,
: :
(37.6)
(54.8)
Libman-Sacks (32.1)
(39.5)
(05.3)
(52.0)
(18.8)
(01.0)
I39.0* , -
I39.1* , -
I39.2* -
,
I39.3* ,
I39.4* , -
I39.8*
,
I40
I40.0
(9597).
I40.1
I40.8
I40.9 ,
567
I41* ,
I41.0* , -
:
(36.8)
(54.8)
(39.5)
(52.0)
(18.8)
I41.1* ,
():
(J10.8)
(J11.8)
(26.8)
I41.2*
,
:
Chagas () (57.2)
(57.0)
(58.8)
I41.8* ,
(05.3)
(D86.8)
I42
: , :
(99.4)
(90.3)
(I25.5)
I42.0
I42.1
568
I42.2
I42.3 ()
()
Lffler
I42.4
I42.5
I42.6
I42.7 ,
-
( ).
I42.8
I42.9 ,
()()
I43* ,
I43.0* -
,
(36.8)
I43.1*
(85.)
I43.2*
(63.9)
I43.8* , -
(10.0)
(05.9)
569
I44
I44.0 ,
I44.1 ,
, I II
Mobitz, I II
, I II
Wenckebach
I44.2 ,
I44.3
I44.4
I44.5
I44.6
I44.7 ,
I45
I45.0
I45.1
I45.2
I45.3
I45.4
I45.5
: (I45.9)
570
I45.6
:
Lown-Ganong-Levine
Wolff-Parkinson-White
I45.8
[V]
I45.9 ,
Morgagni-Adams-Stokes (MAS-)
I46
: (R57.0)
:
, -
(0007, 08.8)
(75.4)
I46.0
I46.1 ,
: :
(R96.)
:
(I44I45)
(I21I22)
I46.9 ,
571
I47
: :
, -
(0007, 08.8)
(75.4)
(R00.0)
I47.0 [re-entry]
I47.1
:
[V]
I47.2
I47.9 ,
Bouveret-Hoffmann
I48
I49
: (R00.1)
:
, -
(0007, 08.8)
(75.4)
(29.1)
I49.0
I49.1
I49.2 -
I49.3
572
I49.4 -
:
I49.5
()-()
I49.8
:
I49.9 ,
()
I50
: :
, -
(0007, 08.8)
(75.4)
(I11.0)
(I13.)
-
(I97.1)
(29.0)
I50.0
(
)
I50.1
573
I50.9 ,
,
I51
: I51.4I51.9, -
(I11.)
(I13.)
(I23.)
(I00I09)
I51.0 ,
():
I51.1 ,
I51.2 ,
I51.3 , -
():
I51.4 ,
:
()
574
I51.5
:
I51.6 - ,
-
: - ,
(I25.0)
I51.7
:
I51.8
()()
()()
I51.9 ,
I52*
,
: - -
, (I98.*)
I52.0* -
,
, (39.5)
I52.1* -
,
(65.)
I52.8* ,
(05.3)
575
(I60I69)
: (
I10 I15.)
-
.
: -
(G45.)
(S06.)
(F01.)
I60
:
:
(I69.0)
I60.0 -
I60.1
I60.2 -
I60.3 -
I60.4 -
I60.5 -
I60.6 -
576
I60.7
,
()
:
I60.8
I60.9 ,
()
I61
: (I69.1)
I61.0 , -
I61.1 , -
I61.2 ,
I61.3
I61.4
I61.5
I61.6 -
I61.8
I61.9 ,
577
I62
: (I69.2)
I62.0 ()()
I62.1
I62.9 (), -
I63
: -
, -
: (I69.3)
I63.0 , -
I63.1 , -
I63.2 , -
I63.3 , -
I63.4 , -
I63.5 , -
I63.6 , -
I63.8
I63.9 ,
578
I64 ,
: (I69.4)
I65
,
: , -
-
,
()()
: (I63.)
I65.0
I65.1
I65.2
I65.3 -
I65.8
I65.9 -
I66
,
: , -
() -
() , -
: (I63.)
I66.0
579
I66.1
I66.2
I66.3
I66.4 -
I66.8
I66.9 -
I67
: (I69.8)
I67.0
: (I60.7)
I67.1
:
,
: (Q28.)
(I60.9)
I67.2
I67.3
Binswanger
: (F01.2)
I67.4
I67.5 Moyamoya
I67.6
:
: (I63.6)
580
I67.7 ,
I67.8
()
I67.9 ,
I68*
,
I68.0* (85.)
I68.1*
,
:
(32.8)
(52.0)
(18.8)
I68.2* , -
(32.1)
I68.8* ,
I69
: , -
, I60I67
,
.
,
, .. -
.
I69.0
I69.1
581
I69.2
I69.3
I69.4 ,
I69.8
,
(I70I79)
I70
:
:
:
: (I67.2)
(I25.1)
(55.1)
(I27.0)
I70.0
I70.1
Goldblatt
: (I12.)
582
I70.2
() Mnckeberg
I70.8
I70.9
I71
I71.0 ( )
( ) ( -
)
I71.1
I71.2
I71.3
I71.4 -
I71.5 - -
I71.6 - -
I71.8 ,
I71.9
583
I72
: ()()( )
: ():
(I71.)
(Q27.3)
(I77.0)
( ) (I67.1)
(I60.)
(I25.4)
(I25.3)
(I28.1)
(35.0)
(I77.0)
I72.0
I72.1
I72.2
I72.3
I72.4
I72.8
I72.9
I73
: (69.1)
(3335)
(69.0)
(G45.9)
I73.0 Raynaud
Raynaud:
()
I73.1 [ Buerger]
584
I73.8
:
[ Schultze]
[ Nothnagel]
E
I73.9 ,
I74
: :
:
: :
(I63.0I63.2, I65.1)
(I63.0I63.2, I65.2)
(I63.3I63.5, I66.9)
(I21I25)
(55.0)
(I63.0I63.2, I65.9)
(I26.)
(N28.0)
(34.)
(I63.0I63.2, I65.0)
:
, -
(0007, 08.2)
,
(88.)
I74.0
Leriche
585
I74.1
I74.2 -
I74.3 -
I74.4 ,
I74.5
I74.8
I74.9
I77 -
: () (3036)
(31.0)
(I28.)
I77.0 ,
,
: (Q27.3)
(I67.1)
(I25.4)
I77.1
586
I77.2
:
-
I77.3
I77.4
I77.5
I77.6 ,
: :
[ Takayasu] (31.4)
, (I67.7)
(I25.8)
(I70.)
(31.531.6)
(I70.)
(I70.)
I77.8 -
I77.9 ,
I78
I78.0
Rendu-Osler-Weber
587
I78.1 ,
:
: :
(D22.)
(D22.)
(Q82.5)
(D22.)
(D22.)
(D22.)
(Q82.5)
(Q22.5)
(Q82.5)
(Q82.5)
(Q82.5)
I78.8
I78.9 ,
I79* ,
,
I79.0* ,
(52.0)
I79.1* ,
(52.0)
I79.2* , -
(1014
.5)
I79.8* , -
,
588
,
,
(I80I89)
I80
:
: :
:
, -
(0007, 08.7)
,
(22., 87.)
,
(G08)
, (I67.6)
, (G95.1)
( ) (75.1)
(I87.0)
(I82.1)
, , -
( ).
I80.0
I80.1
I80.2
I80.3 , -
589
I80.8
I80.9
I81
()
: (75.1)
I82
: :
(I63.6, I67.6)
(I21I25)
,
(G08)
, (I67.6)
, (G95.1)
(I80.)
(55.0)
(I81)
(I26.)
:
, -
(0007, 08.8)
,
(22., 87.)
I82.0 Budd-Chiari
I82.1
I82.2
I82.3
I82.8
I82.9
()
590
I83
: :
(22.0)
(87.8)
I83.0
, I83.9,
( , )
I83.1
, I83.9,
I83.2 -
, I83.9, -
I83.9
[ ]
I84
:
: :
(87.2)
(22.4)
I84.0
I84.1
:
591
I84.2
I84.3
I84.4
:
I84.5
I84.6
I84.7 ,
,
I84.8 ,
, :
I84.9 ,
I85
I85.0
I85.9
I86
: (35.0)
(I83.9)
592
I86.0
I86.1
I86.2
I86.3
: :
(87.8)
(22.1)
I86.4
I86.8
I87
I87.0
I87.1
()()
: (I28.8)
I87.2 ()()
I87.8
I87.9 ,
I88
: , -
(L04.)
