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-10

1 ( 1)



International
ICD - 10
Statistical
Classification
of Diseases and
Related Health
Problems

Tenth Revision

Volume 1

World Health Organization


Geneva
1992

- 10



,

1 ( 1)
-

-
,
.



2003
1*
-





,




, -

2
3
* 1 - -
. IXIII, XIV
XXI, ,
, .

,
; 10
: 1 ;
2 ; 3

1. I. : 10
(NLM Classification: WB 15)
ISBN 92 4 154419 8 (v. 1) ISBN 9548541122 (. 1)
ISBN 92 4 154420 1 (v. 2) ISBN 9548541130 (. 2)
ISBN 92 4 154421 X (v. 3) ISBN 9548541149 (. 3)
World Health Organization, 1992
, 2003


2 .
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.

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........................................................................................................ 1


................................................................................................... 5


.................................. 7

............................................................. 30


,
I ..................................... 119
II ............................................................................... 204
III ,
, .............. 289
IV ,
............................... 313
V ........................................ 359
VI ......................................................... 453
VII .............................................. 499
VIII .................................... 533
IX .................................. 547
X .................................................... 597
XI ........................................ 636
XII ....................................... 691
XIII -
.............................................................. 726

10 -


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Australian Institute of Health
GPO Box 570
Canberra ACT 2601,
Australia
Office of Population Censuses and Surveys
St. Catherines House
Kingsway 10
London WC2B 6JP
England
National Center for Health Statistics
6525 Belcrest Road
Hyattsville, MD 20782
United States of America

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Peking Union Medical College Hospital
Chinese Academy of Medical Sciences
Beijing 100730
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INSERM
44 Chemin de Ronde
F-78110 Le Vsinet
France ( )
Department of Social Medicine
University Hospital
S-751 85 Uppsala
Sweden ( )
Faculdade de Sade Publica/Universidade de So Paulo
Avenida Dr Arnaldo 715,
0255 So Paulo, SP
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Centro Venezolano de Clasificatin de Enfermedades
Edificio Sur, 90 Piso
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1. , 1975 ., . 1.
, , 1977, . iii - xxiv.
2. Report of the Expert Committee on the Internatioinal Classification of
Diseases - 10th Revision: First Meeting. Geneva, World Health Organiza-
tion, 1984 (unpublished document DES/EC/ICD-10/84.34).
3. Report of the Expert Committee on the Internatioinal Classification of
Diseases - 10th Revision: Second Meeting. Geneva, World Health Organi-
zation, 1987 (unpublished document WHO/DES/EC/ICD-10/83.38).
4. Report of the Preparatory Meeting on ICD-10. Geneva, World Health Or-
ganization, 1983 (unpublished document DES/ICD-10/83.19).
5. Lay reporting of health information. Geneva, World Health Organization,
1978.
6. International Conference on Health Statistics for the Year 2000. Budapest,
Statistical Publishing House, 1984.
7. Report of the Consultation on Primary Care Classification. Geneva,
World Health Organization, 1985 (unpublished document DES/PHC/
85.7).
8. International Classification of Impairments, Disabilities, and Handicaps.
Geneva, World Health Organization, 1980.
9. WHO Official Records, No. 233, 1976, p. 18.
10. International Classification of Procedures in Medicine. Geneva, World
Health Organization, 1978.

29


I

(0099)

(0009)
00
01
02
03
04
05
06
07
08
09

(1519)
15 , -

16 , -

17
18
19

(2028)
20
21
22
23
24
25
26
27
28 ,

30

(3049)
30 [ Hansen]
31 ,
32
33
34
35
36
37
38
39
40
41
42
43
44
46
48 ,
49

, (5064)
50
51
52
53
54
55 ()
56 ,
57
58 ,
59
60 [herpes simplex]
63 , , -

64 , ,

, (6569)
65
66

31

67 []
68
69 ,

, (7074)
70 , Chlamydia psittaci
71
74 ,

(7579)
75
77 [ ]
78 -
79

(8089)
80
81
82
83 ,
84 ,
85 ,
86 ,
87
88 , -

89 ,

,
(9099)
90 [ ]
91 , -
92 ,
93 , , -

94 , ,
95
96
98 ,
99 ,

32

, -
(0009)
00 - [herpes simplex]
01 [varicella]
02 Herpes zoster
03
04 ,
05
06 [ ]
07
08 ,
,
09 ,
,

(1519)
15
16
17
18
19 ,

, [HIV]
(2024)
20 ,
[HIV],
21 ,
[HIV],
22 ,
[HIV],
23 ,
[HIV],
24 ,
[HIV],

(2534)
25
26
27
30

33

33 ,
34

(3549)
35
36
37
38
39
40
41
42
43
44
45
46
47
48 ,
49 ,

(5064)
50 , Plasmodium falciparum
51 , Plasmodium vivax
52 , Plasmodium malariae
53
54 ,
55
56
57 Chagas
58
59
60 ,
64 ,

(6583)
65 []
66
67
68
69

34

70
71 ,
72
73
74
75
76
77
78
79
80
81 ,
82 ,
83

, (8589)
85
86
87
88
89 ,

(9094)
90
91
92
94 -

, (9597)
95 , -

96 , -

97 , -

(99)
99

35

II

(C00D48)

(C00C97)

, -
(C00C14)
C00
C01
C02

C03
C04
C05
C06

C07
C08

C09
C10
C11
C12
C13
C14
,


(C15C26)
C15
C16
C17
C18
C19
C20
C21
C22 -

36

C23
C24

C25
C26


(C30C39)
C30

C31
C32
C33
C34
C37
C38 ,

C39


(C40C41)
C40

C41


(C43C44)
C43
C44

-
(C45C49)
C45
C46 Kaposi
C47 -

37

C48 -

C49

(C50)
C50

(C51C58)
C51
C52
C53
C54
C55 -

C56
C57

C58

(C60C63)
C60
C61
C62
C63

(C64C68)
C64 ,

C65
C66
C67
C68

, -
(6972)
C69
C70

38

C71
C72 , -

-
(7375)
C73
C74
C75

, -
(7680)
C76

C77 -

C78

C79
C80

, -
(8196)
C81 Hodgkin []
C82 []
C83
C84 -
C85
C88
C90 -

C91 []
C92 []
C93
C94
C95
C96 -
,

39

() -
(97)
C97 ()

in situ (D00D09)
D00 in situ ,
D01 in situ -

D02 in situ
D03 in situ
D04 in situ
D05 in situ
D06 in situ
D07 in situ
D09 in situ

(D10D36)
D10 ,

D11 -

D12 , ,

D13 -

D14 -

D15 -

D16 -

D17
D18
D19
D20 -

D21

D22

40

D23
D24
D25
D26
D27
D28 -

D29
D30
D31 -

D32
D33

D34
D35 -

D36 -

(D37D48)
D37 -

D38
,
D39

D40

D41 -

D42

D43

D44 -

D45
D46

41

D47
,
D48 -

III
,
,
(D50D89)

, (D50D53)
D50
D51 12-
D52
D53 ,

(D55D59)
D55 ,
D56
D57 -
D58
D59

(D60D64)
D60 () [-
]
D61
D62
D63* ,
D64

,
(D65D69)
D65 [ -
]
D66 VIII
D67 IX
D68

42

D69

(D70D77)
D70
D71 - -

D72
D73
D74
D75
D76 , -

D77* -
,

, (D80D89)
D80
D81
D82 ,
D83
D84
D86
D89 , -

IV
,

(0090)

(E00E07)
00
01 , ,

02 ,
03
04
05 []

43

06
07

(1014)
10
11
12 ,
13
14 ,


(1516)
15
16

(2035)
20
21 -

22
23
24 Cushing
25
26
27
28
29
30 ,
31
32
34
35* , -

(4046)
40
41
42
43 - ,
44 -

44

45 , -

46 - ,

(5064)
50
51
52 []
53
54
55 D
56
58
59
60
61
63
64

(6568)
65
66
67
68

(7090)
70
71

72
73
74
75 -

76
77
78 -

79
80

45

83
84
85
86 []
87 - --

88
89 , -
,
90*
,

V

(F00F99)

, ,
(F00F09)
F00* Alzheimer
F01
F02* ,
F03 ,
F04 ,

F05 , -

F06 , -

F07 , -
,
F09 , -

,
(F10F19)
F10 , -

46

F11 , -

F12 , -

F13 , -

F14 , -

F15 , -
( )
F16 , -

F17 , -

F18 , -

F19 , -

, (F20F29)
F20
F21
F22
F23
F24
F25
F28
F29 ,

[ ] (F30F39)
F30
F31
F32
F33
F34 [ -
]
F38 []
F39 [],

47

,
(F40F48)
F40
F41
F42 -
F43
F44 []
F45
F48

,
(F50F59)
F50
F51
F52 , -

F53 , -
,
F54 , -
,
F55 ,
F59 ,
,

(F60F69)
F60
F61
F62 , -

F63
F64
F65
F66 , -

F68 -

F69 , -

48

(F70F79)
F70
F71
F72
F73
F78
F79 ,

(F80F89)
F80
F81
F82 -

F83
F84
F88
F89 ,

, -
(F90F98)
F90
F91
F92
F93 ,
F94 ,

F95
F98 , -

(F99)
F99

49

VI

(G00G99)

(G00G09)
G00 ,
G01* ,
G02* , -

G03 ,
G04 ,
G05* , , -

G06
G07* -
,
G08
G09 -

,
(G10G13)
G10 Huntington
G11
G12
G13* ,
,

(G20G26)
G20 Parkinson
G21
G22* ,
G23
G24
G25
G26* ,

50


(G30G32)
G30
G31 , -

G32* -
,

(G35G37)
G35
G36
G37 -

(G40G47)
G40
G41
G43
G44
G45 []

G46*
G47

,
(G50G59)
G50
G51
G52
G53* , -

G54
G55* , -

G56
G57
G58
G59* ,

51


(G60G64)
G60
G61
G62
G63* ,
G64

- (G70G73)
G70 Myasthenia gravis - -

G71
G72
G73* - -
,


(G80G83)
G80
G81
G82
G83

(G90G99)
G90 []
G91
G92
G93
G94* , -

G95
G96
G97 ,

G98 , -

G99* , -

52

VII

(0059)

, (0006)
00
01
02
03* ,
04
05
06* , -

(1013)
10
11
13* ,

, , (1522)
15
16
17
18
19* , -

20
21
22* , -

(2528)
25
26
27
28* , -

53

(3036)
30
31
32* , -

33
34
35
36* ,

(4042)
40
42* ,

(4345)
43
44
45* -
,

(4648)
46
47 [2-]
48* [2-]
,

,
, (4952)
49
50
51
52

(5354)
53
54

(5559)
55
57

54

58* , -

59 -

VIII

(6095)
(6062)
60
61
62* , -

(6575)
65
66
67* , -

68 []
69 []
70
71
72
73
74
75*
,

(8083)
80
81
82* ,
83

55

(9095)
90 , (-
)
91
92
93 ,
94* , -

95
,

IX

(I00I99)

(I00I02)
I00
I01
I02

(I05I09)
I05
I06
I07
I08
I09

(I10I15)
I10 []
I11
I12 [ ]
I13
I15

(I20I25)
I20
I21
I22

56

I23
I24
I25


(I26I28)
I26
I27
I28

(I30I52)
I30
I31
I32* ,
I33
I34
I35
I36
I37
I38
I39* ,

I40
I41* ,
I42
I43* ,
I44
I45
I46
I47
I48
I49
I50
I51
I52* , -

(I60I69)
I60
I61

57

I62
I63
I64 ,
I65 , -

I66 , -

I67
I68* , -

I69
, (I70I79)
I70
I71
I72
I73
I74
I77
I78
I79* , -
,
, , -
(I80I89)
I80
I81
I82
I83
I84
I85
I86
I87
I88
I89

58


(I95I99)
I95
I97 ,

I98* ,

I99

X

(J00J99)
(J00J06)
J00 []
J01
J02
J03
J04
J05 []
J06

(J10J18)
J10 ,
J11 ,
J12 ,
J13 , Streptococcus pneumoniae
J14 , Haemophilus influenzae
J15 ,
J16 , , -

J17* ,
J18

59


(J20J22)
J20
J21
J22 ,

(J30J39)
J30
J31 ,
J32
J33
J34
J35
J36
J37
J38 , -

J39

(J40J47)
J40 ,
J41 -
J42 ,
J43
J44
J45
J46 [status asthmaticus]
J47

, (J60J70)
J60
J61 , -

J62 , ,
J63 ,
J64 ,
J65 ,
J66 ,

60

J67 ,
J68 ,
, ,
J69 ,
J70 ,

, -
(J80J84)
J80 [] -

J81
J82 ,
J84


(J85J86)
J85
J86

(J90J94)
J90 ,
J91* ,
J92
J93
J94

(J95J99)
J95 , -

J96 ,
J98
J99* ,

61

XI

(0093)

, (0014)
00
01
02
03
04
05
06
07 [ -
]
08
09 ,
10
11
12
13
14

, (2031)
20
21
22
23* , -

25
26
27
28
29
30
31

(3538)
35
36

62

37 ,
38

(4046)
40
41
42
43
44
45
46 ,

(5052)
50 Chron [ ]
51
52

(5563)
55
56
57
58
59
60
61
62
63

(6567)
65
66
67* , -

(7077)
70
71
72 ,
73 ,
74

63

75
76
77* , -

,
(8087)
80 []
81
82
83
85
86
87* , -
,

(9093)
90
91
,
92
93* ,

XII

(L00L99)

(L00L08)
L00
L01
L02 ,
L03
L04
L05
L08

64

(L10L14)
L10
L11
L12
L13
L14* ,

(L20L30)
L20
L21
L22
L23
L24 [irritant]
L25 ,
L26
L27
L28
L29
L30

(L40L45)
L40
L41
L42
L43
L44
L45* , -

(L50L54)
L50
L51 Erythema multiforme
L52 Erythema nodosum
L53
L54* ,

65

,
(L55L59)
L55
L56 , -

L57 ,

L58
L59 ,

(L60L75)
L60
L62* ,
L63
L64
L65
L66
L67
L68
L70
L71
L72
L73
L74
L75

(L80L99)
L80
L81
L82
L83 Acanthosis nigricans
L84
L85
L86* ,
L87
L88
L89
L90
L91

66

L92
L93
L94
L95 ,
L97 ,
L98 , -

L99* ,

XIII
-

(0099)

(0025)

(0003)
00
01*
,
02
03* , -

(0514)
05
06
07*
08 []
09* [] ,

10
11
12
13
14* ,

67

(1519)
15
16 [ ]
17 [ ]
18 -
19

(2025)
20
21
22
23
24
25 ,

(3036)
30
31
32 lupus erithematodes
33
34
35
36* ,

(4054)

(4043)
40
41
42
43

(4549)
45
46
47
48
49* ,

68

(5054)
50
51
53 ,
54

(6079)
(6063)
60
61
62
63* ,

(6568)
65
66
67
68*
,

(7079)
70 , , -

71
72
73* , -

75
76 ,
77
79 ,

(8094)

(8085)
80
81
82* ,
83

69

84
85

(8690)
86
87
88 Paget [ ]
89
90* ,

(9194)
91
92
93
94

-
(9599)
95 -

96 -
,
99 ,

XIV
-
(N00N99)
(N00N08)
N00
N01
N02
N03
N04
N05 ,
N06
N07 ,
N08* ,

70

(N10N16)
N10
N11
N12 , -

N13
N14 ,

N15
N16* ,

(N17N19)
N17
N18
N19 ,

(N20N23)
N20
N21
N22* , -

N23 ,

(N25N29)
N25 , -

N26 ,
N27
N28 ,

N29* , -

(N30N39)
N30
N31 , -

N32

71

N33* ,

N34
N35
N36
N37* ,
N39

(N40N51)
N40
N41
N42
N43
N44
N45
N46
N47 ,
N48
N49 , -

N50
N51* , -

(N60N64)
N60
N61
N62
N63 ,
N64

(N70N77)
N70
N71 ,
N72
N73
N74* -
,
N75
N76

72

N77* , -

(N80N98)
N80
N81
N82
N83 , -

N84
N85 , -

N86
N87
N88
N89
N90
N91 ,
N92 ,
N93
N94 ,

N95

N96
N97
N98 ,

- (N99)
N99 -
,

73

XV
,
(0099)

, (0008)
00 []
01
02
03
04
05
06 ,
07
08 , -

, -
, (1016)
10 , , -

11
12 -

13 -

14 -

15
16 ,

,
(2029)
20
21
22
23 -

24
25

74

26 ,

28
29

,
-
(3048)
30
31 ,
32 -

33 -

34 -

35 -

36 -

40
41

42
43
44
45 [abruptio placentae]
46 ,
47
48

(6075)
60
61
62
63
64 -

65
66

75

67 , -
,
68 , [-
]
69 -

70
71
72
73
74 -

75 , -

(8084)
80
81 - -

82
83

84

, (8592)
85
86
87
88
89
90 ,
91 ,
92 , -

, (9599)
95
96 ,
42 , -
97

76

98 ,
, , -

99 , , -
,

XVI
,

(P00P96)


, ,
(P00P04)
P00 ,

P01 -

P02 ,
,
P03

P04 -
,

, -
(P05P08)
P05
P07 ,
,
P08 ,

(P10P15)
P10 ,

P11
P12

77

P13
P14
P15

- ,
(P20P29)
P20
P21
P22
P23
P24
P25 ,

P26 ,
P27 , -

P28 ,

P29 - , -

, (P35P39)
P35
P36
P37
P38
P39 , -


(P50P61)
P50
P51
P52 -

P53
P54
P55
P56 ,
P57

78

P58 ,
P59
P60 -

P61

-
, (P70P74)
P70 ,

P71

P72
P74 -


(P75P78)
P75*
P76
P77
P78 -

, ,
(P80P83)
P80
P81
P83 ,

, (P90P96)
P90
P91
P92 ,
P93 , -
,
P94
P95
P96 ,

79

XVII
[ ],

(Q00Q99)

[ ]
(Q00Q07)
Q00
Q01
Q02
Q03
Q04 [ ]
Q05 Spina bifida
Q06 [ ]

Q07 [ ]

[ ] , ,
(Q10Q18)
Q10 [ ] ,

Q11 ,
Q12 [ ]
Q13 [ ]

Q14 [ ]

Q15 [ ]
Q16 [ ] , -

Q17 [ ]
Q18 [ ] -

[ ] -
(Q20Q28)
Q20 [ ] -

80

Q21 [ ] -

Q22 [ ]

Q23 [ ] -

Q24 [ ]
Q25 [ ]
Q26 [ ]
Q27 [ ] -

Q28 [ ]

[ ]
(Q30Q34)
Q30 [ ]
Q31 [ ]
Q32 [ ] -

Q33 [ ]
Q34 [ ] -

[ ] (Q35Q37)
Q35 [ ]
Q36 [ ]
Q37 [ -
]

[ ]
(Q38Q45)
Q38 [ ] , -

Q39 [ ]
Q40 [ ]

Q41 ,
Q42 ,
Q43 [ ]

81

Q44 [ ] ,

Q45 [ ] -

[ ]
(Q50Q56)
Q50 [ ] , -

Q51 [ ] -

Q52 [ ]

Q53
Q54
Q55 [ ]

Q56

[ ]
Q60Q64)
Q60
Q61
Q62

Q63 [ ]
Q64 [ ] -

[ ] -
(Q65Q79)
Q65
Q66
Q67 - , , -

Q68 -
Q69
Q70
Q71
Q72

82

Q73
Q74 [ ]
()
Q75 [ ]

Q76 [ ]

Q77 -

Q78
Q79 [ ] --
,

[ ] (Q80Q89)
Q80
Q81 Epidermolysis bullosa
Q82 [ ]
Q83 [ ]
Q84 [ ]

Q85 ,
Q86 [ ], -
, -

Q87 [
],
Q89 [ ], -

, (Q90Q99)
Q90 Down
Q91 Edward Patau
Q92 , -

Q93 ,
Q95 -
,
Q96 Turner
Q97 , -

83

Q98 , -

Q99 ,

XVIII
, ,
,

(R00R99)

, - -
(R00R09)
R00
R01
R02 ,
R03 -

R04
R05
R06
R07
R09 , --

,
(R10R19)
R10
R11
R12
R13
R14
R15
R16 ,
R17
R18
R19 , -

84

,
(R20R23)
R20
R21
R22 ,

R23

, -
(R25R29)
R25
R26
R27
R29 , -
-

,
(R30R39)
R30 ,
R31
R32 ,
R33
R34
R35
R36
R39 , -

, , -
, (R40R46)
R40 ,
R41 ,

R42
R43
R44 ,

R45 , -

85

R46 , -

, (R47R49)
R47 ,
R48
,
R49

(R50R69)
R50
R51
R52 ,
R53
R54
R55 []
R56 ,
R57 ,
R58 ,
R59
R60 ,
R61
R62
R63 , -

R64
R68
R69

, ,
(R70R79)
R70 -
[]
R71
R72 ,
R73
R74
R75 -
[HIV]

86

R76 , -

R77
R78 ,

R79

, , -
(R80R82)
R80
R81
R82 , -

, ,
,
(R83R89)
R83 ,
R84 ,

R85 ,

R86 ,

R87 ,

R89 ,
,

, -
, -
(R90R94)
R90 , -
-

R91 , -

R92 , -

87

R93 , -
-

R94 , -

(R95R99)
R95
R96
R98
R99

XIX
,

(S00T98)

(S00S09)
S00
S01
S02
S03 , -

S04
S05
S06
S07
S08
S09
(S10S19)
S10
S11
S12
S13 , -

S14
S15

88

S16
S17
S18
S19
(S20S29)
S20
S21
S22 (), -

S23 , -

S24
S25
S26
S27
S28

S29

, , -
(S30S39)
S30 ,
S31 ,
S32
S33 , -

S34 -
,
S35 ,
S36
S37
S38 , -

S39 ,

(S40S49)
S40
S41
S42

89

S43 , -

S44
S45 -

S46

S47
S48
S49

(S50S59)
S50
S51
S52
S53 , -

S54
S55
S56
S57
S58
S59

(S60S69)
S60
S61
S62
S63 , -

S64
S65
S66
S67
S68
S69

(S70S79)
S70 -

90

S71
S72
S73 , -

S74
S75

S76 -

S77
S78

S79

(S80S89)
S80
S81
S82 , -

S83 , -

S84
S85
S86
S87
S88
S89

(S90S99)
S90
S91
S92
S93 , -

S94
S95
S96
S97
S98

91

S99

, (0007)
00 ,
01 ,
02 ,
03 , , -

04 ,
05 , -

06 , , -

07 ,

, -
(0814)
08
09 -

10
11
12
13
14


(1519)
15
16
17
18
19 -

(2032)

,
(2025)
20
21

92

22
,
23
24
,
25 -


(2628)
26 , -

27
28

-
(2932)
29
30
31 , -

32 , -

(3335)
33
34
35 , , -

, -
(3650)
36
37

38 , -
,
39 , -

40 []

93

41
42 , , -

43 , -

44 , -

45 , , -
,
46 , -
-
47 , -

48 ,

49 ,
, , -
,
50 -
,

,
(5165)
51
52
53

54
55
56
57
58
59 ,
60
61 ,

62 ,

63

94

64 -

65


(6678)
66
67
68
69
70
71
73 [-
]
74
75
78 ,

(79)
79 ,

, -
(8088)
80 , , -

81 ,
82 , -
,
83 , - ,

84 ,
,
85 , ,

86
87 ,
88
,

95

, -
(9098)
90
91
92
93
94 , ,

95 ,
96 ,

97 ,

98 -

XX

(V01Y98)

(V01V99)

, (V01V09)
V01 ,
V02 ,

V03 , , -

V04 , -

V05 , -

V06 , -

V09 ,

96

, (V10V19)
V10 , -

V11 ,
V12 ,

V13 , , -

V14 , -

V15 , -

V16 ,

V17 , -

V18 ,

V19 ,

, (V20V29)
V20 ,

V21 ,
V22 ,

V23 , ,

V24 , -

V25 , -

V26 ,

V27 ,

V28 ,

97

V29 , -

, , -
(V30V39)
V30 ,
-

V31 ,

V32 ,


V33 ,
, -

V34 ,
-

V35 ,
-

V36 ,


V37 ,
-

V38 ,

V39 ,

,
(V40V49)
V40 , -

V41 , -

98

V42 ,

V43 , -
,

V44 , -

V45 , -
-

V46 , -

V47 , -

V48 , -

V49 ,

,
(V50V59)
V50 ,
-

V51 ,

V52 ,


V53 ,
, -

V54 ,
-

V55 ,
-

99

V56 ,


V57 ,
-

V58 ,

V59 ,

,
(V60V69)
V60 ,

V61 ,

V62 ,


V63 ,
,

V64 ,
-

V65 ,
-

V66 ,
-

V67 ,

V68 ,

V69 ,

100

, -
(V70V79)
V70 , -

V71 , -

V72 , -

V73 , -
, -

V74 , -

V75 , -

V76 , -

V77 , -

V78 ,

V79 , -

, (V80V89)
V80 , -
,
V81 ,

V82 ,

V83 , ,
, -

V84 , ,
,

101

V85 , ,
, -

V86 , -
, -
, , -

V87 ,

V88 ,

V89 -

(V90V94)
V90 -

V91
V92 ,
,
V93 , -


V94


(V95V97)
V95 ,
,
V96 ,
, ,

V97

(V98V99)
V98
V99 ,

102

(W00X59)

(W00W19)
W00 ,
W01 ,

W02 , ,
-
W03

W04

W05 ,
W06 ,
W07 ,
W08 ,
W09 ,
W10
W11
W12
W13 ()
W14
W15 ( )
W16 , ,

W17
W18
W19 ,

(W20W49)
W20 ,
W21
W22
W23 , ,

W24 , -

W25
W26 ,
W27

103

W28
W29 -

W30
W31
W32
W33 , -

W34
W35 ,
W36 ,
W37 , ,

W38 , -

W39
W40
W41
W42
W43
W44
W45
W49

(W50W64)
W50 , , , ,

W51
W52 ,

W53
W54
W55
W56
W57 -

W58
W59
W60 -

104

W64
(W65W74)
W65
W66
W67
W68
W69
W70
W73
W74 ,
(W75W84)
W75
W76
W77

W78
W79 , -

W80 ,

W81

W83
W84 ,

, , -
-
(W85W99)
W85 ,
W86 ,

W87 ,
W88
W89
W90
W91 ,
W92
W93

105

W94 -

W99 -

, (0009)
00 () -

01 ()

02
03 -

04
05 ()
06 -

08 , -

09 ,

() (1019)
10 , , -

11
12
13
14
15
16 ,

17 ,
18
19 -

(2029)
20
21
22

106

23 ,
24 () -

25
26
27
28
29

(3039)
30
31
32
33
34
35
36 ,

37
38
39

(4049)
40 ,

41 , -
, , , -

42 -
[],
43 -
,
44 -
,
45
46 ,

47 -

107

48
49 -

, (5057)
50
51
52
53
54
57 ,
(5859)
58
59

(6084)
60 -
,
61 ,
, , -
,
62 -
[],
63
,
64
,
65
66 -

67 -

68
69

70 , -

71
72

108

73 ,

74

75 -

76 ,
77 , -

78
79
80
81

82

83
84

(85Y09)
85 ,

86
87
88
89

90 -

91 ,
92
93
94 , -

95

96
97 ,
98 ,

109

99
Y00
Y01
Y02

Y03
Y04
Y05
Y06
Y07
Y08
Y09

(Y10Y34)
Y10 , -
,
Y11 , , -
, , -
,
Y12 [-
], , -

Y13 , -
, -

Y14
, ,

Y15 ,
Y16 , -
, -

Y17 -
,
Y18 , -

Y19 -
,
Y20 , ,
Y21 ,

110

Y22 , -

Y23 , -
,
Y24 -
,
Y25 ,
Y26 , ,
Y27 , , -

Y28 ,
Y29 ,
Y30 , , -

Y31 , ,

Y32 , -

Y33 ,

Y34

(Y35Y36)
Y35
Y36

(Y40Y84)
, , -
(Y40Y59)
Y40
Y41

Y42 , -

Y43
Y44 ,
Y45 , -

Y46

111

Y47 , []

Y48
Y49 ,
Y50 , , -

Y51 , -

Y52 , - -

Y53 , -

Y54 , ,

Y55 ,

Y56 ,
, , , -

Y57
Y58
Y59
-
(Y60Y69)
Y60 , ,

Y61

Y62 -

Y63 -

Y64
Y65 -

Y66
Y69
,

112

, ,

(Y70Y82)
Y70 ,
Y71
- ,
Y72 , ,

Y73 ,
,
Y74 -
,
Y75 , ,

Y76 , -
,
Y77 , ,

Y78 , -

Y79 , -

Y80 ,

Y81 , -
,
Y82 ,

, -
, -
(Y83Y84)
Y83 ,
,
-

Y84 ,
,

113


(Y85Y89)
Y85
Y86
Y87 , -
[],
Y88

Y89

, -
, (Y90Y98)
Y90 , -

Y91 , -

Y95
Y96 ,
Y97 ,
Y98 ,

XXI
,

(Z00Z99)

, -
(Z00Z13)
Z00 ,

Z01 ,

Z02
Z03

Z04
Z08 -

114

Z09 ,

Z10

Z11 -

Z12 -

Z13 -

, -
(Z20Z29)
Z20 -

Z21 ,
[HIV]
Z22
Z23
Z24

Z25

Z26 -

Z27 -

Z28
Z29

, , -
(Z30Z39)
Z30
Z31
Z32
Z33 ,
Z34
Z35 , -

115

Z36 [-
]
Z37
Z38
Z39

,
-
(Z40Z54)
Z40
Z41 ,
Z42
Z43
Z44
Z45
Z46
Z47
Z48
Z49 ,
Z50 , -

Z51
Z52
Z53 , -

Z54

, -
(Z55Z65)
Z55 ,
Z56 ,
Z57
Z58 ,
Z59 , -

Z60 ,
Z61 , -

Z62 ,

116

Z63 , , -

Z64 , -

Z65 ,

, -
(Z70Z76)
Z70 ,

Z71 ,
,
Z72 ,
Z73 ,

Z74 , , -

Z75 , -

Z76 , -

, -
,
(Z80Z99)
Z80
Z81 -

Z82 , -
,
Z83
Z84
Z85
Z86
Z87 -

Z88 , -

Z89

117

Z90 ,
Z91 , -

Z92
Z93 ,
Z94
Z95
Z96
Z97
Z98
Z99
,

118
I

(0099)

: ,

:
(Z22.)
,

, -
, ( -
, -
[HIV]) (O98.)
, -
( ,
,
,
[HIV]) (3539)
(J00J22)

:
0009
1519
2028
A3049
5064 ,
6569 ,
7074 ,
7579
8089
9099 , -

0009 , -

1519

119

2024 ,
[HIV]
2534
3549
5064
6583
8589 ,
9094
9597 ,
99


(0009)
00
00.0 , 01, -
cholerae

00.1 , 01, -
eltor
-
00.9 ,

01
01.0
, Salmonella typhi
01.1
01.2
01.3
01.4 ,
, Salmonella paratyphi

120

02
: ( ), -
Salmonella , -
S. typhi S. paratyphi
02.0

02.1
02.2
(-):
(01.3*)
(G01*)
(90.2*)
(J17.0*)
(N16.0*)
02.8
02.9 ,

03
03.0 , Shigella dysenteriae
[ Shiga-Kruse]
03.1 , Shigella flexneri

03.2 , Shigella boydii

03.3 , Shigella sonnei
D
03.8
03.9 ,

121

04
: (05.)
(18.3)
04.0 , Es-
cherichia coli
04.1 , Es-
cherichia coli
04.2 , Es-
cherichia coli
04.3 ,
Escherichia coli
04.4 , Escheri-
chia coli
, Escherichia coli
04.5 , Campylobacter
04.6 , Yersinia enterocolitica
: (28.2)
04.7 , Clostridium difficile
04.8
04.9 ,

05

: , Escherichia coli
(04.004.4)
(32.)
-
(02.)

