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2017 | ANNUAL REPORT

To those who say


“impossible, impractical, unrealistic,”
we say:

CHALLENGE ACCEPTED
ALNYLAM is harnessing the RNA interference (RNAi) pathway—a
naturally occurring biological mechanism of gene silencing—for
the advancement of a potential new class of innovative medicines.
This is a revolutionary approach that has the potential to transform
the care of patients with genetic diseases.

750+ Employees and growing

7 Programs currently in
clinical development

5,000 Study participants

20,000 Doses administered

25+ Clinical studies to date

1
TO OUR STOCKHOLDERS

It is my pleasure to inform you that our 2017 Annual Meeting of Stockholders will be conducted entirely online on May 10, 2018
at 8:00 a.m. ET. Alnylam joins a growing list of forward-looking companies conducting virtual annual meetings to increase
stockholder accessibility, improve meeting efficiency and reduce costs. Stockholders will be able to listen, vote and submit
questions from their home or any remote location with internet connectivity. Information on how to participate in this year’s
virtual meeting can be found in the attached 2017 Notice of Annual Meeting of Stockholders and Proxy Statement.

2017 WAS A MONUMENTAL YEAR FOR ALNYLAM. reported encouraging Phase 1 and Phase 2 open-label extension
data, initiated the ATLAS Phase 3 program, and aligned with the

O
ur 15-year journey from possibility to patients has
FDA on a robust risk mitigation strategy that led to the agency’s
culminated in the first-ever regulatory filings for
lifting of a temporary clinical hold. With inclisiran, our partners at
an RNAi therapeutic, with the potential to bring
The Medicines Company reported positive results from the
a whole new class of innovative therapies to the
ORION-1 Phase 2 study and initiated the ORION Phase 3 program
forefront of medicine.
with enrollment in ORION-9, ORION -10 and ORION-11
The presentation of positive results from our APOLLO Phase 3 now complete.
study of patisiran was followed closely by our filings of a New
Turning to our earlier stage programs, we reported encouraging
Drug Application with the U.S. Food and Drug Administration
interim results from our Phase 1/2 study for lumasiran (formerly
(FDA) and a Marketing Authorisation Application with the
known as ALN-GO1) for the treatment of primary hyperoxaluria
European Medicines Agency (EMA). Thanks to our phenomenal
type 1 and initiated a Phase 2 trial for cemdisiran (formerly known
team and their remarkable fortitude, both filings were
as ALN-CC5) in patients with atypical hemolytic-uremic syndrome.
completed in record time — less than 90 days after announcing
We also reported highly encouraging results from our Phase 1
topline APOLLO results — highlighting our keen sense of
trial for ALN-TTRsc02, a next-generation investigational RNAi
urgency and commitment to excellence. Notably, both the U.S.
therapeutic targeting TTR, which we believe has the potential
and European regulatory agencies have now accepted our fil-
to offer a promising potential treatment option for patients
ings, and patisiran is currently under Priority Review status with
with ATTR amyloidosis.
the FDA and under accelerated assessment by the EMA, signaling
the potential for an expedited review. Patisiran was also recently From a strategic standpoint, we recently restructured our rare
granted a Breakthrough Therapy Designation by the FDA. disease alliance with Sanofi Genzyme, originally established in
2014. As a result of this restructuring, Alnylam now has global
Beyond patisiran, we are advancing three programs in late commercialization rights to our ATTR amyloidosis programs,
stages of development: givosiran for the treatment of acute namely patisiran and ALN-TTRsc02. In turn, Sanofi has obtained
hepatic porphyrias, and, with our strategic partners, fitusiran for
the treatment of hemophilia and rare bleeding disorders, and
inclisiran for the treatment of hypercholesterolemia.

