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Medical Refer to: Specht EE: Congenital dislocation of the hip (Medical

Progress). West J Med 124:18-28, Jan 1976

PROGRESS

Congenital Dislocation of the Hip


ELMER E. SPECHT, MD, Portland

Congenital dislocation or subluxation of the hip (congenital acetabular dyspla-


sia) is a coniplete or partial displacement of the femoral head out of the ace-
tabulum. The physical signs essential for diagnosis are age related. In new-
borns the tests for instability are the most sensitive. After the neonatal
period, and until the age of walking, tightness of the adductor muscles is the
most reliable sign. Early diagnosis is vital for successful treatment of this par-
tially genetically determined condition. Various therapeutic measures, rang-
ing from abduction splinting to open reduction and osteotomy, may be required.
Following diagnosis in the first month of life, the average treatment time in one
recent series was only 2.3 months from initiation of therapy to attainment of a
normal hip. When the diagnosis was not made until 3 to 6 months of age, ten
months of treatment was required to achieve the same outcome. When the
diagnosis is not made, or the treatment is not begun until after the age of 6,
a normal hip will probably not develop in any patient.

"There are persons,. who, from birth or from dis- either a complete dislocation of the head of the
ease, have dislocations outward of both the thighs; femur from the acetabulum or a partial displace-
in them, then, ihe bones are affected in like man- ment (subluxation) from the socket. Inadequate
ner, but the fleshy parts in their case lose their development of the roof of the socket (dysplasia)
strength less; . . . They have the equal use of and laxity or elongation of the ligaments and
both their legs, for in walking they totter equally capsule of the joint may be primary pathogenic
to this side and that."' Thus Hippocrates, in features; both will be discussed in greater detail
About Articulations described hip dislocations in later. True congenital dislocation of the hip must
the second century B.C. be distinguished from teratologic dislocations such
CONGENITAL DISLOCATION of the hip is a geneti- as may occur in arythrogryposis multiplex con-
cally influenced condition in which there is a genita, diastrophic dwarfism, Larsen's syndrome
disturbance of the normal anatomy of the hip, and other rare generalized mesenchymal dis-
orders. It should also be distinguished from the
From the Division of Orthopedics and Rehabilitation, University paralytic dislocations which may occur in cerebral
of Oregon Health Sciences Center, Portland.
Reprint requests to: E. E. Specht, MD, Division of Orthopedics
and Rehabilitation, University of Oregon Health Sciences Center,
palsy, myelomeningocele, and following paralytic
3181 SW Sani Jackson Park Road, Portland, OR 97201. anterior poliomyelitis. In true congenital disloca-

18 JANUARY 1976 * 124 * 1


CONGENITAL DISLOCATION OF THE HIP

tion of the hip there are no other consistent Etiology


abnormalities, with the possible exception of Pare noted as early as 1678 that familial cases
generalized joint laxity which is otherwise not occurred, and all epidemiologic studies clearly
disabling. It has been estimated2 that 5,300 new indicate that heredity plays a very significant role
cases occur annually in the United States. in cause. The recurrence risk among siblings of
Congenital dislocation of the hip has interested affected persons is about 40 times as great as the
physicians and surgeons alike for centuries. incidence expected in the general population.
Paletta, in 1775, was the first to use the term sub- Only one large survey of twins with congenital
luxation. As early as 1784 Camper is said to have hip dislocations has been reported, in Germany,
commented on the preponderance of affected and a much higher concordance rate for mono-
females. Dupuytren,3 in 1826, described the zygotic (41 percent) than for dizygotic twins (2.8
autopsy findings in the case of a 74-year-old man percent) was found. This clearly indicates the role
who also suffered from "retention of urine, ter- of genetic influences, but also indicates that other
minating fatally." He speculated that "the posi- factors must be operative. The proportions of
tion of the lower extremities of the fetus in utero affected second and third degree relatives is also
is such, that the thighs are very much bent on the increased, but drops rapidly toward the incidence
belly, from which it follows that the heads of the found in the general population with decreasing
thigh bones are continuously pressing against the closeness of the relationship, thus conforming most
lower and back part of the capsular ligament-a closely to the model for polygenic inheritance.
circumstance which, although without effect in Among the environmental factors closely re-
well-formed individuals, might, I apprehend, have lated is breech delivery, which is reported as hav-
an injurious influence in such as are weak, or of ing occurred in 11 to 40 percent of cases,9 in
lax, unresisting fibre. If this premise is conceded, contrast to the expected 2 to 4 percent. In addi-
there is not much difficulty in imagining that dis- tion, some series report a birth order effect, with
location may result . first-born children being most commonly af-
fected.'0 Several surveys have also reported an
Incidence increased incidence of congenital dislocation of
the hip during the winter months." "2
The incidence of congenital dislocation of the
hip varies with the gene pool studied, high fre- Additional environmental factors which have
quencies being reported in certain inbred Italian attracted attention are the supposedly deleterious
populations, in Israel, among certain American effects of swaddling, a custom in certain Euro-
pean and American Indian populations,'3 and the
Indian tribes and among the Japanese. Substantial allegedly salutary effects of carrying an infant
and very similar frequencies have also been re- astride the back. The former holds the hips ad-
ported from Sweden, Great Britain and the north- ducted, whereas the latter holds the hips ab-
ern part of the United States,4 an observation that ducted, consequently allowing better seating of
suggests a similar genetic derivation of the in- the femoral heads in the sockets. In implied
habitants of these areas, as history in fact sub- agreement, the American Academy of Pediatrics
stantiates. The condition is by no means uncom- has adopted as a symbol a modified version of the
mon in other population groups, although in famous Della Robbia terra-cottas (of the Spedale
Africans and Chinese very low incidences have degli Innocenti in Florence) of a swaddled infant
been reported. Incidence figures are somewhat in which the constricting garments have been
confused by the fact that if careful examinations loosened. Results of experiments with animals
of newborn infants are routinely done, a very have in fact shown that dislocations of the hips
high proportion of unstable hips can be found.5 can be provoked by immobilizing the hindlegs in
The majority of these, however, become stable abnormal positions; however, the general caveat
in the first few weeks of life,5-7 and likely repre- regarding extrapolation from animals to humans
sent the substrate upon which other factors, should be heeded.
probably environmental, act to produce true per- Some authors` believe that sudden extension
sistent dislocations, the frequency of which is of the hip after delivery of an infant, as might
about 1.1 per 1,000 live births in the United occur in the common practice of holding the new-
States.4'8 born infant by the ankles and slapping the back