(6162)
05.0

122

05.1
, Clostri-
dium botulinum
05.2 , Clostridium
perfringens [Clostridium welchii]

Pig-bel
05.3 , Vibrio pa-
rahaemolyticus
A05.4 , Bacillus
cereus
05.8 -

05.9 ,

06
: , Entamoeba histoly-
tica
: (07.)
06.0


06.1
06.2
06.3

06.4

06.5 (J99.8*)
( )
06.6 (G07*)
( )(
)

123

06.7
06.8
:

(N51.2*)
06.9 ,

07
07.0

07.1 []
07.2
07.3
, Isospora belli Isospora hominis


07.8



07.9 ,
,
(-):


08

: -
(J10.8, J11.8)
08.0

124

08.1 , Nor-
walk
Small round structured virus enteritis
08.2
08.3
08.4 ,
(-):



08.5

09

. , , -
09, ,

,
52.9.
[]








: , ,
(00
08)
(52.9)
(P78.3)

125

(1519)
: , Mycobacterium tuberculosis
Mycobacterium bovis
: (P37.0)
, (J65)
(90.)
(J65)

15 ,


15.0 , -
-

(-):



15.1 ,

, 15.0,

15.2 , -

, 15.0, -

15.3 , -

, 15.0, ,

126

15.4 ,

:





: (15.7)
15.5 , , -

:




15.6 ,



: -
,
(15.7)
15.7 , -

15.8 , -






:



15.9 -
, -

127

16 ,


16.0

(-):




16.1

, 16.0,

16.2 -


(-)
( -
-
)

16.3 ,


:

(
)

:
, (16.7)

128

16.4 , ,


:

(
)

16.5 , -


(
:


)

: (16.7)
16.7 ,


(-):


16.8 , -
-


(

:
)

16.9
,


129

17
17.0 (G01*)
( )(
)

17.1 (G07*)

17.8 -

(G07*)

(G07*)
(-):
(G07*)
(G05.0*)
(G05.0*)
(G63.0*)
17.9 ,
(G99.8*)

18
18.0
:
(01.1*)
(M01.1*)
(M49.0*)
(-):
(M01.1*)
(H75.0*)
(M90.0*)
(M90.0*)
(M90.0*)
(M68.0*)
(M68.0*)

130

18.1 -
:
(N33.0*)
(N74.0*)
(N29.1*)
(N51.*)
(N29.1*)

(N74.1*)
18.2

: :
(15.4, 16.3)

(18.3)

(15.4, 16.3)
18.3 , -

:
(93.0*)
()() (K93.0*)

:

(93.0*)
(K67.3*)
18.4
,
:

:

(H03.1*)

: (L93.)
(M32.)

131

18.5
:
(H32.0*)
(H19.0*)
(H19.2*)
(H22.0*)
() ()
(H19.2*)
: , (A18.4)
18.6
(67.0*)
: (A18.0)
18.7 (E35.1*)
Addison
18.8
:
(I39.8*)
(I41.0*)
(K23.0*)
(I32.0*)
(E35.0*)
(I68.1*)

19
: :



19.0 -

19.1 -

19.2 -

19.8
19.9

132


(2028)
20
: , Yersinia pestis
20.0
20.1 -
20.2
20.3
20.7
20.8



20.9 ,

21
:
, Francisella tula-
rensis

21.0 -
21.1 -

21.2
21.3

21.7
21.8
21.9 ,

133

22
: , Bacillus anthrcis
22.0
(-):


22.1



22.2 -
22.7
22.8
(G01*)
22.9 ,

23
: :



23.0 , Brucella melitensis
23.1 , Brucella abortus
23.2 , Brucella suis
23.3 , Brucella canis
A23.8
23.9 ,

24
24.0
, Pseudomonas mallei

134

24.1
:


24.2
24.3
24.4 ,
, Pseudomonas pseudomallei
Whitmore

25
25.0

25.1



25.9 ,

26
26.0

26.7 , Erysipelothrix
26.8
26.9 ,

27
27.0 -
, Leptospira interrogans, -
icterohaemorrhagiae
27.8
27.9 ,

135

28 ,

28.0
28.1

28.2
: , Yersinia enterocolitica
(04.6)
(20.)
28.8 , -

28.9 ,


(3049)
30 [ Hansen]
: , Mycobacterium lep-
rae
: (92)
30.0
I
30.1

30.2

30.3

30.4
BL
30.5
LL

136

30.8
30.9 ,

31 ,

: (30.)
(1519)
31.0 , Mycobac-
terium
, Mycobacterium:
avium
intracellulare [Battey bacillus]
kansasii
31.1 , Mycobacterium
Buruli
, Mycobacterium:
marinum
ulcerans
31.8 , Mycobacterium
31.9 , Mycobacterium, -


32
:
: ()
(P37.2)
32.0
32.1
:
(G01*)
(G05.0*)
32.7

137

32.8
:
(I68.1*)
(I39.8*)
-
32.9 ,

33

34

35

: ():
(33)
(34)

36
36.0


36.1
36.2

36.3
: (L08.1)
36.8
:
(H13.1*)
(I41.0*)
(G63.0*)
36.9 ,

138

37
37.0 , Bordetella pertussis
37.1 , Bordetella parapertussis
37.8 , Borde-
tella
37.9 ,

38
: (J02.0)

39
39.0 (G01*)
39.1 Weterhouse-Friderichsen (E35.1*)


39.2
39.3
39.4 ,

39.5
:
(I52.0*)
(I39.8*)
(I41.0*)
(I32.0*)
39.8
:
(M01.0*)
(H13.1*)
(G05.0*)
(H48.1*)
(M03.0*)

139

39.9 ,

40
: (75.3)
:
,
(0307, 08.0)
(88.0)
, -
(80.2)
(36.036.1)
(81.4)
(85)
40.0 ,
40.1 ,
40.2 , D
40.3 , Streptococcus pneu-
moniae

40.8
40.9 ,

140

41
: (49.9)
(75.3)
:
, -
(0307, 08.0)
(88.0)
, -
(80.2)
( )():
(42.7)
(22.7)
(37.7)
Erysipelothrix (26.7)
(28.2)
(54.8)
- (00.7)
(32.7)
(39.239.4)
(36.)
(81.4)
(85)
(40.)
(21.7)
:
(24.1)
(20.7)
(48.3)
41.0 , Staphyloccocus aureus
41.1 , -

, -

41.2 , -

41.3 , Haemophilus influen-
zae

141

41.4 ,
: (48.0)
41.5 , -

, -

41.8
41.9 ,

42
: (47.1)
42.0
42.1
42.2
42.7
42.8
42.9 ,

43
43.0
43.1
43.8
43.9 ,

44
44.0
Oroya
44.1

44.8

142

44.9 ,

46
: -
(86.8)

48 ,

: (47.1)
48.0
(-) Clostridium:


48.1
48.2 [
Pontiac]
48.3
: (R57.8)
(41.9)
48.4
, Haemophilus aegyptius
48.8

49

: -
, (95
96)
,
(74.9)
(39.9)
,
(79.9)
,
(69.9)

143

49.0 ,
49.1 ,
49.2 , Haemophilus influen-
zae,
49.3 , , -

49.8 -

49.9 ,

,

(5064)
: ,
[HIV] (2024)
(N34.1)
Reiter (02.3)

A50
50.0
,

():



(-):





144

50.1
, , -
-

50.2 ,
,
50.3

(H19.2*)
, (H58.8*)
: Hutchinson (50.5)
50.4 [ -
]

(-):



(-):
(G05.0*)
(G01*)
(G63.0*)

-
.
: Hutchinson (50.5)

145

50.5 -

, --
-

Clutton (M03.1*)
Hutchinson-(-):


(-) (-):
(I98.*)
:
(M03.1*)
(M90.2*)

50.6
, , -
--
-
50.7 ,
-
50.9 ,

51
51.0

51.1
51.2
51.3

(-):
(L99.8*)
(L99.8*)

146

51.4
(-)(-) (-)(-):
(N74.2*)
(H22.0*)

(G01*)
(M63.0*)
, (H58.8*)
(M90.1*)
51.5
(), ,
--
- -

51.9 ,
52
52.0 -
- (I98.0*)
(-):
(I79.0*)
(I39.1*)
(I79.1*)
(I68.1*)
(I39.8*)
(I41.0*)
(I32.0*)
(I39.3*)
52.1
Charcot (M14.6*)
(-) (-):
(H94.0*)
(G05.0*)
(G01*)
(H48.0*)
(G63.0*)
(H48.1*)
(G22*)

147

52.2
52.3 ,
()
()

52.7
(N08.0*)
() ,

52.052.3
(-)(-) (-)(-):
(M73.1*)
(H32.0*)
(H19.0*)
(N74.2*)
(L99.8*)
, (H58.8*)
(K67.2*)
() ( ):
(M90.2*)
(K77.0*)
(J99.8*)
(M63.0*)
(M68.0*)
52.8
(), ,
--
, -

52.9 ,

53
53.0 ,


148

53.9 ,
, Treponema pallidum
()
: -
(50.2)

54
54.0 -
- -

:




: :
- (54.1)
(54.1)
54.1 -
-


54.2
-
(-):
(N51.1*)
(N74.3*)
(N51.1*)
(N51.0*)
: (A54.8)
54.3
:
(H13.1*)
(H22.0*)

149

54.4 - -

:
(M01.3*)
(M73.0*)
(M90.2*)
(M68.0*)
(M68.0*)
54.5
54.6
54.8
(-)(-):
(G07*)
(I39.8*)
(G01*)
(I41.0*)
(I32.0*)
(K67.1*)
(J17.0*)


: (A54.2)
54.9 ,

55 ()

Durand-Nicolas-Favre

150

56 ,

: , , -
Chlamydia trachomatis
: (-):
(55)
(-):
(39.1)
(23.1)
, 74.
56.0 -
-
:




56.1
-
(-):
(N51.1*)

(N74.4*)
(N51.1*)
56.2 - ,

56.3
56.4
56.8 ,

57

151

58 ,

59
: (07.8)
59.0
()
(N51.0*) Trichmonas (vaginalis)
59.8
59.9 ,

60 -
[herpes simplex]
60.0 -
-
:
(N77.1N77.1*)
(N51.*)
60.1 -

60.9 - , -

63 ,
,
: (08.1)
(D26.0)
63.0 ()
63.8 ,

152

64 ,
,

,

(6569)
: (27.)
(5053)

65
Bejel

Njovera

66
: bouba
()
pian
66.0

,

,
66.1 --



153

66.2
- -

() () ()
() ()

66.3

() ()


66.4

()
66.5

66.6


() ()
()

()

66.7


66.8
, , -

66.9 ,

67 []
67.0
()
[]
()

154

67.1


[]


67.2
- (I98.1*)
:
[]


67.3

[]
67.9 ,

68
:
: (69.2)
68.0
, Borrelia recurrentis
68.1
, Borrelia, -
Borrelia recurrentis
68.9 ,

69 ,

69.0



155

69.1 Vincent

():



- Vincent:


69.2
, Borrelia burg-
dorferi
69.8
69.9 ,

,

(7074)
70 ,
Chlamydia psittaci


71
: (94.0)
71.0

71.1
()
:


71.9 ,

156

74 ,

: (J16.0)
(-) (-):
(39.1)
(23.1)
, -
(5556)
74.0 (13.1*)

74.8
(K67.0*)
74.9 ,

(7579)
75
: , Ehrlichia sennetsu
(79.8)
75.0 ,
Rickettsia prowazekii
()
()
75.1 [ Brill]
Brill-Zinsser
75.2 , Rickettsia typhi
( )
75.3 , Rickettsia tsutsugamushi
()
(Tsutsugamushi)

157

75.9 ,
()

77
[ ]
77.0 , Rickettsia
rickettsii

Sao Paulo
77.1 , Rickettsia
conorii






77.2 , Rickettsia
siberica


77.3 , Rickettsia aus-
tralis

77.8
77.9 ,

78 -
, Coxiella burnetti

158

79
79.0


79.1 ,
Rickettsia akari
Kew Garden

79.8
, Ehrlichia sennetsu
79.9 ,
,



(8089)
: :
(91)
(94.1)

80
80.0 ,
80.1 ,

80.2 ,

80.3 ,
80.4
80.9 ,

159

81

: prion
81.0 Creutzfeldt-Jakob

81.1
Dawson-
Van Bogaert
81.2

81.8


81.9 -
,
Prion

82
82.0
82.1
82.9 ,

83 ,

: , -

: (92.2)
83.0
83.1
83.2
83.3 St Louis

160

83.4
, Kunjin-
83.5

La Crosse
83.6 , Rocio-
83.8 ,
83.9 , ,

84 ,

:
84.0 [ -
- ]
84.1
84.8
Louping
, Powassan-
84.9 ,

85 ,

: :
,
,
:
(G93.3)
, :
- [herpes simplex] (00.4)
- (05.0)
(26.2)
(80.)
- (02.0)
(87.2)

161

85.0 (G05.1*)

85.1 (G05.1*)

85.2 , , -

85.8

Economo-Cruchet

86 ,
:

87
: , :
- [herpes simplex] (00.3)
- (05.1)
(26.1)
(80.)
- (02.1)
87.0 (G02.0*)


87.1 (G02.0*)
87.2

87.8
87.9 ,

162

88
,

: :
(86)
(87.9)
88.0 [
]
88.1
88.8

89
,

,


(9099)
90 [ ]
: , dengue-
(91)

91 ,
dengue-

92 ,

: (33.1)

163

92.0 , Chikungunya-
Chikungunya
92.1 Onyong-nyong
92.2
(-) (-):

,
92.3 -
92.4 - [ ]
92.8 , -

92.9 , ,

93 ,
,
93.0 , -

93.1


93.2
93.8 , -

, Piry-
,
[ ]

94 ,
,

164

95
95.0

95.1
95.9 ,

96
96.0 Junin

96.1 Machupo

96.2 Lassa
96.8
96.9 ,

98 ,

: chikungunya (92.0)
dengue (91)
98.0 (
-)

98.1 Omsk
98.2 Kyasanur
98.3 Marburg
98.4 Ebola

165

98.5
:



, Hantaan-

98.8

99 ,

,

(0009)
00 - [herpes simplex]

: - (60.)
- (35.2)
-- (27.0)
(08.5)
00.0

00.1 -
:


:

() - 2

166

00.2 - -

-
00.3 - (G02.0*)
00.4 - (G05.1*)
-

00.5 -
-:
(H13.1*)
(H03.1*)
(H22.0*)
(H22.0*)
(H19.1*)
(H19.1*)
(H22.0*)
00.7 -
-
00.8 -
-(-):
(77.0*)

00.9 - ,

01 [varicella]
01.0 (G02.0*)
01.1 (G05.1*)


01.2 (J17.1*)
01.8
01.9

167

02 [herpes zoster]
:
zona
02.0 (G05.1*)

02.1 (G02.0*)
02.2 -

(-):
(G53.0*)
(G63.0*)
(G53.0*)
02.3
:
(H03.1*)
(H13.1*)
(H22.0*)
(H22.0*)
(H19.2*)
(H19.2*)
(H19.0*)
02.7
02.8
02.9

03 1

04 ,

1
1980 .
,
.

168

05
: morbilli
: (81.1)
05.0 , (G05.1*)

05.1 , (G02.0*)

05.2 , (J17.1*)

05.3 , (H67.1*)

05.4
05.8
(H19.2*)
05.9

06 [ ]
: (35.0)
06.0
:
(G05.1*)
(G02.0*)
(G05.1*)
06.8
(-):
(01.4*)
(J17.1*)
06.9

169

07
:


: () (63.0)
:
(D41.4)
(D26.0)
(D14.1)

08 ,

,

: , -
(93.8)
08.0


[ ]

: , -
(04)
08.1
08.2 ( )
08.3 ( )
08.4


08.5

170

08.8 , -



Tana-
Yaba-

09 ,
,

:


(1519)
: (25.1)
- [herpes simplex] (00.8)
(94.2)

15
15.0
15.9
() ()

16
16.0 - ()

16.1 - ()

16.2 -

171

16.9

()()

17
17.0 -() -

17.1
17.2
17.8
, ()(),

18
18.0 -
18.1 -

18.2
18.8
18.9 ,

19 ,
19.0
19.9

172

,
[HIV]
(2024)
: 2023 -

, -
-
.
: , -
[HIV] (Z21)

20 ,
[HIV],


: HIV (23.0)
20.0 , HIV, -

, HIV,
20.1 , HIV,

20.2 , HIV, -
-
20.3 , HIV,

20.4 , HIV, -

20.5 , HIV,

20.6 , HIV, -
, Pneumocystis carinii

173

20.7 , HIV, -

20.8 , HIV,

20.9 , HIV, -

, HIV, ,

21 ,
[HIV],


21.0 , HIV, Kaposi-

21.1 , HIV, Burkitt-

21.2 , HIV,

21.3 , HIV,
, -

21.7 , HIV, -

21.8 , HIV,

21.9 , HIV, -

174

22 ,
[HIV],


22.0 , HIV, -

HIV
22.1 , HIV,

22.2 , HIV,

, HIV, -

[ ]
22.7 , HIV, -
,
:


. 2.

23 ,
[HIV],

23.0 HIV-
23.1 , HIV, (-
)
23.2 , HIV, -
, -

23.8 , HIV,

175

24 ,
[HIV],

[]

- []


(2534)
25
: (35.1)
(27.1)
25.0 (J17.1*)
25.1 (K77.0*)
25.2 (K87.1*)
25.8
25.9 ,

26
: :


26.0 (N51.1*)
26.1 (G02.0*)
26.2 (G05.1*)
26.3 (K87.1*)

176

26.8
(-):
(M01.5*)
(I41.1*)
(N08.0*)
(G63.0*)
26.9 ,
:

27
:

Pfeiffer
27.0 --
, Epstein-Barr
27.1
27.8
27.9 ,

30
: , :
[herpes simplex] (00.5)
(02.3)
30.0 ,
(H19.2*)


30.1 , (H13.1*)


30.2

177

30.3
() (H13.1*)
, :
- 24
- 70
()()
30.8 (H13.1*)
Newcastle
30.9 ,

33 ,

33.0
Bornholm
33.1 Ross River

Ross River
33.2
33.3 , -


33.8

34

: (25.9)
- [herpes simplex]
(00.9)
(33.3)
, -
(97.)
34.0 ,

178

34.1 ,


34.2 ,
34.3 ,
34.4 ,
34.8 -

34.9 ,

(3549)
: ,
(J67.)
(G84.0)

35
:
, Epidermophy-
ton, Microsporum Trichophyton
, -
36.
35.0




35.1



179

35.2


35.3



35.4

35.5

35.6

35.8
:


35.9 ,

36
36.0
:


36.1



36.2

36.3
36.8
36.9 ,

180

37
:

: (37.5)
37.0

37.1
37.2
:


: (L22)
37.3 (N77.1*)



37.4
:
(N51.2*)
(N37.0*)
37.5 (G02.1*)
37.6 (I39.8*)
37.7
37.8
:


37.9 ,

38
38.0
38.1

181

38.2 ,
38.3
38.4 (G02.1*)
38.7

38.8
38.9 ,

39
39.0 , His-
toplasma capsulatum
39.1 ,
Histoplasma capsulatum
39.2 ,
39.3

39.4 ,

39.5 , Histoplasma duboisii

39.9 ,

40
: (41.)
(48.0)
40.0
40.1
40.2 ,
40.3

182

40.7

40.8
40.9 ,

41
:
Lutz
41.0
41.7

41.8
41.9 ,

42
42.0 (J99.8*)
42.1
42.7

42.8
42.9 ,

43
43.0

43.1

43.2
43.8
43.9 ,

183

44
:
44.0
44.1
44.2
44.7

44.8
44.9 ,

45
45.0
45.1
(G02.1*)

45.2
45.3
45.7

45.8
45.9 ,

46
46.0
46.1
46.2
46.3

46.4

184

46.5 ,
46.8

46.9 ,

47
47.0
,

47.1
47.9 ,

48 ,

48.0

Lobo
48.1
48.2
, Pseudallescheria boydii
: (47.0)
48.3

48.4
48.7
, ,

,
-
. -
,
.

185

48.8

49 ,


(5064)
: (06.)
(07.)

50 , Plasmodium
falciparum
: , -
Plasmodium falciparum -

50.0 , Plasmodium falciparum


50.8
, Plasmodium falciparum
,
Plasmodium falciparum,
50.9 , Plasmodium falciparum,

51 , Plasmodium
vivax
: , -
Plasmodium vivax
, Plasmodium
falciparum
: , Plasmodium falciparum
(50.)

186

51.0 , Plasmodium vivax -



51.8 , Plasmodium vivax -

51.9 , Plasmodium vivax

, Plasmodium vivax,

52 , Plasmodium
malaria
: , -
Plasmodium malariae
, Plasmodium falciparum
Plasmodium vivax
: Plasmodium:
falciparum (50.)
vivax (51.)
52.0 , Plasmodium malaria

52.8 , Plasmodium malariae

52.9 , Plasmodium malariae

, Plasmodium malariae,

53

53.0 , Plasmodium ovale
: Plasmodium:
falciparum (50.)
malariae (52.)
vivax (51.)

187

53.1 ,
: Plasmodium:
falciparum (50.)
malariae (52.)
ovale (53.)
vivax (51.)
53.8 , -

54 ,

55
55.0
-
--
55.1
55.2 -
55.9 ,

56
56.0
, Trypanosoma brucei gambiense
-
56.1
-
, Tripanosoma brucei rhodesiense
56.9 ,

, -

188

57 Chagas
:
, Trypanosoma cruzi
57.0 Chagas
(I41.2*, I98.1*)
Chagas :
, (I98.1*)
(I41.2*)
57.1 Chagas

Chagas
57.2 Chagas () -
(I41.2*, I98.1*)

Chagas () ():

, (I98.1*)
(I41.2*)
, -
Chagas
57.3 Chagas () -

57.4 Chagas () -

57.5 Chagas ()

58
: , Toxoplasma gondii
: (37.1)
58.0
(H32.0*)
58.1 (K77.0*)
58.2 (G05.2*)

189

58.3 (J17.3*)
58.8
:
(I41.2*)
(M63.1*)
58.9 ,
59
, Pneumocystis carinii

60 ,

: (07.2)
(07.3)
(A07.8)
60.0

60.1
, Acanthamoeba (H13.1*)
, Acanthamoeba (H19.2*)
60.2
(G05.2*)
60.8

64 ,

(6583)
65 []
:
65.0 , Schistosoma
haematobium [ ]

190

65.1 , Schistosoma man-


soni [ ]
65.2 , Schistosoma japo-
nicum [ ]
65.3

65.8
, Schistosoma:
intercalatum
mattheei
mekongi
65.9 ,

66
66.0
, :

Opisthorchis (felineus)(viverrini)
66.1
, -

, Clonorchis sinensis
,

66.2
, Dicrocoelium dendriticum
,
66.3
, Fasciola:
gigantica
hepatica
indica
,

191

66.4
, Paragonimus
,

66.5
, Fasciolopsis buski

66.8 ,





66.9 ,

67
: []
67.0 , chino-
coccus granulosus
67.1 , Echino-
coccus granulosus
67.2 , Echinococcus
granulosus
67.3 -
, Echinococcus granulosus
67.4 , Echinococcus granulosus,

67.5 , Echino-
coccus multilocularis
67.6 -
, Echinococcus multilocu-
laris

192

67.7 , Echinococcus multilocu-


laris,
67.8 ,
67.9 ,

68
: (69.)
68.0 , Taenia solium
()
68.1 , Taenia saginata
()
, Taenia saginata
68.9 ,

69
: ,
Taenia solium
69.0
69.1
69.8
69.9 ,

70
70.0
, Diphyllobothrium (latum)(pacificum)
( )
()
: (70.1)

193

70.1
, :
Sparganum (mansoni)(proliferum)
Spirometra larva

71 ,

71.0
()
()
71.1
()
71.8

71.9 ,
, ,

72

, Dracunculus medinensis

73
, Onchocerca volvulus

74
: (73)
()
(J82)
74.0 , Wuchereria bancrofti
:

194

74.1 , Brugia malayi


74.2 , Brugia timori
74.3

,
, Loa loa
74.4
, Mansonella:
zzardi
erstans
streptocerca
74.8

74.9 ,

75
, Trichinella species

76
:
76.0
, Ancylostoma species
76.1
, Necator americanus
76.8
76.9 ,

77
:

77.0

195

77.8
77.9 ,

78
: (81.2)
78.0
78.1
78.7
78.9 ,

79

80

()

81 ,

: , Para-
strongylus cantonensis (83.2)
81.0
, Anisakis
81.1

, Capillaria philippinensis
: (83.8)
81.2
81.3
, Parastrongylus costa-
ricensis

196

81.4
,
65.081.3 81.8

81.8
, :
Oesophagostomum []
Ternidens diminutus []

82 ,
82.0 ,
82.9 ,

83
: :
(81.1)
(81.1)
83.0 ,
[
Larva migrans]

83.1

83.2 a, Parastron-
gylus cantonensis
(G05.2*)
: (81.3)
83.3

83.4 (88.3)
: (88.3)
83.8

197





83.9 ,

: (82.0)

(8589)
85
85.0 , Pediculus humanus
capitis

85.1 , Pediculus humanus
corporis

85.2 ,
85.3
, :

Phthirius pubis
85.4
, -
85.085.3

86
,

87
: ,

198

87.0

87.1

87.2
87.3

87.4
87.8


87.9 ,

88
88.0

, :
Demodex species
Dermanyssus gallina
Liponyssoides sanguineus

: (86)
88.1 [ ]
88.2

88.3

: (83.4)
88.8
, Vandellia cirrhosa

199

88.9 ,
()

89 ,



(9094)
:
, 0089,
.
, , -
,
- , , -
.
, -

, . 2.