For givosiran, we reported positive Phase 1 data, initiated the


ENVISION Phase 3 study, and reached alignment with the FDA on
a pivotal trial design that we believe will significantly accelerate
givosiran’s clinical development path, providing the opportunity
for potential regulatory approval in 2019. With fitusiran, we

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global development and commercialization rights to fitusiran. the U.S. and EU in mid- and late 2018, respectively. Further, in
This restructured agreement allows the parties to develop both light of our recently acquired rights to commercialize patisiran
products in a comprehensive manner. Specifically, this allows in rest-of-world (ROW) territories, we plan to file for regulatory
us to address the full spectrum of ATTR amyloidosis disease approvals in ROW countries, starting with Japan in mid-2018. We
treatment and prevention, and to maintain a sustained also plan to report an interim analysis from the ENVISION Phase
leadership role in the therapeutic management of this 3 trial for givosiran and, in the event of a favorable readout, file
devastating disease. Further, upon approval of patisiran, the for accelerated regulatory approval in late 2018. Further, we plan
restructured agreement enables the potential for near-term to support the efforts of our partners Sanofi Genzyme and The
acceleration of product revenue growth based on the newly Medicines Company with respect to the ATLAS and ORION Phase
acquired rights to commercialize patisiran in regions outside 3 programs for fitusiran and inclisiran, respectively, and initiate a
of North America and Western Europe. Phase 3 trial for ALN-TTRsc02.

In addition, we entered into a new strategic partnership with COMMERCIAL READINESS WILL BE A TOP PRIORITY IN 2018
AHEAD OF OUR FIRST PRODUCT LAUNCH.
Vir Biotechnology to advance our pre-clinical portfolio of siRNA
therapeutics toward infectious diseases, including ALN-HBV02, In addition to our significant pipeline advancements, we made
and further optimized our GalNAc conjugate delivery platform important progress on our broader business objectives in 2017.
with a next-generation Enhanced Stabilization Chemistry Plus To prepare for our first product launch, we have been actively
(ESC+) design conferring greater target specificity and a wider expanding our commercial and medical affairs capabilities
therapeutic index. globally, onboarding and training our field force, and enhancing
our disease awareness and patient identification efforts. Overall,
With seven active clinical programs, including three in late-stage
we hired close to 200 employees in 2017 and are now more than
development and one in registration in the U.S. and Europe,
750 strong. Despite such deep investments for Alnylam’s future,
we believe our 2017 progress brings us within arm’s reach of
we ended the year with a healthy cash balance of over $1.7
achieving our Alnylam 2020 vision of building a multi-product,
billion, raising over $1.0 billion in capital through two
commercial-stage, global biopharmaceutical company with a
separate financings.
deep pipeline and a sustainable product engine.
As we approach commercialization, we are poised to execute
WE BELIEVE OUR ACCOMPLISHMENTS IN 2017 HAVE
POSITIONED US WELL FOR THE NEXT PHASE OF on Alnylam’s abiding mission: to deliver medicines with
ALNYLAM’S JOURNEY.
transformative potential to those who are most in need. This
We envisage 2018 to be the year when we transition from a fuels our passion for the work that we do. I am thankful and
research and development organization to an innovative, proud of everything we have accomplished in 2017, and your
patient-centric, global commercial organization committed to steadfast support has made that possible.
patient access. We will continue to invest in our discovery engine Best,
and plan to maintain a robust pipeline to continue to create
long-term value for stockholders.

With that vision in mind, and assuming regulatory approvals,


John Maraganore, Ph.D.
we expect to initiate the commercial launch for patisiran in CHIEF EXECUTIVE OFFICER

3
PAT I S I R A N INVESTIGATIONAL
TREATMENT FOR

HEREDITARY ATTR AMYLOIDOSIS

D I S E A S E O V E R V I E W

~50,000 people worldwide


Hereditary transthyretin- and tissues, such as the
mediated (hATTR) amyloidosis peripheral nerves and heart.
is an inherited, progressively
Major unmet medical need
debilitating, and often fatal
exists, with significant morbidity
disease caused by mutations
and a life expectancy of 2.5 to
in the transthyretin (TTR) gene.
15 years from symptom onset.
Mutations in TTR cause
abnormal amyloid proteins to
accumulate and damage organs

4
The only investigational therapy for the treatment of
hATTR amyloidosis, whether investigational or approved,
to demonstrate reversal of certain disease manifestations
in a majority of patients in a clinical study.