THE WESTERN JOURNAL OF MEDICINE 19


CONGENITAL DISLOCATION OF THE HIP

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Figure 1.-Barlow's maneuver. With one hand grasping Figure 2.-Ortolani's maneuver (sign of jerking into
the symphysis in front and the sacrum in back, lateral place). After provocation of a dislocation by Barlow's
pressure is applied to the medial thigh with the thumb maneuver, as shown in Figure 1, the hip should be ab-
of the other hand while longitudinal pressure is applied ducted to about 80 degrees while the proximal femur
with the palm to the knee on the side being examined. is lifted anteriorly with the fingers placed along the
The hip, which has been flexed 90 degrees, is then lateral thigh. A positive sign is a sensation of a jerk or
adducted. A positive sign is a sensation of abnormal snap with reduction into the socket. A click is not
movement, indicating dislocation of the femoral head necessarily heard and a click wihout a sensation of ab-
from the acetabulum. The hands are reversed for ex- normal motion is probably not significant. (Reproduced
amining the other hip. This sign and Ortolani's sign by permission from Specht EE: Am Fam Physician 9:
may be found only in the first few weeks of life. (Re- 88-96, Feb 74)
produced by permission from Specht EE: Am Fam
Physician 9:88-96, Feb 74)
to drain respiratory secretions, is deleterious, at therefore giving an incidence of joint laxity in 50
least in the presence of laxity of the capsule and percent in the offspring of an affected person.
ligamentum teres. Obviously this far exceeds the risk factor in con-
It has long been recognized that females are genital dislocation, but environmental factors
about five times more commonly affected than vary, and necessarily modify the genetic predispo-
males, and a hormonal effect has been inferred. sition in such families.
Some observers14 have in fact reported that estro- Results in other familial studies"')"7 indicate
gen excretion levels are higher in affected infants that defective development of the acetabulum,
than in normals, but others15 have failed to con- with a resulting shallow socket (primary acetabu-
firm this. The belief, however, that female infants lar dysplasia), a concept popularized by Hart,'8
are more sensitive to the hormones of pregnancy may be polygenically inherited, and that those
and that these hormones cause greater ligamen- cases diagnosed after the neonatal period may
tous laxity than in the male, holds some currency. represent the dysplastic rather than the ligamen-
Findings in several studies', have shown that both tous laxity type.'9'20 It is thus possible that two
patients and first degree relatives of patients have genetic systems, one autosomal dominant and the
an unusual degree of joint laxity. This is prob- other polygenic, may interact and in turn be
ably inherited as an autosomal dominant trait, acted upon by environmental factors.

20 JANUARY 1976 * 124 * 1


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:,7
CONGENITAL DISLOCATION OF THE HIP