90
90.0

90.1 --

90.2 -

90.8 -

90.9

91

200

92

94

94.0
94.1
94.2
94.8

94.9

,

(9597)
: -
.
,
, -
.

95
,

95.0 , -

95.1 , -

95.2 D ,

95.3 Streptococcus pneumonia ,

201

95.4 , -

95.5 ,

95.6 Staphylococcus aureus ,

95.7 , -

95.8 ,

96
,
96.0 Mycoplasma pneumoniae [M. pneumoniae] -
,
Pleuro-pneumonia-like-organism [PPLO]
B96.1 Klebsiella pneumonia [K. pneumonia] -
,
96.2 Escherichia coli [E. coli] ,

96.3 Haemophilus influenzae [H. influenzae] -
,
96.4 Proteus (mirabilis)(morganii) -
,
96.5 Pseudomonas (aeruginosa)(mallei)(pseudomallei) -
,
96.6 Bacillus fragilis [B. fragilis] -
,
96.7 Clostridium perfringens [C. perfringens] -
,
96.8
,

202

97
,
97.0 , -

97.1 , -


-
97.2 , -

97.3 , -



97.4 -
,
97.5 ,

97.6 , -

97.7 , -

97.8 ,


(99)
99

203
II

(00D48)

:
0075 , -
,
, ()

0014 , -

1526 -

3039

4041

4344
4549 -

50

5158 -

6063 -

6468

6972 , -


7375

7680 , -

8196 , -
,

204

97 (-
)
D00D09 in situ
D10D36
D37D48
( . 280)

1. , , -

7680 -
,
, ,
.
.

2.
,
. -
-
, IV.
, ,
, 74,
27.5; , Cushing,
D35.2, 24.0.

3.
()
: , -
; ; ,
; ( );
; ;
.
- ,
, -
. -
.
II -
, , .

205


.
. 616643,
1, 2, ,
.

(),
, -
. 6 : -
;
( , , .. , in
situ, , -
); -
, -
.

4. II
-
.8 ( 5). ,
,
.7.

5. , -
.8
(, -
)
0075 -
().
,
. -
, -
,
, -
.8 (,
),
. ,
16.0 (), -
,
02.8. ,
, ,

206

02.1,
. ,
, -
( ).
, ,
(, 67.) -
,
.
,
, -
.
:
02.8 ,

08.8 ,

14.8 , ,
-

21.8 , , -

24.8 ,

26.8 ,

39.8 , -
-

41.8 ,

49.8 ,
-

57.8 , -

63.8 , -

68.8 ,

207

72.8 -
,

,
26.8 ( , -
).

6.

,

, (25.9).

7. -

, ,
,
.
3
. -
II -
, -
.

8.
()
II
, . -
,
- , -
II (0077, 80).

[ (), -
, in situ ].
( -
, , -
)
-
.

208


(0097)


,
(0014)
00

: (43.0, 44.0)
00.0
:


[vermilion border]
00.1
:



00.2 ,

00.3 ,
:


()

00.4 ,
:



209

00.5 , ,
, :




00.6
00.8 ,

[ 5 . 206]
00.9 ,

01



02

02.0
- ,
: (01)
02.1

02.2
- ,

02.3 - ,


02.4
: (09.9)

210

02.8 ,

[ 5 . 206]
,
-
0102.4
02.9 ,

03

:

:
(41.041.1)
03.0
03.1
03.9 ,

04

04.0
-
04.1
04.8 ,

[ 5 . 206]
04.9 ,

05

05.0

211

05.1
:
(11.3)
05.2 ()
05.8 ,

[ 5 . 206]
05.9 ,

06


06.0


06.1
() ()()
() ()()
06.2
06.8 ,
-

[ 5 . 206]
06.9 ,
,

07
()

212

08


:
,


(06.9)
(07)
08.0 ()

08.1 ()
08.8 ,
-

[ 5 . 206]
-
,
0708.1
08.9 ,
()

09
()
: (02.4)
(11.1)
09.0
09.1 () ()
09.8 ,

[ 5 . 206]

213

09.9 ,
:


10
()
: (09.)
10.0
10.1
,
- (-)
: () (32.1)
10.2
10.3
10.4
[ ]
10.8 ,

[ 5 . 206]

10.9 ,

11
()
11.0

11.1

214

11.2
Rosenmuller


11.3

()() -

:

()
11.8 ,

[ 5 . 206]
11.9 ,

12

13

: (12)
13.0
13.1 , -

:

()
: , -
(32.1)
13.2

215

13.8 ,

[ 5 . 206]
13.9 ,

14

,
: (06.9)
14.0 ,
14.2 Waldeyer ()
14.8 ,
,

[ 5 . 206]
,
, -
0014.2

216



(1526)
15

: -
:
.0.2
.3.5
,
,
,
, -
.
15.0
15.1
15.2
15.3
15.4
15.5
15.8 ,

[ 5 . 206]
15.9 ,

217

16

16.0




16.1
16.2
16.3

16.4


16.5 ,
, 16.116.4
16.6 ,
, 16.016.4
16.8 ,

[ 5 . 206]
16.9 ,

17

17.0 ()
17.1
17.2
: - (18.0)
17.3 Meckel

218

17.8 ,

[ 5 . 206]
17.9 ,

C18
()
18.0
-
18.1
18.2
18.3
18.4
18.5
18.6
18.7
()
: (19)
18.8 ,

[ 5 . 206]
18.9 ,

19


()

20
()

219

21

21.0 ,
: (-):
(43.5, 44.5)
(43.5, 44.5)
(43.5, 44.5)
21.1

21.2
21.8 ,
,

[ 5 . 206]


,
, -
2021.2

22


: (24.9)

(78.7)
22.0 ,


22.1

22.2
22.3
Kupffer

220

22.4
22.7
22.9 , -

23

24


: (22.1)
24.0




24.1 Vater
24.8 ,

[ 5 . 206]
,

,

22.024.1
24.9 -
,

25

25.0
25.1

221

25.2
25.3
25.4

25.7

25.8 ,

[ 5 . 206]
25.9 , -

26


: (48.)
26.0 ,

26.1
: Hodgkin (81.)
(8285)
26.8 ,
-

[ 5 . 206]
-
,
1526.1
: (16.0)
26.9 -


222



(3039)
:
: (45.)

30

30.0



()

: (41.0)
(76.0)
(72.2)

(11.3)
(43.3, 44.3)
30.1



: () (43.2, 44.2)
() (41.0)
(49.0)
() (43.2, 44.2)

31

31.0
( Highmore) ()
31.1

223

31.2
31.3
31.8 ,

[ 5 . 206]
31.9 , -

32

32.0
()
()
32.1
,
( )


()

: (10.1)
:
(13.1)
(13.1)
(13.1)
32.2
32.3
32.8 ,

[ 5 . 206]
32.9 , -

224

33

34

34.0

( )
34.1 ,
34.2 ,
34.3 ,
34.8 ,

[ 5 . 206]
34.9 ,

37

38
,
: (45.)
38.0

: (49.3)
38.1
38.2
38.3 ,
38.4

225

38.8 ,
,

[ 5 . 206]

39


: (76.1)
(76.1)
39.0 ,
39.8 ,


[ 5 . 206]

,
3039.0
39.9



(4041)
: (96.7)
(49.)

40


40.0 ()

226

40.1
40.2
40.3
40.8 ,
-

[ 5 . 206]
40.9 , -

41


: (40.)
:
(49.0)
(32.3)
(40.)
(30.0)
41.0
() ()

: , -
:
(31.0)
(03.0)
() (41.1)
41.1 ()

: , -
:
(03.9)
(03.1)
(41.0)

227

41.2
: (41.4)
41.3 ,
41.4 ,
41.8 ,
-

[ 5 . 206]
-
, -
4041.4
41.9
,



(4344)
43
: 872879 -
/3
:
(5152, 60., 63.)
43.0
: (00.000.2)
43.1 ,

43.2

43.3

228

43.4 -

43.5
:




: (21.0)
43.6 , -

43.7 , -

43.8 ,


[ 5 . 206]
43.9 ,
()

44

: :


: Kaposi (46.)
(43.)
(5152, 60.,
63.)
44.0

:
(00.)

229

44.1 , -

: (49.0)
44.2
: (49.0)
44.3
44.4
44.5
:




: (21.0)
44.6 ,

44.7 , -

44.8 ,

[ 5 . 206]
44.9 , -



(4549)
45
: 905
/3

230

45.0
:
(38.4)
45.1



()()
: -
(48.)
45.2
: -
(38.0)
45.7
45.9 ,

46 Kaposi
: 9140
/3
46.0 Kaposi
46.1 Kaposi
46.2 Kaposi ()
46.3 Kaposi
46.7 Kaposi
46.8 Kaposi
46.9 Kaposi,

47


:

231

47.0 ,
: (69.6)
47.1 ,

47.2 ,

47.3
47.4
47.5
47.6 -
,
47.8 ,
-

[ 5 . 206]
47.9 ,

48

: Kaposi (46.1)
(45.)
48.0
48.1



:


48.2 ,

232

48.8 ,
-

[ 5 . 206]

49

:




,



( )
: :
(4041)
(32.3)
(30.0)
(50.)
Kaposi (46.)
(45.)

(47.)
(48.)
(48.0)
49.0 ,

:


: (69.6)
49.1 ,

49.2 ,

233

49.3



: (50.)
(38.0)
(38.138.3)
(37)
49.4


49.5



49.6 , -


49.8 ,


[ 5 . 206]

, -
4749.6
49.9 , -

234



(50)
50

:
: (43.544.5)
50.0
50.1
50.2
50.3
50.4
50.5
50.6
50.8 ,

[ 5 . 206]
50.9 ,

235



(5158)
:

51

51.0 ()

51.1
51.2
51.8 ,

[ 5 . 206]
51.9 ,

52
()

53
()
53.0
53.1
53.8 ,

[ 5 . 206]
53.9 ,

236

54

54.0

54.1
54.2
54.3 ()
54.8 ,

[ 5 . 206]
54.9 ,

55

56

57


57.0


57.1
57.2
57.3

57.4 ,
57.7

237

57.8 ,

[ 5 . 206]
,

5157.7, 58
-
-
57.9 ,
-

58



: () (D39.2)
:
(O01.9)
(D39.2)
(D39.2)



(6063)
:

60

60.0

60.1
60.2

238

60.8 ,

[ 5 . 206]
60.9 ,

61

62

62.0
[ ]
[ ]
62.1

62.9 , -

63


63.0
63.1
63.2

63.7
( )

239

63.8 ,

[ 5 . 206]
,

6063.7
63.9 ,
-



(6468)
64
,

: :
(65)
(65)

65


66

: (67.6)

67

67.0

240

67.1
67.2
67.3
67.4
67.5

67.6 ()
67.7
67.8 ,

[ 5 . 206]
67.9 ,

68


: - :
(57.9)
(63.9)
68.0
: (67.5)
68.1
68.8 ,

[ 5 . 206]
,

6468.1
68.9 -
,

241


,

(6972)
69

: (49.0)
(43.1, 44.1)
(72.3)
69.0
69.1
69.2
69.3
69.4

69.5


69.6





: (41.0)
69.8 ,
-

[ 5 . 206]
69.9 ,

242

70
()
70.0
70.1
70.9 , -

71

: (72.272.5)
(69.6)
71.0 , ()
()
(Corpus callosum)
()
71.1
71.2
71.3
71.4
71.5
: (71.7)
71.6
71.7

()
71.8 ,

[ 5 . 206]
71.9 ,

243

72
,


: (70.)
-
(47.)
72.0
72.1 ( )
72.2 ()

72.3
72.4
72.5

72.8 ,


[ 5 . 206]

,
-
7072.5
72.9 ,

244

(7375)
73

74

74.0 ()
74.1
74.9 ,

75


: (74.)
(25.4)
(56)
(62.)
(37)
(73)
75.0
75.1
75.2
75.3 ()
75.4
75.5

245

75.8 , -

:
,
.
75.9
,


,

(7680)
76

: ():
:
(57.9)
(63.9)
, -
(8196)
(80)
76.0 ,


76.1



76.2

246

76.3

, , :
()
()
76.4
76.5
76.7
76.8 ,
-

[ 5 . 206]

77

:
, (8188,
96.)
77.0 ,

77.1
77.2
77.3 -


77.4

77.5
77.8
77.9 ,

247

78


78.0

78.1 -

78.2 -

78.3

78.4 -

78.5 -

78.6 -


78.7 -

78.8

79

79.0 -

79.1 -
,

248

79.2 -

79.3 -

79.4

79.5

79.6 -

79.7 -

79.8

80




:
() ()




249


,

(8196)
: , 8285 -
, ,
-
. , -
,
, ;
-
.
: 959994
/3
:
(77.)

81 Hodgkin
: 965966 -
/3
81.0
-
81.1
81.2
81.3
81.7 Hodgkin
81.9 Hodgkin,

250

82 []

:

969
/3
82.0 ,
82.1 , -
,
82.2 ,
82.7
82.9 ,

83
: 9593, 9595, 967
968 -
/3
83.0 ()
83.1 ()
83.2 , ()
83.3 ()

83.4 ()
83.5 ()
83.6 ()
83.7 Burkitt
83.8
83.9 ,

251

84 -

: 970
/3
84.0 Mycosis fungoides
84.1 Sezary
84.2 -
84.3
Lennert
84.4 -
84.5 -
: -
-
, -
.

85

: 95909592, 9594,
971 -
/3
85.0
85.1 - ,
: -
-
, -
.
85.7
:


252

85.9 ,


88

: 976
/3
88.0 Waldenstrom
88.1 -
88.2 -
Franklin
88.3

88.7 -

88.9 , -

90

: 973, 9830
/3
90.0
Kahler

: (90.2)
90.1
90.2 ,


253

C91
: 982, 99409941
/3
91.0
: -
(91.1)
91.1
91.2
91.3
91.4

91.5 -
91.7
91.9 ,

92
: :


986988, 9930
/3
92.0
: -
(92.1)
92.1
92.2
92.3


92.4
92.5

254

92.7
92.9 ,

93
:
989
/3
93.0
: -
(93.1)
93.1
93.2
93.7
93.9 ,

94
: 984, 9850, 9900,
9910, 99319932
/3
: (91.4)
(90.1)
94.0

Di Guglielmo
94.1
Heilmeyer-Schner
94.2
:
()
()
94.3
94.4

255

94.5
94.7

95
: 980
/3
95.0


: -
(95.1)
95.1
95.2
95.7
95.9 ,

96
,

: 972, 974 -
/3
96.0 Letterer-Siwe
:


96.1

256

96.2
(-):



: (94.3)
() (Q82.2)
96.3
96.7
,
96.9 , -
,


()

(97)
97
()

:
-
, 2.

257

in situ
(D00D09)
: in situ -

. , -
(CIN) , -
(CIN III) -
, in situ.
.
-
III -
; I II

, .
: Bowen

-
/2
Queyrat

D00 in situ ,

: in situ (D03.)
D00.0 ,
:

,


: , -
(D02.0)
:
(D02.0)
(D02.0)
(D03.0, D04.0)
D00.1
D00.2

258

D01 in situ

: in situ (D03.)
D01.0
: (D01.1)
D01.1
D01.2
D01.3
: :
(D03.5, D04.5)
(D03.5, D04.5)
(D03.5, D04.5)
D01.4
: Vater (D01.5)
D01.5 ,
Vater
D01.7

D01.9 ,

D02 in situ

: in situ (D03.)
D02.0
,
( )
: :
(D00.0)
, (D00.0)
(D00.0)
D02.1
D02.2

259

D02.3



: () () (D03.2, D04.2)
:
(D09.7)
(D03.3, D04.3)
D02.4 ,

D03 in situ
: 872879 -
/2
D03.0 in situ
D03.1 in situ ,

D03.2 in situ
D03.3 in situ

D03.4 in situ

D03.5 in situ
:


()( )

D03.6 in situ ,

D03.7 in situ ,

D03.8 in situ
D03.9 in situ,

260

D04 in situ
: Queyrat () (D07.4)
in situ (D03.)
D04.0
: (D00.0)
D04.1 ,
D04.2
D04.3
D04.4
D04.5
:




: (D01.3)
(D07.)
D04.6 ,

D04.7 , -

D04.8
D04.9 ,

D05 in situ
: in situ
(D04.5)
in situ ()
(D03.5)
D05.0 in situ
D05.1 in situ
D05.7 in situ

261

D05.9 in situ ,

D06 in situ

:
[CIN], III ,

: in situ (D03.5)
(N87.2)
D06.0
D06.1
D06.7
D06.9 ,

D07 in situ

: in situ (D03.)
D07.0
D07.1
[VIN], III ,

: (N90.2)
D07.2
[VIN], III
,
: (N89.2)
D07.3
D07.4
Queyrat
D07.5
D07.6

262

D09 in situ

: in situ (D03.)
D09.0
D09.1
D09.2
: (D04.1)
D09.3
: (D01.7)
(D07.3)
(D07.6)
D09.7 in situ
D09.9 in situ,


(D10D36)
: -
/0

D10
,
D10.0
()( )()( )
: (D22.0, D23.0)
D10.1
[Tonsilla Lingualis]
D10.2

263

D10.3

: -
(D16.4, D16.5)
(D10.0)

(D10.6)
D10.4 ()
() ()
: (D10.1)
(D10.6)
:
(D10.5)
(D10.5)
D10.5
,
:



: :
(D14.1)
(D14.1)
D10.6


D10.7
D10.9 ,

D11

: -
, -
-


(D10.3)

264

D11.0
D11.7
:


D11.9 ,

D12
, ,

D12.0

D12.1
D12.2 ()
D12.3 ()


D12.4 ()
D12.5
D12.6 ,


()
D12.7
D12.8
D12.9
: :
(D22.5, D23.5)
(D22.5, D23.5)
(D22.5, D23.5)

265

D13


D13.0
D13.1
D13.2 ()
D13.3
D13.4

D13.5
D13.6
: (D13.7)
D13.7


D13.9 -



266

D14

D14.0 ,

: () (D22.2, D23.2)
:
(D16.4)
(D16.4)
(D21.0)
()() (D22.2, D23.2)
:
(D36.7)
(D22.3, D23.3)
(D33.3)
:
(J33.8)
() (H74.4)
() (J33.)
(D10.6)
D14.1
( )
: , (D10.5)
(J38.1)
D14.2
D14.3
D14.4 ,

D15


: (D19.)
D15.0
D15.1
: (D21.3)

267

D15.2
D15.7
D15.9 ,

D16

: :
(D21.0)
(D21.0)
(D14.1)
(D14.0)
(D21.)
D16.0
D16.1
D16.2
D16.3
D16.4
()

: (D16.5)
D16.5
D16.6
: (D16.8)
D16.7 ,
D16.8 ,
D16.9 ,

D17

: 885888 -
/0

268

D17.0 -
, -

D17.1 -

D17.2 -

D17.3 -
-

D17.4 -

D17.5 -

: (D17.7)
D17.6 -

D17.7 -



D17.9 -
,

D18

: 912917 -
/0
: (D22.)
D18.0

269

D18.1

D19

: 905
/0
D19.0
D19.1
D19.7
D19.9 ,

D20


: -

(D17.7)
(D19.)
D20.0
D20.1

270

D21


:




,



( )
: :
(D16.)
(D14.1)
(D14.0)
(D24)
(D18.0)
(D17.)
(D18.1)
-
(D36.1)
(D20.1)
(D20.0)
:
(D25.)
(), (D28.2)
(D18.)
D21.0 , -

:


: (D31.6)
D21.1 -
,

271

D21.2 -
,
D21.3




: (D15.1)
(D15.2)
(D15.0)
D21.4
D21.5
: :
(D25.)
(), (D28.2)
D21.6 , -


D21.9 ,

D22
: 872879 -
/0
:




D22.0
D22.1 , -

D22.2 -

272

D22.3

D22.4

D22.5
:




D22.6 , -

D22.7 , -

D22.9 ,

D23

: :



: -
(D17.0 D17.3)
(D22.)
D23.0
: (D10.0)
D23.1 , -

D23.2
D23.3
D23.4

273

D23.5
:




: (D12.9)
(D28 D29)
D23.6 ,

D23.7 , -

D23.9 ,

D24

:


: -
(N60.)
(D22.5, D23.5)

D25
:
889 -
/0

D25.0
D25.1
D25.2
D25.9 ,

274

D26

D26.0
D26.1
D26.7
D26.9 ,

D27

D28


:

D28.0
D28.1
D28.2

() ()
D28.7
D28.9 ,

D29

:
D29.0

275

D29.1
: ()
(N40)
:
(N40)
(N40)
(N40)
D29.2
D29.3
D29.4

D29.7



D29.9 ,

D30

D30.0
: :
(D30.1)
(D30.1)
D30.1
D30.2
: (D30.3)
D30.3
:


D30.4
: (D30.3)
D30.7

276

D30.9 ,

D31

: (D21.0)
(D33.3)
(D22.1, D23.1)
D31.0
D31.1
D31.2
D31.3
D31.4

D31.5

-
D31.6 ,





: (D16.4)
D31.9 ,

D32
()
D32.0
D32.1
D32.9 ,

277

D33


: (D18.0)
(D32.)
-
(D36.1)
(D31.6)
D33.0 ,







: (D33.1)
D33.1 ,



D33.2 ,
D33.3

D33.4
D33.7 -

D33.9 , -

()

D34

278

D35

: (D13.7)
(D27)
(D29.2)
(D15.0)
D35.0
D35.1
D35.2
D35.3
D35.4 ()
D35.5
D35.6
D35.7
D35.8
D35.9 ,

D36

D36.0
D36.1
: (D31.6)
D36.7

D36.9 ,

279



(D37D48)
: D37D48 -
, ..
-
. -
-
/1.

D37


D37.0 ,
:





: , -
(D38.0)
:
(D38.0)
(D38.0)
(D48.5)
D37.1
D37.2
D37.3
D37.4
D37.5

280

D37.6 ,
Vater
D37.7
:






: :
(D48.5)
(D48.5)
(D48.5)
D37.9 ,

D38
,


: (D48.7)
D38.0
,
( )
: :
(D37.0)
(D37.0)
(D37.0)
D38.1 ,
D38.2
D38.3
D38.4

281

D38.5




: ()() (D48.5)
:
(D48.7)
(D48.5)
D38.6 ,

D39


D39.0
D39.1
D39.2
()



: (O01.9)
D39.7

D39.9 ,

D40


D40.0
D40.1
D40.7

282

D40.9 ,

D41


D41.0
: (D41.1)
D41.1
D41.2
D41.3
D41.4
D41.7
D41.9 ,

D42


D42.0
D42.1
D42.9 ,

283

D43


: -
(D48.2)
D43.0 ,







: (D43.1)
D43.1 ,



D43.2 ,
D43.3
D43.4
D43.7 -

D43.9 ,
()

D44


: (D37.7)
(D39.1)
(D40.1)
(D38.4)
D44.0

284

D44.1
D44.2
D44.3
D44.4
D44.5 ()
D44.6
D44.7
D44.8

D44.9 ,

D45
9950 -
/1

D46
: 998
/1
D46.0 ,

D46.1
D46.2
D46.3

D46.4 ,
D46.7
D46.9 ,

()

285

D47
,

: 974, 976, 996
997 -
/1
D47.0 -



: () (Q82.2)
D47.1
( )
,
()
D47.2
D47.3 ()

D47.7
, -

D47.9 -
,
,

D48


: ( ) (Q85.0)

286

D48.0
: :
(D48.1)
(D38.0)
(D38.5)
(D48.1)
(D48.1)
D48.1
:


: :
(D48.0)
(D38.0)
(D38.5)

(D48.6)
D48.2
: (D48.7)
D48.3
D48.4
D48.5
:




: (D37.7)
(D39.7, D40.7)
(D37.0)
D48.6

()
: (D48.5)

287

D48.7



: (D48.1)
(D48.5)
D48.9 -
,



288
III

,
,

(D50D89)
: () (M35.9)
,
(P00P96)
,
(O00O99)
,
(Q00Q99)
, -
(E00E99)
, -
[HIV] (B20B24)
, -
(S00T98)
(C00D48)
, ,
, -
(R00R99)


:
D50D53 ,
D55D59
D60D64
D65D69 , -

D70D77
D80D89 ,

:
D63* ,
D77* -
,

289

,
(D50D53)
D50
: :


D50.0 , ,
()
()
: (D62)
,
(P61.3)
D50.1
Kelly-Paterson
Plummer-Vinson
D50.8
D50.9 ,

D51 B12-
: B12 (E53.8)
D51.0 B12- , -

:
Addison
Biermer
()

D51.1 B12- , -

B12
Immerslund (-Grasbeck)

290

D51.2 II
D51.3 B12- ,


D51.8 B12-
D51.9 B12- ,

D52
D52.0 ,

D52.1 , -



( XX).
D52.8
D52.9 ,
, ,

D53 ,
: , -
B12
D53.0 ,


: Lesch-Nyhan (E79.1)
D53.1 ,


: Di Guglielmo (C94.0)
D53.2
: (E54)

291

D53.8 ,
, :



: , -
, :
(E61.0)
(E61.5)
(E60)
D53.9 , ,

: (D64.9)


(D55D59)
D55 ,

: , -
(D59.2)
D55.0 , -6--
[G6PD]

G6PD-
D55.1 , -

, ( G6PD),
(HMP) -

, (), I

292

D55.2 ,

:
, (), II

-
-
D55.3 ,

D55.8 ,
D55.9 , , -

D56
D56.0
: ,
(P56.)
D56.1
Cooley

-



D56.2 -
D56.3
D56.4
[HPFH]
D56.8
D56.9 ,
( )
()()( )

293

D57 -
: (D58.)
- (D56.1)
D57.0 -
Hb-SS
D57.1 -
-(-):



D57.2 - -

:
Hb-SC
Hb-SD
Hb-SE
D57.3
Hb-S
S
D57.8 -

D58

D58.0
()
()
Minkowski-Chauffard
D58.1
()
()()

294

D58.2

Heinz
:
Hb-C
Hb-D
Hb-E


: (D75.0)
Hb-M (D74.0)
-
(D56.4)
(D75.1)
(D74.)
D58.8

D58.9 ,

D59
D59.0


( XX).
D59.1
( )( )
, -

:


:
()()
()()
: Evans (D69.3)

(P55.)

(D59.6)

295

D59.2 -




( XX).
D59.3 -
D59.4
:



-
( XX).
D59.5 [
Marchiafava-Micheli]
: (R82.3)
D59.6 ,

:



-
( XX).
: (R82.3)
D59.8
D59.9 ,
,

296


(D60D64)
D60 ()
[]
: ()( -
)( )
D60.0 () -

D60.1 () -

D60.8 ()
D60.9 () , -

D61
: (D70)
D61.0
() :



Blackfan-Diamond

Fanconi

D61.1


( XX).
D61.2 , -

-
( XX).

297

D61.3
D61.8
D61.9 ,


D62
: ,
(P61.3)

D63* , -

D63.0* (C00D48)
D63.8* , -

D64
: :
(D46.4)
(D46.2)
(D46.3)
(D46.1)
(D46.0)
D64.0
,
D64.1 ,

-
.
D64.2 ,

-
( XX).