U.S. and EU commercial launch expected


in mid- and late 2018, respectively

MET PRIMARY EFFICACY ENDPOINT of a change in mNIS+7 score


(a measure of neuropathy) relative to placebo and all secondary
endpoints with statistical significance in APOLLO Phase 3 study

ENCOURAGING SAFETY AND TOLERABILITY PROFILE relative to


placebo with up to 18 months of dosing and a low rate of
treatment discontinuations

RECEIVED BREAKTHROUGH THERAPY DESIGNATION, Priority Review


status, and expansion of Orphan Drug designation to the
treatment of transthyretin-mediated amyloidosis from the
FDA and accelerated assessment from EMA

“In the past people were hesitant to get


Kipper tested, but with potential treatments on
LIVING WITH the horizon, people are like, ‘maybe I do
h AT T R A M Y L O I D O S I S
want to know,’ because there might be
something that can help.”

5
GIVOSIRAN INVESTIGATIONAL
TREATMENT FOR

ACUTE HEPATIC PORPHYRIAS (AHPs)

D I S E A S E O V E R V I E W

5,000 patients with sporadic


attacks in U.S./EU
1,000 patients with recurrent
attacks in U.S./EU
• AHPs are a family of ultra-rare orphan diseases causing
incapacitating and potentially fatal attacks, leading to frequent
hospitalizations and chronic pain

• Predominantly female

6
73% Mean decrease in annualized attack
rate relative to placebo in a Phase 1 study

Reported positive interim Phase 1 randomized,


placebo-controlled study results in patients with acute
intermittent porphyria with recurrent attacks1

GENERALLY WELL TOLERATED WITH UP TO 12 MONTHS OF DOSING


No drug-related serious adverse events; one fatal case of acute
pancreatitis complicated by pulmonary embolism, considered
unlikely related to givosiran

RECEIVED BREAKTHROUGH THERAPY DESIGNATION from FDA


and PRIME designation from the EMA for the prophylaxis of attacks
in patients with AHPs

INITIATED THE ENVISION PHASE 3 STUDY


• Achieved alignment with the FDA to use reduction of urinary
biomarker ALA as a surrogate endpoint reasonably likely to predict
clinical benefit

• Interim readout based on ~30 patients expected in mid-2018

• Expect NDA submission in late 2018 and potential FDA approval in


mid-2019, assuming favorable interim Phase 3 results

“I am bound and determined to do


Nichol whatever I can to ensure that future
LIVING WITH PORPHYRIA generations do not have to go through
what I have gone through as a result
of this illness.”

1. As of data cut-off date of April 21, 2017

7
OT H E R P R O G R A M S TO WATC H

FITUSIRAN INCLISIRAN
Investigational treatment for hemophilia A or B Investigational treatment for
with or without inhibitors and potentially other hypercholesterolemia
rare bleeding disorders
R E S U L T S: (FROM ORION-1 PHASE 2 STUDY)2
R E S U L T S: (PHASE 2 OPEN-LABEL EXTENSION STUDY)
1
Lowering of LDL-C: 52.6% average and 81%
~80% lowering of antithrombin in response to monthly maximum as measured on Day-180 following 300 mg
subcutaneous dose of 50 or 80 mg in a Phase 1/2 study subcutaneous administration on Day-1 and Day-90
in a Phase 1/2 study
• Increase in thrombin generation to the lower
range of normal • Time-adjusted mean lowering of > 50% for the
6-month period from Day-90 through Day-270
• Median annual bleeding rate (ABR)=1 for all patients
• Optimal dosing regimen determined
• Median ABR = 0 for patients with inhibitors
• No material safety issues reported
• Adverse events mild to moderate in severity, with the ex-
ception of a fatal thrombotic event, resulting in temporary
N E X T S T E P S: (BY THE MEDICINES COMPANY)
clinical hold considered possibly related to study drug
• ORION-9, 10 and 11 pivotal Phase 3 studies initiated
N E X T S T E P S:
• Enrollment in ORION-9, 10, 11 now complete
• Transfer of development and commercialization
• Expect to initiate enrollment in ORION-4 cardiovascular
activities to Sanofi Genzyme expected to be
outcome (CVOT) study in mid-2018
substantially complete in mid-2018
• Dosing in ATLAS to begin shortly

8
CLINICAL DEVELOPMENT PIPELINE
F O C U S E D I N 3 S T R A T E G I C T H E R A P E U T I C A R E A S ( S T A r s ):
GENETIC MEDICINES CARDIO-METABOLIC DISEASES HEPATIC INFECTIOUS DISEASES