Figure 3.-Adduction contracture. In the infant or child


over 1 or 2 months of age, limitation of abduction of
the flexed hips is probably the most reliable sign of
congenital dislocation. Note the prominent "bowstring-
ing" of the adductor tendon in the proximal thigh on the
dislocated right side, as well as the limitation of abduc-
tion in comparison with the normal side. (Reproduced
by permission from Specht EE:' Am Fam Physician 9:
88-96, Feb 74)
Genetic Counseling
7f
or subluxed hip is abducted while being held in
90 degrees of flexion. There is nothing audible
about this "click," and in fact most clicks are not
significant.'5'25 It is the palpable, and sometimes
visible, reduction of the dislocated head into the
socket that constitutes a positive finding.
Barlow's maneuver consists essentially of pro-
voking a dislocation by longitudinal pressure
along the femur, with the hip flexed and adducted
and then reducing it in the same manner as in the
Ortolani maneuver. The infant must be relaxed
while these maneuvers are being carried out, and
a crying infant must be reexamined; in fact, re-
peated examinations26'27 throughout the first year
of life are essential if cases are not to be
missed.25'26'28-30 Unfortunately, roentgenography
cannot be relied upon to resolve doubt remaining
The empiric recurrence risks have been calcu- after clinical examination°5 26'3' in the newborn
lated"2 as follows: (1) with normal parents, the period. Only following ossification of the capital
risk to subsequent brothers of an index patient is femoral epiphyses at age four months or so can
1 percent, to subsequent sisters, 11 percent. (2) If roentgenograms clearly delineate the relationship
one parent has a congenital hip dislocation the of the femoral head to the acetabulum.
risk to a son is 6 percent, to a daughter 17 per- Ortolani's and Barlow's tests are of great value
cent. (3) If there are one parent and one child in the first few weeks of life, while the hip can
in an affected family, the risk to a second child still be reduced easily; however, once the head of
rises dramatically to 36 percent. The implications the femur has migrated laterally and proximally
of these data are obvious; at the very least care- onto the lateral surface of the ilium and the ad-
ful and repeated examinations of all infants in ductors have become relatively shortened and
such families must be started at birth. tight, other signs must be sought. Following the
first month or so of life in an affected infant,
Problems in Early Diagnosis abduction of the flexed hip, normally possible to
There is general agreement among authorities at least 60 or 70 degrees,4 becomes limited (Fig-
that the earlier treatment is started, the better the ure 3). It is of course helpful to compare abduc-
prognosis-a concept popularized by Putti.22 tion on one side with the other, but it should be
Considerable advances have been made since the borne in mind that bilateral involvement is not
adoption of Ortolani's technique23 for diagnosis uncommon, in fact more common in some series,31
in the newborn period. Von Rosen24 in 1962 re- and one must know the normal measurements.
ported his results in the application of Ortolani's Shortening of the extremity (Figure 4), conse-
technique, which is described in the accompany- quent to proximal displacement of the femoral
ing illustrations. This and Barlow's6 description of head, can be detected by careful comparison of
a maneuver which provokes dislocation in un- the lengths of the extended legs or by the method
stable hips have undoubtedly greatly increased of Galeazzi in which the hips and knees are
the numbers of infants who present for early flexed to about 45 degrees while holding the heels
treatment. Every physician who examines chil- equidistant from the buttocks on the examining
dren should be thoroughly conversant with these table. In the bent-knee method the dislocated side
techniques which are described and illustrated will show the knee to be lower, that is closer to
again (Figures 1 and 2) without apology. One bit the table.
of confusion regarding Ortolani's "sign of the Asymmetry of the inguinal and buttocks skin
click" bears some mention. The English word creases, and relative prominence of the greater
click is an unfortunate translation of the Italian trochanter on the affected side are all useful later
scatto which has no English cognate, and which signs. Asymmetry of the thigh folds, however, is
means a "jumping up" or "jerking into place," not useful-yielding a very high incidence of false
which in fact is what happens when the dislocated positives. After the child begins to walk, very
THE WESTERN JOURNAL OF MEDICINE 21
CONGENITAL DISLOCATION OF THE HIP

late in the game to make a diagnosis, the char- quency of dislocation and subluxation combined
acteristic painless abductor lurch (Trendelenberg was 20 percent in one series of infants who had
gait) toward the affected side, and an external presented for torticollis. The diagnostic inference
rotation attitude of the involved leg may be is clear; all such infants should be carefully ex-
noted. amined, and probably x-ray studies should be
We still find late cases and the question done as well.
has been raised20 if they represent a different
group of "stiff hips" than those which present Roentgenographic Features
early with instability. This would fit nicely with The diagnosis of congenital dislocation is essen-
the thesis of two genetic entities'6 with a common tially a clinical one; however, roentgenograms
end result, but as yet the proof is lacking.20 In can be of considerable help-especially in fol-
any case, it should be reiterated that one normal lowing progress under treatment. Efforts have
examination in the nursery does not relieve the been made6 28,13 to use roentgenograms in the
physician of further diagnostic efforts. newborn period, but opinions vary considerably
A significantly higher incidence of congenital as to their efficacy,",2 and most authorities agree
dislocation and subluxation of the hip in infants that normal findings on x-ray films do not exclude
affected by congenital muscular torticollis has the possibility that a dislocatable hip was x-rayed
been noted by two groups of authors.'2 The fre- while in the reduced position31 and the finding
therefore gave a false sense of security (Figure
5). After the age of 4 to 6 months, at which time
the capital femoral epiphyses ossify, roentgeno-
grams in the anteroposterior and "frog-leg" lateral
positions will satisfactorily delineate the relation-
ships between the femoral head and the acetabu-
i-
.X
lum. A horizontal line drawn transversely across
II A, 1-.i
I
the pelvis through the centers of both triradiate

.l.'I

Figure 4.-Asymmetry of the thigh and inguinal Figure 5.-This roentgenogram shows the difficulty in
creases. Bilateral asymmetry of the thigh creases alone evaluating x-ray studies of the hips in newborns. Al-
is an unreliable sign but asymmetry of the inguinal or though the hips appear symmetric and are not obvi-
gluteal creases, especially with apparent shortness of ously displaced superiorly, there is a suggestion of
the thigh, is a good indication of hip dislocation. Note lateral subluxation bilaterally. The acetabulums appear
that the infant's left knee is higher than the right and normal. This infant had positive Barlow and Ortolani
the prominence of the greater trochanter on the left is signs and was treated with a splint because of the
more pronounced and more proximal than on the right. positive clinical findings, in spite of the equivocal x-ray
The left hip is dislocated. (Reproduced by permission findings. (Reproduced by permission from Specht EE:
from Specht EE: Am Fam Physician 9:88-96, Feb 74) Am Fam Physician 9:88-96, Feb 74)