298

D64.3
:

,
D64.4
()
: Blackfan-Diamond (D61.0)
Di Guglielmo (C94.0)
D64.8


D64.9 ,

,

(D65D69)
D65
[ ]
,

[DIC]
,
:


: ( ):
, -
(O00O07, O08.1)
(P60)
, -
(O45.0, O46.0, O67.0, O72.3)

299

D66 VIII
VIII ( )
:



: VIII
(D68.0)

D67 IX
Christmas
:
IX ()

o B

D68
: , :
, -
(O00O07, O08.1)
,
(O45.0, O46.0, O67.0, O72.3)
D68.0 von Willebrand

VIII

: ()
(D69.8)
VIII:
(D66)
(D66)
D68.1 XI
C

300

D68.2 -


:
AC

:
I []
II []
V []
VII []
X [Stuart-Prower]
XII [Hageman]
XIII []
()

Owren
D68.3 , -


:

-VIIIa
-IXa
-Xa
-XIa
-

( XX).
D68.4 -

, :

K
: K (P53)
D68.8

[SLE]

301

D68.9 ,

D69
:
(D89.0)
(D89.1)
()
(D47.3)
(D65)

(M31.1)
D69.0
:

Henoch(-Schonlein)
:




D69.1
Bernard-Soulier [ ]
Glanzmann

()()

: von Willebrand (D68.0)
D69.2
:



D69.3
Evans

302

D69.4
:
(Q87.2)

(P61.0)
Wiskott-Aldrich (D82.0)
D69.5
-
( XX).
D69.6 ,
D69.8
()

D69.9 ,



(D70D77)
D70


Kostmann
:





()



, , -
( XX).
: (P61.5)

303

D71
-

( )

D72

: (D75.8)
(D80D89)
(D70)
() (D46.9)
D72.0
( )( ) :
Alder
May-Hegglin
Pelger-Huet
:
:



: Chediak(-Steinbrinck)-Higashi
(E70.3)
D72.1
:

304

D72.8 -

:




()

()

D72.9 ,

D73
D73.0
,

: () (Q89.0)
D73.1
: :
(R16.1)
(Q89.0)
D73.2
D73.3
D73.4
D73.5
,

: (S36.0)
D73.8



D73.9 ,

305

D74
D74.0
NADH-
M [ Hb-M]
,
D74.8
( )

-
( XX).
D74.9 ,

D75

: (R59.)
(D89.2)
:
(I88.9)
(L04.)
(I88.1)
()() (I88.0)
D75.0
:


: (D58.1)

306

D75.1
:

:








: :
(P61.1)
vera (D45)
D75.2
: ()
(D47.3)
D75.8 -


D75.9 , -

D76 ,


: Letterer-Siwe (C96.0)
(C96.1)
:
(C96.1)
(C91.4)
(I89.8)
(C85.7)
(C96.0)

307

D76.0 Langerhans, -


Hand-Schuller-Christian
X ()
D76.1

,
Langerhans
D76.2

.
D76.3
()

D77* -
,

[] (B65.)

,

(D80D89)
:
, , -
[HIV]

: () (M35.9)
- -
(D71)
, -
[HIV] (B20B24)

308

D80

D80.0
( )
X- [Bruton] (
)
D80.1
B-, -

[CVAgamma]

D80.2 A [IgA]
D80.3 -
G [IgG]
D80.4 M [IgM]
D80.5 M [IgM]
D80.6 -


D80.7
D80.8

-
D80.9 -
,

D81

:
( ) (D80.0)
D81.0 -

309

D81.1 -
T- B-
D81.2 -
B-
D81.3 [ADA]
D81.4 Nezelof
D81.5 -- [PNP]
D81.6
I

D81.7
II
D81.8
-
D81.9 ,

D82 , -

: - [Louis-Bar] (G11.3)
D82.0 Wiskott-Aldrich

D82.1 Di George

:


D82.2
D82.3 -
, Epstein-Barr
X-
D82.4 E [IgE]

310

D82.8 , -

D82.9 , ,

D83
D83.0 -
B--

D83.1 -
T-
D83.2 -
B- T-
D83.8

D83.9 ,

D84
D84.0 -1 [LFA-1]

D84.1
C1 [C1-INH]
D84.8
D84.9 ,

D86
D86.0
D86.1
D86.2

D86.3

311

D86.8
(H22.1*)
-
(G53.2*)
(-):
(M14.8*)
(I41.8*)
(M63.3*)
[Heerfordt]
D86.9 ,

D89
,

: (R77.1)
(D47.2)

(T86.)
D89.0


D89.1
:





(-):


D89.2 ,
D89.8 ,
,
D89.9 , , -

312
IV

,


(E00E90)

: , ,
, II. -
(. E05.8, E07.0, E16E31, E34.),

-
, -
,
,
.
: ,
(O00O99)
, ,
, -
(R00R99)
-
, -
(P70P74)

:
E00E07
E10E14
E15E16 -

E20E35
E40E46
E50E64
E65E68
E70E90

313

:
E35* , -

E90*
,


(E00E07)
E00
: ,
, -
,
.

, -
-
.
.

(F70F79).
: - -
(E02)
E00.0 - ,

,
E00.1 - ,
:


E00.2 - ,
,
E00.9 - ,
-

314
,

E01 ,
,

: - (E00.)
- -
(E02)
E01.0 () , -

E01.1 () ,

,
E01.2 (), , -


E01.8 ,

,

E02 ,

E03
: ,
(E00E02)

(E89.0)
E03.0
() :


:
(P72.0)

315

E03.1
( )
:


E03.2 ,

-
( XX).
E03.3
E03.4 ()
:
(E03.1)
E03.5
E03.8
E03.9 ,

E04
: :

(03.0)

, (E00E02)
E04.0
:
()

E04.1
()()

()

316
,

E04.2

()
E04.8
E04.9 ,

()

E05 []
: -
(E06.2)
(P72.1)
E05.0

Graves

E05.1 -


E05.2

E05.3
E05.4 , (factitia)
E05.5
E05.8

-
( XX).
E05.9 ,

(I43.8*)

317

E06
: (O90.5)
E06.0
:



(B95B97).
E06.1
:
de Quervain



: (E06.3)
E06.2
: ((E06.3)
E06.3
Hashimoto
()



E06.4


( XX).
E06.5
:
:



Riedel
E06.9 ,

318
,

E07
E07.0
C-

E07.1

Pendred
:
(P72.0)
E07.8
-




E07.9 ,

319


(E10E14)
, -
,
( XX).
E10E14:
.0
:




.1
:



.2
(N08.3*)
(N08.3*)
Kimmelstiel-Wilson (N08.3*)
.3
:
(H28.0*)
(H36.0*)
.4
:
(G73.0*)
(G99.0*)
(G59.0*)
(G63.2*)
(G99.0*)
.5
:

(I79.2*)

320
,

.6
(M14.2*)
(M14.6*)
.7
.8
.9

E10
[ - ]
:



I
: ():
(E12.)
(P72.2)
,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(E89.1)

321

E11
[ - ]
: ()( )( -
):



II

: ():
(E12.)
(P70.2)
,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(E89.1)

E12 ,

[ - ]
: , -
:


: ,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(P70.2)
(E89.1)

322
,

E13
[ - ]
: ():
(E10.)
(E12.)
(P70.2)
(E11.)
,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(E89.1)

E14 ,
[ - ]
:
: ():
(E10.)
(E12.)
(P70.2)
(E11.)
,
(O24.)
:
(R81)
(E74.8)
(R73.0)
(E89.1)

323




(E15E16)
E15
-




, ,
( XX).

E16

E16.0


( XX).
E16.1

:


-

E16.2 ,
E16.3
-

324
,

E16.4

ZollingerEllison
E16.8 -

:
-



E16.9 -
,

(E20E35)
: (N64.3)
(N62)

E20
: Di George (D82.1)
-
(E89.2)
(R29.0)
-
(P71.4)
E20.0
E20.1
E20.8

325

E20.9 ,

E21


: :
(M83.)
(E55.0)
E21.0

( von Reck-
linghausen)
E21.1 ,

:
(N25.8)
E21.2
:
(E83.5)
E21.3 ,
E21.4

E21.5 , -

E22
: Cushing (E24.)
Nelson (E24.1)
:
ACTH, Cushing
(E27.0)
ACTH (E24.0)
- TSH (E05.8)

326
,

E22.0
, (M14.5*)

: :
(E34.4)
(E34.4)
- -
(GHRH) (E16.8)
E22.1

, ,
( XX).
E22.2 -

E22.8

E22.9 ,

E23

: , -

: -
(E89.3)

327

E23.0



:



Kallmann
Lorain-Levi
( )

:



Sheehan
Simmonds
E23.1


( XX).
E23.2
: (N25.1)
E23.3 ,

: Prader-Willi (Q87.1)
Russell-Silver (Q87.1)
E23.6


E23.7 ,

328
,

24 Cushing
E24.0 Cushing
ACTH

E24.1 Nelson
E24.2 Cushing
-
(
XX).
E24.3 ACTH
E24.4 -Cushing
E24.8 Cushing
E24.9 Cushing,

E25
: ,
,
, -
-

:

-

:
-


-

( )
E25.0 ,


21-

329

E25.8


, ,
( XX).
E25.9 ,

E26
E26.0
Conn
, -
()
E26.1
E26.8
Bartter
E26.9 ,

E27

E27.0 -

ACTH, Cushing

: Cushing (E24.)
E27.1 -

Addison

: (E85.)
Addison (A18.7)
Waterhouse-Friderichsen (A39.1)
E27.2

330
,

E27.3 -



( XX).
E27.4 -

:




: [Addison-Schilder]
(E71.3)
Waterhouse-Friderichsen (39.1)
E27.5


E27.8
-
E27.9 ,

E28
: (E23.0)
-
(E89.4)
E28.0

, , -
( XX).
E28.1


, , -
( XX).

331

E28.2

Stein-Leventhal
E28.3



: (N95.1)
(Q99.1)
Turner (Q96.)
E28.8

E28.9 ,

E29
: (E34.5)
(N46)
(E23.0)
Klinefelter (Q98.0Q98.2,Q98.4)

(E89.5)
() (E34.5)
E29.0

E29.1

5-- ( )


, , -
( XX).
E29.8
E29.9 ,

332
,

E30 ,

E30.0


E30.1

: Albright (-McCune)(-Sternberg)
(Q78.1)
-
(E22.8)
(E25.0)
-
(E25.)
-
(E25.)
E30.8

30.9 ,

E31
: - [Louis-Bar] (G11.3)
[Steinert] (G71.1)
(E20.1)
E31.0
Schmidt
E31.1
: (D44.8)
E31.8 a a
E31.9 ,

E32
:
(D82.1)
(G70.0)

333

E32.0

E32.1
E32.8
E32.9 ,

E34
: (E20.1)
E34.0
: -
,
, .
E34.1 -

E34.2 , -

E34.3 ,
:


Laron

: (E34.8)
Russsell-Silver (Q87.1)
(D82.2)
:
(Q77.4)
(Q77.4)

( )
(E45)
(E23.0)
(N25.0)

334
,

E34.4

E34.5


Reifenstein
()
E34.8


E34.9 ,
:

35*
,
E35.0* ,

(A18.8)
E35.1* , -

(A18.7)
Waterhouse-Friderichsen () (A39.1)
E35.8* -
,

335


(E40E46)
: -
, -
. -
,

-
. , -
-
. -
, ,
.
-
, -
, -
3 -
;

2 3 -
; -
1 2
.
: (K90.)
(D50D53)
- (64.0)
(B22.2)
(T73.0)

E40


: (E42)

E41

: (E42)

336
,

E42
- [ E43]:

E43 -
,
[] , -
, -
- 3
( , -
). ,
3 -
.

E44 -

E44.0 -
,
, 2 3 -

( , ).
, -
- -
2 3 -
.
E44.1 -
,
, 1 2 -

( , ).
,
- 1
2 .

337

E45 ,
-
:


, -

E46 - ,


-


(E50E64)
: (D50D53)

E50 A
: A (E64.1)
E50.0 A -

E50.1 A Bitot

Bitot
E50.2
E50.3 A

E50.4 A
E50.5 A
E50.6 A -

338
,

E50.7 A

E50.8 A

A (L86*)
E50.9 A,
A

E51
: (E64.8)
E51.1 -
-:

(I98.8*)
E51.2 Wernicke
E51.8
E51.9 ,

E52 []
:
(-)

()
: (E64.8)

E53
B
: B (E64.8)
B12- (D51.)
E53.0

E53.1
B6
: -
(D64.3)

339

E53.8 B
:





B12
E53.9 B,

E54
C

: (D53.2)
C (E64.2)

E55 D
: (M83.)
o (M80M81)
(E64.3)
E55.0 ,
:


: :
(K90.0)
Crohn (K50.)
(E64.3)
(N25.0)
D- (E83.3)
E55.9 D,
D

E56
:
(E64.8)
E56.0 E

340
,

E56.1 K
: ,
K (D68.4)
K (P53)
E56.8
E56.9 ,

E58
: (E83.5)
(E64.8)

E59
Keshan
: (E64.8)

E60

E61

, ,
( XX).
:
(E83.)
,
(E00E02)

(E64.)
E61.0
E61.1
: (D50.)
E61.2
E61.3
E61.4
E61.5

341

E61.6
E61.7
E61.8 ,
E61.9 ,

E63
: (E86)
(R62.8)

(P92.)

(E64.)
E63.0 [EFA]
E63.1
E63.8 ,
E63.9 ,
(I43.2*)

E64

E64.0 -
: , -
(E45)
E64.1 A
E64.2 C
E64.3
E64.8
E64.9 ,

342
,



(E65E68)
E65

E66
: (E23.6)
:
(E88.2)
[ Dercum] (E88.2)
Prader-Willi (Q87.1)
E66.0 ,
E66.1


( XX).
E66.2 -

Pickwick
E66.8

E66.9 ,

E67
: (R63.2)
(E68)
E67.0 A
E67.1
E67.2 B6

343

E67.3 D
E67.8

E68



(E70E90)
: (E34.5)
(E25.0)
Ehlers-Danlos (Q79.6)
, -
(D55.)
Marfan (Q87.4)
5-a (E29.1)

E70 -

E70.0
E70.1
E70.2




344
,

E70.3
:

-
:
Chediak(-Steinbrinck)-Higashi
Cross
Hermansky-Pudlak
E70.8

:


E70.9 -
,

E71


E71.0
E71.1 -

-




E71.2
,
E71.3
[Addison-Schilder]
-
: Refsum (G60.1)
Schilder (G37.0)
Zellweger (Q87.8)

345

E72

: -
(R70R89)
:

(E70.)

(E71.0E71.2)
(E71.3)
(E79.)
(M10.)
E72.0 -



Fanconi(-de Toni)(-Debre)
Hartnup
Lowe
:
(E70.8)
E72.1 -





: II (D51.2)
E72.2




: (E72.4)

346
,

E72.3 -




E72.4
( I, II )
E72.5

( I, II)


E72.8 -

:
b-
g-
E27.9 , -

E73
E73.0
E73.1
E73.8
E73.9 ,

E74

: (E16.3)
(E10E14)
(E16.2)
(E76.0E76.3)

347

E74.0

:
Andersen
Cori
Forbes
Hers
McArdle
Pompe
Tauri
Von Gierke

E74.1

-1,6-

E74.2


E74.3 -

-

: (E73.)
E74.4 -

:

:


: (D55.)
E74.8 -




348
,

E74.9 , -

E75


: , I-III (E77.0E77.1)
Refsum (G60.1)
E75.0 GM2
:
Sandhoff
Tay-Sachs
GM2 :



E75.1
:

GM1
GM3
IV
E75.2
:
Fabry(-Anderson)
Gaucher
Krabbe
Niemann-Pick
Farber


: [Addison-Schilder]
(E71.3)
E75.3 ,

349

E75.4
:
Batten
Bielschowsky-Jansky
Kufs
Spielmeyer-Vogt
E75.5
[van Bogaert-Scherer-Epstein]
Wolman
E75.6 ,

E76

E76.0 , I
:
Hurler
Hurler-Scheie
Scheie
E76.1 , II
Hunter
E76.2
b-
, III, IV, VI, VII
:
Maroteaux-Lamy ()()
Morquio(-)()
Sanfilippo ( B)( C)( D)
E76.3 ,
E76.8 -

E76.9 -
,

350
,

E77

E77.0

II [I- ]
III [-Hurler ]
E77.1



[ I]
E77.8 -

E77.9 , -

E78

: (E75.0E75.3)
E78.0

Fredrickson, IIa

,

[LDL]
E78.1

Fredrickson, IV
, B

-
[VLDL]

351

E78.2

Fredrickson, IIb III


, C
-
Xanthoma tuberosum
: [van Bogaert-
Scherer-Epstein] (E75.5)
E78.3
Fredrickson, I V
, D

E78.4

E78.5 ,
E78.6



()
--

E78.8 -

E78.9 , -

352
,

E79

: (N20.0)

(D81.)
(M10.)
(D53.0)
(Q82.1)
E79.0 -


E79.1 Lesch-Nyhan
E79.8 -


E79.9 -
,

E80

:
E80.0


E80.1
E80.2

:

()
-
( XX).
E80.3
[Takahara]

353

E80.4 Gilbert
E80.5 Crigler-Najjar
E80.6
Dubin-Johnson
Rotor
E80.7 , -

E83
: -
(E58E61)

(E20E21)
D (E55.)
E83.0
Menkes ( ) ( -
)
Wilson
E83.1

: :
(D50.)
(D64.0D64.3)
E83.2

E83.3



D-:


: (M83.)
o (M80M81)
E83.4

354
,

E83.5


: (M11.1M11.2)
(E21.0E21.3)
E83.8
E83.9 ,

E84
:
E84.0
E84.1
(P75*)
E84.8
E84.9 ,

E85
: Alzheimer (G30.)
E85.0


E85.1
()
E85.2 ,
E85.3

E85.4

E85.8
E85.9 ,

355

E86




: (P74.1)
:
(R57.1)
(T81.1)
(T79.4)

E87
-
-
E87.0
[Na]
[Na]
E87.1
[Na]
: -
(E22.2)
E87.2
:

- ()


: (E10E14)
.1
E87.3
:



E87.4 - -

356
,

E87.5
[K]
[K]
E87.6
[K]
E87.7
: (R60.)
E87.8 - ,



E88

: X () (D76.0)

, -
,
( XX).
E88.0 ,

a-1-

:
(E78.)
(D47.2)

(D89.0)
Waldenstrom (C88.0)
E88.1 ,

: Whipple (K90.8)
E88.2 ,
:

[Dercum]

357

E88.8

Launois-Bensaude

E88.9 , -

E89 ,
,

E89.0


E89.1


E89.2

E89.3

E89.4

E89.5
E89.6 (-)

E89.8

E89.9
,

E90*

,

358
V

(F00F99)

:
: , ,
, -
(R00R99)

:
F00F09 , , -

F10F19 , -

F20F29 ,
F30F39 [ ]
F40F48 , -

F50F59 , -

F60F69
F70F79
F80F89
F90F98 , -

F99

:
F00* Alzheimer
F02* ,

359

, ,

(F00F09)
,
,
,
, .
( , ,
) ( -
,
).
[] (F00F03) ,
, ,
, ,
, , , , ,
. . -
, ,
-
.
Alzheimer, , -
.

.

F00* Alzheimer
(G30.)
-

. ,
, , -
.

360

F00.0* Alzheimer -
(G30.0)
Alzheimer, 65-
, -
.
Alzheimer, 2
,


F00.1* Alzheimer -
(G30.1)
Alzheimer, 65-
, 70 -,
.
Alzheimer, 1


,
F00.2* Alzheimer,
(G30.8)

F00.9* Alzheimer,
(G30.9)
F01
, -
, -
. ,
. .
:
F01.0

, . -
.
F01.1
, -
,
.

361

F01.2
, -

. -
, -
Alzheimer.
F01.3
F01.8
F01.9 ,

F02* ,

, ,
, Alzheimer -
. , -
.
F02.0* Pick (G31.0)
, , -
,
, , -
, , -
.
F02.1* Creutzfeldt-Jacob
(A81.0)
, -
,
.
, -
. , -
.
F02.2* Huntington (G10)
, -
. -
. -
. ,
10-15 .
Huntington

362

F02.3* Parkinson (G20)


,
Parkinson. , -
.
:
paralysis agitans

F02.4* ,
[HIV] (B22.0)
, , HIV
, -
, HIV , -
.
F02.8* , -

:
(E75.)
(G40.)
(E83.0)
(E83.5)
, (E01, E03.)
(T36T65)
(G35)
(52.1)
[] (E52)
(M30.0)
(M32.)
(B56., B57.)
B12 (E53.8)

363

F03 ,
:



:
:



: -
(F05.1)
(R54)

F04 ,


-

.
.
,
, , . -
.
,
: :
(R41.3)
(R41.1)
(F44.0)
(R41.2)
:
(F10.6)
-
(F11F19 .6)

364

F05 ,

,
-
, , , , ,
-. -
, .
: :

()



: delirium tremens,
(F10.4)
F05.0 ,
F05.1
, , -
(F00F03).
F05.8 ,

F05.9 ,

F06 ,



,
, ,
, ,
,
.
: , :
(F05.)
, F00
F03
(F10
F19)

365

F06.0
, -
, ,
.
, -
. -
.
()
: (F10.5)
(F20.)
F06.1
() () -
, .
.
: (F20.2)
:
(R40.1)
(F44.2)
F06.2 [] -

, -
. -
. ,
, -
.
- -


: :
(F23.)
(F22.)
,
(F11F19 .5)
(F20.)

366

F06.3 [-
]
,
,
, , , -
( F30F38), -
.
: ,
(F30F39)
F06.4
, -
(F41.1), (F41.0)
, -
.
: , -
(F41.)
F06.5
, -
,
-
, ( F44.), -
.
: [ ],
(F44.)
F06.6 [] -

, -
, -
( ) , -
.
: ,
(F45.)

367

F06.7
, ,

, .
-
. -
, .
,
(F00F03), (F05.).
-
-
, F10F99. -
,
, -
, ,
. -
(F07.1) (F07.2)
, - , - -
, , - .
F06.8 ,



F06.9 ,

,
(-):

F07
, ,



,
.

368

F07.0
,
,
, .
,
.
:


():




: :
(F62.0)
(F62.1)
(F07.2)
(F07.1)
(F60.)
F07.1

. -

, .
: (F07.0)
F07.2
( -
, ) -
, , , -
, -
, ,
, .
()
,

369

F07.8 -
, , -

-

F07.9 -
, ,
,

F09
,
:


: (F29)

,


(F10F19)

, -
( -
).
, .
, -
,
.

-
. : , , -
, -
, ,

370

-
.
. -
, , ( -
), - -
. , -
, ( -
.0), ( .1), (
.2) ( .3.9).
,
, -
, F19 (,
).
: ,
(F55)

F10F19 :
.0
,
, , , -
, . -
-
, ,
. -
, , , , -
.
-
.

(bad trips) ( )
,



.1
, .
( -
) ( -
).

371

.2
, ,

,
,
,
, -
.
-
( , ),
( )
- .



.3
, -
, -
. -
,
.
.

.4
, ,
.3,
F05.. .
,
F05.8.
Delirium tremens ()
.5
, -
,
-
. (
, ), , -
( ),
( ) ,
.
, ,
.

372

:




: -
, -
(F10F19 .7)
.6
, -
. -
, -
.
,
. , . -

.
,
,
,
: (F04)
.7
, -
, , -
, ,
. -

. , -
- , ,
, -
. (flash-
backs) -
,
, -
.


-

(flashbacks)
, -

373


:


: :
(F10F19 .6)
(F10F19
.5)
.8
.9 ,

F10. ,

[ - ]

F11. ,

[ - ]

F12. ,

[ - ]

F13. ,


[ - ]

F14. ,

[ - ]

374

F15. ,

( )
[ - ]

F16. ,


[ - ]

F17. ,

[ - ]

F18. ,


[ - ]

F19. ,



[ - ]
,
,
- -
.
,
, , -
, -
.
:

375

(F20F29)
-
, , -
-
. , -
.

F20
- -
,
, , . -
,
-
. -
; ;
; ,
; , -
;
.
-
, ,
-
.
,
,
. -
-
. -
, -
, F06.2, ,
F10F19 .5.
: :
() (F23.2)
(F25.2)
(F23.2)
(F21)

376

F20.0
, -
, -
, , . -
, ,
, .

: (F22.8)
(F22.0)
F20.1
, ,
,
,
. ,
, . -
.
, - -
.
.


F20.2
-
, -
, .
-
. -
.
() -
.

:


377

F20.3
, -
,
(F20.0F20.2)
,
.

: -
(F23.2)

(F20.5)
(F20.4)
F20.4
, ,
. ,
, , ,
.
.
,
(F32.).
, -
(F20.0F20.3).
F20.5
,
- -
, ,
, : ;
; ; ; -
; -
, ,
; .

Restzustand ()

F20.6
, ,
,
-
. -
( )
,
.

378

F20.8



:
(F23.2)
F20.9 ,

F21
,
, -
,
. -
; ;
; -
; , -
; ;
; , -
, -
,
. , -
-
.

:







: Asperger (F84.5)
(F60.1)

F22
, -
-
,
. -
-
F23..

379

F22.0
, -
, , -
.
.
(), ,
,
,
.
, ,
, , -
.



()
Sensitiver Beziehungswahn
: (-):
(F60.0)
(F23.3)
(F23.3)
(F20.0)
F22.8
, -
-
, (F20.).



F22.9 ,

380

F23

,
, -
-
.

-. -
. ,
,
,
(F05.). -
, . -
, -
, .
( ), -
, -
.
F23.0

,
,
. -

.
, -
(F20.).
,
, -
. ,
(F22.).
Bouffee delirante -

-

F23.1 -

, -
,
F23.0. , -
. -
, (F20.).
Bouffee delirante

381

F23.2
, -
-
(F20.), - .
, , F23.0, .
, -
(F20.).
()

(-) (-):




: [] -
(F06.0)
(F20.8)
F23.3 -

,
,
(F20.). -
, -
(F22.).


F23.8
,

F23.0F23.3.
F23.9 , -


382

F24
,
.
; (-
) ,
.
Folie deux
:

F25
,
, ,
, -
. ,
-
, , -
,
F20F29.
-
.
F25.0 ,
, , -
, , -
, -
.
, , -
, .
,
,
F25.1 ,
, ,
, ,
,
.
, , -
, .
,
,

383

F25.2 ,


F25.8
F25.9 ,

F28

,
(F20.),
(F22.), -
(F23.),
(F30.2) (F32.3).

F29 ,

: (F99)

(F09)


[ ]
(F30F39)
, -
( -
) .
.

, , -
.

.

384

F30
-
.
, -
(, , -
) -
(F31.).
: ,

F30.0
,
, , -
, -
. , -
, ,
, ,
. -
, -
. -
-
.
F30.1
-

. ,
,
. -
. , -
. -
, -
, , .
F30.2
, F30.1,
( )
( , ), -
, -
, -
.
:
,
,

385

F30.8
F30.9 ,

F31
, ,
-
.
(-
),
().
.
: -(-):



: ,
(F30.)
(F34.0)
F31.0 , -


(, , )
.
F31.1 , -

, (-
F30.1) (-
, , ) .
F31.2 , -

, (
F30.2) (,
, ) .
F31.3 , -

, -
(F32.0 F32.1)
, -
.

386

F31.4 , -

, -
(F32.2)
, -
.
F31.5 , -

, -
(F32.3) -
, -
.
F31.6 , -

, , -
,
,
.
: -
(F38.0)
F31.7 ,
,

(, , -
), -
. . -
-
.
F31.8
II

F31.9 ,

387

F32
, -
, -
. , -
, -
. , -
. , -

. -
,

-
, , -
,
, ,
. -
, .
: :



: (F43.2)

(F33.)
,
,
F91. (F92.0)
F32.0
.
, -
.
F32.1
-

.

388

F32.2 -

, -
,
, .
-
.





F32.3
F32.2,
, , ,
, -
. , -
, . -
-
.
:




F32.8


F32.9 ,

389

F33
, -
, (F32.), -

(). -

(), ,
. -
(F33.2 F33.3)
- -
, , .

; , -
. -

, . , -
-
(F31.).
: :




:
(F38.1)
F33.0 ,

, -
, , F32.0,
.
F33.1 ,

, -
, , F32.1, -
.

390

F33.2 ,

, -
, , ,
F32.2, .

, ,
- , ,

, ,
F33.3 ,

, -
, , , -
F32.3, .
,
- , ,

:
,



F33.4 , -

-
F33.0F33.3,
.
F33.8
F33.9 , -

391

F34
[ ]
-
,
,
.
- , -
.
-

.
F34.0
, -
, -
,

(F31.) (F33.).
-
.
.



F34.1

, ,
, -
,
(F33.).
(-):




: ( )
(F41.2)
F34.8
[ ]
F34.9 [-
],

392

F38
[ ]
,
F30F34, -
.
F38.0 [
]

F38.1
[ ]

F38.8
[ ]

F39
[ ],

393

,

(F40F48)
: , -
, F91. (F92.8)

F40
, ,
, , -
.
. -
-
, -
, .
-
. -
.
-
,
.
F40.0
,
, ,
, . -
, ,
.
, .
, -
,
.

394

F40.1
,
. -

. ,
, .
,
.
.


F40.2 ()
, :
, , , , ,
,
, ,
. , ,
,
.




: () (F45.2)
(F45.2)
F40.8
F40.9 ,

F41
, -
, .
, -
, - -
.