(R59.)
,
[HIV], -
(23.1)
I88.0
()()
593
I88.1 , -
, ,
I88.8
I88.9 ,
I89
: :
(74.)
()
(N50.8)
(R59.)
(Q82.0)
(I97.2)
I89.0 ,
I89.1
:
: (L03.)
I89.8 -
()
I89.9 -
,
594
(I95I99)
I95
: - (R57.9)
(26.5)
(R03.1)
I95.0
I95.1
,
: [ Shy-
Drager] (G90.3)
I95.2 ,
( ).
I95.8
I95.9 ,
I97
,
: (81.1)
I97.0
I97.1
595
I97.2
I97.8 -
,
I97.9 -
,
I98*
,
: ,
, -
I98.0* -
- :
(52.0)
, (50.5)
I98.1* -
,
-:
, Chagas ( -
) (57.2)
[] (67.2)
I98.2* , -
:
(7071, 74.)
(B65)
I98.8* -
,
I99 -
596
X
(J00J99)
: -
, -
- (-
J40).
: ,
(P00P96)
(A00B99)
,
(O00O99)
,
(Q00Q99)
, -
(E00E90)
, -
(S00T98)
(C00D48)
, ,
, -
(R00R99)
:
J00J06
J10J18
J20J22
J30J39
J40J49
J60J70 ,
J80J84 , -
J85J86 -
J90J94
J95J99
597
:
J17* ,
J91* ,
J99* , -
(J00J06)
: ,
(J44.1)
J00 []
()
:
:
: (J31.1)
:
(J02.9)
(J02.)
(J31.2)
:
(J31.0)
(J30.1J30.4)
(J31.0)
(J30.0)
598
J01
:
(-)(-)
() ()
(9597).
: , (J32.)
J01.0
J01.1
J01.2
J01.3
J01.4
J01.8
, , -
J01.9 ,
J02
:
: :
(J36)
(J39.1)
(J39.0)
(J06.0)
(J31.2)
J02.0
: (A38)
599
J02.8 ,
(9597).
: ( ):
(27.)
:
(J10.1)
(J11.1)
(08.5)
herpes simplex
(B00.2)
J02.9 ,
():
()
J03 ()
: (J36)
:
(J02.9)
(J02.)
(J02.0)
J03.0
J03.8 ,
(9597).
: ,
herpes simplex (B00.2)
600
J03.9 ,
():
J04
(9597).
: [] -
(J05.)
() (J38.5)
J04.0
():
: (J37.0)
, :
(J10.1)
(J11.1)
J04.1
():
: (J42)
J04.2
() ()
: (J37.1)
601
J05 []
(9597).
J05.0 []
J05.1
J06
: (J22)
:
(J10.1)
(J11.1)
J06.0
J06.8 -
J06.9 , -
:
,
602
(J10J18)
J10 ,
: Haemophilus influenzae
[H. influenzae]:
(49.2)
(G00.0)
(J14)
J10.0 ,
(),
J10.1 ,
:
J10.8 ,
,
:
()
J11 ,
: -
: Haemophilus influenzae
[H.influenzae]:
(49.2)
(G00.0)
(J14)
603
J11.0 ,
(),
J11.1 , -
:
e
J11.8 ,
,
:
()
J12 ,
: , ,
: (35.0)
:
:
(J69.0)
:
(74.0)
(29.0)
(89.0)
(24.9)
(J69.)
(23.0)
(J10.0, J11.0)
(J84.9)
(J69.1)
J12.0
604
J12.1 , -
J12.2 ,
J12.8
J12.9 ,
J13 , Streptococcus
pneumoniae
, S. pneumoniae
: , S. pneumo-
niae (23.6)
,
(J15.3J15.4)
J14 , Haemophilus
influenzae
, . influenzae
: , . influen-
zae (23.6)
J15 ,
: , -
, S. pneumoniae H. influen-
zae
: , (J16.0)
(23.)
(48.1)
J15.0 , Klebsiella pneumoniae
J15.1 , Pseudomonas
J15.2 ,
J15.3 ,
J15.4 ,
: , :
(J15.3)
Streptococcus pneumoniae (J13)
605
J16 ,
,
: (70)
(59)
:
(J18.9)
(23.)
J16.0 ,
J16.8 , -
J17* ,
J17.0* , -
:
(A42.0)
(A22.1)
(A54.8)
(A43.0)
(A02.2)
(A21.2)
(A01.0)
(37.)
606
J17.1* ,
:
(B25.0)
(05.2)
(B06.8)
(01.2)
J17.2*
:
(B44.0B44.1)
(B37.1)
(B38.0B38.2)
(B39.)
J17.3*
:
a (B77.8)
a (B65.)
a (B58.3)
J17.8* , -
():
(A70)
- (A78)
(I00)
, (69.8)
607
J18
: (J85.1)
-
(J70.2J70.4)
:
:
(J69.0)
:
(74.0)
(29.0)
(89.0)
(24.9)
(J69.)
(23.9)
(J84.9)
(J69.1)
, (J67
J70)
J18.0 ,
: (J21.)
J18.1 ,
J18.2 ,
J18.8
J18.9 ,
608
(J20J22)
: (-):
(J44.1)
(J44.0)
J20
: :
15
():
,
: :
15 (J40)
(J45.0)
:
(J42)
- (J41.1)
(J44.)
(J41.0)
:
(J40)
(J42)
(J44.)
J20.0 , Mycoplasma pneumo-
niae
J20.1 , Haemophilus influen-
zae
J20.2 ,
609
J20.3 , -
J20.4 ,
J20.5 , --
J20.6 ,
J20.7 ,
J20.8 ,
J20.9 ,
J21
:
J21.0 , --
J21.8 ,
J21.9 ,
()
J22
,
( ) ( -
)
:
() (J06.9)
610
(J30J39)
J30
:
: (J45.0)
(J31.0)
J30.0
J30.1 ,
,
J30.2
J30.3
J30.4 ,
J31 ,
J31.0
():
: :
(J30.1J30.4)
(J30.0)
611
J31.1
: , (J00)
J31.2
():
: , (J02.9)
J32
:
()()
(9597).
: (J01.)
J32.0
()
J32.1
J32.2
J32.3
J32.4
J32.8
(), ,
J32.9 ,
()
612
J33
: (D14.0)
J33.0
:
J33.1
Woakes
J33.8
:
J33.9 ,
J34
: (I86.8)
J34.0 ,
()
J34.1
J34.2
()(-
)
J34.3
J34.8
613
J35
J35.0
: :
(J03.9)
(J03.)
J35.1
J35.2
J35.3 -
J35.8 -
( )
J35.9 , -
()
J36
(9597).
: (J39.0)
:
(J03.9)
(J03.)
(J35.0)
614
J37
(9597).
J37.0
:
()
: :
(J04.0)
(J04.0)
() (J05.0)
J37.1
, ()
,
: :
(J04.2)
(J04.2)
:
(J04.1)
(J04.1)
(J42)
J38
,
: (Q31.4)
:
() (J05.0)
(J04.0)
(J95.5)
(R06.1)
J38.0
J38.1
: (D14.1)
615
J38.2
() () ()
J38.3
(-) (-)
J38.4
:
: :
[] (J05.0)
(J04.0)
J38.5
()
J38.6
J38.7
616
J39
: (J22)
(J06.9)
,
, ,
(J68.2)
J39.0
: (J36)
J39.1
J39.2
: :
(J31.2)
(J02.9)
J39.3
,
J39.8 -
J39.9 ,
617
(J40J47)
: (84.)
J40 ,
: , ,
15
J20..
:
: :
(J45.0)
(J45.9)
()
(J68.0)
J41 -
: :
(J42)
(J44.)
J41.0
J41.1 -
J41.8 , - -
618
J42 ,
:
: :
(J44.)
:
- (J41.)
(J44.)
(J44.)
(J44.9)
J43
: :
(J98.3)
, ,
(J68.4)
(J98.2)
(25.0)
(J98.2)
() (81.8)
(79.7)
() (J44.)
()
(J44.)
J43.0 MacLeod
(-):
J43.1 e
J43.2
J43.8
619
J43.9 ,
( ) ():
J44
: (-):
:
()
:
:
: (J45.)