22 JANUARY 1976 * 124 * 1


CONGENITAL DISLOCATION OF THE HIP

cartilages in the acetabula and a vertical line epiphyses. In a normal hip, the ossific nucleus of
dropped from the lateral margin of the bony roof the femoral head lies below the horizontal line
of the socket to intersect the horizontal line at and medial to the vertical line. As subluxation
right angles is useful in detecting abnormally occurs the ossific nucleus is either bisected by
lateral and superior position of the capital femoral the vertical line or lies lateral to it. Similarly,
proximal migration of the femoral head, which
ultimately comes to rest superior to the horizontal
line, occurs.
Another useful measurement in following prog-
ress in treatment, and in diagnosis in late cases
at least, is the so-called acetabular index34 (Fig-
ures 6 and 7) which might better be called the
roof-slope angle. Lines drawn along the acetabu-

Figure 6.-Shenton's lines and the acetabular index.


In this patient, the left hip is obviously displaced both
laterally and superiorly, as shown by the disruption of
Shenton's line (medial neck to superior obturator fossa)
on the left. On the normal right side, the typical shep-
herd's-crook configuration of this imaginary line is
preserved. The acetabular index, which simply indicates
the slope of the roof expressed as degrees of angula-
tion from the horizontal, is increased on the left side.
(Reproduced by permission from Specht EE: Am Fam
Physician 9:88-96, Feb 74)

Figure 8.-Typical superior displacement of the left


hip, as seen in the anteroposterior view (A, above) and
Figure 7.-A frog-leg lateral view of the same hips as the frog-leg lateral view (B, below). Note the failure of
shown in Figure 6. This view shows the relative under- acetabular development and the relative hypoplasia
development of the capital femoral epiphysis on the pa- of the entire femoral head and neck on the left. Note
tient's left side. Delayed development cannot be de- also that the left hip cannot be abducted as well as the
tected until this ossification center becomes visible on right hip, because of tightness of the adductor muscles.
x-ray studies, usually at 4 to 6 months of age. (Repro- This is a roentgenogram of a 3-year-old girl, untreated
duced by permission from Specht EE: Am Fam Physi- at the time. (Reproduced by permission from Specht
cian 9:88-96, Feb 74) EE: Am Fam Physician 9:88-96, Feb 74)

THE WESTERN JOURNAL OF MEDICINE 23


CONGENITAL DISLOCATION OF THE HIP

lar roof and extended to intersect the horizontal slope of the acetabular roof, adductor tightness
line will form an acute angle which is easily meas- and actual dislocation of the head) simple abduc-
ured, and which is increased in dysplasia and dis- tion splinting by any of several devices6" 1'24'31'38
location. This angle normally becomes more will almost invariably result in a normal
acute with increasing age. The normal values for hip.6"'1124"28 In fact such treatment is probably best
this angle have been described27 and can be help- considered prophylactic.
ful in diagnosing dysplasia, particularly if there Following the first few weeks of life, however,
is a pronounced discrepancy between the two the difficulty in attaining normal clinical and
sides. With sufficiently early and successful treat- roentgenographic findings is greatly increased38-40
ment the acetabular index declines to normal, hence the considerable efforts expanded on early
whereas the slope increases and assumes a bi- diagnosis and treatment.
labiate appearance if dislocation persists (Figures Although there are exceptions,41 most ortho-
8A and 8B). paedic surgeons42'43 believe that nonoperative
A line can be projected along the medial por- management, as propounded by Putti22 some 40
tion of the femoral neck, the calcar femorale, and years ago, is best until the child begins to walk,
extended medially to intersect the margins of the and perhaps later. Opinions vary on details and a
obturator foramen in the anteroposterior projec- review of the literature suggests that there are no
tion (Figure 6). Normally this medial projection hard data on precisely when conservative man-
will correspond exactly with the superior margin agement ceases to be appropriate. Most would
of the foramen; if there has been proximal dis- agree that up to the age of 6 months or so, abduc-
placement of the head, however, the line will be tion splinting, or the Pavlik harness44 currently
disrupted and will pass more toward the triradi- gaining favor, is indicated until the clinical and
ate cartilage. An additional measurement of roentgenographic findings revert to normal in
value in appraising adequacy of reduction and both dysplasia without frank dislocation and in
coverage of the head by the roof is the center- dislocation. This may be a matter of some months,
edge angle of Wiberg35 in which an angle is con- and a period of immobilization equal to the
structed by a line drawn from the center of the elapsed time between birth and initiation of treat-
head through the lateral margin of the acetabu- ment has been suggested as a guideline to dura-
lum, intersecting at that point-with the vertical tion. Demonstration, by x-ray films taken in the
line described above. This "CE angle" is normally abduction device, that the hip is in fact reduced
more than 20 degrees, and declines to zero as the is essential. Between the ages of 6 and 12 months,
center of the laterally-displaced head comes to gentle manipulation under anesthesia may be re-
lie on the vertical line. quired to attain reduction. This should be fol-
Arthrography36 is used by some surgeons to lowed by a period of immobilization in a cast in
evaluate adequacy of reduction and to delineate the position of maximal stability. In recent years
the condition and position of the acetabular there has been increasing awareness of the danger
labrum (the limbus) and other soft tissues inter- of prolonged immobilization in either the frog-leg
posed between the head and the medial wall of (Lorenz) position of extreme abduction45 or the
the acetabulum, but its usefulness is limited. In internal rotation position of Lange-both of
our hands tomography37 has been useful to ascer- which subject the posterior retinacular vessels,
tain that a concentric reduction, without posterior which supply the capital femoral epiphysis, to ex-
displacement, has been obtained when the patient treme mechanical distortion. It is commonly be-
is in a cast or splint. lieved, and probably correctly so, that these
bizarre positions may contribute to the develop-
Treatment ment of avascular necrosis of the femoral head
(osteochondrosis), and instances have been re-
Treatment of congenital dislocation of the hip ported in which the previously normal hip in uni-
is perhaps more clearly age-related than any other lateral cases developed avascular necrosis during
condition in medicine, a fact that reflects progres- treatment.4'; It should also be noted that this conm-
sion of secondary pathologic changes. In an infant plication is never seen in untreated patients, and
with dislocatable hips due to ligamentous laxity can fairly be said to be iatrogenic. In an effort
(a primary change occurring before the develop- to avoid this catastrophe, a position involving
ment of secondary changes, such as increased somewhat more flexion but considerably less ab-