395

F41.0 [ -
]
-
(),
, .
, -
, ,
, (-
).
, . -
, -
.
-
.
(-):


: (F40.0)
F41.1
, , -

(.. ).

, , , ,
, , .
, -
.
(-):



: (F48.0)
F41.2 -
, -
, -
, .

, -
, ,
.
( )

396

F41.3
,
F42F48.
, .
F41.8

F41.9 ,

F42 -
- -
.
, ,
.
-
. , -
.
.
, -
.
, -
. -

. -
.
, .
:
-
: - (-
) (F60.5)
F42.0 -

,
, .
-
, ,
. -
-
- ,
-
.

397

F42.1 [-
]
(
), ,
-
.

. -
.
F42.2
F42.8 -
F42.9 - ,

F43

, -
,
,
,
, -
, ,
. -
( ) -

, , -

, , -
( -
, , -
). , , ,
-
. -
- -
-
.

, ,
.
F43.0
, -
-

.

398

. , -
-
, -
, -
. - -
( -
F44.2) (
).
(, , ).
-
-
- ( ). -
(F44.0) .
,
.
:





F43.1

( -), -

.
(
, ) -

, , -
. -
-
(flashback), -
, , -
, ,
,
, . -
,
- . -
,
.
.
, -
.
,
(F62.0).

399

F43.2
, -
,
-
. -
(
, ) -
(, ), -
( , -
, , -
).

,
,
. -
, ( ), -
,
,
-
. -
, . -

, .



: , -
(F93.0)
F43.8
F43.9 ,

F44 []

, ( )
,
, -
,
. -
,
. , -
, ,

.
.
, ,

400

, -
. -
,
. -

. ,
.

.
,
, . ,
-
, -
(F45.0).

.
: :




: [ ]
(Z76.5)
F44.0
,
, -
,
. -
, -
, .
-
(F44.1). , -
.
,
.
: ,

(F10F19 .6)
:
(R41.3)
(R41.1)
(R41.2)

(F04)
(G40.)

401

F44.1
-
, , -
. -
,
-
.
: (G40.)
F44.2
-

, , -
.

.
: (F06.1)
:
(F40.1)
(F20.2)
(F31F33)
(F30.2)
F44.3
, -
-
. ,
,
.
: , :
-
(F23.)

(F07.0)
(F07.2)

(F10F19 .0)
(F20.)

402

F44.4
-
.
,
, , , , ,
.
:


F44.5

,
, , ,
.
.
F44.6
, -
, -
, .
-
, .
.
-
.

F44.7 [] -

,
F44.0F44.6.
F44.8 []
Ganzer

(-):


F44.9 [] , -

403

F45

,
, -
, -
. , -
-
.
: (F44.)
(F98.4)
(F80.0)
(F80.8)
(F98.8)
,
, -
(F54)
, e -
(F52.)
(F98.8)
,
(F95.)
Tourette (F95.2)
(F63.3)
F45.0
,
-
. -
, , -

.

. -
, ,
. -
(- ) -
-
(F45.1).
Briquet

: [ ]
(Z76.5)

404

F45.1
,
, , -

.

F45.2
,

.

.
-
.
, .
,
.

( )



: (F22.8)

(F22.)

405

F45.3
,
,
, -
-, ,
- . , -

. , -

, , , -
-
. -
,
, , , -
.

Da Costa


:











: ,
,
(F54)

406

F45.4 -

, ,


, -
-
.
-
. ,
-
.
(-):



: (54.9)
:
(R52.9)
(R52.0)
(R52.2)
() (R52.1)
(G44.2)
F45.8
,
, : ;
; -
;
.
(-):

, globus hystericus



F45.9 ,

407

F48
F48.0
-
, , -
. -
,
-

. -
,
.

, -
. -
, -
. -

, ,
. -
, .


.
: (R53)
[burn-out] (Z73.0)
(R53)
(G93.3)
(F48.8)
F48.1 -
,
, , -
,
. ,
-
, -
. -
, , .

. -
, , -
- . -
.

408

F48.8
Dhat
,



F48.9 ,

,


(F50F59)
F50
: (R63.0)

(R63.3)

(F98.2)
(R63.2)
F50.0
, , -
.
-
, , , -
- , .
,

. -
-
.
, ,
,
.
: (R63.0)
(F50.8)

409

F50.1
,
,
. , -
, ,
, -
. -
,
.
F50.2
,
, -
, ,
,
. -
, , -
.

. , , -
-
.


F50.3
,
, -
. -
,
.
F50.4 , -

, -
, , .

: (E66.)
F50.5 , -

,
(F44.) (F45.2),
, .
21. (-

410

), -

.

: (R11)
(R11)
F50.8


: (F98.3)
F50.9 ,

F51
-
, . , -

-

,
.
, -
,
.
, -
.
,
,
, -
.
: () (G47.)
F51.0
, -
/ ,
, , -
.

,
.
: () (G47.0)

411

F51.1 []

(
), -
.
,
.
: () (G47.1)
(G47.4)
F51.2 --

-
,
, .
:



: - (-
) (G47.2)
F51.3 [ ]
, -
.
, ,
, ,
.
.
F51.4
, -
, .

. ,
, .
, ,
( ).
F51.5
, .
. -
, -
, .

. -

412

, -
.
.

F51.8
F51.9 ,

F52 ,

, -
-
, . -
-
, .
: Dhat (F48.8)
F52.0


.


F52.1 -


, (
),
, -
( ).
()
F52.2
(-
-
).
.



: (N48.4)

413

F52.3
, .
( )( )

F52.4
,
-
.
F52.5
, ,
.
, .

: () (N94.2)
F52.6
( ) ,
. -
-
. ,
(-
).

: () (N94.1)
F52.7


F52.8 ,

F52.9 , -
,

F53 ,
,

, -
( ),
, -
, ,
,
.

414

F53.0 , -
, -

:


F53.1 ,
,


F53.8 ,
,

F53.9 ,

F54
,
,
-
, ,
,
.
, ( -
, , ) -
.
, -

:
F54 J45.
F54 L23L25
F54 K25.
F54 K58.
F54 K51.
F54 L50.

.
: (G44.2)

415

F55 , -


,
: () , -
, , () () -
, ,
.

, -
. -
-
.
( )

, , -
; -
, ,
F10F19.
():





: ( )
(F10F19)

F59 ,

,

416



(F60F69)
-
, -
.

, -
, , -
-. (F60.), -
(F61.)
(F62.) ,
-
. -
,
, , , -, . -
-
-
. , , -
.

F60
-
; ,
,
; -
;
; -
, .

417

F60.0
,

;
, -
-
; -
/ ;
.

, , .
():
-



-
: (F22.0)
(F22.8)
(-):
(F22.0)
(F20.0)
(F22.0)
F60.1
,
, ,
, . -

.
: Asperger (F84.5)
(F22.0)
(F84.5)
(F20.)
(F21)
F60.2
, -

. -
. -
, .
-
, ; -

418

-
,
.
():





: (F91.)
(F60.3)
F60.3
,
,
.
-
. -
, -
. : -
, -
; (border-
line) , :
, ;
; -
, -
, .
():

(borderline)

:
(F60.2)
F60.4
,
, -
, ,
, , ,
, , , -
-
.
():

419

F60.5
,
, , , -
, , -
. -
, -
.
():


-
: - (F42.)
F60.6 [ ]
, -
, . -
,
, -
-
.
F60.7
, -

( ) ,
, , -
-, -
, .

.
.
():




F60.8
():




-

420

F60.9 ,

F61

, -
,
, , F60.. -
-,
F60..
:
-
, F60.,
, - -
;
, -
F60. F62. -
-
.
: (Z73.1)

F62 ,


,
, -
, -
. -
,
, ,
, . -

, .

-
.
: ,
, -
(F07.)

421

F62.0

- ,
.
, -
-
. -
, , -
, ,
.
(F43.1).
:


(-):




:
(F43.1)
F62.1 -

- ,
-
. -

-
. -

; , -
, , -
, , ; -
, -
; -
, , -
; -
, -

; -
.

422

F62.8

F62.9 ,

F63
, -
.
, ,
-
.
, .

, -
.
: -
(F10
F19)
, -
(F65.)
F63.0
,
,
, , , -
.

: -
(F30.)
(Z72.6)

(F60.2)

423

F63.1 [-
]
,
,
, ,
. -
-
.
: () ():

(F60.2)
-
(F10F19,
.0)
,

(Z03.2)
(F91.)
(F00F09)
(F20.)
F63.2 []
, , -
,
. -
, , . -
-

.
: ,
(F00F09)
, -
(F00F09)
,
-

(Z03.2)

424

F63.3
,
-
. -
-
. ,
-
.
:
(F98.4)
F63.8
,
-
-
. -

.

F63.9 , -

F64
F64.0

, -
, -
. -
,
- .
F64.1

, -
, -
.
.

,
: (F65.1)

425

F64.2
,
( )
,
-
, . -

. -
-
( );
. -
,
; -
F66..
: - (F66.1)

(F66.0)
F64.8
F64.9 ,

F65
:
F65.0

.
.

, .
.
, (
).
F65.1


. -

-
,
. -
.

426

F65.2
-
(
) , -
. , -
, -
.
F65.3

( -
). ,
.
F65.4
( ,
), -
.
F65.5
, -
, . -
, ; -
.
, .


F65.6 -


.
- , -
.
F65.8
,
: ,
,
, -
.


F65.9 ,

427

F66
,

:
.
F66.0

,
. - ,
, ,
, -
( ), , -
.
F66.1 -
(-
, ) ,
-
, ,
.
F66.2
(-
, )

.
F66.8
F66.9 , -

428

F68

F68.0 -

,
, ,
-
.
, (-
)
.

F68.1 -
, -
[ ]

, -
.
,
. -
.

Munchausen

: (L98.1)
, ( -
) (Z76.5)
F68.8 -


F69
,

429


(F70F79)
, -
, -
-
, .. , , .
, ,
.
-
.
. -
-
.
.

, , -
.
.

F70F79 :
.0
.1 , -

.8
.9
,
, , ,
, .

430

F70
IQ ( ) -
50 69 (
9 12 ).
. -
-
.
:

F71
IQ 35 49 ( -
6 9 ).

, -
, -
.

.
:

F72
IQ 20 34 ( -
3 6 ).
-
.
:

F73
IQ 20 (
3 ). -
, , -
.
:

F78

F79 ,
: (-):

431


(F80F89)
, , : (1)
; (2)
, -
; (3) -
.
, - -
. -
, -
,
.

F80

, -
.
-
, ,
.
-
-
, , -
.
F80.0
,
, ,
.
:





: ( ):
(R47.0)
(R48.2)
(H90H91)
(F70F79)

432


:
(F80.1)
(F80.2)
F80.1
,
-
,
. -
, .
,
: [
Landau-Kleffner] (F80.3)
, -
(F80.2)
(R47.0)
(F94.0)
(F70F79)

(F84.)
F80.2
,

.
, -
.

,
Wernicke

: [
Landau-Kleffner] (F80.3)
(F84.0F84.1)
:
(R47.0)
(F80.1)
(F94.0)
,
(H90H91)
(F70F79)

433

F80.3 [ Lan-
dau-Kleffner]
, , -
, ,
, . -
-
. -
- , -
.
-
,
.

. - - -
.
: :
(R47.0)
(F84.0F84.1)
-
(F84.2F84.3)
F80.8

F80.9 , -

F81

,
. -
-
, -
.

434

F81.0
-
,
,
. -
,
, , -
.
, -
,
.

. -

.



: (R48.0)
(R48.0)
,
(F93.)
F81.1


, -
, -
.
, -
.
( -
)
: (R48.8)
:

(F81.0)
(Z55.8)

435

F81.2 -

,
-
.
, -
, - -
, , ,
.
(-)(-) :


Gertsmann
: (R48.8)
:

(F81.3)
(Z55.8)
F81.3
, -
, -
, -

. , -
F81.2 F81.0
F81.1.
: :
(F81.2)
(F81.0)
(F81.1)
F81.8


F81.9 ,


:

436

F82

, -
,
-
. -
, -
-
-
,
.

(-) :


:
(R26.)
(R27.0)

(F70F79)

F83

,

,
, -
. ,

. -
-
, . ,
, , -

: F80., F81. F82.

437

F84

,
,
, , -
.
.

-
.
F84.0
,
: () , -
() -
-
, ,
, .
, -
,
, (
) .

(-):


Kanner
: (F84.5)
F84.1
,
-
, ,
. , -

-

, ( -
, , -
, ), -
. -
-
.

438



-
(F70F79).
F84.2 Rett
, ,
-
-
, . -
7 24 .
, -
.
,
. -
, -
.
.
F84.3
,
-
. , -
, -
, .
;
, ; -
, , -
. -
,
.


Heller


, , -
.
: Rett (F84.2)

439

F84.4 ,

-
.
(IQ 34),
,
. -
( , IQ )
(
), . -
(
,
). -
, .
IQ
.
F84.5 Asperger
, -
-
, , ,
, . -

, . -
. -

. -
.


F84.8
F84.9 , -

F88

F89 -
,

440


,

(F90F98)
F90
, (-
),
, ,
,
, , , -
. -
. ,
-
, -
. -
,
.
. -
,
. -
.
: (F41.)
[ -
] (F30F39)
-
(F84.)
(F20.)
F90.0



: , -
(F90.1)
F90.1
,

F90.8

441

F90.9 ,


F91
,
, .
-
. - -
-
( ). -

,
.
,
: -
; ;
; , , -
, ; -
. ,
, ,
.
: [ -
] (F30F39)

(F84.)
(F20.)
, :
(F92.)
(F90.1)
F91.0 ,

, -
( ,
),
, , -
. -
F91., -
. /
.

442

F91.1
, -
( -
F91., , -
)
.


F91.2
,
( -
F91., ,
), , -
.
,

,


F91.3 -

, -
, -
, , -
- .

F91.. -
.
, - , -

,
, -
.
F91.8
F91.9 ,

443

F92

, -
,
, -
.
(F91.)
(F93.), -
(F40F48),
(F30F39).
F92.0

(F91.) (F32.), -
,
,
.
.
(F91.),
(F32.)
F92.8 -


(F91.)
, , -
, .
(F91.), :
(F93.)
(F40F48)
F92.9 ,

444

F93 ,

- ,
, . -

-
, -
(F40F48).
: ,
,
(F92.)
F93.0 ,

, -
-
.
, (), -
(
), -
.
: [ -
] (F30F39)
(F40F48)
-
(F93.1)
-
(F93.2)
F93.1 -
, ,
( )
, .
, ,
( ),
(F40F48).
:
(F41.1)

445

F93.2

, -
. -
, -
,
.


F93.3
( )
-
-
.
, -
, -
.

F93.8


:
(F64.2)
F93.9 ,

F94
,

, -
, -
, , (
) -
,
. , -

.

446

F94.0
, -
, -
, () .

, , ,
.

:
(F84.)
(F20.)
-
(F80.)

(F93.0)
F94.1 , -

,
-
, -
(-
, -
, , -
). -

, .
,
,
, .
: Asperger (F84.5)
,
(F94.2)
(T74.)


-
, -
(Z61.4Z61.6)

447

F94.2 , -

, -

, . -
, ,
-
,
. -
.


: Asperger (F84.5)
(F43.2)
(F90.)
,
(F94.1)
F94.8

F94.9 -
,

F95
,
. , , , -
( )
, .
, -
, -
. -
, ,
. -
, , . -
-
, . -
-
( ) (-
), ().
F95.0
, -
12 .
, .

448

F95.1 -

,
( -
), ( -
) .
F95.2
[ Tourette]
, -

, -
.
.
,
, ,
. -
, (-
).
F95.8
F95.9 ,

F98
,

, -
, .
,
,
,
.
: (R06.8)
-
(F64.2)
Kleine-Levin (G47.8)
- (F42.)
, -
(F51.)

449

F98.0
,
, -

, -
,
.

. -
-
.
()()



: (R32)
F98.1
, -
, , -
.
-
,
-
, -
.

- , -
(F93.) (F91.).



-

.
: (R15)
F98.2

, -
.
-
, , -
. ,
, (
).

450


:
(F50.)

(R63.3)
(P92.)
(F98.3)
F98.3
( ,
.).
- ( ), -
.
. - -
, -
F70F79 .
F98.4
, , , ( -
) ,
. -
, -
. , -
, : , , -
, ,
. : -
, ,
, . -
- -
(
).
, :
, -
.
/
: (R25.)
-
(G20G25)
(F98.8)
(F98.8)
, - -
(F00F95)
(F98.8)
(F95.)
(F63.3)

451

F98.5

, ,
, .
, -
, .
: (F95.)
(F98.6)
F98.6
, ,
, -
.
, -
.
: (F98.5)
(F95.)
F98.8 -
, -

,




F98.9 -
, , -


(F99)
F99


: (F06.9)

452
VI


(G00G99)

: ,
(0096)
(0099)
,
(0099)
,
(Q00Q99)
, -
(0090)
, -
(S00T98)
(00D48)
, ,
, -
(R00R99)

:
G00G09
G10G13 ,

G20G26
G30G32 -

G35G37
G40G47
G50G59 ,
G60G64

G70G73 -
G80G83
G90G99

453

:
G01* ,
G02* , -

G05* , , -

G07* -
,
G13* ,
, ,
G22* ,
G26* -
,
G32*
,
G46*
G53* , -

G55* ,

G59* ,
G63* ,
G73* -
,
G94* , -

G99* , -

454



(G00G09)
G00 ,

:




: :
(G04.2)
(G04.2)
G00.0
, Haemophilus influenzae
G00.1
G00.2
G00.3
G00.8 ,
:
Friedlander
Escherichia coli
Klebsiella
G00.9 ,
:


455

G01* ,

():
(22.8)
(54.8)
(27.)
(32.1)
(69.2)
(39.0)
(52.1)
(02.2)
:
(50.4)
(51.4)
(17.0)
(01.0)
: -
,
(G05.0*)

G02*
,

: -
, -
(G05.1G05.2*)
G02.0* ,

( ):
(87.1)
(87.0)
herpes simplex (B00.3)
(27.)
(05.1)
(26.1)
(06.0)
(01.0)
herpes zoster (B02.1)

456

G02.1*
():
(37.5)
(38.4)
(B45.1)
G02.8* -
,
:
(56.)
Chagas (57.4)

G03 ,

:



: (G04.)
(G04.)
G03.0

G03.1
G03.2 [Mollaret]
G03.8 , -

G03.9 ,
()

457

G04 ,
:


: (G93.3)
:
(G93.4)
(G31.2)
(G92)
(G35)
:
(G37.3)
(G37.4)
G04.0



-
( ).
G04.1
G04.2 ,

G04.8 ,

G04.9 , ,
()

G05* ,
,
: -
,

458

G05.0* , -
,
, ():
(32.1)
(39.8)
:
(50.4)
(52.1)
(17.8)
G05.1* ,
,
, ():
(85.1)
(25.8)
(85.0)
herpes simplex (B00.4)
(J10.8, J11.8)
(05.0)
(26.2)
(01.1)
(06.0)
herpes zoster (02.0)
G05.2* ,
,

, :
(56.)
Chagas ( ) (57.4)
,
(naegleria) (60.2)
(58.2)
(83.2)
G05.8* , ,

lupus (M32.1)

459

G06


(9597).
G06.0
():
[ ]



:



G06.1
() [ ]
:



G06.2 ,

G07*
,

:
(06.6)
(54.8)
(17.8)
(65.)
:
(17.8)
(17.1)

460

G08

(-):





: :
:
, -
(0007, 08.7)
,
(22.5, 87.3)
(I67.6)
-
(G95.1)

G09

: -
,
G00G08 ( -
,
*) ,
.
,
, -

, . -


-
, 2.

461

,

(G10G13)
G10 Huntington
Huntington

G11
:
(G60.)
(G80.)

(7090)
G11.0
G11.1
: 20- -
.
:

[ Hunt]

Friedreich (-)
-
G11.2
: 20- .
G11.3 -

- [ Louis-Bar]
: Cockayne (Q87.1)
(Q82.1)
G11.4
G11.8

462

G11.9 ,
(-) (-):



G12

G12.0 , I [Werd-
nig-Hoffman]
G12.1
[Fazio-Londe]
:

, II

, III [Kugelberg-Welander]
-
G12.2

:


:


G12.8 -

G12.9 ,

463

G13* ,
,
,
G13.0*
(0097)
[Denny-Brown] (00
D48)
G13.1* , -
,
(00D48)
G13.2* , -
(00.1, 03.)
G13.8* , -
, ,

(G20G26)
G20 Parkinson

Paralysis agitans
Parkinson:

(-)
(-)

G21
G21.0


( ).

464

G21.1 , -



( ).
G21.2 ,


( ).
G21.3
G21.8
G21.9 ,

G22* ,

(52.1)

G23

: (G90.3)
G23.0 Hallervorden-Spatz

G23.1 [Steele-
Richardson-Olszewski]
G23.2
G23.8 -


G23.9 , -

465

G24
:
: (G80.3)
G24.0 ,


( ).
G24.1

G24.2
G24.3
: (43.6)
G24.4

G24.5
G24.8
G24.9 ,

G25

G25.0

: (R25.1)
G25.1 ,


( ).
G25.2

466

G25.3
,


( ).
: (G51.4)
(G40.)
G25.4 ,


( ).
G25.5

: , (I02.0)
Huntington (G10)
(I02.)
Sydenham (I02.)
G25.6 ,



( ).
: de la Tourette (F95.2)
(F95.9)
G25.8 -



G25.9 , -

G26*
,

467



(G30G32)
G30
:
: :
, (G31.1)
(F03)
(R54)
G30.0
: 65-
.
G30.1
: 65-
.
G30.8
G30.9 ,

G31
,

: Reye (G93.7)
G31.0
Pick

G31.1 , -

: (G30.)
(R54)

468

G31.2 ,

:
:




[] ,

G31.8

[ Alpers]
[ Leigh]
G31.9 , -

G32*
,

G32.0*
,

12 (53.8)
G32.8* -
,

469



(G35G37)
G35
:




G36

: -
(G04.8)
G36.0 [ Devic]

: (H46)
G36.1
[ Hurst]
G36.8

G36.9 ,

G37

G37.0

Schilder
: [Addison-Schilder]
(71.3)

470

G37.1 corpus callosum


G37.2
G37.3 -


: (G35)
[ Devic] (G36.0)
G37.4
G37.5 [Balo]
G37.8 -

G37.9
,

(G40G47)
G40
: Landau-Kleffner (F80.3)
(R56.8)
(G41.)
Todd (G83.8)
G40.0 () ()
--

-

-

471

G40.1 () () -
-


, -

G40.2 () () -
-

, -

, -

G40.3 -

(-):

()
[]
[grand mal]

:
-
[ , petit
mal]
:




-

472

G40.4 -

:

-

Lennox-Gastaut


West
G40.5
[Kozevnikof]
, :







( ).
G40.6 Grand mal ( [petit
mal] ),
G40.7 [petit mal], grand
mal,
G40.8
,

G40.9 ,
:


473

G41
G41.0 grand mal ( -
)
-
:
[Kozhevnikof] (G40.5)
G41.1 petit mal ( )

G41.2
G41.8
G41.9 ,

G43
: (R51)
G43.0 [ ]
G43.1 [ ]
:





:



G43.2
G43.3
G43.8


G43.9 ,

474

G44
: (G50.1)
(R51)
(G50.0)
G44.0

:


G44.1 ,

G44.2



G44.3
G44.4 , -
,


( ).
G44.8

G45
[]
: (91.0)
G45.0 -

G45.1 ()
G45.2 -

G45.3

475

G45.4
: (R41.3)
G45.8

G45.9 ,

G46*
(I60I67)
G46.0* (I66.0)
G46.1* (I66.1)
G46.2* (I66.2)
G46.3* (I60I67)
:
Benedikt
Claude
Foville
Millard-Gubler
Wallenberg
Weber
G46.4* (I60I67)
G46.5* (I60I67)
G46.6* (I60I67)
G46.7* (I60I67)
G46.8* -
(I60I67)

476

G47
: (F51.5)

(F51.)
(F51.4)
(F51.3)
G47.0
[]
G47.1 []
G47.2 -



G47.3
:


: Pickwick (66.2)
(28.3)
G47.4
G47.8
Kleine-Levin
G47.9 e ,

477

,

(G50G59)
: ,
-


(79.2)

(26.8)
(54.1)

G50
: 5-
G50.0


G50.1
G50.8
G50.9 ,

G51
: 7-
G51.0 Bell

G51.1 ganglion geniculi
: ganglion genicu-
li (02.2)
G51.2 Melkersson
Melkersson-Rosenthal
G51.3
G51.4

478

G51.8
G51.9 ,

G52

: :
(8-) (93.3)
(2-) (46, 47.0)
,
(49.049.2)
G52.0
1-
G52.1 n. glossopharingeus
9-

G52.2 n. vagus
(10-)
G52.3
12-
G52.7


G52.8

G52.9 , -

G53*
,
G53.0* herpes zoster(02.2)
(-):
ganglion geniculi

479

G53.1* -
, -
(0099)
G53.2* -
(D86.8)
G53.3* -
(00D48)
G53.8*
,

G54

:
-


(5051)
(79.2)
:


-
(54.1)



(47.)
G54.0

G54.1 -
G54.2 , -

G54.3 , -

G54.4 - , -

480

G54.5
Parsonage-Aldren-Turner

G54.6
G54.7

G54.8
G54.9 , -

G55*
,

G55.0*
(00D48)
G55.1*
(50
51)
G55.2*
(47.)
G55.3*
(4546, 48., 53
54)
G55.8*
,

G56
: -
-

G56.0
G56.1

481

G56.2

G56.3
G56.4
G56.8

G56.9 ,

G57
: -
-

G57.0
: :
(54.3)

(51.1)
G57.1

G57.2
G57.3 n. fibularis
()
G57.4 n. tibialis
G57.5
G57.6 n. plantaris
Morton
G57.8

G57.9 ,

G58
G58.0

482

G58.7
G58.8
G58.9 ,

G59* ,

G59.0* (1014 -
.4)
G59.8* , -



(G60G64)
: (79.2)
(79.2)
(26.8)
(54.1)

G60

G60.0
:
Charcot-Marie-Tooth
Djerine-Sottas
, I-IV

( )(-
)
Roussy-Levy
G60.1 Refsum
G60.2

483

G60.3
G60.8
Morvan
Nelaton
:


G60.9 , -

G61
G61.0 Guillain-Barr
(-)
G61.1
-
( ).
G61.8
G61.9 ,

G62
G62.0


( ).
G62.1
G62.2 ,

-
(
).

484

G62.8


( ).
G62.9 ,

G63* ,

G63.0* -
,
:
(36.8)
(27.)
(30.)
(69.2)
(26.8)
herpes zoster (B02.2)
(52.1)
(50.4)
(17.8)
G63.1* (00D48)
G63.2* (1014 -
.4)
G63.3*
(00
07, 1516, 2034, 7089)
G63.4* (40
64)
G63.5* -
(3035)
G63.6* - -
(0025, 4096)

485

G63.8* , -

(N18.8)

G64

-

(G70G73)
G70 Myasthenia gravis
-
: (05.1)
Myasthenia gravis (94.0)
G70.0 Myasthenia gravis
, -

( ).
G70.1 -
-
(
).
G70.2
G70.8 -
G70.9 - , -

486

G71
: arthrogryposis multiplex congenita (Q74.3)

(7090)
(60.)
G71.0
:
- , -
Duchenne Becker
[Becker]
-
[Emery-Dreifuss]

--
-


-
[Duchenne]
: :
(G71.2)

(G71.2)
G71.1
[Steinert]
:



:

[Thomsen]
[Becker]
[Isaacs]



, , -
( ).

487

G71.2
:



:




:
()

G71.3 , -

G71.8
G71.9 ,

G72
: arthrogryposis multiplex congenita (Q74.3)
(33.)
(62.2)
(60.)
(33.2)
G72.0

, , -
( ).
G72.1
G72.2 , -

-
(
).

488

G72.3
():




G72.4 ,
G72.8
G72.9 ,

G73* -
,

G73.0*
:
(1014 .4)
[] (05.)
G73.1* Eaton-Lambert (80)
G73.2*
(00D48)
G73.3* ,

G73.4* ,

G73.5*
:
(21.021.3)
(20.)
(05.)