BREAKTHROUGH REGISTRATION/ COMMERCIAL


HUMAN POC1 DESIGNATION EARLY STAGE LATE STAGE COMMERCIAL2 RIGHTS

PATISIRAN
HEREDITARY ATTR AMYLOIDOSIS - Global

GIVOSIRAN
ACUTE HEPATIC PORPHYRIAS - Global

FITUSIRAN
15-30%
HEMOPHILIA AND RARE
BLEEDING DISORDERS royalties

Milestones
INCLISIRAN & up to 20%
HYPERCHOLESTEROLEMIA
royalties

ALN-TTRSC02
Global
ATTR AMYLOIDOSIS

LUMASIRAN
PRIMARY HYPEROXALURIA TYPE 1 - Global

CEMDISIRAN
Global
COMPLEMENT-MEDIATED DISEASES

1. POC,
POC,
C pro
proo
pr
rooff of
o concept – defin
ined
in ed a
ass h
having dem
emonsttrate
rated targe
get gene knockdown and/or add
dditiona
na
al e
evid
idence of activ
activi
ivvi
vity
ty in clinical
cl studiies
2. Inclu
Inclu
lu
udes
dess marketing applic
plic
iccatio
atio
ttiion su
submis
bmission
si s
As of Ma
M rc
rch 2018

ALN-TTRsc02 LUMASIRAN CEMDISIRAN


(FORMERLY ALN-GO1) (FORMERLY ALN-CC5)

Investigational treatment Investigational treatment Investigational treatment


for ATTR amyloidosis for primary hyperoxaluria for complement-mediated
type 1 (PH1) diseases
Low volume, subcutaneous
dosing in a Phase 1 study No drug-related serious adverse
No serious adverse events or
events or discontinuations Phase 2
reported in a Phase 1 study study initiated in atypical
discontinuations due to AEs
reported hemolytic uremic syndrome
66% (aHUS)

~80% mean maximal reduction

knockdown at nearly in urinary oxalate (N=4)

1 year after a in response to monthly

single low dose3 subcutaneous doses of


1 mg/kg for 3 months4

1. As of data cut-off date of June 15, 2017 2. Data presented at European Society of Cardiology Congress, August 28, 2017 3. As of data cut-off date of May 31, 2017 4. As of data cut-off date of October 3, 2017
9
Building a Commercial Organization

We
e have been expanding our commercial
org
ganization and capabilities globally in prepa-
ratio
on for our first potential product launch. We
on
plan
n to continue this growth trajectory in 2018
as we onboard 250+ employe
ees with marketing,
sale
es, patient access/services
s, distribution and
prod
duc
uct reimbursement experrtise to deploy in
ACHIEVING
A C H I E V I N G ALNYLAM
A L N Y L A M 2020
2 0 2cu
0 omer-f
custtomer-ffacing activities on a global scale.

ACHIEVING ALNYLAM 2020

Patient Focus

Patient identification efforts for hATTR amyloidosis

• Alnylam Act™-free genetic screening to detect TTR muta-


tions in patients with neuropathy and cardiomyopathy

Educational campaigns
• Patient and physician-geared websites to raise
awareness and promote accurate diagnosis:
• hATTRamyloidosis.com
• hATTRbridge.com
Expanded access/comp
pas
assi
sion
sionat
onate
ate us
u e pr
progra
ams

•P
Prrov
rov
ovid
idess acc
cces
esss to pat
es atis
isir
isir
iran
an to el
e iggib
ble pat
atie
ients
ie
in U.S
S. an
andd EU

• Mo
More
re tha
han
n 10
1000 eliggible pattientss ha
have
ve beg
egun
un
trea
treattment with patisiran und nder
er the
hese
se pro
rogr
grams

Advo
Advocacy
cy

• Wo
Work
rrkkin
ing co
olllab
borat
ati
tiv
ivel
elyy wi
with
th pat
atie
ientt adv
d ocac
acyy gr
g oups to
improve care for hATTR amyylo loid
idos
osis patientts
10
Alnylam’s pledge to continuously invest in its
discovery engine is a reflection of its commitment
to scientific excellence and a precursor to a deep
and sustainable pipeline, making the Company an
attractive partner of choice to both industry and
academic peers with a palate for disruptive innovation.