(J45.9)
(J47)
:
:
(J42)
- (J41.)
(J42)
(J42)
(J43.)
,
(J60J70)
J44.0
-
: (J10J11)
J44.1 -
,
620
J44.8
:
()
J44.9 , -
:
J45
: (J46)
()
(J44.)
(J44.)
(J82)
,
(J60J70)
(J46)
J45.0
:
J45.1
J45.8
, J45.0 J45.1
J45.9 ,
621
J47
: (Q33.4)
() (15
16)
,
(J60J70)
: , J45.
J60
: (J65)
J61 ,
: (J92.0)
(J65)
J62 , ,
: ()
: (J65)
J62.0 ,
622
J62.8 , , -
J63 ,
: (J65)
J63.0 ( )
J63.1 ( )
J63.2
J63.3 ( )
J63.4
J63.5
J63.8 , -
J64 ,
: (J65)
J65 ,
, J60J64,
, 1516.
J66 , -
: (J67.1)
(J67.0)
, -
(J67.)
-
(J68.3)
J66.0
,
623
J66.1
J66.2
J66.8 ,
J67 ,
: ,
,
: ,
, , (J68.0)
J67.0 [ ]
,
J67.1 ( )
(-):
J67.2
J67.3
-
J67.4
, Aspergillus clavatus
J67.5
J67.6
, Cryptostroma corticale
624
J67.7
, , -
,
[ ]
J67.8 ,
J67.9 , -
()
J68 ,
, ,
-
( XX).
J68.0 , -
, ,
()
J68.1 , -
, ,
()
J68.2 , -
, , ,
J68.3 ,
, ,
625
J68.4 ,
, ,
() ()
,
()()
,
()
J68.8 , -
, ,
J68.9 ,
, , ,
J69 ,
-
( XX).
:
(24.)
J69.0 , -
( ):
( )
: Mendelson (J95.4)
J69.1 ,
J69.8 ,
,
626
J70 ,
-
( XX).
J70.0 ,
J70.1 ,
,
J70.2 ,
J70.3 ,
J70.4 , -
,
J70.8 , -
J70.9 ,
(J80J84)
J80
[]
627
J81
()
: (J18.2)
:
() (J68.1)
(J60J70)
(I50.1)
J82 ,
Loffler
()
: :
(44.)
(J70.2J70.4)
(5083)
-
(3036)
J84
: , -
(J70.2
J70.4)
(J98.2)
,
(J60J70)
, -
HIV- (22.1)
J84.0 a -a
a a
a
628
J84.1 -
()
Hammn-Rich
: ():
-
, , (J68.4)
(J70.1)
J84.8 -
J84.9 ,
(J85J86)
J85
J85.0
J85.1
: , -
(J10J16)
J85.2
J85.3
629
J86
: :
(9597).
: (1516)
J86.0
J86.9
(J90J94)
J90 ,
: () (J94.0)
(R09.1)
(1516)
J91* ,
J92
:
J92.0
J92.9
630
J93
: :
(25.1)
(S27.0)
( ) (15
16)
(J86.)
J93.0
J93.1
J93.8
J93.9 ,
J94
: (R09.1)
:
(S27.2)
(S27.1)
(
) (1516)
J94.0
J94.1
J94.2
J94.8
J94.9 ,
631
(J95J99)
J95
,
: () (81.8)
,
(J70.0J70.1)
J95.0
J95.1
J95.2 -
J95.3 ,
J95.4 Mendelson
: :
(74.0)
(29.0)
(89.0)
J95.5
J95.8
J95.9 -
,
632
J96 ,
: - (R09.2)
(J95.)
(R09.2)
[] :
(J80)
(22.0)
J96.0
J96.1
J96.9 ,
J98
: :
(R06.8)
(28.4)
(G47.3)
(28.3)
J98.0 ,
(-):
J98.1
: ():
(P28.0P28.1)
( ) (15
16)
633
J98.2
: :
(J43.9)
(25.0)
() (81.8)
(79.7)
J98.3
J98.4
()
J98.5 , -
: (J85.3)
J98.6
: , (Q79)
(44.)
(Q79.0)
J98.8
J98.9 ,
()
634
J99* ,
J99.0* (M05.1)
J99.1* -
:
(33.033.1)
(M33.2)
Sjogren (M35.0)
(-):
(M32.1)
(M34.8)
Wegener (M31.3)
J99.8* , -
:
(A06.5)
(M45)
(D89.1)
(B42.0)
(A52.7)
635
I
(0093)
: ,
(0096)
(0099)
,
(O00O99)
,
(O00O99)
, -
(0090)
, -
(S00T98)
(C00D48)
, ,
, -
(R00R99)
:
0014 ,
2031 ,
3538
4046
5052
5563
6567
7077
8087 , -
9093
636
:
23* ,
67* , -
77* ,
87* , -
,
93* ,
,
(0014)
00
: (01.)
00.0
00.1
[ ]
637
00.2
[]
: Karabelli,
-
00.3
: (03.6)
00.4
() () (-
)
Turner
: Hutchinson
(50.5)
(00.3)
00.5 ,
638
00.6
(
)
( ,
)
:
()
[]
00.7
00.8
00.9 ,
01
: -
(07.3)
01.0
, .
01.1
, .
02
02.0
[ ]
02.1
02.2
02.3
639
02.4
02.8
02.9 ,
03
: (F45.8)
(02.)
(F45.8)
03.0
:
03.1
:
03.2
:
:
03.3
()
640
03.4
03.5
03.6 []
:
() :
:
03.7
: [] (03.6)
03.8
, -
, -
( XX).
03.9 ,
641
04
04.0
:
:
()()
04.1
04.2
:
04.3 -
04.4 ,
04.5
04.6
[]
04.7
[]
642
04.8
:
()
: (09.0)
04.9 -
05
05.0
:
(69.1)
,
herpes simplex (B00.2)
05.1
():
05.2
: (04.4)
(04.7)
(04.6)
05.3
:
643
05.4
05.5
05.6 ,
06
:
(08.2)
:
(05.1)
(05.0)
(05.1)
06.0
()()(-
)()
06.1
06.2
,
-
( XX).
06.8
06.9
,
644
07
[ ]
:
(Q67.4)
(10.8)
07.0
, :
( ) ( )
( ) ( )
: (22.0)
Robin (Q87.0)
07.1
( ) ( )
( ) ( )
07.2
() ()
() ()
:
645
07.3
,
-
: -
(01.)
07.4 ,
07.5
, :
,
: (F45.8)
(F45.8)
07.6
, , Costen
-
: :
(S03.0) -
(S03.4)
07.8
07.9 ,
08
08.0 ,
08.1 , , -
646
08.2
08.3 []
08.8
08.9 ,
09 ,
:
-
: (04.8)
09.0 ,
:
09.1 ()
:
647
09.2
:
: (10.0)
Stafne (10.0)
09.8 , -
Epstein
09.9 ,
10
10.0
Stafne
:
10.1 ,
: (06.8)
10.2
()
()()()
, -
,
( XX).
648
10.3
10.8
:
10.9 ,
11
11.0
11.1
K11.2
: (26.)
[Heetfordt] (D86.8)
11.3
11.4
: (Q38.4)
11.5
11.6
:
11.7
: (R68.2)
649
11.8
-
Mikulicz
: Sjogren (35.0)
11.9 ,
12
: cancrum oris (69.0)
(13.0)
(69.0)
,
herpes simplex (B00.2)
(69.0)
12.0
()()
Bednar
12.1
:
650
12.2
: ():
(04.604.7)
(05.2)
(J36)
(11.3)
(14.0)
13
:
: -
(0506)
(09.)
(14.)
(12.)
13.0
:
: (53.0)
, (L55L59)
, :
(37.8)
(53.0)
K13.1
651
13.2 ,
,
,
: (13.3)
13.3
13.4 -
13.5
13.6 ,
: ,
( )
(K06.2)
13.7 -
14
:
(K13.2)
(13.3)
() (Q38.2)
(13.5)
652
14.0
()
: (14.4)
14.1
14.2
14.3
[ ]
papillae foliate
Lingua villosa nigra
14.4
14.5
: (Q38.3)
14.6
14.8
14.9 ,
653
,
(2031)
: (44.)
20
:
-
( XX).