489

G73.6* -

:
(74.0)
(75.)
G73.7* ,
:
(0506)
(34.8)
Sjogren (35.0)
lupus (32.1)



(G80G83)
G80
: Little
: (G11.4)
G80.0
()
G80.1
G80.2
G80.3

G80.4
G80.8

G80.9 ,

490

G81
: -
, -
() () -
,
,
,
.
-
,
.
: (G80.)
G81.0
G81.1
G81.9 ,

G82
: -
, -

, -
, -
, . -
-
-
, .
: (G80.)
G82.0
G82.1
G82.2 ,

()
G82.3
G82.4
G82.5 ,

491

G83
: -
, -

, -
, -
, . -
-
-
, .
: () (),
G80G82
G83.0
()

G83.1

G83.2

G83.3 ,
G83.4 cauda equina
, cauda
equina
: (G95.8)
G83.8
Todd ()
G83.9 ,

492

(G90G99)
G90
[]
: -
, (G31.2)
G90.0
,
G90.1 [Riley-Day]
G90.2 Horner
Bernard(-Horner)
G90.3
[Shy-Drager]
: (I95.1)
G90.8 []

G90.9 [] -
,

G91
:
: :
(Q03.)

(37.1)
G91.0
G91.1
G91.2
G91.3 ,

493

G91.8
G91.9 ,

G92
-
(
).

G93
G93.0


: -
(91.1)
(Q04.6)
G93.1 , -

: :
, -
(0007, 08.8)
,
(29.2, 74.3, 89.2)
(8088)
(21.9)
G93.2
: (I67.4)
G93.3 -


G93.4 ,
: :
(G31.2)
(G92)

494

G93.5

( )
:
(S06.2)
(S06.3)
G93.6
: :
(11.0)
(S06.1)
G93.7 Reye

( ).
G93.8
,

( ).
G93.9 ,

G94*
,
G94.0* -
, (0099)
G94.1* (00D48)
G94.2* ,

G94.8*
,

G95
: (G04.)
G95.0

495

G95.1
()(-
)





: ,
(G08)
G95.2 ,
G95.8

:



( ).
: :
(N31.9)
cauda equina
(G83.4)
- -
-
(N31.)
G95.9 ,

G96

G96.0
: (G97.0)
G96.1 , -

()()

496

G96.8

G96.9 , -

G97
,

G97.0
G97.1
G97.2 -

G97.8 -

G97.9
,

G98 ,

G99*
,
G99.0* -

(85.)
(1014
.4)
G99.1* []
, -

497

G99.2* ,

(47.0)
:
(50.0,
51.0)
(00D48)
(47.)
G99.8*
,

498
VII


(H0059)

: ,
(0096)
(0099)
,
(0099)
,
(Q00Q99)
, -
(0090)
, -
(S00T98)
(C00D48)
, ,
, -
(R00R99)


:
H00H06 ,
H10H13
H15H22 , ,
H25H28
H30H36
H40H42
H43H45
H46H48
H49H52 , -
,
H53H54
H55H59

:
H03* ,
H06* , -

499

H13* ,

H19* , -

H22* , -

H28* , -

H32* ,

H36* , -

H42* ,
H45* -
,
H48* -
,
H58* ,

,

(H00H06)
H00
H00.0
A



H00.1

H01
H01.0
: (H10.5)

500

H01.1
:





H01.8
H01.9 ,

H02
: (Q10.0Q10.3)
H02.0
H02.1
H02.2
H02.3
H02.4
H02.5 ,



: (G24.5)
() (F95.)
(G25.6)
H02.6
H02.7 -




H02.8


H02.9 ,

501

H03* ,

H03.0* , -

, Demodex (B88.0)
:
(B55.)
(B74.3)
(B73)
(B85.3)
H03.1* -
,
:
- [herpes simplex] (B00.5)
(30.)
(08.1)
(18.4)
(66.)
herpes zoster (B02.3)
H03.8* , -

(L01.0)

H04
: (Q10.4
Q10.6)
H04.0

H04.1


:


H04.2

502

H04.3 -

()
,


a
: (39.1)
H04.4

:
(-)
a

H04.5


:

()

H04.6

H04.8
H04.9 ,

H05
: (Q10.7)
H05.0






H05.1

503

H05.2
c ()



H05.3



H05.4
H05.5 ( )


H05.8

H05.9 ,

H06*
,

H06.0* , -

H06.1* , -

(67.)
(B87.2)
H06.2* -
(05.)
H06.3* , -

504


(H10H13)
H10
: (16.2)
H10.0
H10.1
H10.2
H10.3 ,
: (39.1)
H10.4
H10.5
H10.8
H10.9 ,

H11 k
: (16.2)
H11.0
: (11.8)
H11.1
:




H11.2

H11.3

505

H11.4
:



H11.8

H11.9 ,

H13*
,
H13.0* (B74.)
H13.1* ,

( ):
(60.1)
() (30.1)
(74.0)
(36.8)
(54.3)
() () (30.3)
- [herpes simplex] (B00.5)
(39.8)
Newcastle (30.8)
herpes zoster (B02.3)
H13.2* ,
H13.3* (L12.)
H13.8* ,

506

, ,

(H15H22)
H15
H15.0
H15.1
H15.8

( )
: (44.2)
H15.9 ,

H16
H16.0
:
:






Mooren
H16.1
:


()

()


507

H16.2
:

( )




H16.3
H16.4
()
()
H16.8
H16.9 ,

H17
H17.0 ()
H17.1
H17.8 () -

H17.9 ,

H18
H18.0
()
Kayser-Fleischer
Krukenberg
Staehli

, , -
( ).
H18.1
H18.2

508

H18.3



H18.4


: Mooren (H16.0)
H18.5
:
:




Fuchs
H18.6
H18.7
:



: (Q13.3
Q13.4)
H18.8



H18.9 ,

19*
,
H19.0* , -

(52.7)
(18.5)
herpes zoster (02.3)

509

H19.1* , -
herpes simplex (B00.5)

H19.2* -
,
(30.0)
() :
(60.1)
(05.8)
(50.3)
(18.5)
herpes zoster (02.3)
H19.3* , -

(M35.0)
H19.8* -
,
Down (Q90.)

20
H20.0

,

H20.1
H20.2 ,
H20.8
H20.9 ,

21

: (44.1)
H21.0
: (S05.1)

510

H21.1


H21.2
:
()


()()


H21.3 , -

, :




: (21.2)
H21.4

:


H21.5



()
:



: (Q13.2)
H21.8
H21.9 ,

511

22*
,

H22.0* , -

:
(54.3)
- [herpes simplex] (00.5)
() (51.4)
(18.5)
herpes zoster (B02.3)
H22.1* ,
:
(45)
(D86.8)
H22.8*
,


(2528)
25
:
(H40.1)
H25.0
:



()()
()
H25.1
brunescens

512

H25.2 ,

H25.8

H25.9 ,

26
: (Q12.0)
H26.0 ,
H26.1
-
( ).
H26.2


( )
H26.3 ,

, , -
( ).
H26.4

Soemmerring
H26.8
H26.9 ,

27
: (Q12.)
, -
(85.2)
(Z96.1)
H27.0
H27.1

513

H27.8
H27.9 ,

28*
,

H28.0* (1014
.3)
H28.1* -
,
, k
(20.)
(40
46)
H28.2* , -

(G71.1)
H28.8* , -


(3036)
30
H30.0
:



514

H30.1
:




: (H35.0)
H30.2
Pars planitis
H30.8
Harada
H30.9 ,




H31
H31.0
( )
()

H31.1



: (35.3)
H31.2

(-)(-
)()

: (72.4)
H31.3
:

515

H31.4
H31.8
H31.9 ,

32*
,
H32.0*
,
:
(52.7)
(58.0)
(18.5)
H32.8* ,

33
:
(35.7)
H33.0

H33.1
ora serrata


: (Q14.1)

(35.4)
H33.2



: (35.7)

516

H33.3



Operculum

:
(59.8)
-
(35.4)
H33.4
-

H33.5

34
: (G45.3)
H34.0
H34.1
H34.2
Hollenhorst
:
:



H34.8
:




H34.9 ,

517

35
H35.0 -


:






:


Coats


H35.1

H35.2

: -
(33.4)
H35.3


()


Kuhnt-Junius
()(-
)


, , -
( ).

518

H35.4
:






: (33.3)
H35.5
:
()()()



Stargardt
H35.6
H35.7 ,


H35.8
H35.9 ,

36* ,

H36.0* (1014
.3)
H36.8* , -

(I70.8)
- (D57.)

(75.)

519

(4042)
40
: (44.5)
(Q15.0)

(15.3)
H40.0

H40.1
()( ):




H40.2
()( ):



H40.3 ,
-
.
H40.4 ,

-
.
H40.5 ,

-
.

520

H40.6 ,


, , -
( ).
H40.8
H40.9 ,

42* ,

H42.0* ,
-

:
(85.)
Lowe (72.0 )
H42.8* , -

(73)



(4345)
43
H43.0
: -
(59.0)
H43.1
H43.2
H43.3

521

H43.8
:


: -
(33.4)
H43.9 ,

44
: ,

H44.0


H44.1


H44.2
H44.3


H44.4
H44.5



H44.6 ( )

:





522

H44.7 ( )

:






H44.8


H44.9 ,

45*
,

H45.0* ,

H45.1* ,
:
(69.1)
(73)
(83.0)
H45.8*
,

523



(4648)
46
(-):
,


:
(47.0)
[Devic] (G36.0)

47 [2-]

H47.0 , -




H47.1 ,
H47.2

H47.3


H47.4
H47.5
, nuclei geniculate -

H47.6
H47.7 ,

524

48* [2-]
,

H48.0* , -

(52.1)
H48.1* ,

:
(52.1)
(39.8)
(G35)
H48.8*
,

,

,
(4952)
: (55)

49
: :
(52.5)
(51.2)
(G23.1)
H49.0 3- [n. ocumotorius]
H49.1 4- [n. trochlearis]
H49.2 6- [n. abducent]
H49.3 ()

525

H49.4
H49.8

Kearns-Sayre
H49.9 ,

50
H50.0
()(), -

H50.1
()(), -

H50.2


H50.3
:

()()

H50.4




H50.5



H50.6
Brown
,

526

H50.8
Duane
H50.9 ,

51

H51.0
H51.1 [
]
H51.2
H51.8 -

H51.9 , -

52

H52.0
H52.1
: (44.2)
H52.2
H52.3
H52.4
H52.5
()()



H52.6
H52.7 ,

527


(5354)
53
H53.0 ,
, :



H53.1








: (R44.1)
H53.2

H53.3




H53.4


()()

:
()
Bjerrum

528

H53.5









: (H53.1)
H53.6
: (50.5)
H53.8
H53.9 ,

54
:
-.
: (G45.3)
H54.0
3, 4, 5
H54.1 ,

3, 4, 5
1 2
H54.2
1 2
H54.3
9
H54.4
3, 4 5
[ ]
H54.5
1 2
[ ]

529

H54.6
9 [-
]
H54.7 ,
9

: - -
,
, -
6-10 1972 .1
H54 1 2 ,
3, 4 5, -
9. -
, -
- 100, 50 -
,
3, 50 -
4, -
.
-

: :

6/18 6/60
1 3/10 (0.3) 1/10 (0.1)
20/70 20/200
6/60 3/60
2 1/10 (0.1) 1/20 (0.5)
20/200 20/400
3/60 1/60 (
1 )
3
1/20 (0.05) 1/50 (0.02)
20/400 5/300 (20/1200)
1/60 ( -
1 )
4
1/50 (0.02)
5/300
5

1
WHO Technical Report Series 518, 1973.

530


(5559)
55

:




57

H57.0
H57.1
H57.8

H57.9 ,

58*
,

H58.0* ,

Argil Robertson, (52.1)
H58.1* , -

531

H58.8*
,
,
:
(50.0)
(50.3)
() (51.4)
(52.7)

59

: :
(85.2)
, -
(T85.3)
(Z96.1)
H59.0

H59.8

-

H59.9 -
,

532
VIII

(6095)
: ,
(0096)
(0099)
,
(0099)
,
(Q00Q99)
, -
(0090)
, -
(S00T98)
(00D48)
, ,
, -
(R00R99)

:
6062
6575
8083
9095

:
62* ,

67* ,

75*
, .
82* , -

94* , -

533


(6062)
60
H60.0





H60.1
:


H60.2
H60.3
:



H60.4
()
H60.5 ,
:






H60.8

H60.9 ,

534

61
H61.0

:


H61.1
:


: ,
(95.1)
H61.2

H61.3

H61.8

H61.9 ,

62*
,
H62.0* , -

(46)
H62.1* ,

:
- [herpes simplex] (00.1)
herpes zoster (02.8)

535

H62.2*
:
(44.8)
(37.2)
(36.9)
H62.3*
,
H62.4* ,

(L01.)
H62.8* ,



(6575)
65
:
H65.0

H65.1
Otitis media, :
()()()




: (70.0)
titis media acuta (66.9)
H65.2

536

H65.3

otitis media:



: (74.1)
H65.4

:




()
H65.9 ,
:








()

66

:
H66.0
H66.1


[]

537

H66.2 -

- []
H66.3

H66.4 ,

H66.9 ,
Otitis media:


67*
,
H67.0* -
,
Otitis media :
(38)
(18.6)
H67.1* ,

Otitis media :
(J10J11)
(05.3)
H67.8* ,

68

H68.0
H68.1


538

69
H69.0
H69.8
H69.9 ,

70
H70.0



H70.1



H70.2
pars petrosa () ()
H70.8
H70.9 ,

71

: (60.4)
-
(90.5)

72
: :


: (S09.2)
H72.0
H72.1
pars flaccida
H72.2

539

H72.8 :
(-):



H72.9 ,

73
H73.0


: otitis media (H65H66)
H73.1

: otitis media (H65H66)
H73.8
H73.9 ,

74

H74.0
H74.1

: (65.3)
H74.2
H74.3



H74.4
H74.8 -

H74.9 , -

540

H75*
,

H75.0* ,

(18.0)
H75.8* -
,


(8083)
H80
:
H80.0 , , -

H80.1 , , -

H80.2 ,
, :


H80.8
H80.9 ,

H81
: :
(R42)
(88.0)
H81.0 Meniere

, , Meniere

541

H81.1
H81.2
H81.3
Lermoyez
:



H81.4

H81.8
H81.9 , -

H82* ,

H83
H83.0
H83.1
H83.2



H83.3


H83.8
H83.9 ,

542


(9095)
H90 ,
()

:
: , (91.3)
(91.9)
a :
(H91.9)
(83.3)
(91.0)
() (91.2)
H90.0 () -

H90.1 -

H90.2 ,
, ,

H90.3
H90.4 -

H90.5 ,

:





543

H90.6

H90.7
,
H90.8 ,

H91
: (93.2)
a ,
90.
(61.2)
a
(83.3)
(F44.6)
(93.0)
H91.0

( ).
H91.1

H91.2

H91.3 ,
H91.8
H91.9 ,
:


H92
H92.0

544

H92.1
:
(G96.0)
H92.2 ( )
: (
)

H93 ,

H93.0

: (91.1)
H93.1 ()
H93.2




: (R44.0)
H93.3
8-
H93.8
H93.9 ,

H94*
,
H94.0*
,
(52.1)
H94.8* ,

545

H95
,

H95.0 -

H95.1



H95.8

H95.9
,

546
IX



(I00I99)

: ,
(0096)
(0099)
,
(0099)
,
(Q00Q99)
, -
(0090)
, -
(S00T98)
(00D48)
, ,
, -
(R00R99)
(30
36)
-
(G45.)
:
I00I02
I05I09
I10I15
I20I25
I26I28 [ ]

I30I52
I60I69
I70I79 ,
I80I89 , , -

I95I99 -

547

:
I32* ,
I39* ,

I41* ,
I43* ,
I52* ,

I68* ,

I79* , -
,
I98* -
,


(I00I02)
I00

I01
:
(I05I09), -
,
. ,
-
,

2.
I01.0
, I00,
()
: , (I30.)

548

I01.1
, I00,

I01.2
, I00,
I01.8
, I00,


I01.9 ,
, I00,

:
,
,

I02
: Sydenham
:
(G25.5)
Huntington (G10)
I02.0


I01.
I02.9

549



(I05I09)
I05

: , I05.0
I05.2I05.9,

: , (I34.)
I05.0
() ()
I05.1
:


I05.2

I05.8
()
I05.9 ,
() ()

I06
: , (I35.)
I06.0
()
I06.1
:

550

I06.2
-

I06.8
I06.9 ,
()

I07

: , -

: , (I36.)
I07.0
() ()
I07.1
() ()
I07.2
I07.8
I07.9 ,

I08
: , -

: (I38)
-
(I09.1)
I08.0
, -

I08.1 -

551

I08.2

I08.3 , -

I08.8
I08.9 ,

I09
I09.0
: , (I51.4)
I09.1

:
()
()
: (I38)
I09.2

:


: , (I31.)
I09.8

I09.9 ,
:


: (05.3)

552


(I10I15)
: ,
(1011, 1316)
(I20I25)
(29.2)
(I27.0)

I10 []

()()()(-
)()()
: :
(I60I69)
(35.0)

I11
: I50., I51.4
I51.9,
I11.0 () -


I11.9 () -

553

I12
[ ]
: N18., N19.
N26.
I10

()(-
)


: (I15.)
I12.0

I12.9

I13

: I11. -
I12.
:
-
-
I13.0
()
I13.1

I13.2
() -
,
I13.9
,

554

I15
: :
(I60I69)
(35.0)
I15.0 -
I15.1 , -

I15.2 , -

I15.8
I15.9 ,


(I20I25)
:
, I21I25,

.
-

.
: (I10I15)

.

I20
I20.0
:




555

I20.1
:

Prinzmetal


I20.8

I20.9 ,
:



I21
: ,
4
(28 ) -
:
(I23.)
:
(I25.2)

4 ( 28 -
) (I25.8)
(I22.)
(I24.1)
I21.0 -

()():
( )
-
-
-

556

I21.1 -

()():

( )
-
-
I21.2

():
-
-

( )
()
-
-
-

I21.3 -


I21.4

I21.9 ,
()

I22
:
: -
4 ( 28 )
(I25.8)
I22.0
()():
( )
-
-
-

557

I22.1
()():

( )
-
-
I22.8

():
-
-

( )
()
-
-
-

I22.9 -

I23

: , :

(I21I22)

(I31., I51.)
I23.0

I23.1

I23.2

558

I23.3 -
-

: (I23.0)
I23.4 -

I23.5 -

I23.6 , -


I23.8

I24

: (I20.)

(29.4)
I24.0 , -

()():



: -
4 ( 28 )
(I25.8)
I24.1 Dressler

I24.8
:

559

I24.9 ,
: ()
(I25.9)

I25
: - (I51.6)
I25.0 - -

I25.1
(-) ((-)):




I25.2

,
,

I25.3
:


I25.4
,
: () (Q24.5)
I25.5
I25.6
I25.8
I21I22 I24.,
4
( 28 )
I25.9 ,
()

560

[
]

(I26I28)
I26
: (-) ()():



: :
, -
(0007, 08.2)
,
(88.)
I26.0 -


I26.9 -

I27
I27.0
() ()(-
)
I27.1
I27.8
I27.9 ,
-
[cor pulmonale] ()

561

I28
I28.0
I28.1
I28.8



I28.9 - ,


(I30I52)
I30
:
: () (I01.0)
I30.0
I30.1
:







(9597).
I30.8
I30.9 ,

562

I31
:
(I23.)
(I97.0)
(S26.)
, (I09.2)
I31.0
Accretio cordis


I31.1
Concretio cordis

I31.2 ,
I31.3 ()

I31.8


I31.9 ,

()

I32* ,

I32.0* , -

:
(54.8)
(39.5)
(52.0)
(18.8)
I32.1*
,

563

I32.8* ,

():
(32.1)
(32.1)
(N18.8)

I33
: (I01.1)
(I38)
I33.0
()():







(9597).
I33.9 ,


I34

: ():
(I05.9)
(I05.8)
(I05.0)
, :
(I08.0)
(I05.0)
(I05.)

564

I34.0 ()
():
,

I34.1 ()

: arfan (Q87.4)
I34.2 ()
I34.8
I34.9 , -

I35

: (I42.1)
,
(I08.0)
(I06.)
I35.0 ()
I35.1 ()
():
,

I35.2 ()
I35.8
I35.9 ,

I36

: (I07.)
(I07.)
I36.0 ()

565

I36.1 () -

():
,

I36.2 ()

I36.8

I36.9 ,

I37
: (I09.8)
I37.0
I37.1
:
,

I37.2
I37.8
I37.9 ,

I38

()
:



,

-
()
: (I42.4)
(I09.1)

566

I39*
,

: :
(37.6)
(54.8)
Libman-Sacks (32.1)
(39.5)
(05.3)
(52.0)
(18.8)
(01.0)
I39.0* , -

I39.1* , -

I39.2* -
,
I39.3* ,

I39.4* , -

I39.8*
,

I40
I40.0


(9597).
I40.1
I40.8
I40.9 ,

567

I41* ,

I41.0* , -

:
(36.8)
(54.8)
(39.5)
(52.0)
(18.8)
I41.1* ,

():
(J10.8)
(J11.8)
(26.8)
I41.2*
,
:
Chagas () (57.2)
(57.0)
(58.8)
I41.8* ,

(05.3)
(D86.8)

I42
: , :
(99.4)
(90.3)
(I25.5)
I42.0
I42.1

568

I42.2

I42.3 ()
()
Lffler
I42.4

I42.5
I42.6
I42.7 ,

-
( ).
I42.8
I42.9 ,
()()

I43* ,

I43.0* -
,
(36.8)
I43.1*
(85.)
I43.2*
(63.9)
I43.8* , -

(10.0)
(05.9)

569

I44

I44.0 ,
I44.1 ,
, I II
Mobitz, I II
, I II
Wenckebach
I44.2 ,


I44.3

I44.4
I44.5
I44.6

I44.7 ,

I45
I45.0
I45.1

I45.2
I45.3
I45.4

I45.5


: (I45.9)

570

I45.6

:



Lown-Ganong-Levine
Wolff-Parkinson-White
I45.8
[V]

I45.9 ,

Morgagni-Adams-Stokes (MAS-)

I46
: (R57.0)
:
, -
(0007, 08.8)
(75.4)
I46.0

I46.1 ,
: :
(R96.)
:
(I44I45)
(I21I22)
I46.9 ,

571

I47
: :
, -
(0007, 08.8)
(75.4)
(R00.0)
I47.0 [re-entry]
I47.1
:

[V]


I47.2
I47.9 ,
Bouveret-Hoffmann

I48

I49
: (R00.1)
:
, -
(0007, 08.8)
(75.4)

(29.1)
I49.0
I49.1

I49.2 -

I49.3

572

I49.4 -




:


I49.5
()-()
I49.8
:



I49.9 ,
()

I50
: :
, -
(0007, 08.8)
(75.4)
(I11.0)
(I13.)
-
(I97.1)
(29.0)
I50.0

(
)
I50.1




573

I50.9 ,
,

I51

: I51.4I51.9, -
(I11.)
(I13.)

(I23.)
(I00I09)
I51.0 ,
():



I51.1 ,

I51.2 ,

I51.3 , -

():




I51.4 ,

:

()

574

I51.5
:



I51.6 - ,
-
: - ,
(I25.0)
I51.7
:



I51.8
()()
()()
I51.9 ,

I52*
,
: - -
, (I98.*)
I52.0* -
,
, (39.5)
I52.1* -
,
(65.)
I52.8* ,

(05.3)

575


(I60I69)
: (
I10 I15.)
-
.
: -
(G45.)
(S06.)
(F01.)

I60
:
:
(I69.0)
I60.0 -

I60.1

I60.2 -

I60.3 -

I60.4 -

I60.5 -

I60.6 -

576

I60.7
,
()
:



I60.8


I60.9 ,
()

I61
: (I69.1)
I61.0 , -


I61.1 , -



I61.2 ,
I61.3
I61.4
I61.5
I61.6 -

I61.8
I61.9 ,

577

I62

: (I69.2)
I62.0 ()()
I62.1

I62.9 (), -

I63
: -
, -

: (I69.3)
I63.0 , -

I63.1 , -

I63.2 , -

I63.3 , -

I63.4 , -

I63.5 , -

I63.6 , -

I63.8
I63.9 ,

578

I64 ,


: (I69.4)

I65
,

: , -
-
,
()()

: (I63.)
I65.0
I65.1
I65.2
I65.3 -

I65.8
I65.9 -

I66
,

: , -

() -
() , -

: (I63.)
I66.0

579

I66.1
I66.2
I66.3
I66.4 -

I66.8

I66.9 -

I67
: (I69.8)
I67.0
: (I60.7)
I67.1
:

,
: (Q28.)
(I60.9)
I67.2

I67.3
Binswanger
: (F01.2)
I67.4
I67.5 Moyamoya
I67.6

:


: (I63.6)

580

I67.7 ,
I67.8

()
I67.9 ,

I68*
,
I68.0* (85.)
I68.1*
,
:
(32.8)
(52.0)
(18.8)
I68.2* , -


(32.1)
I68.8* ,

I69
: , -
, I60I67
,
.
,
, .. -

.
I69.0
I69.1

581

I69.2

I69.3
I69.4 ,

I69.8

,

(I70I79)
I70
:



:




:


: (I67.2)
(I25.1)
(55.1)
(I27.0)
I70.0
I70.1
Goldblatt
: (I12.)