24 JANUARY 1976 * 124 * 1


CONGENITAL DISLOCATION OF THE HIP

increasing number of advocates in keeping with


the desire to minimize the risk to the vascular
supply of the head (Figure 9). When the adduc-
tors have shortened and the head is lying high on
the lateral wall of the ilium, any attempt to reduce
it into the acetabulum, several centimeters dis-
tally, and at the same time to abduct the thigh
to achieve stability of the reduction will neces-
sarily exert leverage on the head and cause com-
pression of the vessels, which it is believed can
be lessened by sectioning the structures medial
to the head and neck. Some authorities hold that
the adductors are of major concern in this regard,
while others41 believe the focus of attention should
be on the iliopsoas tendon. Statistical validation
of either position is lacking, but animal studies
have indicated a decreased incidence of vascular
Figure 9.-Complications of treatment. The left hip is
changes following adductor tenotomy.
displaced superiorly and laterally from the acetabulum, Open reduction enjoys some advocacy4l before
Shenton's line is disrupted and the capital femoral 2 years of age, and is increasingly used in those
epiphysis has undergone avascular necrosis. This hip over 2 years old;39 it is currently usually com-
had been treated by closed reduction and immobiliza-
tion in a plaster cast. Prognosis is poor. (Reproduced bined with osteotomy of the innominate bone,47-53
by permission from Specht EE: Am Fam Physician 9: and sometimes with derotational osteotomy of
88-96, Feb 74) the proximal femoral diaphysis to correct ante-
version. Two kinds of innominate osteotomy have
duction of the hips, a so-called "human position," been described for use early in life and have ap-
has been advocated.4; Conclusive data on the proximately the same usefulness. The pericapsular
incidence of complications in its use are not yet osteotomy of Pemberton47'50"52 depends on some
available. plasticity of the triradiate cartilage to allow a
Casts used during this age range will become hinge motion to occur and hence may be more
uriniferous quite quickly, and skin problems may useful in younger children and where it is desir-
arise. In some instances the substitution of a plas- able to make the socket somewhat smaller. The
tic splint or the cloth harness of Pavlik may be procedure described by Salter48'49'5",52 lends itself
satisfactory after a month or two of plaster im- better to management of older children because
mobilization, but again, maintenance of a con- the bend comes by levering the wing of the ilium
centric reduction must be confirmed by biplane or laterally and downward over the femoral head
tomographic roentgenography. after it is reduced into the acetabulum. We have
Between the ages of 1 and 3 years, secondary seen instances where the osteotomy was neatly
changes such as increased slope of the roof of the done but the head was never reduced into the
acetabulum, inversion of the limbus, fibrofatty true acetabulum. Both of these procedures should
masses filling the acetabulum, increased femoral be done only if the head can be pulled down
anteversion (which will be discussed later), poorly opposite the true socket by preliminary traction,
formed femoral head, thickening and hourglass and the acetabulum must be identified at opera-
constriction of the capsule, hypertrophy and elon- tion by its normal cartilaginous surface, which is
gation of the ligamentum teres, and tightness of invariably present.54 To conceive of these pro-
the muscle origins and insertions about the hip cedures as primarily innominate osteotomies is
(particularly the adductors and the iliopsoas) are erroneous. They are primarily open reductions
fully developed. Management during this period with osteotomies to improve bony coverage of
is the subject of considerable discussion and di- the head.
versity of opinion. Closed reduction following Another promising advance in managing this
preliminary skin traction39'4243'45 is probably the difficult problem is the addition of subtrochanteric
method used most between ages 1 and 2. Prelimi- resection osteotomy55-58 in which 1 to 2 cm of
nary subcutaneous adductor tenotomy39-43 has an bone are excised from the proximal femur, de-