: (22.1)
- (21.0)
(21.0)
21
21.0
-
21.9
22
: (I85.)
22.0
: (Q39.5)
654
22.1
:
:
-
( XX).
22.2
: -
(Q39.3)
22.3
: (
) (S27.8)
22.4
: (22.0)
22.5 ,
,
: (Q39.6)
22.6 Mallory-Weiss
22.8
22.9 ,
655
23*
,
23.0* (A18.8)
23.1* Chagas (57.3)
23.8* ,
2528 -
:
.0
.1
.2
.3
.4 ,
.5 ,
.6 ,
.7 ,
.9 , -
25
[. - ]
: ()
() :
, , -
( XX).
: (29.0)
(27.)
656
26
[. - ]
: ()
() ():
, , -
( XX).
: (27.)
27
[. - ]
:
: (78.8)
28
[. - ]
: () :
: (63.3)
29
:
(52.8)
Zollinger-Ellison (16.8)
29.0
()
: () (25.)
657
29.1
29.2
29.3
29.4
29.5 ,
:
29.6
Mntrier
29.7 ,
29.8
29.9 ,
30
:
(F45.3)
(F45.3)
(F45.3)
(R12)
31
:
: (57.0
57.1)
(92.092.2)
31.0
658
31.1
: (Q40.0)
31.2 -
: ,
(Q40.2)
-
(31.8)
31.3 ,
: :
(Q40.0)
(F45.3)
(F45.3)
31.4
: (Q40.2)
31.5
,
:
(Q41.0)
31.6
31.7
: (D13.1)
31.8 -
31.9 , -
659
(3538)
35
35.0
() :
()
35.1
35.9 ,
:
36
:
37 ,
38
38.0
38.1
38.2
38.3
38.8
38.9 ,
660
(4046)
:
.
: :
[ ]
40
:
:
()
40.0
40.1
40.2
40.3
():
40.4
661
40.9
()
41
41.0
41.1
41.2
41.3
():
41.4
41.9
()
42
:
: (Q79.2)
K42.0
:
662
42.1 a
42.9
43
: :
43.0
:
43.1
43.9
44
: () ( )
: :
(Q79.0)
(Q40.1)
44.0 -
:
44.1
663
44.9 -
45
: :
,
45.0 -
, 45:
45.1
, 45, -
45.8 -
46 ,
:
:
: (N81.5)
664
46.0
, 46:
46.1
, 46, -
46.9 -
(5052)
:
: (58.)
(59.3)
50 Crohn [ ]
: o
: (51.)
50.0 Crohn
Crohn [ ] :
:
: Crohn (50.8)
665
50.1 Crohn
:
Crohn [ ] :
: Crohn (50.8)
50.8 Crohn
Crohn
50.9 Crohn,
Crohn
51
51.0 ()
51.1 ()
51.2 ()
51.3 ()
51.4
51.5
51.8
51.9 ,
52
52.0
52.1
( XX).
666
52.2
52.8
52.9 ,
, ,
: , , , :
(-) (09)
(-) ,
(09)
(59.1)
()
(78.3)
(F45.3)
(5563)
55
: -
(77)
55.0
(-):
(-), ()():
667
55.1
:
:
55.2
55.8
55.9 ,
:
56
:
(Q41Q42)
(K55.1)
(84.1)
,
76.
(K31.5)
(91.3)
(62.4)
(4046)
668
56.0
:
: , (56.3)
(56.7)
(56.6)
56.1
:
: (38.8)
56.2
56.3 ,
56.4
:
56.5 []
[] -
56.6
56.7 ,
669
57
:
()()
: (Q43.8)
(38.2)
Meckel (Q43.0)
57.0 -
:
(57.4)
57.1
: ,
(57.5)
57.2 -
:
(57.4)
57.3
:
(57.5)
57.4 -
57.5
57.8 , -
670
57.9 ,
58
:
58.0
58.9
59
: (R19.4)
(31.)
(90.)
(F45.3)
59.0
59.1
59.2 ,
59.3 ,
( XX).
: ():
Chagas (57.3)
() (Q43.1)
Hirschsprung (Q43.1)
59.4
59.8 -
59.9 ,
671
60
: (61.)
60.0
60.1
60.2 ,
60.3
60.4
: :
(N82.3)
(N32.1)
60.5
61
:
61.0
: (61.4)
61.1
: (61.3)
61.2
61.3
fossa ischiorectalis
61.4
62
:
:
(91.4)
(R15)
(I84.)
(51.2)
672
62.0
62.1
: (D12.8)
62.2
62.3
62.4
()
62.5
: (54.2)
62.6
:
: (60.)
(51.)
62.7
62.8
()
62.9 ,
63
63.0
: :
(61.)
(35.1)
(57.)
63.1 ()
: () :
(35.0)
(26.)
(57.)
673
63.2
: ():
(60.)
(38.3)
(31.6)
(N82.2N82.4)
(N32.1)
63.3
: ():
(62.6)
(26.)
(28.)
(28.)
(28.)
, (27.)
(K51)
63.4
63.5
: (D12.6)
(D12.6)
63.8
63.9 ,
674
(6567)
65
: :
(81.6)
(85.0)
(81.6)
-
(81.6)
(78.078.1)
(N73.3N73.5)
(85.0)
(O85)
:
, -
(O00O07, O08.0)
(35.)
(57.)
65.0
():
():
(9597).
675
65.8
:
, :
65.9 ,
66
: (R18)
66.0
():
()
: [] ():
(N73.6)
(56.5)
66.1
: (S36.8)
66.8
66.9 ,
67*
,
67.0* (A74.8)
676
67.1* (A54.8)
67.2* (A52.7)
67.3* (A18.3)
67.8* -
,
(7077)
: (83.1)
(R17)
Reye (G93.7)
(1519)
Wilson (83.0)
70
70.0
70.1
70.2
70.3
70.4
:
70.9 ,
677
71
: :
()
()
( XX).
: (70.)
Budd-Chiari (I82.0)
71.0
c
71.1
()(),
71.2 ,
71.3 ,
71.4 ,
71.5 ,
, -
71.6
,
71.7
678
71.8
:
71.9 ,
72 ,
: :
:
,
() -
:
(70.4)
, :
, -
(O00O07, O08.8)
,
(O26.6)
(55
59)
(1519)
(71.1)
72.0
72.1
72.9 ,
679
73 ,
: ():
(70.1)
(71.)
, (75.3)
, (75.2)
(1519)
73.0 ,
73.1 ,
73.2 , -
,
73.8 , -
73.9 ,
74
: (70.2)
(76.1)
( ):
(70.3)
(78.8)
(71.7)
74.0
74.1
74.2
74.3
74.4
74.5 ,
680
74.6
( ):
75
: ,
(73.)
:
(72.0)
(1519)
(71.)
75.0
:
: (06.4)
(83.0)
(75.1)
75.1
: (75.0)
75.2
75.3 ,
75.4
75.8
681
75.9 ,
76
: (70.)
(85.)
()
(Q44.6)
(I82.0)
(R16.0)
(I81)
(71.)
76.0 , -
76.1
:
( )
76.2
: -
(72.)
76.3
76.4
76.5
: Budd-Chiri (I82.0)
76.6
76.7
: (O90.4)
76.8
682
76.9 ,
77*
,
77.0* -
,
():
(B25.1)
herpes simplex (B00.8)
(B58.1)
(B65.)
(B65.)
(A52.7)
77.8* , -
:
(J63.2)
(D86.8)
,
(8087)
80 []
80.0
, 80.2, -
80.1
, 80.2, -
()
683
80.2
()
:
80.3
, 80.5, -
80.4
, 80.5, -
( )
80.5 -
:
:
()
80.8
81
: (80.)
81.0
:
()
684
81.1
81.8
81.9 ,
82
: -
(R93.2)
(91.5)
82.0
: (80.)
82.1
82.2
82.3
82.4
82.8
82.9 ,
685
83
: , :
(8182)
(8182)
(91.5)
83.0
:
: (75.0)
(80.380.4)
(74.3)
83.1
: (80.)
83.2
83.3
K83.4 Oddi
83.5
83.8
83.9 ,
686
85
:
:
()
86
: (84.)