582

I70.2

() Mnckeberg
I70.8
I70.9

I71
I71.0 ( )
( ) ( -
)
I71.1
I71.2

I71.3
I71.4 -

I71.5 - -

I71.6 - -

I71.8 ,


I71.9



583

I72
: ()()( )
: ():
(I71.)
(Q27.3)
(I77.0)
( ) (I67.1)
(I60.)
(I25.4)
(I25.3)
(I28.1)
(35.0)
(I77.0)
I72.0
I72.1
I72.2
I72.3
I72.4
I72.8
I72.9

I73
: (69.1)
(3335)
(69.0)
(G45.9)
I73.0 Raynaud
Raynaud:


()
I73.1 [ Buerger]

584

I73.8

:
[ Schultze]
[ Nothnagel]
E

I73.9 ,

I74
: :


:


: :
(I63.0I63.2, I65.1)
(I63.0I63.2, I65.2)
(I63.3I63.5, I66.9)
(I21I25)
(55.0)
(I63.0I63.2, I65.9)
(I26.)
(N28.0)
(34.)
(I63.0I63.2, I65.0)
:
, -
(0007, 08.2)
,
(88.)
I74.0

Leriche

585

I74.1

I74.2 -

I74.3 -

I74.4 ,


I74.5
I74.8
I74.9

I77 -

: () (3036)
(31.0)
(I28.)
I77.0 ,

,
: (Q27.3)
(I67.1)
(I25.4)


I77.1

586

I77.2



:
-

I77.3
I77.4
I77.5
I77.6 ,


: :
[ Takayasu] (31.4)
, (I67.7)
(I25.8)
(I70.)
(31.531.6)
(I70.)
(I70.)
I77.8 -

I77.9 ,

I78
I78.0
Rendu-Osler-Weber

587

I78.1 ,
:



: :
(D22.)
(D22.)
(Q82.5)
(D22.)
(D22.)
(D22.)
(Q82.5)
(Q22.5)
(Q82.5)
(Q82.5)
(Q82.5)
I78.8
I78.9 ,

I79* ,
,

I79.0* ,

(52.0)
I79.1* ,
(52.0)
I79.2* , -

(1014
.5)
I79.8* , -
,

588

,
,

(I80I89)
I80
:



: :
:
, -
(0007, 08.7)
,
(22., 87.)
,
(G08)
, (I67.6)
, (G95.1)
( ) (75.1)
(I87.0)
(I82.1)

, , -
( ).
I80.0

I80.1
I80.2


I80.3 , -

589

I80.8
I80.9

I81
()
: (75.1)

I82
: :
(I63.6, I67.6)
(I21I25)
,
(G08)
, (I67.6)
, (G95.1)
(I80.)
(55.0)
(I81)
(I26.)
:
, -
(0007, 08.8)
,
(22., 87.)
I82.0 Budd-Chiari
I82.1
I82.2
I82.3
I82.8
I82.9

()

590

I83
: :
(22.0)
(87.8)
I83.0
, I83.9,

( , )
I83.1
, I83.9,


I83.2 -

, I83.9, -

I83.9


[ ]


I84
:

: :
(87.2)
(22.4)
I84.0
I84.1
:



591

I84.2

I84.3
I84.4
:




I84.5

I84.6

I84.7 ,
,

I84.8 ,
, :




I84.9 ,

I85
I85.0
I85.9

I86
: (35.0)

(I83.9)

592

I86.0
I86.1

I86.2
I86.3
: :
(87.8)
(22.1)
I86.4
I86.8

I87
I87.0
I87.1

()()
: (I28.8)
I87.2 ()()
I87.8
I87.9 ,

I88
: , -
(L04.)
(R59.)
,
[HIV], -
(23.1)
I88.0
()()

593

I88.1 , -

, ,

I88.8
I88.9 ,

I89

: :
(74.)
()
(N50.8)
(R59.)
(Q82.0)
(I97.2)
I89.0 ,

I89.1
:



: (L03.)
I89.8 -

()

I89.9 -
,

594



(I95I99)
I95
: - (R57.9)
(26.5)

(R03.1)
I95.0
I95.1
,
: [ Shy-
Drager] (G90.3)
I95.2 ,


( ).
I95.8

I95.9 ,

I97
,

: (81.1)
I97.0
I97.1



595

I97.2


I97.8 -
,
I97.9 -
,

I98*
,

: ,
, -

I98.0* -
- :
(52.0)
, (50.5)
I98.1* -
,
-:
, Chagas ( -
) (57.2)
[] (67.2)
I98.2* , -

:
(7071, 74.)
(B65)
I98.8* -
,

I99 -

596
X


(J00J99)

: -
, -
- (-
J40).
: ,
(P00P96)
(A00B99)
,
(O00O99)
,
(Q00Q99)
, -
(E00E90)
, -
(S00T98)
(C00D48)
, ,
, -
(R00R99)

:
J00J06
J10J18
J20J22

J30J39
J40J49
J60J70 ,
J80J84 , -

J85J86 -

J90J94
J95J99

597

:
J17* ,
J91* ,
J99* , -

(J00J06)
: ,
(J44.1)

J00 []
()

:


:


: (J31.1)
:
(J02.9)
(J02.)
(J31.2)
:
(J31.0)
(J30.1J30.4)
(J31.0)
(J30.0)

598

J01
:

(-)(-)
() ()


(9597).
: , (J32.)
J01.0

J01.1
J01.2
J01.3
J01.4
J01.8
, , -

J01.9 ,

J02
:
: :
(J36)
(J39.1)
(J39.0)
(J06.0)
(J31.2)
J02.0

: (A38)

599

J02.8 ,


(9597).
: ( ):
(27.)
:
(J10.1)
(J11.1)
(08.5)
herpes simplex
(B00.2)
J02.9 ,
():





()

J03 ()
: (J36)
:
(J02.9)
(J02.)
(J02.0)
J03.0
J03.8 ,


(9597).
: ,
herpes simplex (B00.2)

600

J03.9 ,
():




J04

(9597).
: [] -
(J05.)
() (J38.5)
J04.0
():





: (J37.0)
, :
(J10.1)
(J11.1)
J04.1
():


: (J42)
J04.2

() ()
: (J37.1)

601

J05 []


(9597).
J05.0 []

J05.1

J06


: (J22)
:
(J10.1)
(J11.1)
J06.0
J06.8 -

J06.9 , -

:
,

602


(J10J18)
J10 ,

: Haemophilus influenzae
[H. influenzae]:
(49.2)
(G00.0)
(J14)
J10.0 ,
(),
J10.1 ,


:







J10.8 ,
,
:


()

J11 ,
: -

: Haemophilus influenzae
[H.influenzae]:
(49.2)
(G00.0)
(J14)

603

J11.0 ,
(),

J11.1 , -


:




e
J11.8 ,
,

:



()

J12 ,

: , ,

: (35.0)
:
:
(J69.0)
:
(74.0)
(29.0)
(89.0)
(24.9)

(J69.)
(23.0)
(J10.0, J11.0)
(J84.9)
(J69.1)
J12.0

604

J12.1 , -

J12.2 ,
J12.8
J12.9 ,

J13 , Streptococcus
pneumoniae
, S. pneumoniae
: , S. pneumo-
niae (23.6)
,
(J15.3J15.4)

J14 , Haemophilus
influenzae
, . influenzae
: , . influen-
zae (23.6)

J15 ,

: , -
, S. pneumoniae H. influen-
zae
: , (J16.0)
(23.)
(48.1)
J15.0 , Klebsiella pneumoniae
J15.1 , Pseudomonas
J15.2 ,
J15.3 ,
J15.4 ,
: , :
(J15.3)
Streptococcus pneumoniae (J13)

605

J15.5 , Escherichia coli


J15.6 , --

, Serratia marcescens
J15.7 , Mycoplasma pneumoniae
J15.8
J15.9 ,

J16 ,
,

: (70)
(59)
:
(J18.9)
(23.)
J16.0 ,
J16.8 , -

J17* ,

J17.0* , -

:
(A42.0)
(A22.1)
(A54.8)
(A43.0)
(A02.2)
(A21.2)
(A01.0)
(37.)

606

J17.1* ,

:
(B25.0)
(05.2)
(B06.8)
(01.2)
J17.2*
:
(B44.0B44.1)
(B37.1)
(B38.0B38.2)
(B39.)
J17.3*
:
a (B77.8)
a (B65.)
a (B58.3)
J17.8* , -

():
(A70)
- (A78)
(I00)
, (69.8)

607

J18
: (J85.1)
-
(J70.2J70.4)
:
:
(J69.0)
:
(74.0)
(29.0)
(89.0)
(24.9)

(J69.)
(23.9)
(J84.9)
(J69.1)
, (J67
J70)
J18.0 ,
: (J21.)
J18.1 ,
J18.2 ,
J18.8
J18.9 ,

608



(J20J22)
: (-):
(J44.1)
(J44.0)

J20
: :
15
():






,
: :
15 (J40)
(J45.0)
:
(J42)
- (J41.1)
(J44.)
(J41.0)
:
(J40)
(J42)
(J44.)
J20.0 , Mycoplasma pneumo-
niae
J20.1 , Haemophilus influen-
zae
J20.2 ,

609

J20.3 , -
J20.4 ,
J20.5 , --

J20.6 ,
J20.7 ,
J20.8 ,
J20.9 ,

J21
:
J21.0 , --

J21.8 ,
J21.9 ,
()

J22
,
( ) ( -
)
:
() (J06.9)

610

(J30J39)
J30
:
: (J45.0)
(J31.0)
J30.0
J30.1 ,
,


J30.2
J30.3

J30.4 ,

J31 ,

J31.0

():







: :
(J30.1J30.4)
(J30.0)

611

J31.1
: , (J00)
J31.2

():



: , (J02.9)

J32
:

()()


(9597).
: (J01.)
J32.0
()

J32.1

J32.2

J32.3

J32.4

J32.8
(), ,

J32.9 ,
()

612

J33
: (D14.0)
J33.0
:


J33.1
Woakes
J33.8
:




J33.9 ,

J34

: (I86.8)
J34.0 ,

()

J34.1
J34.2
()(-
)
J34.3
J34.8

613

J35

J35.0
: :
(J03.9)
(J03.)
J35.1

J35.2

J35.3 -

J35.8 -



( )


J35.9 , -

()

J36




(9597).
: (J39.0)
:
(J03.9)
(J03.)
(J35.0)

614

J37

(9597).
J37.0
:


()
: :
(J04.0)
(J04.0)
() (J05.0)
J37.1
, ()
,
: :
(J04.2)
(J04.2)
:
(J04.1)
(J04.1)
(J42)

J38
,
: (Q31.4)
:
() (J05.0)
(J04.0)

(J95.5)
(R06.1)
J38.0


J38.1
: (D14.1)

615

J38.2
() () ()


J38.3


(-) (-)


J38.4
:



: :
[] (J05.0)
(J04.0)
J38.5
()
J38.6
J38.7






616

J39

: (J22)
(J06.9)
,
, ,
(J68.2)
J39.0

: (J36)
J39.1


J39.2



: :
(J31.2)
(J02.9)
J39.3
,
J39.8 -

J39.9 ,

617



(J40J47)
: (84.)

J40 ,

: , ,
15

J20..
:




: :
(J45.0)
(J45.9)
()
(J68.0)

J41 -

: :
(J42)
(J44.)
J41.0
J41.1 -
J41.8 , - -

618

J42 ,
:



: :
(J44.)
:
- (J41.)

(J44.)
(J44.)

(J44.9)

J43
: :
(J98.3)
, ,
(J68.4)
(J98.2)
(25.0)
(J98.2)
() (81.8)
(79.7)
() (J44.)
()
(J44.)
J43.0 MacLeod
(-):


J43.1 e

J43.2
J43.8

619

J43.9 ,
( ) ():



J44

: (-):
:
()

:


:



: (J45.)
(J45.9)
(J47)
:
:
(J42)
- (J41.)
(J42)
(J42)
(J43.)
,
(J60J70)
J44.0
-

: (J10J11)
J44.1 -
,

620

J44.8

:
()


J44.9 , -

:

J45
: (J46)
()
(J44.)
(J44.)
(J82)
,
(J60J70)
(J46)
J45.0
:





J45.1


J45.8
, J45.0 J45.1
J45.9 ,

621

J46 [status asthmaticus]


J47

: (Q33.4)
() (15
16)

,

(J60J70)
: , J45.

J60



: (J65)

J61 ,


: (J92.0)
(J65)

J62 , ,

: ()
: (J65)
J62.0 ,

622

J62.8 , , -

J63 ,

: (J65)
J63.0 ( )
J63.1 ( )
J63.2
J63.3 ( )
J63.4
J63.5
J63.8 , -

J64 ,
: (J65)

J65 ,
, J60J64,
, 1516.

J66 , -

: (J67.1)
(J67.0)
, -
(J67.)
-
(J68.3)
J66.0
,

623

J66.1
J66.2
J66.8 ,

J67 ,

: ,

,

: ,
, , (J68.0)
J67.0 [ ]


,
J67.1 ( )
(-):


J67.2


J67.3

-

J67.4
, Aspergillus clavatus
J67.5
J67.6
, Cryptostroma corticale

624

J67.7

, , -
,
[ ]

J67.8 ,






J67.9 , -

()

J68 ,
, ,

-
( XX).
J68.0 , -
, ,
()
J68.1 , -
, ,
()
J68.2 , -
, , ,

J68.3 ,
, ,

625

J68.4 ,
, ,
() ()


,
()()
,
()
J68.8 , -
, ,
J68.9 ,
, , ,

J69 ,

-
( XX).
:
(24.)
J69.0 , -

( ):

( )



: Mendelson (J95.4)
J69.1 ,


J69.8 ,

,

626

J70 ,

-
( XX).
J70.0 ,

J70.1 ,

,
J70.2 ,

J70.3 ,

J70.4 , -
,
J70.8 , -

J70.9 ,

(J80J84)
J80
[]

627

J81

()
: (J18.2)
:
() (J68.1)
(J60J70)

(I50.1)

J82 ,


Loffler
()
: :
(44.)
(J70.2J70.4)
(5083)
-
(3036)

J84

: , -
(J70.2
J70.4)
(J98.2)
,
(J60J70)
, -
HIV- (22.1)
J84.0 a -a
a a
a

628

J84.1 -


()
Hammn-Rich

: ():
-
, , (J68.4)
(J70.1)
J84.8 -

J84.9 ,



(J85J86)
J85
J85.0
J85.1
: , -
(J10J16)
J85.2

J85.3

629

J86
: :





(9597).
: (1516)
J86.0
J86.9


(J90J94)
J90 ,


: () (J94.0)
(R09.1)
(1516)

J91* ,

J92
:
J92.0
J92.9

630

J93
: :
(25.1)
(S27.0)
( ) (15
16)
(J86.)
J93.0
J93.1
J93.8
J93.9 ,

J94
: (R09.1)
:
(S27.2)
(S27.1)
(
) (1516)
J94.0

J94.1
J94.2

J94.8

J94.9 ,

631


(J95J99)
J95
,

: () (81.8)
,
(J70.0J70.1)
J95.0




J95.1

J95.2 -

J95.3 ,

J95.4 Mendelson
: :
(74.0)
(29.0)
(89.0)
J95.5
J95.8

J95.9 -
,

632

J96 ,

: - (R09.2)

(J95.)
(R09.2)
[] :
(J80)
(22.0)
J96.0
J96.1
J96.9 ,

J98
: :
(R06.8)
(28.4)
(G47.3)
(28.3)
J98.0 ,




(-):


J98.1


: ():
(P28.0P28.1)
( ) (15
16)

633

J98.2

: :
(J43.9)
(25.0)
() (81.8)
(79.7)
J98.3
J98.4

()


J98.5 , -





: (J85.3)
J98.6



: , (Q79)
(44.)
(Q79.0)
J98.8
J98.9 ,
()

634

J99* ,

J99.0* (M05.1)
J99.1* -

:
(33.033.1)
(M33.2)
Sjogren (M35.0)
(-):
(M32.1)
(M34.8)
Wegener (M31.3)
J99.8* , -

:
(A06.5)
(M45)
(D89.1)
(B42.0)
(A52.7)

635
I

(0093)

: ,
(0096)
(0099)
,
(O00O99)
,
(O00O99)
, -
(0090)
, -
(S00T98)
(C00D48)
, ,
, -
(R00R99)


:
0014 ,
2031 ,
3538
4046
5052
5563
6567
7077
8087 , -

9093

636

:
23* ,

67* , -

77* ,

87* , -
,
93* ,

,

(0014)
00

: (01.)
00.0


00.1


[ ]

637

00.2









[]


: Karabelli,
-

00.3



: (03.6)
00.4


() () (-
)

Turner
: Hutchinson
(50.5)
(00.3)
00.5 ,





638

00.6

(
)
( ,
)
:

()
[]
00.7
00.8


00.9 ,

01
: -

(07.3)
01.0
, .
01.1
, .

02
02.0
[ ]
02.1
02.2
02.3

639

02.4


02.8
02.9 ,

03

: (F45.8)
(02.)
(F45.8)
03.0
:

03.1
:







03.2
:

:





03.3

()

640

03.4

03.5
03.6 []
:


() :






:


03.7

: [] (03.6)
03.8


, -
, -
( XX).
03.9 ,

641

04

04.0
:


:

()()

04.1

04.2

:


04.3 -


04.4 ,


04.5


04.6
[]


04.7
[]

642

04.8
:
()


: (09.0)
04.9 -

05
05.0
:
(69.1)
,
herpes simplex (B00.2)
05.1
():





05.2



: (04.4)
(04.7)
(04.6)
05.3

:


643

05.4

05.5
05.6 ,

06

:
(08.2)
:
(05.1)
(05.0)
(05.1)
06.0
()()(-
)()
06.1

06.2
,

-
( XX).
06.8






06.9
,

644

07
[ ]
:
(Q67.4)

(10.8)
07.0
, :


( ) ( )
( ) ( )
: (22.0)
Robin (Q87.0)
07.1

( ) ( )
( ) ( )
07.2
() ()



() ()
:




645

07.3





,

-

: -
(01.)
07.4 ,
07.5

, :


,
: (F45.8)
(F45.8)
07.6
, , Costen


-

: :
(S03.0) -
(S03.4)
07.8
07.9 ,

08
08.0 ,
08.1 , , -

646

08.2
08.3 []
08.8



08.9 ,

09 ,

:
-

: (04.8)
09.0 ,
:







09.1 ()

:




647

09.2
:




: (10.0)
Stafne (10.0)
09.8 , -




Epstein


09.9 ,

10
10.0

Stafne
:


10.1 ,

: (06.8)
10.2

()
()()()


, -
,
( XX).

648

10.3


10.8



:


10.9 ,

11
11.0
11.1
K11.2
: (26.)
[Heetfordt] (D86.8)
11.3
11.4
: (Q38.4)
11.5

11.6
:




11.7



: (R68.2)

649

11.8
-

Mikulicz




: Sjogren (35.0)
11.9 ,

12
: cancrum oris (69.0)
(13.0)
(69.0)
,
herpes simplex (B00.2)
(69.0)
12.0
()()
Bednar



12.1
:



650

12.2


: ():
(04.604.7)
(05.2)
(J36)
(11.3)
(14.0)

13

:
: -
(0506)
(09.)
(14.)
(12.)
13.0
:







: (53.0)
, (L55L59)
, :
(37.8)
(53.0)
K13.1

651

13.2 ,


,

,

: (13.3)
13.3
13.4 -




13.5

13.6 ,

: ,
( )
(K06.2)
13.7 -

14
:

(K13.2)


(13.3)
() (Q38.2)
(13.5)

652

14.0


()
: (14.4)
14.1


14.2
14.3
[ ]

papillae foliate
Lingua villosa nigra
14.4

14.5



: (Q38.3)
14.6


14.8




14.9 ,

653

,

(2031)
: (44.)

20

:



-
( XX).
: (22.1)
- (21.0)
(21.0)

21
21.0
-
21.9

22
: (I85.)
22.0


: (Q39.5)

654

22.1

:

:




-
( XX).
22.2





: -
(Q39.3)
22.3

: (
) (S27.8)
22.4



: (22.0)
22.5 ,
,
: (Q39.6)
22.6 Mallory-Weiss
22.8

22.9 ,

655

23*
,
23.0* (A18.8)
23.1* Chagas (57.3)
23.8* ,

2528 -
:
.0
.1
.2
.3
.4 ,
.5 ,
.6 ,
.7 ,
.9 , -

25
[. - ]
: ()
() :



, , -
( XX).
: (29.0)
(27.)

656

26
[. - ]
: ()
() ():



, , -
( XX).
: (27.)

27

[. - ]
:

: (78.8)

28
[. - ]
: () :







: (63.3)

29
:
(52.8)
Zollinger-Ellison (16.8)
29.0
()
: () (25.)

657

29.1
29.2
29.3
29.4

29.5 ,
:


29.6


Mntrier
29.7 ,
29.8
29.9 ,

30

:
(F45.3)
(F45.3)
(F45.3)
(R12)

31

:
: (57.0
57.1)
(92.092.2)
31.0

658

31.1

: (Q40.0)
31.2 -

: ,
(Q40.2)
-
(31.8)
31.3 ,
: :
(Q40.0)
(F45.3)
(F45.3)
31.4
: (Q40.2)
31.5



,
:
(Q41.0)
31.6


31.7
: (D13.1)
31.8 -




31.9 , -

659


(3538)
35
35.0
() :

()

35.1

35.9 ,
:



36
:

37 ,

38
38.0
38.1

38.2
38.3
38.8

38.9 ,

660

(4046)
:
.
: :

[ ]

40
:
:




()

40.0

40.1
40.2


40.3

():





40.4

661

40.9

()

41
41.0

41.1
41.2


41.3

():





41.4

41.9

()

42
:
: (Q79.2)
K42.0
:




662

42.1 a

42.9

43
: :


43.0
:





43.1

43.9

44
: () ( )

: :
(Q79.0)
(Q40.1)
44.0 -

:




44.1

663

44.9 -

45
: :
,





45.0 -

, 45:





45.1
, 45, -

45.8 -

46 ,
:

:




: (N81.5)

664

46.0

, 46:




46.1
, 46, -

46.9 -


(5052)
:
: (58.)
(59.3)

50 Crohn [ ]
: o
: (51.)
50.0 Crohn
Crohn [ ] :



:


: Crohn (50.8)

665

50.1 Crohn
:


Crohn [ ] :



: Crohn (50.8)
50.8 Crohn
Crohn
50.9 Crohn,
Crohn

51
51.0 ()
51.1 ()
51.2 ()
51.3 ()
51.4
51.5
51.8
51.9 ,

52

52.0
52.1

( XX).

666

52.2

52.8


52.9 ,


, ,


: , , , :
(-) (09)
(-) ,

(09)
(59.1)
()
(78.3)
(F45.3)


(5563)
55
: -
(77)
55.0
(-):



(-), ()():



667

55.1
:




:


55.2
55.8
55.9 ,
:


56

:
(Q41Q42)
(K55.1)
(84.1)
,
76.

(K31.5)

(91.3)
(62.4)
(4046)

668

56.0
:



: , (56.3)
(56.7)
(56.6)
56.1
:




: (38.8)
56.2



56.3 ,

56.4

:


56.5 []
[] -

56.6





56.7 ,

669

57
:
()()

: (Q43.8)
(38.2)
Meckel (Q43.0)
57.0 -


:
(57.4)
57.1


: ,
(57.5)
57.2 -


:
(57.4)
57.3


:
(57.5)
57.4 -


57.5


57.8 , -

670

57.9 ,

58
:
58.0
58.9

59
: (R19.4)
(31.)
(90.)
(F45.3)
59.0
59.1
59.2 ,
59.3 ,



( XX).
: ():
Chagas (57.3)
() (Q43.1)
Hirschsprung (Q43.1)
59.4

59.8 -


59.9 ,

671

60
: (61.)
60.0
60.1
60.2 ,
60.3
60.4

: :
(N82.3)
(N32.1)
60.5

61
:

61.0

: (61.4)
61.1

: (61.3)
61.2
61.3
fossa ischiorectalis
61.4

62
:
:
(91.4)
(R15)
(I84.)
(51.2)

672

62.0
62.1
: (D12.8)
62.2

62.3

62.4
()
62.5
: (54.2)
62.6
:


: (60.)
(51.)
62.7
62.8
()

62.9 ,

63
63.0
: :
(61.)
(35.1)
(57.)
63.1 ()
: () :
(35.0)
(26.)
(57.)

673

63.2
: ():
(60.)
(38.3)
(31.6)
(N82.2N82.4)
(N32.1)
63.3

: ():
(62.6)
(26.)
(28.)
(28.)
(28.)
, (27.)
(K51)
63.4
63.5
: (D12.6)
(D12.6)
63.8
63.9 ,

674


(6567)
65
: :
(81.6)
(85.0)
(81.6)
-
(81.6)
(78.078.1)
(N73.3N73.5)
(85.0)
(O85)
:
, -
(O00O07, O08.0)
(35.)

(57.)
65.0
():









():





(9597).

675

65.8

:


, :


65.9 ,

66
: (R18)
66.0
():
()







: [] ():
(N73.6)
(56.5)
66.1
: (S36.8)
66.8
66.9 ,

67*
,

67.0* (A74.8)

676

67.1* (A54.8)
67.2* (A52.7)
67.3* (A18.3)
67.8* -
,


(7077)
: (83.1)
(R17)
Reye (G93.7)
(1519)
Wilson (83.0)

70
70.0
70.1
70.2
70.3

70.4
:





70.9 ,

677

71
: :
()

()


( XX).
: (70.)
Budd-Chiari (I82.0)
71.0
c

71.1

()(),

71.2 ,

71.3 ,

71.4 ,

71.5 ,

, -

71.6
,
71.7

678

71.8

:




71.9 ,

72 ,

: :


:

,

() -


:
(70.4)
, :
, -
(O00O07, O08.8)
,
(O26.6)
(55
59)
(1519)
(71.1)
72.0
72.1
72.9 ,

679

73 ,

: ():
(70.1)
(71.)
, (75.3)
, (75.2)
(1519)
73.0 ,

73.1 ,

73.2 , -

,
73.8 , -

73.9 ,

74
: (70.2)
(76.1)
( ):
(70.3)
(78.8)
(71.7)
74.0
74.1
74.2
74.3

74.4
74.5 ,

680

74.6
( ):






75

: ,
(73.)
:
(72.0)
(1519)
(71.)
75.0
:





: (06.4)
(83.0)
(75.1)
75.1

: (75.0)
75.2
75.3 ,
75.4
75.8

681

75.9 ,

76
: (70.)

(85.)
()
(Q44.6)
(I82.0)
(R16.0)
(I81)
(71.)
76.0 , -

76.1
:
( )


76.2

: -
(72.)
76.3
76.4

76.5
: Budd-Chiri (I82.0)
76.6
76.7
: (O90.4)
76.8

682

76.9 ,

77*
,
77.0* -
,
():
(B25.1)
herpes simplex (B00.8)
(B58.1)
(B65.)
(B65.)
(A52.7)
77.8* , -

:
(J63.2)
(D86.8)

,

(8087)
80 []
80.0
, 80.2, -

80.1
, 80.2, -
()

683

80.2


()
:


80.3
, 80.5, -

80.4
, 80.5, -
( )
80.5 -


:



:

()
80.8

81
: (80.)
81.0


:
()




684

81.1
81.8
81.9 ,

82
: -
(R93.2)
(91.5)
82.0



: (80.)
82.1

82.2

82.3



82.4

82.8







82.9 ,

685

83
: , :
(8182)
(8182)
(91.5)
83.0
:








: (75.0)
(80.380.4)

(74.3)
83.1



: (80.)
83.2

83.3

K83.4 Oddi
83.5
83.8





83.9 ,

686

85

:


:

()


86
: (84.)
-
(D13.7)
(90.3)
86.0
86.1
:




86.2
86.3
86.8





:

:


687

86.9 ,

87* ,

,
87.0* -
,
87.1* ,

(B25.2)
(B26.3)

(9093)
90
: -
(91.2)
90.0



90.1


90.2 , -


: :
(Q43.8)
(91.2)
90.3

688

90.4 , ,

, :




: (90.0)
(73.)
90.8
Whipple (14.8*)
90.9 ,

91
,

: (28.)
:
(52.0)
(52.0)
(62.7)
91.0 -

91.1
:



91.2 -
,

: :
(83.2)

(81.3)
91.3

689

91.4
91.5
91.8
,
91.9 -
,

92

:
(54.054.3)
92.0
92.1
92.2 ,
:


: (29.0)
(62.5)
(2528)
92.8 -

92.9 ,

93*
,

93.0* ,
(18.3)
: (67.3*)
93.1* Chagas (B57.3)
93.8* -
,

690
XII

(L00L99)
: ,
(P00P96)
(00B99)
,
(0099)
,
(Q00Q99)
, -
(E00E90)
, -
(S00T98)
(I89.8)
(00D48)
, ,
, -
(R00R99)
(30
36)
:
L00L08
L10L14
L20L30
L40L45
L50L54
L55L59 , -

L60L75
L80L99
:
L14* ,
L45* ,

691

L54* ,
L62* ,
L86* ,
L99* -
,

(L00L08)
-
(B95B97).
: (H00.0)
(L30.3)
, I,
:
(A46)
(A26.)
- [herpes simplex] (B00.)
(A60.)
(B08.1)
(B35B49)
, (B85B89)
(B07)
()():
(M79.3)
(L93.2)
(M54.0)
[Weber-Christian] (M35.6)
( ):
(K13.0)
(B37.)
(E53.0)
(L98.0)
(B02.)