THE WESTERN JOURNAL OF MEDICINE 25


CONGENITAL DISLOCATION OF THE HIP

pending on the tension of the muscles about the otomies,71 in which the proximal femur is tran-
hip as seen at the operating table. One of the sected, the proximal fragment is adducted against
remaining problems in open reduction and in- the pelvis and the distal fragment is abducted
nominate osteotomy is the pernicious tendency relative to the proximal. It is held that the dis-
of the head to redislocate while in the cast, or placed proximal fragment helps to support the
perhaps even while the cast is being applied. This pelvis, minimizing the abductor lurch which oc-
is a consequence of two factors, persistent femoral curs during gait. Early postoperative results have
anteversion and tension on the muscles crossing been described as encouraging, but there are no
the hip joint. Both of these factors can be dealt series of significant size over a period of years,
with at one sitting by subtrochanteric resection and some question must arise as to the effect on
and derotation osteotomy combined with open the knee of such realignments of the proximal
reduction. The concept of derotation osteotomy femur.
in the management of femoral anteversion is not
new, 9'59-61 and while some contend it is unneces- Complications and Prognosis
sary, others are equally convinced it is on occa-
sion critical to obtaining the best result. The The most common complications of treatment
question of future leg-length discrepancy must are failure to obtain concentric reduction, loss of
inevitably arise when bone is resected from one motion from operative intervention, the possi-
leg, and no long-term results are yet available; bility of postoperative infection of the joint and
however, it should be noted that sacrifice of 2 cm avascular necrosis of either the affected or the
or so of bone, the average necessary, will likely normal hip (Figure 9). Premature epiphyseal
eventuate in only a 1/2 cm discrepancy because fusion of the knee has also been described,72
of the well-known tendency of the adjacent Sequellae of failure to obtain reduction, or of no
epiphyses to overgrow following fracture and treatment, are the development of premature de-
other insults. A 1/2 cm, or even a 1 cm disparity generative joint disease.36'3 We have seen symp-
in leg lengths is negligible compared to the long- toms of easy fatigability and discomfort occur
term sequellae of persistent hip dislocation or in adolescence; however, most patients do remark-
repeated operative intrusion and resultant loss of ably well at this age in spite of an unsightly lurch-
motion. ing gait, in which the center of gravity is shifted
In children over the age of 7 or 8 who first toward the affected hip during the stance phase
appear for treatment, and perhaps in some in of gait, thus causing the trunk to sway laterally.
which there has been failure of previous treat- This occurs because the lever arm of the abductor
ment, the advisability of salvage procedures arises. muscles of the hip, which must maintain the
In times gone by the Hey-Groves-Colonna cap- pelvis level, is mechanically deficient. This allows
sular arthroplasty62-64 and various shelf pro- the pelvis to tilt abnormally away from the af-
cedures65,6' were widely used and still enjoy some fected hip when it is bearing weight. The effort to
support,67 but other authors68'69 contend that at compensate for this deficiency and prevent falling
least in the bilateral cases nothing should be done results in the shift of the center of gravity de-
after the age of 7 or so. Another procedure gain- scribed above.
ing advocacy in older children and young adults The usual course of a dislocated hip is one of
with persistent dislocations is the innominate increasing pain and disability during early middle
osteotomy of Chiari, which should be viewed as age, a time when most women need to remain
a salvage procedure when traction and reduction active in the care of their families. During this
do not appear feasible. In this procedure the ilium period many will require reconstructive arthro-
is cut through above the femoral head, which is plasties74,75- a subject in itself and beyond the
then displaced medially under the buttress of the scope of this paper. Thus one can see the crucial
osteotomy. Preliminary results are encouraging, need for early diagnosis and skillful management.
and the provision of bony stock above the femoral With the virtual disappearance of poliomyelitis
head will undoubtedly be helpful should subse- as a crippler of young people, there is probably
quent reconstruction be necessary. no single area in which the primary care physician
Other procedures which should be mentioned can be so effective in the prevention of late
for completeness, but which appear to have fallen crippling. Nowhere else is the proverbial ounce
from favor are the so-called pelvic support oste- of prevention (in this context a high index of