-
(D13.7)
(90.3)
86.0
86.1
:
86.2
86.3
86.8
:
:
687
86.9 ,
87* ,
,
87.0* -
,
87.1* ,
(B25.2)
(B26.3)
(9093)
90
: -
(91.2)
90.0
90.1
90.2 , -
: :
(Q43.8)
(91.2)
90.3
688
90.4 , ,
, :
: (90.0)
(73.)
90.8
Whipple (14.8*)
90.9 ,
91
,
: (28.)
:
(52.0)
(52.0)
(62.7)
91.0 -
91.1
:
91.2 -
,
: :
(83.2)
(81.3)
91.3
689
91.4
91.5
91.8
,
91.9 -
,
92
:
(54.054.3)
92.0
92.1
92.2 ,
:
: (29.0)
(62.5)
(2528)
92.8 -
92.9 ,
93*
,
93.0* ,
(18.3)
: (67.3*)
93.1* Chagas (B57.3)
93.8* -
,
690
XII
(L00L99)
: ,
(P00P96)
(00B99)
,
(0099)
,
(Q00Q99)
, -
(E00E90)
, -
(S00T98)
(I89.8)
(00D48)
, ,
, -
(R00R99)
(30
36)
:
L00L08
L10L14
L20L30
L40L45
L50L54
L55L59 , -
L60L75
L80L99
:
L14* ,
L45* ,
691
L54* ,
L62* ,
L86* ,
L99* -
,
(L00L08)
-
(B95B97).
: (H00.0)
(L30.3)
, I,
:
(A46)
(A26.)
- [herpes simplex] (B00.)
(A60.)
(B08.1)
(B35B49)
, (B85B89)
(B07)
()():
(M79.3)
(L93.2)
(M54.0)
[Weber-Christian] (M35.6)
( ):
(K13.0)
(B37.)
(E53.0)
(L98.0)
(B02.)
692
L00
Ritter
: [Lyell]
(L51.2)
L01
: (L40.1)
(L00)
L01.0 [ ] [ ]
Bockhart
L01.1
L02 ,
:
: (K61.)
():
(N76.4)
(N48.2, N49.)
L02.0 ,
: (H60.0)
(H00.0)
[ ] (L02.8)
:
(H04.0)
(H04.3)
(K12.2)
(J34.0)
(H05.0)
(K12.2)
L02.1 ,
693
L02.2 ,
[ ]
: (N61)
(L02.4)
(P38)
L02.3 , -
: (L05.0)
L02.4 , -
L02.8 ,
[ ]
L02.9 , -
694
L03
:
: :
(K61.)
(H60.1)
:
(N76.4)
(N48.2, N49.)
(H00.0)
(H04.3)
(K12.2)
(J34.0)
[Wells] (L98.3)
[Sweet]
(L98.2)
()() (I89.1)
L03.0
L03.1
L03.2
L03.3
[ ]
: (P38)
L03.8
[ ]
695
L03.9 ,
L04
: ()
()
: (R59.)
,
[HIV], -
(B23.1)
:
(I88.9)
, -
(I88.1)
, (I88.0)
L04.0 ,
L04.1
L04.2
L04.3
L04.8
L04.9 ,
L05
: (-)
(-)
L05.0
L05.9
696
L08
L08.0
:
: (L88)
L08.1
L08.8
L08.9 ,
(L10L14)
: [ Hailey-
Hailey] (Q82.8)
(L00)
[ Lyell]
(L51.2)
L10
: (L00)
L10.0
L10.1
L10.2
L10.3 (fogo selvagem)
L10.4
Senear-Usher
697
L10.5 ,
( ).
L10.8
L10.9 ,
L11
L11.0
: () [Darier-
White] (Q82.8)
L11.1 [Grover]
L11.8
L11.9 ,
L12
: (O26.4)
(L40.1)
L12.0
L12.1
L12.2
L12.3
: () (Q81.)
L12.8
L12.9 ,
L13
L13.0
Duhring
698
L13.1
Sneddon-Wilkinson
L13.8
L13.9 ,
L14*
,
(L20L30)
: -
.
: ( ) (D71)
:
(L85.3)
(L98.1)
(L88)
(L13.0)
(L71.0)
(I83.1I83.2)
,
(L55L59)
L20
: (L28.0)
L20.0 Besnier
L20.8
:
,
()()
()
:
699
L20.9 ,
L21
: (L30.3)
L21.0
L21.1
L21.8
L21.9 ,
L22
:
L23
:
: (T78.4)
()():
(L30.9)
(L25.9)
(L22)
, (L27.)
(H01.1)
(L24.)
(L71.0)
(H60.5)
, -
(L55L59)
L23.0
L23.1 -
700
L23.2
L23.3
( ).
: (T88.7)
(L27.0L27.1)
L23.4
L23.5
L23.6 -
: ,
(L27.2)
L23.7 , -
L23.8
L23.9
701
L24
:
: (T78.4)
()():
(L30.9)
(L23.)
(L25.9)
(L22)
(L27.)
(H01.1)
(L71.0)
(H60.5)
, -
(L55L59)
L24.0
L24.1 -
L24.2
:
L24.3
L24.4
( ).
: (T88.7)
,
(L27.0L27.1)
702
L24.5
L24.6 -
: ,
(L27.2)
L24.7 , -
L24.8
L24.9
L25 ,
: ,
: (T78.4)
()():
(L30.9)
(L23.)
(L27.)
(H01.1)
(L24.)
(L71.0)
(H60.5)
, -
(L55L59)
L25.0 , -
703
L25.1
,
( ).
: (T88.7)
,
(L27.0L27.1)
L25.2 ,
L25.3 ,
L25.4
,
: (L27.2)
L25.5 ,
,
L25.8 ,
L25.9 -
(-):
()
()
L26
Hebra
: Ritter (L00)
704
L27
: (-):
(T88.7)
, -
(T78.0T78.1)
(T78.4)
(L23L25)
:
(L56.1)
(L56.0)
(L50.)
L27.0 -
( ).
L27.1 -
( ).
L27.2
:
(L23.6, L24.6, L25.4)
L27.8 ,
L27.9 ,
L28
L28.0
L28.1
705
L28.2
:
Hebra
mitis
L29
: (L98.1)
(F45.8)
L29.0
L29.1
L29.2
L29.3 ,
L29.8
L29.9 ,
L30
: :
(L23L25)
(L85.3)
(L41.3)
(I83.1I83.2)
L30.0
L30.1 []
L30.2
L30.3
L30.4
706
L30.5
L30.8
L30.9 ,
(L40L45)
L40
L40.0
L40.1
Von Zumbusch
L40.2
L40.3
L40.4
L40.5 (M07.0M07.3*, M09.0*)
L40.8
L40.9 ,
L41
: (L94.5)
L41.0 Pityriasis lichenoides et varioliformis acuta
Mucha-Habermann
L41.1 Pityriasis lichenoides chronica
L41.2
707
L41.3
L41.4
L41.5
L41.8
L41.9 ,
L42
L43
: (L66.1)
L43.0
L43.1
L43.2
( ).
L43.3 ()
L43.8
L43.9 ,
L44
L44.0
L44.1
L44.2
L44.3
L44.4 [Gianot-
ti-Crosti]
L44.8
708
L44.9 ,
L45*
,
(L50L54)
: (A69.2)
(L71.)
L50
: (L23.)
(T78.3)
(E88.0)
Quincke (T78.3)
:
(T78.3)
(P83.8)
(L28.2)
(Q82.2)
(T80.6)
(L56.3)
L50.0
L50.1
L50.2
L50.3
L50.4
L50.5
L50.6
709
L50.8
:
L50.9 ,
L53
: :
(L59.0)
(L23
L25)
(L30.4)
L53.0
( ).
: (P83.1)
L53.1 Erythema annulare centrifugum
L53.2 Erythema marginatum
L53.3
L53.8
710
L53.9 ,
L54* ,
L54.0* Erythema marginatum (I00)
L54.8* ,
,
(L55L59)
L55
L55.0
L55.1
L55.2
L55.8
L55.9 ,
L56 ,
L56.0
( ).
L56.1
( ).
711
L57 ,
L57.0
:
L57.1
L57.2 Cutis rhomboidalis nuchae
L57.3 Civatte
L57.4
L57.5
L57.8 , -
L57.9 , -
,
712
L58
L58.0
L58.1
L58.9 ,
L59
,
L59.0 [dermatitis ab igne]
L59.8
,
L59.9 , -
,
(L60L75)
: (Q84.)