692

L00


Ritter
: [Lyell]
(L51.2)

L01
: (L40.1)
(L00)
L01.0 [ ] [ ]
Bockhart
L01.1

L02 ,

:

: (K61.)
():
(N76.4)
(N48.2, N49.)
L02.0 ,
: (H60.0)
(H00.0)
[ ] (L02.8)
:
(H04.0)
(H04.3)
(K12.2)
(J34.0)
(H05.0)
(K12.2)
L02.1 ,

693

L02.2 ,

[ ]




: (N61)
(L02.4)
(P38)
L02.3 , -


: (L05.0)
L02.4 , -




L02.8 ,

[ ]

L02.9 , -

694

L03
:
: :
(K61.)
(H60.1)
:
(N76.4)
(N48.2, N49.)
(H00.0)
(H04.3)
(K12.2)
(J34.0)
[Wells] (L98.3)
[Sweet]
(L98.2)
()() (I89.1)
L03.0




L03.1



L03.2
L03.3

[ ]




: (P38)
L03.8
[ ]

695

L03.9 ,

L04
: ()
()
: (R59.)
,
[HIV], -
(B23.1)
:
(I88.9)
, -
(I88.1)
, (I88.0)
L04.0 ,
L04.1
L04.2


L04.3

L04.8
L04.9 ,

L05
: (-)
(-)
L05.0
L05.9

696

L08

L08.0
:



: (L88)
L08.1
L08.8

L08.9 ,


(L10L14)
: [ Hailey-
Hailey] (Q82.8)
(L00)
[ Lyell]
(L51.2)

L10
: (L00)
L10.0
L10.1
L10.2
L10.3 (fogo selvagem)
L10.4
Senear-Usher

697

L10.5 ,


( ).
L10.8
L10.9 ,

L11
L11.0
: () [Darier-
White] (Q82.8)
L11.1 [Grover]
L11.8
L11.9 ,

L12
: (O26.4)
(L40.1)
L12.0
L12.1

L12.2

L12.3
: () (Q81.)
L12.8
L12.9 ,

L13
L13.0
Duhring

698

L13.1
Sneddon-Wilkinson
L13.8
L13.9 ,

L14*
,


(L20L30)
: -
.
: ( ) (D71)
:
(L85.3)
(L98.1)
(L88)
(L13.0)
(L71.0)
(I83.1I83.2)
,
(L55L59)

L20
: (L28.0)
L20.0 Besnier
L20.8
:
,
()()
()
:

699

L20.9 ,

L21
: (L30.3)
L21.0

L21.1
L21.8
L21.9 ,

L22
:


L23
:
: (T78.4)
()():
(L30.9)
(L25.9)
(L22)
, (L27.)
(H01.1)
(L24.)
(L71.0)
(H60.5)
, -
(L55L59)
L23.0


L23.1 -

700

L23.2

L23.3



( ).
: (T88.7)

(L27.0L27.1)
L23.4
L23.5





L23.6 -

: ,
(L27.2)
L23.7 , -

L23.8
L23.9

701

L24
:
: (T78.4)
()():
(L30.9)
(L23.)
(L25.9)
(L22)
(L27.)
(H01.1)
(L71.0)
(H60.5)
, -
(L55L59)
L24.0
L24.1 -

L24.2
:






L24.3

L24.4



( ).
: (T88.7)
,
(L27.0L27.1)

702

L24.5



L24.6 -

: ,
(L27.2)
L24.7 , -

L24.8

L24.9

L25 ,
: ,
: (T78.4)
()():
(L30.9)
(L23.)
(L27.)
(H01.1)
(L24.)
(L71.0)
(H60.5)
, -
(L55L59)
L25.0 , -

703

L25.1
,


( ).
: (T88.7)
,
(L27.0L27.1)
L25.2 ,
L25.3 ,



L25.4
,
: (L27.2)
L25.5 ,
,
L25.8 ,
L25.9 -

(-):
()
()

L26
Hebra
: Ritter (L00)

704

L27

: (-):

(T88.7)
, -
(T78.0T78.1)
(T78.4)
(L23L25)
:
(L56.1)
(L56.0)
(L50.)
L27.0 -



( ).
L27.1 -



( ).
L27.2
:
(L23.6, L24.6, L25.4)
L27.8 ,
L27.9 ,

L28
L28.0


L28.1

705

L28.2
:

Hebra
mitis

L29
: (L98.1)
(F45.8)
L29.0
L29.1
L29.2
L29.3 ,
L29.8
L29.9 ,

L30
: :
(L23L25)
(L85.3)
(L41.3)
(I83.1I83.2)
L30.0
L30.1 []
L30.2



L30.3

L30.4

706

L30.5
L30.8
L30.9 ,


(L40L45)
L40
L40.0


L40.1

Von Zumbusch
L40.2
L40.3
L40.4
L40.5 (M07.0M07.3*, M09.0*)
L40.8

L40.9 ,

L41
: (L94.5)
L41.0 Pityriasis lichenoides et varioliformis acuta
Mucha-Habermann
L41.1 Pityriasis lichenoides chronica
L41.2

707

L41.3
L41.4
L41.5
L41.8
L41.9 ,

L42

L43
: (L66.1)
L43.0
L43.1
L43.2


( ).
L43.3 ()

L43.8
L43.9 ,

L44
L44.0
L44.1
L44.2
L44.3
L44.4 [Gianot-
ti-Crosti]
L44.8

708

L44.9 ,

L45*
,


(L50L54)
: (A69.2)
(L71.)

L50
: (L23.)
(T78.3)
(E88.0)
Quincke (T78.3)
:
(T78.3)
(P83.8)
(L28.2)
(Q82.2)
(T80.6)
(L56.3)
L50.0
L50.1
L50.2
L50.3
L50.4
L50.5
L50.6

709

L50.8
:


L50.9 ,

L51 rythema multiforme


L51.0 erythema multiforme
L51.1 erythema multiforme
Stevens-Johnson
L51.2 [Lyell]
L51.8 erythema multiforme
L51.9 Erythema multiforme,

L52 Erythema nodosum

L53
: :
(L59.0)
(L23
L25)
(L30.4)
L53.0


( ).
: (P83.1)
L53.1 Erythema annulare centrifugum
L53.2 Erythema marginatum
L53.3
L53.8

710

L53.9 ,

L54* ,

L54.0* Erythema marginatum (I00)
L54.8* ,


,
(L55L59)
L55
L55.0
L55.1
L55.2
L55.8
L55.9 ,

L56 ,

L56.0


( ).
L56.1


( ).

711

L56.2 [berloque dermatitis]


L56.3
L56.4
L56.8 , -

L56.9 , -
,

L57 ,


L57.0
:



L57.1
L57.2 Cutis rhomboidalis nuchae
L57.3 Civatte
L57.4

L57.5
L57.8 , -




L57.9 , -
,

712

L58
L58.0
L58.1
L58.9 ,

L59
,
L59.0 [dermatitis ab igne]
L59.8
,
L59.9 , -
,


(L60L75)
: (Q84.)

L60
: (R68.3)
(L03.0)
L60.0
L60.1
L60.2
L60.3
L60.4 Beau
L60.5
L60.8
L60.9 ,

713

L62* ,

L62.0* , -
(M89.4)
L62.8* , -

L63
L63.0 ()
L63.1
L63.2
L63.8
L63.9 ,

L64
:
L64.0 , -



( ).
L64.8
L64.9 ,

L65


, , -
( ).
: (F63.3)
L65.0

714

L65.1
L65.2
L65.8 -

L65.9 ,

L66
L66.0
L66.1

L66.2 ,
L66.3
L66.4 Folliculitis ulerythematosa reticulata
L66.8
L66.9 ,

L67

: (Q84.1)
(Q84.1)
(L65.0)
L67.0
L67.1

()

:

,

715

L67.8

L67.9 ,

L68
:
: (Q84.2)
(Q84.2)
L68.0

, , -
( ).
L68.1

, , -
( ).
L68.2
L68.3
L68.8
L68.9 ,

L70
: (L73.0)
L70.0
L70.1
L70.2

L70.3
L70.4
L70.5 Acn excorie des jeunes filles
L70.8

716

L70.9 ,

L71
L71.0

, , -
( ).
L71.1
L71.8
L71.9 ,

L72

L72.0
L72.1


L72.2
L72.8

L72.9 -
,

L73
L73.0
L73.1
L73.2
L73.8

L73.9 ,

717

L74
: (R61.)
L74.0
L74.1
L74.2

L74.3 ,
L74.4

L74.8
L74.9 ,

L75
: [] (L30.1)
(L73.2)
L75.0
L75.1
L75.2
Fox-Fordyce
L75.8
L75.9 ,

(L80L99)
L80

718

L81
: (Q82.5)

Peutz-Jeghers (Q85.8)
L81.0
L81.1
L81.2
L81.3
L81.4 , -


L81.5 ,
L81.6 ,

L81.7

L81.8


L81.9 ,

L82

Leser-Trelat

L83 Acanthosis nigricans


L84
Callus
Clavus

719

L85

: (L91.)
L85.0
: (Q80.)
L85.1 [-
]
:
(Q82.8)
L85.2 ( )
L85.3

L85.8 -


L85.9 ,

L86* ,


(E50.8)

L87

: () (L92.0)
L87.0 , -
[ Kyrle]

L87.1
L87.2
L87.8
L87.9 ,

720

L88

L89



: ()
(N86)

L90
L90.0 Lichen sclerosus et atrophicus
L90.1 Schweninger-Buzzi
L90.2 Jadassohn-Pellizzari
L90.3 Pasini-Pierini
L90.4
L90.5
()

,

: (L91.0)
(L91.0)
L90.6
L90.8
L90.9 ,

L91
L91.0


: (L73.0)
(L90.5)

721

L91.8
L91.9 ,

L92

: (L57.5)
L92.0 Granuloma annulare
granuloma annulare
L92.1 , -

: (E10E14)
L92.2 Granuloma faciale [ -
]
L92.3 -

L92.8 -

L92.9 -
,

L93
: :
(18.4)
(A18.4)
(M34.)
(M32.)

, , -
( ).
L93.0

L93.1

722

L93.2
:

L94

:
(M30M36)
L94.0 [morphea]

L94.1
En coup de sabre
L94.2
L94.3
L94.4 Gottron
L94.5
L94.6
L94.8 -

L94.9 -
,

723

L95 ,
: (L81.7)
Henoch(-Schn-
lein) (D69.0)
(M31.0)
()():
(M79.3)
(L93.2)
(M54.0)
(Weber-Christian) (M35.6)
(M30.0)
(M05.2)
(T80.6)
(L50.)
Wegener (M31.3)
L95.0
( )
L95.1 Erythema elevatum diutinum
L95.8
L95.9 ,

L97 ,

: (L89)
(R02)
(L00L08)
,
A00B99
(I83.0, I83.2)

L98
,
L98.0
L98.1

L98.2 [Sweet]

724

L98.3 [Wells]
L98.4 ,



: (L89)
(R02)
(L00L08)
, A00
B99
, (L97)
(I83.0, I83.2)
L98.5


: (K13.7)
(E03.9)
L98.6 -

: (E78.8)
L98.8

L98.9 ,

L99*
,

L99.0* (E85.)


L99.8* -
,
:
(A51.3)
(A51.3, A52.7)

725
XIII

(0099)

: ,
(0096)
(0099)
(T79.6)
,
(0099)
, -
(S00T98)
, -
(0090)
,
(Q00Q99)
, ,
, -
( R00R99)
(C00D48)

:
0025
0003
0514
1519
2025
3036
4054
4043
4549
5054

726
-

6079
6063
6568 -

7079
8094
8085

8690
9194
9599 - -

:
01* -
,
03* , -

07*
09* ,
14* ,
36* -
,
49* ,
63* , -

68*
,
73* ,

82* ,
90* ,

727

XIII -
, -
. -
-
, , -

(. ). ,
, -
, , -
744, 752 788.
0
1


2
3

4


5


6 []
[]
7


8





9

728
-

(0025)
, ( )


(00-03)
: , -
. -
:
) , -

;
) ,
: ,
,
, -
; ,
, -
,
.

00
[ .728]
00.0
00.1
00.2
00.8 ,


(95-96).
00.9 ,

729

01*
,

[ .728]
: (14.8*)

(03.*)
01.0* (39.8)
: (03.0*)
01.1* (18.0)
: (49.0*)
01.2* (69.2)
01.3* , -

:
[ Hansen] (30.)
(02.2)
(01.)
(54.4)
01.4* (06.8)
01.5* ,

:
nyong-nyong (92.1)
( 26.8)
01.6* (3549)
01.8* -
,

02
[ .728]
: Behet (M35.2)
(I00)

730
-

02.0
02.1
02.2
02.3 Reiter-Leroy
02.8
02.9 ,

03*
,

[ .728]
: -
,
(01.*)
03.0* (39.8)
: (01.0*)
03.1*
Clutton (50.5)
: Charcot -
(14.6*)
03.2* ,

:
, Yersinia enterocolitica (04.6)
(1519)
: (01.401.5*)
03.6* , -

(I33.0)

731


(0514)
05
[ .728]
: (I00)
:
(45)
(08.)
05.0 Felty

05.1
(J99.0*)
05.2
05.3

(-):
(I52.8*)
(I39.*)
(I41.8*)
(G73.7*)
(I32.8*)
(G63.6*)
05.8
05.9 ,

06
[ .728]
06.0
06.1 Still
: Still (08.2)
06.2

732
-

06.3
06.4
: (13.0)
06.8
06.9 ,

07*

[ .728]
: -
(09.*)
07.0* -
(L40.5)
07.1* (L40.5)
07.2* (L40.5)
07.3* (L40.5)
07.4* Crohn [ -
] (50.)
07.5* (51.)
07.6*

08 []
[ .728]
: , 16-
3
: Felty (05.0)
(33.0)
08.0


08.1
: (45)

733

08.2
Still
: Still -
(06.1)
08.3 ()

08.4
08.8
08.9 ,

09* []
,
[ .728]
: Whipple (14.8*)
09.0* (L40.5)
09.1* Crohn [-
] (50.)
09.2* (51.)
09.8* , -

10
[ .728]
10.0


[ ] (I43.8*)
10.1
10.2


( ).

734
-

10.3 , -

10.4
10.9 ,

11
[ .728]
11.0
11.1
11.2

11.8
11.9 ,

12
[ .728]
: (13.9)
(J38.7)
(1519)
12.0 [Jaccoud]
12.1 Kaschin-Beck
12.2 ()
12.3
12.4
12.5
: ():
(19.1)
(17.217.3)
(M16.4M16.5)
- (18.2
18.3)
(19.1)

735

12.8 ,

13
[ .728]
: (1519)
13.0 ,
13.1 ,
13.8

13.9 ,

14* ,

: ():
(36.236.3*)
(36.4*)
(36.1*)

(07.*)
(09.*)
(49.4*)
14.0* ,

:
- () (D57.)
Lesch-Nyhan (E79.1)
14.1* -

(21.)
14.2* (1014
.6)
: (14.6*)

736
-

14.3* (78.8)
14.4* (85.)
14.5*
,

:
(22.0)
(83.1)
(0003)
[] (05.)
14.6*
Charcot (52.1)
(1014 -
.6)
14.8* , -

:
:
(L51.)
(L52.)
(D86.8)
Whipple ( 90.8)

(1519)
: -
. -
.
: (47.)

15
:
:
(1619)

737

15.0 ()
15.1 Heberden ( )
15.2 Bouchard ( )
15.3

15.4 ()
15.8
15.9 ,

16 [
]
16.0 ,
16.1
:


16.2 ,
16.3
:


16.4 ,
16.5
:


16.6 ,
16.7
:

738
-

16.9 ,

17 [
]
17.0 ,
17.1
:


17.2 ,
17.3
:


17.4 ,
17.5
:


17.9 ,

18 -

18.0 -
,
18.1 --

- :


18.2 --
,

739

18.3 -

-
:


18.4 --
,
18.5 --

- :


18.9 - , -

19
[ .728]
: (47.)
(20.2)
(15.)
19.0

19.1

19.2

19.8
19.9 ,

740
-


(2025)
: (4054)

20

:
(Z89.)
(-):
(Q71.3, Q72.3)

(Q66., Q68Q70,
Q74.)
20.0 (-)


: (65.3)

[Dupuytren] (72.0)
(R68.3)
20.1 Hallux valgus ()

20.2 Hallux rigidus
20.3 ()
Hallux varus
20.4 -
()
20.5 (-) (-
)
20.6 (-) , -

741

21

[ .728]
: (Z89.)
-
(20.)
(-):
(Q71Q73)

(Q65Q66, Q68Q74)
coxa plana (91.2)
21.0 ,
: metatarsus valgus (Q66.6)
pes calcaneovalgus (Q66.4)
21.1 ,
: metatarsus varus (Q66.2)
tibia vara (M92.5)
M21.2
21.3 [pes eqiinus] (-
)
21.4 [pes planus] ()
: (Q66.5)
21.5 , ,

:
(Q66.8)
21.6 -

:
(21.1M20.6)
21.7 ()
21.8 -

21.9 ,

742
-

22 ()
: (S83.0)
22.0
22.1
22.2
22.3
22.4
22.8
22.9 ,

743

23

, -
, -
23.; -
. 728.
0
1

2

3

4

5

6

7
9
: (24.6)
(21.)
(22.)
-

(S80S89)

(24.4)
(22.022.1)
(93.2)
23.0
23.1 ()
23.2

744
-

23.3



23.4
23.5
23.6 (-) -

23.8


23.9 , -

24

[ .728]
: (23.8)
(67.4)

(07.6)

-

24.0
: (23.4)
24.1
: (83.5)
(11.111.2)

(23.)
(70.2)

745

24.2
-
()

: (23.523.8)
(35.7)
24.3 , -

: :
-
- (Q65 -
Q79)
-


(24.4)
24.4
: (22.022.1)
(43.3
43.5)
24.5
: (20
21)
Dupuytren (72.0)

(67.1)
24.6
: (43.2)
(25.6)
24.7
24.8 , -


24.9 ,

746
-

25 ,

[ .728]
: (R26.)
:
(71.4)
(75.3)
(65.2)
,
2021
(R26.2)
25.0
: -


25.1
25.2
25.3
: :
(24.2)
(96.8)
25.4
: (66.6)
25.5
25.6 ,
25.7
25.8
25.9 ,

747



(3036)
: :


() :


:
( -
)

30

30.0
30.1 [Churg-
Strauss]

30.2
30.3 -- [Kawasaki]
30.8 ,
-

31
31.0
Goodpasture
31.1

31.2

748
-

31.3 Wegener

31.4 [Takayasu]
31.5 -

31.6
31.8

31.9 ,

32 lupus erythematodes
: lupus erythematodes () () (L93.0)
32.0 lupus erythematodes


( ).
32.1 lupus erythematodes

lupus erythematodes :
(J99.1*)
(N08.5* , N16.4*)
Libman-Sacks (I39.*)
lupus erythematodes (I32.8*)
32.8 lupus erythematodes
32.9 lupus erythematodes,

33
33.0
33.1
33.2
33.9 ,

749

34
:
: :
(L94.0)
(83.8)
34.0
34.1 CR(E)ST
, ,
,
34.2 ,

-
( ).
34.8
:
(J99.1*)
(G73.7*)
34.9 ,

35

: (L87.1)
35.0 Sjgren
Sjgren :
(J99.1*)
(19.3*)
(N16.4*)
(G73.7*)
35.1

: - (30.8)
35.2 Behet

750
-

35.3
:
(31.5)
35.4 ()
35.5
35.6 [Weber-Christian]
: :
(79.3)
(L93.2)
35.7

: (24.2)
EhlersDanlos (Q79.6)
35.8 -

35.9 ,

()
()

36*
,

: , -
(14.*)
36.0* () (00
D48)
36.1* (00D48)
:
(9195)
(90.0)
(96.1)
36.2* (D66D68)

751

36.3* (D50
D76)
: Schnlein-Henoch
(36.4*)
36.4* ,

Schnlein-Henoch (D69.0)
36.8*
,
:
(D80.)
(70.2)

(4054)
, -
-
50 51; . 728.

0
1 --
2
3
4
5
6
7
8
9

752
-


(4043)
40
[ .752]
: (41.)
:
(Q76.4)
(96.)
40.0
: (42.)
40.1
40.2
40.3
40.4
:


40.5 ,

41
[ .752]
:
: :
(Q67.5)

(Q76.3)
(Q67.5)
(96.)
,
(I27.1)
41.0

753

41.1

41.2
41.3
41.4
, ,
Friedreich, -

41.5
41.8
41.9 ,

42
[ .752]
42.0
Calve
Scheuermann-Mau
: (40.0)
42.1
42.9 ,

43
[ .752]
:
(Q76.2)
(Q76.3Q76.4)
Klippel-Feil (Q76.1)
(Q76.4)
(Q76.4)
spina bifida occulta (Q76.0)
:
Paget ( )(88.)
(8081)

754
-

43.0
43.1
43.2

: (Z98.1)
(96.0)
(45)
43.3 - -

43.4 - -

43.5

: , (99.)
43.6 [torticollis]
: :
() (Q68.0)
(15.2)
-


(F45.8)
(G24.3)
43.8
: (40.)
(41.)
43.9 ,

755

(4549)
45
[ .752]

: Reiter (02.3)
() (08.1)
Behet (M35.2)

46
[ .752]
46.0


46.1 ,
46.2
46.3 ()

(9597).
46.4 ,
46.5
46.8
46.9 ,

47
[ .752]
:

47.0 -
(G99.2*)

756
-

47.1
, -
(G99.2*)
: (43.3
43.5)
47.2
47.8
()
-

47.9 ,

48
[ .752]
48.0

48.1 [Forestier]

48.2
48.3
48.4
[]
48.5 , -



: -
(80.)
-

48.8

48.9 ,

757

49* ,

[ .752]
:
(07.*, 09.*)
49.0* (18.0)
Pott
49.1* (23.)
49.2* (0104)
49.3* -
,
: tabes dorsa-
lis (49.4*)
49.4*
:
(G95.0)
tabes dorsalis (A52.1)
49.5* , -

(79.5)
49.8* ,

758
-


(5054)
: (46.4)
-

50

:



50.0 -
(G99.2*)
50.1 -

: (54.1)
50.2 -

50.3 -

50.8

50.9 -
,

759

51

:
,

51.0 -
-
(G99.2*)
51.1 -
-

,
: (54.1)
51.2

,
51.3

51.4 Schmorl
51.8

51.9 ,

53 ,

[ .752]
53.0

53.1
:
(50.)
[ -
] (G54.0)

760
-

53.2
53.3 ,

Coccygodinia
53.8
53.9 ,

54
[ .752]
: (F45.4)
54.0 , -

: :
(79.3)
(L93.2)
[Weber-Christian] (35.6)
54.1
:





: (79.2)
:
-
(50.1)
-
(51.1)
(47.2)
54.2
: -
(50.)

761

54.3
: (G57.0)
:
-
(51.1)
(54.4)
54.4
: -
(51.1)
54.5



: :
-
(51.2)
(54.4)
54.6
:
(51.)
54.8
54.9 ,

762
-


(6079)

(6063)
: (33.)
(G71G72)
:
(85.)
lupus erythematodes (32.)
(30.0)
(05.3)
(34.)
Sjgren (35.0)

60
[ .728]
60.0


(9597).
60.1
60.2 , -

: -
(L92.3)
60.8
60.9 ,

763

61

[ .728]
61.0
61.1

61.2 -

, -

61.3 , -

,
61.4
: (65.2)
(75.3)
61.5
61.9 , -

62
[ .728]
: (R25.2)
(79.1)
:
(G72.1)
(G72.0)
(G25.8)
62.0
62.1 ()
: (66.)
-

764
-

62.2
: Volkmann (79.6)
(79.6)
(79.6)
62.3 ()
62.4
: (24.5)
62.5 ,
,
62.6
:

62.8

62.9 ,

63* ,

: :
(G73.5*)
(G73.6*)
63.0* , -

:
[ Hansen] (30.)
(51.4, 52.7)
63.1* ,

:
(69.8)
(58.8)
(75)
[] (65.)

765

63.2 * , -

(3549)
63.3* (D86.8)
63.8* , -



(6568)
65
[ .728]
:
(70.0)
-
-

, -
, (70.)
65.0

(9596)
65.1 ()
65.2
: (75.3)
(7577)
65.3

65.4 [de
Quervain]
65.8

766
-

65.9 ,

66

[ .728]
: , -
,


:
-

(75.1)
66.0
66.1

: (66.0)
66.2
66.3
66.4
66.5
- , -

67

:
[Dupuytren] (72.0)
(77.9)
(78.2)
67.0 ()
67.1 ( )
: (24.5)

767

67.2 , -

: () (12.2)
67.3

: (12.3)
67.4
( )
: :

(71.271.3)
(66.6)
67.8 -

67.9 , -

68*
,

68.0* ,

:
(54.4)
(52.7)
(18.0)
68.8*
,

768
-


(7079)
70 ,
,
[ .728]
:
: :
(71.9)
(75.5)
(7677)
70.0 -

70.1
70.2
70.3
70.4
70.5
70.6

70.7

70.8 ,
,
70.9 , -
, ,

769

71
[ .728]
: ( )
(20.1)
, , -
(70.)
(7677)
71.0
71.1
71.2 [Baker]
: (66.0)
71.3

: (66.1)
71.4
: (75.3)
71.5 ,
: :
(71.9)
(75.5)
-
[Pellegrini-Stieda] (76.4)
71.8
71.9 ,

72
[ .728]
: (D48.3)
72.0 [Dupuyt-
ren]
72.1 - -

770
-

72.2

72.3
72.4 () -

72.5 ,
: :
() (35.4)
() (72.3)
(72.2)
72.8
72.9 ,

73*
,
[ .728]
73.0* (54.4)
73.1* (52.7)
73.8* ,

75
: - (89.0)
75.0


75.1
()() supraspinatus -
,

75.2

771

75.3

75.4
75.5
75.8
75.9 ,

76 ,

[ .728]
: ,

-
; --
-
.
: , ,
(70.)
76.0
76.1 -
76.2
76.3 -
76.4 -
[Pellegrini-Stieda]
76.5
76.6

76.7
76.8 , -


.tibialis posterior

772
-

76.9 ,

77
[ .728]
: :
(71.9)
,
(70.)
(46.0)
(25.7)
77.0
77.1

77.2
77.3
77.4
: Morton (G57.6)
77.5
77.8 ,
77.9 ,



79 ,

[ .728]
: (F45.4)
79.0


: (12.3)

773

79.1
: (60.)
79.2
: (G56G58)
:

(54.1)

(54.354.4)
79.3
: ()():
(54.0)
lupus erythematodes (L93.2)
[Weber-Christian] (35.6)
79.4
79.5
: ,
:
(L92.3)
(60.2)
79.6
79.8
79.9 ,

774
-


(8094)



(8085)
80
[ .728]
:

: (84.4)
(48.5)

(48.5)
80.0 -

80.1 -

80.2 -

80.3 ,
-

80.4 -



( ).
80.5
80.8

775

80.9 ,

81
[ .728]
: (80.)
81.0
81.1
81.2
: Sudeck-Leriche (89.0)
81.3 , -

81.4


( ).
81.5
81.6 [Lequesne]
: Sudeck-Leriche (89.0)
81.8

81.9 ,

82* , -

[ .728]
82.0*
(90.0)
82.1* (00
34)
82.8* ,

776
-

83
[ .728]
: :
(55.0)
D- (83.3)
(N25.0)
() (55.0)
(64.3)
D- (83.3)
83.0
83.1
83.2 , -

-

83.3 , -

83.4 ,
83.5 -



( ).
83.8
83.9 ,

84
[ .728]
84.0
84.1 []
: (96.0)
84.2

777

84.3 ,

:
(48.4)
84.4 ,

: (48.5)

(80.)
84.8
84.9 ,

85

[ .728]
: osteogenesis imperfecta (Q78.0)

(Q78.1)
(Q78.2)
(Q78.8)
85.0 ( )
: (10.8)
85.1
85.2
85.3 ,
()
85.4
: (09.1
09.2)
85.5
:
(09.2)

778
-

85.6
: (09.109.2)
- [-
Recklinghausen] (21.0)
85.8 -

,
:
[DISH] (48.1)
85.9 ,


(8690)
: (96.)

86
[ .728]

(9597).
: :
(0102)
(10.2)
(46.2)
86.0
86.1
86.2
86.3
86.4
86.5
86.6

779

86.8
Brodie
86.9 ,

87
[ .728]
: ()
: (9193)
87.0
87.1


( )
87.2
87.3
87.8
87.9 ,

88 Paget [ ]
[ .728]
88.0 Paget
88.8 Paget
88.9 Paget,

89
[ .728]
89.0
-
Sudeck

780
-

89.1 -
( )
89.2
89.3
89.4
Marie-Bamberger

89.5
89.6

(91).
89.8


89.9 ,

90* ,

[ .728]
90.0* (18.0)
: (49.0*)
90.1* , -

(51.4)
90.2* , -

:
(67.2)
(54.4)
(02.2)
(50.5,
52.7)

781

90.3* (70.3)
90.4* (D50D64)
90.5* ,

90.6* (00-
D48)

(4041)
90.7 (C00
D48)
: -
(49.5*)
90.8* ,

(N25.0)

(9194)
: (96.)

91

[ .728]
: (-
) (93.0)
91.0
():

crista iliaca [Buchanan]
[Van Neck]
[Pierson]

782
-

91.1
[Legg-Calve-Perthes]
91.2 Coxa plana
-

91.3
91.8 -

-

91.9 -
,

92
92.0
():
[Panner]
[Haas]
92.1

():
[Burns]
[Brailsford]
92.2
():
os lunatum [Kienbck]
[Mauclaire]
92.3
92.4
():
, [Khler]
, apex patellae [Sinding-Larsen]

783

92.5
():
[Blount]
tuberositas tibiae [Osgood-Schlatter]
Tibia vara
92.6
() :
[Sever]
[Diaz]
[Khler]
[Haglund]
92.7 -

() :
[Freiberg]
[Iselin]
92.8

92.9 ,

,
(-)

93
: (42.)
93.0 ()
[coxa vara retrosa]
93.1 Kienbck
os lunatum
93.2
93.8

784
-

93.9 ,

, (-)

94
[ .728]
94.0 [Tietze]
94.1
94.2
: (22.4)
94.3
94.8
94.9 ,

785

-

(95-99)
95
-

: (-):
(Z89-Z90)
(20-21)
-
(96.)
[.
] (07.)
(40-43)
-
(Q65-Q79)
95.0
: (J34.2)
95.1 ,

:
(61.1)
95.2
95.3
95.4
95.5
:

(33.)
95.8 -

786
-

95.9 - -
,

96 -
,

: (02.0)

(Z95Z97)
, (80
81)
96.0
96.1 ,

96.2
96.3
96.4
96.5
96.6 ,

: , , -
(84.)
96.8 -


96.9 - -
,

787

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: , -

.
, -
, -
99.;
. 728.
0
1
2
3
4
5
6
7 ,

8 , -
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9
99.0
99.1 ()
99.2
99.3
99.4 -
99.5

99.6 -

99.7 - -

788
-

99.8
99.9 ,

789

, ,

,

II -

III , , -

IV , -

VI

VII

VIII

IX -

XI

XII

XIII -

: , ,

790

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