26 JANUARY 1976 * 124 * 1


CONGENITAL DISLOCATION OF THE HIP

suspicion and a willingness to examine carefully 32. Hummer CD, MacEwen GD: The coexistence of torticollis
and congenital dysplasia of the hip. J Bone Joint Surg 54A:1255-
hundreds of babies in order to identify the one at 1256, 1972
33. Andren L, Von Rosen S: The diagnosis of dislocation of
risk) of greater curative value to the patient. To the hip in newborns and the primary results of immediate treat-
ment. Acta Radiol 49:89-95, 1958
reiterate the words of Putti "La cura preambula- 34. Caffey J, Ames R, Silverman WA, et al: Contradiction of
toria non e piu una vuota aspirazione." congenital dysplasia-Predislocation hypothesis of congenital dis-
location of the hip through study of normal variation in acetabular
angles at successive periods in infancy. Pediatrics 17:632-640, 1956
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hip and arthritis deformans (roentgenological study). Acta Orthop
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dislocation. Paper read at the Annual Meeting of the American arthrographic studies of recent cases. Acta Chirur Scandinav 84
Academy of Orthopaedic Surgeons, 1973 (Suppl 63):1-142, 1941
3. Rang M: Anthology of Orthopaedics. Edinburgh and London, 37. Samuelson KM, Nixon GW, Morrow RE: Tomography for
E. and S. Livingstone, Ltd., 1966, pp 128-130 evaluation of congenital dislocation of the hip while in a spica
4. Harris LE, Lipscomb PR, Hodgson JR: Early diagnosis of cast. J Bone Joint Surg 56A: 844-845, 1974
congenital dysplasia and congenital dislocation of the hip. JAMA 38. Ponseti IV, Frigerio ER: Results of treatment of congenital
173:229-233, 1960 dislocation of the hip. J Bone Joint Surg 41A:823-846, 1959
5. Ritter MA: Congenital dislocation of the hip in the new- 39. Lloyd-Roberts GC, Swann M: Pitfalls in the management
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location of the hip. J Bone Joint Surg 44B:292-301, 1962 40. Schwartz DR: Acetabular development after reduction of
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location of the hip-A prospective study. Paper read at the An- 1965
nual Meeting of the American Academy of Orthopaedic Surgeons, 41. Ferguson AB: Primary open reduction of congenital dis-
1971 location of the hip uising a median adductor approach. J Bone
8. Coleman SS: Diagnosis of congenital dislocation of the hip Joint Surg 55A:671-689, 1973
in the newborn infant. JAMA 162:548-554, 1956 42. Coleman SS: Treatment of congenital dislocation of the hip
9. Ramsey PL, Rosenblum H: Early detection and treatment of in the infant. J Bone Joint Surg 47A:590-601, 1965
congenital hip dislocation. J Bone Joint Surg 55A:1312, 1973 43. Ponseti IV: Non-surgical treatment of congenital dislocation
10. Record RG, Edwards JH: Environmental influences related of the hip. J Bone Joint Surg 48A: 1392-1403, 1966
to the aetiology of congenital dislocation of the hip. Br J Prev 44. Glauber A: Treatment of the dysplastic hip with Pavlik's
and Social Med 12:8-22, 1958 bandage. J Bone Joint Surg 53B:152, 1971
11. Weissman SL, Salama R: Treatment of congenital disloca- 45. Gage JR, Winter RB: Avascular necrosis of the capital
tion of the hip in the newborn infant. J Bone Joint Surg 48A: femoral epiphysis as a complication of closed reduction of con-
1319-1327, 1966 genital dislocation of the hip. J Bone Joint Surg 54A:373-388, 1972
12. Slater BCS, Watson GI, McDonald JC: Seasonal variation 46. Gore DR: latrogenic avascular necrosis of the hip in
in congenital abnormalities. Br J Prev Soc Med 18:1-7, 1964 young children. Paper read at the Fortieth Annual Meeting of the
13. Salter RB: Etiology, pathogenesis and possible prevention Amer Acad of Orthop Surgeons, 1973
of congenital dislocation of the hip. Can Med Assoc J 98:933- 47. Pemberton PA: Pericapsular osteotomy of the ilium for
945, 1968 treatment of congenital subluxation and dislocation of the hip.
14. Andren L, Borglin NE: Disturbed urinary excretion pattern J Bone Joint Surg 47A:65-86, 1965
of oestrogens in newborns with congenital dislocation of the hip 48. Salter RB: Innominate osteotomy in the treatment of con-
-I. The excretion of oestrogen during the first few days of life. genital dislocation and subluxation of the hip. J Bone Joint Surg
Acta Endocrinologia 37:423426, 1961 43B:518-539, 1961
15. Thieme WT, Wynne-Davies R, Blair HAF, et al: Clinical 49. Salter RB: Role of innominate osteotomy in the treatment
examination and urinary oestrogen assays in newborn children of congenital dislocation and subluxation of the hip in the older
with congenital dislocation of the hip. J Bone Joint Surg 5OB:546- child. J Bone Joint Surg 48A: 1413-1439, 1966
550, 1968 50. Pemberton PA: Pericapsular osteotomy of the ilium for
16. Wynne-Davies R: Acetabular dysplasia and familial joint the treatment of congenitally dislocated hips. Clin Orthop 98:
laxity-Two etiological factors in congenital dislocation of the hip. 41-54, 1974
J Bone Joint Surg 52B:704-716, 1970 51. Salter RB, Dubos J: The first fifteen years' personal experi-
17. Wilkinson J, Carter C: Congenital dislocation of the hip. ence with innominate osteotomy in the treatment of congenital
J Bone Joint Surg 42B:669-688, 1960 dislocation and subluxation of the hip. Clin Orthop 98:72-103,
18. Hart VL: Primary genetic dysplasia of the hip with and 1974
without classical dislocation. J Bone Joint Surg 24:753-771, 1942 52. Utterback TD, MacEwen GD: Comparison of pelvic oste-
19. Wynne-Davies R: A family study of neonatal and late-diag- otomies for the surgical correction of the congenital hip. Clin
nosis congenital dislocation of the hip. J Med Genet 7:315-333, Orthop 98:104-110, 1974
1970 53. Steel HH: Triple osteotomy of the innominate bone. J
20. James JIP: Editorial. J Bone Joint Surg 54B:1-3, 1972 Bone Joint Surg 55A:343-350, 1973
21. Wynne-Davies R: Heritable Disorders in Orthopaedic Prac- 54. Larsen L: Personal communication
tice. London, Blackwell Scientific Publications, 1973, p 196 55. Dega W, Kr6l J, Polakowski L: Surgical treatment of con-
22. Putti V: Early treatment of congenital dislocation of the genital dislocation of the hip in children-A one-stage procedure.
hip. J Bone Joint Surg 15:16-21, 1933 J Bone Joint Surg 41A:920-934, 1959
23. Ortolani M: Un segno poco noto e sua importanza per la 56. Ashley RK, Larsen U, James PM: Reduction of disloca-
diagnosi precoce di prelussazione congenita dell'anca. Pediatria tion of the hip in older children. J Bone Joint Surg 54A:545-550,
45:129-135, 1937 1972
24. Von Rosen S: Diagnosis and treatment of congenital dis- 57. Sutherland D: Personal communication
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301, 1962 Read at the Forty-second Annual Meeting of the Amer Acad of
25. Smaill GB: Congenital dislocation of the hip in the new- Orthopaedic Surgeons, 1975
born. J Bone Joint Surg 50B:524-536, 1968 59. Platou E: Rotation osteotomy in the treatment of congenital
26. Williamson J: Difficulties of early diagnosis and treatment dislocation of the hip. J Bone Joint Surg 35A:48-54, 1953
of congenital dislocation of the hip in Northern Ireland. J Bone 60. Somerville EW: Reunion annuelle de la societe frangaise
Joint Surg 54B: 13-17, 1972 d'orthop6die et de la traumatologie 1954. Rev Orthop 41:134-140,
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or dysplastic. Clin Orthop 22:7-15, 1962 61. Christensen I: Anteversion deformity and derotation oste-
28. Von Rosen S: Further experience with congenital disloca- otomy in congenital dislocation of the hip. Acta Orthop Scandinav
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1968 62. Colonna PC: Capsular arthroplasty for congenital disloca-
29. Owen R: Early diagnosis of the congenitally unstable hip. tion of the hip-Indications and techniques-Some long-term re-
J Bone Joint Surg 30B:453-454, 1968 sults. J Bone Joint Surg 47A:437-449, 1965
30. Mitchell GP: Problems in the early diagnosis and manage- 63. Trevor D: The place of the Hey-Groves-Colonna operation
ment of congenital dislocation of the hip. J Bone Joint Surg 54B: in treatment of congenital dislocation of the hip. Ann Roy Coll
4-12, 1972 Surgeons England 43:241-258, 1968
31. MacKenzie IG: Congenital dislocation of the hip-The dc- 64. Buehler CE, Coleman SS: Colonna arthroplasty for dislo-
velopment of a regional service. J Bone Joint Surg 54B: 18-39, cation of the hip in the older child. J Bone Joint Sturg 54A:
1972 1799-1800, 1972