L60
: (R68.3)
(L03.0)
L60.0
L60.1
L60.2
L60.3
L60.4 Beau
L60.5
L60.8
L60.9 ,
713
L62* ,
L62.0* , -
(M89.4)
L62.8* , -
L63
L63.0 ()
L63.1
L63.2
L63.8
L63.9 ,
L64
:
L64.0 , -
( ).
L64.8
L64.9 ,
L65
, , -
( ).
: (F63.3)
L65.0
714
L65.1
L65.2
L65.8 -
L65.9 ,
L66
L66.0
L66.1
L66.2 ,
L66.3
L66.4 Folliculitis ulerythematosa reticulata
L66.8
L66.9 ,
L67
: (Q84.1)
(Q84.1)
(L65.0)
L67.0
L67.1
()
:
,
715
L67.8
L67.9 ,
L68
:
: (Q84.2)
(Q84.2)
L68.0
, , -
( ).
L68.1
, , -
( ).
L68.2
L68.3
L68.8
L68.9 ,
L70
: (L73.0)
L70.0
L70.1
L70.2
L70.3
L70.4
L70.5 Acn excorie des jeunes filles
L70.8
716
L70.9 ,
L71
L71.0
, , -
( ).
L71.1
L71.8
L71.9 ,
L72
L72.0
L72.1
L72.2
L72.8
L72.9 -
,
L73
L73.0
L73.1
L73.2
L73.8
L73.9 ,
717
L74
: (R61.)
L74.0
L74.1
L74.2
L74.3 ,
L74.4
L74.8
L74.9 ,
L75
: [] (L30.1)
(L73.2)
L75.0
L75.1
L75.2
Fox-Fordyce
L75.8
L75.9 ,
(L80L99)
L80
718
L81
: (Q82.5)
Peutz-Jeghers (Q85.8)
L81.0
L81.1
L81.2
L81.3
L81.4 , -
L81.5 ,
L81.6 ,
L81.7
L81.8
L81.9 ,
L82
Leser-Trelat
L84
Callus
Clavus
719
L85
: (L91.)
L85.0
: (Q80.)
L85.1 [-
]
:
(Q82.8)
L85.2 ( )
L85.3
L85.8 -
L85.9 ,
L86* ,
(E50.8)
L87
: () (L92.0)
L87.0 , -
[ Kyrle]
L87.1
L87.2
L87.8
L87.9 ,
720
L88
L89
: ()
(N86)
L90
L90.0 Lichen sclerosus et atrophicus
L90.1 Schweninger-Buzzi
L90.2 Jadassohn-Pellizzari
L90.3 Pasini-Pierini
L90.4
L90.5
()
,
: (L91.0)
(L91.0)
L90.6
L90.8
L90.9 ,
L91
L91.0
: (L73.0)
(L90.5)
721
L91.8
L91.9 ,
L92
: (L57.5)
L92.0 Granuloma annulare
granuloma annulare
L92.1 , -
: (E10E14)
L92.2 Granuloma faciale [ -
]
L92.3 -
L92.8 -
L92.9 -
,
L93
: :
(18.4)
(A18.4)
(M34.)
(M32.)
, , -
( ).
L93.0
L93.1
722
L93.2
:
L94
:
(M30M36)
L94.0 [morphea]
L94.1
En coup de sabre
L94.2
L94.3
L94.4 Gottron
L94.5
L94.6
L94.8 -
L94.9 -
,
723
L95 ,
: (L81.7)
Henoch(-Schn-
lein) (D69.0)
(M31.0)
()():
(M79.3)
(L93.2)
(M54.0)
(Weber-Christian) (M35.6)
(M30.0)
(M05.2)
(T80.6)
(L50.)
Wegener (M31.3)
L95.0
( )
L95.1 Erythema elevatum diutinum
L95.8
L95.9 ,
L97 ,
: (L89)
(R02)
(L00L08)
,
A00B99
(I83.0, I83.2)
L98
,
L98.0
L98.1
L98.2 [Sweet]
724
L98.3 [Wells]
L98.4 ,
: (L89)
(R02)
(L00L08)
, A00
B99
, (L97)
(I83.0, I83.2)
L98.5
: (K13.7)
(E03.9)
L98.6 -
: (E78.8)
L98.8
L98.9 ,
L99*
,
L99.0* (E85.)
L99.8* -
,
:
(A51.3)
(A51.3, A52.7)
725
XIII
(0099)
: ,
(0096)
(0099)
(T79.6)
,
(0099)
, -
(S00T98)
, -
(0090)
,
(Q00Q99)
, ,
, -
( R00R99)
(C00D48)
:
0025
0003
0514
1519
2025
3036
4054
4043
4549
5054
726
-
6079
6063
6568 -
7079
8094
8085
8690
9194
9599 - -
:
01* -
,
03* , -
07*
09* ,
14* ,
36* -
,
49* ,
63* , -
68*
,
73* ,
82* ,
90* ,
727
XIII -
, -
. -
-
, , -
(. ). ,
, -
, , -
744, 752 788.
0
1
2
3
4
5
6 []
[]
7
8
9
728
-
(0025)
, ( )
(00-03)
: , -
. -
:
) , -
;
) ,
: ,
,
, -
; ,
, -
,
.
00
[ .728]
00.0
00.1
00.2
00.8 ,
(95-96).
00.9 ,
729
01*
,
[ .728]
: (14.8*)
(03.*)
01.0* (39.8)
: (03.0*)
01.1* (18.0)
: (49.0*)
01.2* (69.2)
01.3* , -
:
[ Hansen] (30.)
(02.2)
(01.)
(54.4)
01.4* (06.8)
01.5* ,
:
nyong-nyong (92.1)
( 26.8)
01.6* (3549)
01.8* -
,
02
[ .728]
: Behet (M35.2)
(I00)
730
-
02.0
02.1
02.2
02.3 Reiter-Leroy
02.8
02.9 ,
03*
,
[ .728]
: -
,
(01.*)
03.0* (39.8)
: (01.0*)
03.1*
Clutton (50.5)
: Charcot -
(14.6*)
03.2* ,
:
, Yersinia enterocolitica (04.6)
(1519)
: (01.401.5*)
03.6* , -
(I33.0)
731
(0514)
05
[ .728]
: (I00)
:
(45)
(08.)
05.0 Felty
05.1
(J99.0*)
05.2
05.3
(-):
(I52.8*)
(I39.*)
(I41.8*)
(G73.7*)
(I32.8*)
(G63.6*)
05.8
05.9 ,
06
[ .728]
06.0
06.1 Still
: Still (08.2)
06.2
732
-
06.3
06.4
: (13.0)
06.8
06.9 ,
07*
[ .728]
: -
(09.*)
07.0* -
(L40.5)
07.1* (L40.5)
07.2* (L40.5)
07.3* (L40.5)
07.4* Crohn [ -
] (50.)
07.5* (51.)
07.6*
08 []
[ .728]
: , 16-
3
: Felty (05.0)
(33.0)
08.0
08.1
: (45)
733
08.2
Still
: Still -
(06.1)
08.3 ()
08.4
08.8
08.9 ,
09* []
,
[ .728]
: Whipple (14.8*)
09.0* (L40.5)
09.1* Crohn [-
] (50.)
09.2* (51.)
09.8* , -
10
[ .728]
10.0
[ ] (I43.8*)
10.1
10.2
( ).
734
-
10.3 , -
10.4
10.9 ,
11
[ .728]
11.0
11.1
11.2
11.8
11.9 ,
12
[ .728]
: (13.9)
(J38.7)
(1519)
12.0 [Jaccoud]
12.1 Kaschin-Beck
12.2 ()
12.3
12.4
12.5
: ():
(19.1)
(17.217.3)
(M16.4M16.5)
- (18.2
18.3)
(19.1)
735
12.8 ,
13
[ .728]
: (1519)
13.0 ,
13.1 ,
13.8
13.9 ,
14* ,
: ():
(36.236.3*)
(36.4*)
(36.1*)
(07.*)
(09.*)
(49.4*)
14.0* ,
:
- () (D57.)
Lesch-Nyhan (E79.1)
14.1* -
(21.)
14.2* (1014
.6)
: (14.6*)
736
-
14.3* (78.8)
14.4* (85.)
14.5*
,
:
(22.0)
(83.1)
(0003)
[] (05.)
14.6*
Charcot (52.1)
(1014 -
.6)
14.8* , -
:
:
(L51.)
(L52.)
(D86.8)
Whipple ( 90.8)
(1519)
: -
. -
.
: (47.)
15
:
:
(1619)
737
15.0 ()
15.1 Heberden ( )
15.2 Bouchard ( )
15.3
15.4 ()
15.8
15.9 ,
16 [
]
16.0 ,
16.1
:
16.2 ,
16.3
:
16.4 ,
16.5
:
16.6 ,
16.7
:
738
-
16.9 ,
17 [
]
17.0 ,
17.1
:
17.2 ,
17.3
:
17.4 ,
17.5
:
17.9 ,
18 -
18.0 -
,
18.1 --
- :
18.2 --
,
739
18.3 -
-
:
18.4 --
,
18.5 --
- :
18.9 - , -
19
[ .728]
: (47.)
(20.2)
(15.)
19.0
19.1
19.2
19.8
19.9 ,
740
-
(2025)
: (4054)
20
:
(Z89.)
(-):
(Q71.3, Q72.3)
(Q66., Q68Q70,
Q74.)
20.0 (-)
: (65.3)
[Dupuytren] (72.0)
(R68.3)
20.1 Hallux valgus ()
20.2 Hallux rigidus
20.3 ()
Hallux varus
20.4 -
()
20.5 (-) (-
)
20.6 (-) , -
741
21
[ .728]
: (Z89.)
-
(20.)
(-):
(Q71Q73)
(Q65Q66, Q68Q74)
coxa plana (91.2)
21.0 ,
: metatarsus valgus (Q66.6)
pes calcaneovalgus (Q66.4)
21.1 ,
: metatarsus varus (Q66.2)
tibia vara (M92.5)
M21.2
21.3 [pes eqiinus] (-
)
21.4 [pes planus] ()
: (Q66.5)
21.5 , ,
:
(Q66.8)
21.6 -
:
(21.1M20.6)
21.7 ()
21.8 -
21.9 ,
742
-
22 ()
: (S83.0)
22.0
22.1
22.2
22.3
22.4
22.8
22.9 ,
743
23
, -
, -
23.; -
. 728.
0
1
2
3
4
5
6
7
9
: (24.6)
(21.)
(22.)
-
(S80S89)
(24.4)
(22.022.1)
(93.2)
23.0
23.1 ()
23.2
744
-
23.3
23.4
23.5
23.6 (-) -
23.8
23.9 , -
24
[ .728]
: (23.8)
(67.4)
(07.6)
-
24.0
: (23.4)
24.1
: (83.5)
(11.111.2)
(23.)
(70.2)
745
24.2
-
()
: (23.523.8)
(35.7)
24.3 , -
: :
-
- (Q65 -
Q79)
-
(24.4)
24.4
: (22.022.1)
(43.3
43.5)
24.5
: (20
21)
Dupuytren (72.0)
(67.1)
24.6
: (43.2)
(25.6)
24.7
24.8 , -
24.9 ,
746
-
25 ,
[ .728]
: (R26.)
:
(71.4)
(75.3)
(65.2)
,
2021
(R26.2)
25.0
: -
25.1
25.2
25.3
: :
(24.2)
(96.8)
25.4
: (66.6)
25.5
25.6 ,
25.7
25.8
25.9 ,
747
(3036)
: :
() :
:
( -
)
30
30.0
30.1 [Churg-
Strauss]
30.2
30.3 -- [Kawasaki]
30.8 ,
-
31
31.0
Goodpasture
31.1
31.2
748
-
31.3 Wegener
31.4 [Takayasu]
31.5 -
31.6
31.8
31.9 ,
32 lupus erythematodes
: lupus erythematodes () () (L93.0)
32.0 lupus erythematodes
( ).
32.1 lupus erythematodes
lupus erythematodes :
(J99.1*)
(N08.5* , N16.4*)
Libman-Sacks (I39.*)
lupus erythematodes (I32.8*)
32.8 lupus erythematodes
32.9 lupus erythematodes,
33
33.0
33.1
33.2
33.9 ,
749
34
:
: :
(L94.0)
(83.8)
34.0
34.1 CR(E)ST
, ,
,
34.2 ,
-
( ).
34.8
:
(J99.1*)
(G73.7*)
34.9 ,
35
: (L87.1)
35.0 Sjgren
Sjgren :
(J99.1*)
(19.3*)
(N16.4*)
(G73.7*)
35.1
: - (30.8)
35.2 Behet
750
-
35.3
:
(31.5)
35.4 ()
35.5
35.6 [Weber-Christian]
: :
(79.3)
(L93.2)
35.7
: (24.2)
EhlersDanlos (Q79.6)
35.8 -
35.9 ,
()
()
36*
,
: , -
(14.*)
36.0* () (00
D48)
36.1* (00D48)
:
(9195)
(90.0)
(96.1)
36.2* (D66D68)
751
36.3* (D50
D76)
: Schnlein-Henoch
(36.4*)
36.4* ,
Schnlein-Henoch (D69.0)
36.8*
,
:
(D80.)
(70.2)
(4054)
, -
-
50 51; . 728.
0
1 --
2
3
4
5
6
7
8
9
752
-
(4043)
40
[ .752]
: (41.)
:
(Q76.4)
(96.)
40.0
: (42.)
40.1
40.2
40.3
40.4
:
40.5 ,
41
[ .752]
:
: :
(Q67.5)
(Q76.3)
(Q67.5)
(96.)
,
(I27.1)
41.0
753
41.1
41.2
41.3
41.4
, ,
Friedreich, -
41.5
41.8
41.9 ,
42
[ .752]
42.0
Calve
Scheuermann-Mau
: (40.0)
42.1
42.9 ,
43
[ .752]
:
(Q76.2)
(Q76.3Q76.4)
Klippel-Feil (Q76.1)
(Q76.4)
(Q76.4)
spina bifida occulta (Q76.0)
:
Paget ( )(88.)
(8081)
754
-
43.0
43.1
43.2
: (Z98.1)
(96.0)
(45)
43.3 - -
43.4 - -
43.5
: , (99.)
43.6 [torticollis]
: :
() (Q68.0)
(15.2)
-
(F45.8)
(G24.3)
43.8
: (40.)
(41.)
43.9 ,
755
(4549)
45
[ .752]
: Reiter (02.3)
() (08.1)
Behet (M35.2)
46
[ .752]
46.0
46.1 ,
46.2
46.3 ()
(9597).
46.4 ,
46.5
46.8
46.9 ,
47
[ .752]
:
47.0 -
(G99.2*)
756
-
47.1
, -
(G99.2*)
: (43.3
43.5)
47.2
47.8
()
-
47.9 ,
48
[ .752]
48.0
48.1 [Forestier]
48.2
48.3
48.4
[]
48.5 , -
: -
(80.)
-
48.8
48.9 ,
757
49* ,
[ .752]
:
(07.*, 09.*)
49.0* (18.0)
Pott
49.1* (23.)
49.2* (0104)
49.3* -
,
: tabes dorsa-
lis (49.4*)
49.4*
:
(G95.0)
tabes dorsalis (A52.1)
49.5* , -
(79.5)
49.8* ,
758
-
(5054)
: (46.4)
-
50
:
50.0 -
(G99.2*)
50.1 -
: (54.1)
50.2 -
50.3 -
50.8
50.9 -
,
759
51
:
,
51.0 -
-
(G99.2*)
51.1 -
-
,
: (54.1)
51.2
,
51.3
51.4 Schmorl
51.8
51.9 ,
53 ,
[ .752]
53.0
53.1
:
(50.)
[ -
] (G54.0)
760
-
53.2
53.3 ,
Coccygodinia
53.8
53.9 ,
54
[ .752]
: (F45.4)
54.0 , -
: :
(79.3)
(L93.2)
[Weber-Christian] (35.6)
54.1
:
: (79.2)
:
-
(50.1)
-
(51.1)
(47.2)
54.2
: -
(50.)
761
54.3
: (G57.0)
:
-
(51.1)
(54.4)
54.4
: -
(51.1)
54.5
: :
-
(51.2)
(54.4)
54.6
:
(51.)
54.8
54.9 ,
762
-
(6079)
(6063)
: (33.)
(G71G72)
:
(85.)
lupus erythematodes (32.)