THE WESTERN JOURNAL OF MEDICINE 27


CONGENITAL DISLOCATION OF THE HIP
65. Bosworth DM, Fielding JW, Liebler WA, et al: Hip shelves 71. Haas J: A subtrochanteric osteotomy for pelvic support. J
in children. J Bone Joint Surg 42A:1223-1238, 1960 Bone Joint Surg 25:281-291, 1943
66. Heyman CH: Long-term results following a bone-shelf oper- 72. Bctting TDJ, Scrase WH: Premature epiphyseal fusion at
ation for congenital and some other dislocations of the hip in the knee complicating prolonged immobilization for congenital
children. J Bone Joint Surg 45A: 1113-1146, 1963 dislocation of the hip. J Bone Joint Surg 47B:280-282, 1965
67. Wilson JC: Surgical treatment of the dysplastic acetabulum 73. Lloyd-Roberts GC: Osteoarthritis of the hip. J Bone Joint
in adolescence. Clin Orthop 98:137-145, 1974 Surg 37B:8-47, 1955
68. Tachdjian MO: Pediatric Orthopedics. Philadelphia, W. B. 74. McCarroll HR: Reconstruction of the adult hip in congenital
Saunders Company, 1972 dysplasia and congenital dislocation. Pacific Med and Surg 73:
69. MacEwen GD: American Academy of Orthopaedic Surgeons, 116-118, 1965
Conference in Children's Orthopaedics, Seattle, 1972 75. Wedge JH, Salter RB: Innominate osteotomy-Its role in
70. Chiari K: Medial displacement osteotomy of the pelvis. the arrest of secondary degenerative arthritis of the hip in the
Clin Orthop 98:55-71, 1974 adult. Clin Orthop 98:214-224, 1974

The Obese Patient


To have a significant impact on life expectancy, in the actuarial sense, one has
to have a weight which deviates by more than 30 percent from the expected
weight for that person at his particular height. Basically, if you are overweight,
you have a risk that is about 4.9 times as great of being diabetic, about 3 times
as great of being hypertensive and of developing hypertensive cardiovascular dis-
ease, and about 21/2 times as likely to develop gallbladder disease with gallstones
and complications therefrom. So, for people who are significantly overweight,
there are substantial medical risks associated with that weight which, therefore,
allow the physician, because of the risk of the obesity as a factor in the develop-
ment of these conditions, to employ methods which have a somewhat higher
risk-to-benefit ratio than for a patient who is less than 30 percent overweight
and who has no medical problems that can be detected.
-GEORGE A. BRAY, MD, Torrance, CA
Extracted from Audio-Digest Family Practice, Vol. 23, No. 5,
in the Audio-Digest Foundation's subscription series of tape-
recorded programs. For subscription information: 1930 Wilshire
Blvd., Suite 700, Los Angeles, CA 90057.

28 JANUARY 1976 * 124 * 1

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