(30.0)
(05.3)
(34.)
Sjgren (35.0)
60
[ .728]
60.0
(9597).
60.1
60.2 , -
: -
(L92.3)
60.8
60.9 ,
763
61
[ .728]
61.0
61.1
61.2 -
, -
61.3 , -
,
61.4
: (65.2)
(75.3)
61.5
61.9 , -
62
[ .728]
: (R25.2)
(79.1)
:
(G72.1)
(G72.0)
(G25.8)
62.0
62.1 ()
: (66.)
-
764
-
62.2
: Volkmann (79.6)
(79.6)
(79.6)
62.3 ()
62.4
: (24.5)
62.5 ,
,
62.6
:
62.8
62.9 ,
63* ,
: :
(G73.5*)
(G73.6*)
63.0* , -
:
[ Hansen] (30.)
(51.4, 52.7)
63.1* ,
:
(69.8)
(58.8)
(75)
[] (65.)
765
63.2 * , -
(3549)
63.3* (D86.8)
63.8* , -
(6568)
65
[ .728]
:
(70.0)
-
-
, -
, (70.)
65.0
(9596)
65.1 ()
65.2
: (75.3)
(7577)
65.3
65.4 [de
Quervain]
65.8
766
-
65.9 ,
66
[ .728]
: , -
,
:
-
(75.1)
66.0
66.1
: (66.0)
66.2
66.3
66.4
66.5
- , -
67
:
[Dupuytren] (72.0)
(77.9)
(78.2)
67.0 ()
67.1 ( )
: (24.5)
767
67.2 , -
: () (12.2)
67.3
: (12.3)
67.4
( )
: :
(71.271.3)
(66.6)
67.8 -
67.9 , -
68*
,
68.0* ,
:
(54.4)
(52.7)
(18.0)
68.8*
,
768
-
(7079)
70 ,
,
[ .728]
:
: :
(71.9)
(75.5)
(7677)
70.0 -
70.1
70.2
70.3
70.4
70.5
70.6
70.7
70.8 ,
,
70.9 , -
, ,
769
71
[ .728]
: ( )
(20.1)
, , -
(70.)
(7677)
71.0
71.1
71.2 [Baker]
: (66.0)
71.3
: (66.1)
71.4
: (75.3)
71.5 ,
: :
(71.9)
(75.5)
-
[Pellegrini-Stieda] (76.4)
71.8
71.9 ,
72
[ .728]
: (D48.3)
72.0 [Dupuyt-
ren]
72.1 - -
770
-
72.2
72.3
72.4 () -
72.5 ,
: :
() (35.4)
() (72.3)
(72.2)
72.8
72.9 ,
73*
,
[ .728]
73.0* (54.4)
73.1* (52.7)
73.8* ,
75
: - (89.0)
75.0
75.1
()() supraspinatus -
,
75.2
771
75.3
75.4
75.5
75.8
75.9 ,
76 ,
[ .728]
: ,
-
; --
-
.
: , ,
(70.)
76.0
76.1 -
76.2
76.3 -
76.4 -
[Pellegrini-Stieda]
76.5
76.6
76.7
76.8 , -
.tibialis posterior
772
-
76.9 ,
77
[ .728]
: :
(71.9)
,
(70.)
(46.0)
(25.7)
77.0
77.1
77.2
77.3
77.4
: Morton (G57.6)
77.5
77.8 ,
77.9 ,
79 ,
[ .728]
: (F45.4)
79.0
: (12.3)
773
79.1
: (60.)
79.2
: (G56G58)
:
(54.1)
(54.354.4)
79.3
: ()():
(54.0)
lupus erythematodes (L93.2)
[Weber-Christian] (35.6)
79.4
79.5
: ,
:
(L92.3)
(60.2)
79.6
79.8
79.9 ,
774
-
(8094)
(8085)
80
[ .728]
:
: (84.4)
(48.5)
(48.5)
80.0 -
80.1 -
80.2 -
80.3 ,
-
80.4 -
( ).
80.5
80.8
775
80.9 ,
81
[ .728]
: (80.)
81.0
81.1
81.2
: Sudeck-Leriche (89.0)
81.3 , -
81.4
( ).
81.5
81.6 [Lequesne]
: Sudeck-Leriche (89.0)
81.8
81.9 ,
82* , -
[ .728]
82.0*
(90.0)
82.1* (00
34)
82.8* ,
776
-
83
[ .728]
: :
(55.0)
D- (83.3)
(N25.0)
() (55.0)
(64.3)
D- (83.3)
83.0
83.1
83.2 , -
-
83.3 , -
83.4 ,
83.5 -
( ).
83.8
83.9 ,
84
[ .728]
84.0
84.1 []
: (96.0)
84.2
777
84.3 ,
:
(48.4)
84.4 ,
: (48.5)
(80.)
84.8
84.9 ,
85
[ .728]
: osteogenesis imperfecta (Q78.0)
(Q78.1)
(Q78.2)
(Q78.8)
85.0 ( )
: (10.8)
85.1
85.2
85.3 ,
()
85.4
: (09.1
09.2)
85.5
:
(09.2)
778
-
85.6
: (09.109.2)
- [-
Recklinghausen] (21.0)
85.8 -
,
:
[DISH] (48.1)
85.9 ,
(8690)
: (96.)
86
[ .728]
(9597).
: :
(0102)
(10.2)
(46.2)
86.0
86.1
86.2
86.3
86.4
86.5
86.6
779
86.8
Brodie
86.9 ,
87
[ .728]
: ()
: (9193)
87.0
87.1
( )
87.2
87.3
87.8
87.9 ,
88 Paget [ ]
[ .728]
88.0 Paget
88.8 Paget
88.9 Paget,
89
[ .728]
89.0
-
Sudeck
780
-
89.1 -
( )
89.2
89.3
89.4
Marie-Bamberger
89.5
89.6
(91).
89.8
89.9 ,
90* ,
[ .728]
90.0* (18.0)
: (49.0*)
90.1* , -
(51.4)
90.2* , -
:
(67.2)
(54.4)
(02.2)
(50.5,
52.7)
781
90.3* (70.3)
90.4* (D50D64)
90.5* ,
90.6* (00-
D48)
(4041)
90.7 (C00
D48)
: -
(49.5*)
90.8* ,
(N25.0)
(9194)
: (96.)
91
[ .728]
: (-
) (93.0)
91.0
():
crista iliaca [Buchanan]
[Van Neck]
[Pierson]
782
-
91.1
[Legg-Calve-Perthes]
91.2 Coxa plana
-
91.3
91.8 -
-
91.9 -
,
92
92.0
():
[Panner]
[Haas]
92.1
():
[Burns]
[Brailsford]
92.2
():
os lunatum [Kienbck]
[Mauclaire]
92.3
92.4
():
, [Khler]
, apex patellae [Sinding-Larsen]
783
92.5
():
[Blount]
tuberositas tibiae [Osgood-Schlatter]
Tibia vara
92.6
() :
[Sever]
[Diaz]
[Khler]
[Haglund]
92.7 -
() :
[Freiberg]
[Iselin]
92.8
92.9 ,
,
(-)
93
: (42.)
93.0 ()
[coxa vara retrosa]
93.1 Kienbck
os lunatum
93.2
93.8
784
-
93.9 ,
, (-)
94
[ .728]
94.0 [Tietze]
94.1
94.2
: (22.4)
94.3
94.8
94.9 ,
785
-
(95-99)
95
-
: (-):
(Z89-Z90)
(20-21)
-
(96.)
[.
] (07.)
(40-43)
-
(Q65-Q79)
95.0
: (J34.2)
95.1 ,
:
(61.1)
95.2
95.3
95.4
95.5
:
(33.)
95.8 -
786
-
95.9 - -
,
96 -
,
: (02.0)
(Z95Z97)
, (80
81)
96.0
96.1 ,
96.2
96.3
96.4
96.5
96.6 ,
: , , -
(84.)
96.8 -
96.9 - -
,
787
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: , -
.
, -
, -
99.;
. 728.
0
1
2
3
4
5
6
7 ,
8 , -
,
9
99.0
99.1 ()
99.2
99.3
99.4 -
99.5
99.6 -
99.7 - -
788
-
99.8
99.9 ,
789
, ,
,
II -
III , , -
IV , -
VI
VII
VIII
IX -
XI
XII
XIII -
: , ,
790