The relationships that Alnylam has cultivated


with key industry partners such as Sanofi Genzyme
and The Medicines Company have been fruitful in
advancing multiple late-stage products
(patisiran, fitusiran and inclisiran).

PART N ER S H IP S

The strategic restructuring The newly conceived This pre-competitive collab-


of the Sanofi alliance alliance with Vir oration with Regeneron and
provides Alnylam with Biotechnology for the others has the potential to
global rights to all ATTR development of RNAi help fund the UK Biobank
amyloidosis products and therapeutics for infectious consortium to accelerate the
provides Sanofi with global diseases is in line with the generation of exome sequence
rights to fitusiran Company’s collaboration data from > 500,000 volun-
strategy in expanding teer participants, greatly
to Strategic Therapeutic enhancing Alnylam’s target
Areas (STArs) outside of identification and validation
Genetic Medicines or efforts, contributing to the
Cardio-Metabolic Diseases sustainability of its RNAi
therapeutics product engine

11
Our Values
Everything we do at Alnylam reflects our core values
that serve as the foundation of our culture

• Sense of Urgency • Innovation & Discovery

• Open Culture • Passion for Excellence


Our Culture
• Commitment to People
We place diversity and inclusion at the forefront
of our core values to exhibit the same dedication to our
people as we do to pioneering new medicines

Our Footprint
We are a global biopharmaceutical company with

>750 employees
headquartered in Cambridge, Massachusetts, with offices
in the UK, Switzerland, France, Germany and other
European countries

Our expanding geographic footprint provides the platform


to access patients worldwide

Alnylam has been named one of the


Boston Globe’s top places to work for
3 years in a row: 2015, 2016, 2017.
We don’t take this for granted and
strive to earn this honor as a commit-
ment to our employees and ultimately
to our patients.
12
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ALNYLAM PHARMACEUTICALS, INC.
ANNUAL REPORT ON FORM 10-K
For the Year Ended December 31,2017
TABLE OF CONTENTS

PART I
ITEM I. BUSINESS................................................................................................................................................................. I
ITEM lA. RISK FACTORS........................................................................................................................................................ 39
ITEM lB. UNRESOLVED STAFF COMMENTS..................................................................................................................... 64
ITEM 2. PROPERTIES............................................................................................................................................................. 65
ITEM 3. LEGAL PROCEEDINGS .......................................................................................................................................... 65
ITEM 4. MINE SAFETY DISCLOSURES.............................................................................................................................. 65
PART II
ITEM 5. MARKET FOR REGISTRANT'S COMMON EQUITY, RELATED STOCKHOLDER MATTERS AND
ISSUER PURCHASES OF EQUITY SECURITIES............................................................................................ 66
ITEM 6. SELECTED CONSOLIDATED FINANCIAL DATA.............................................................................................. 68
ITEM 7. MANAGEMENT'S DISCUSSION AND ANALYSIS OF FINANCIAL CONDITION AND RESULTS OF
OPERATIONS...................................................................................................................................................... 69
ITEM 7A. QUANTITATIVE AND QUALITATIVE DISCLOSURES ABOUT MARKET RISK.......................................... 85
ITEM 8. FINANCIAL STATEMENTS AND SUPPLEMENTARY DATA........................................................................... 86
ITEM 9. CHANGES IN AND DISAGREEMENTS WITII ACCOUNTANTS ON ACCOUNTING AND FINANCIAL
DISCLOSURE....................................................................................................................................................... 126
ITEM 9A. CONTROLS AND PROCEDURES .......................................................................................................................... 126
ITEM 9B. OTHERINFORMATION.......................................................................................................................................... 126
PART II I
ITEM 10. DIRECTORS, EXECUTIVE OFFICERS AND CORPORATE GOVERNANCE................................................... 127
ITEM II. EXECUTIVE COMPENSATION............................................................................................................................. 127
ITEM 12. SECURITY OWNERSHIP OF CERTAIN BENEFICIAL OWNERS AND MANAGEMENT AND RELATED
STOCKHOLDERMATTERS.............................................................................................................................. 127
ITEM 13. CERTAIN RELATIONSHIPS AND RELATED TRANSACTIONS, AND DIRECTOR INDEPENDENCE....... 127
ITEM 14. PRINCIPAL ACCOUNTANT FEES AND SERVICES........................................................................................... 127
PART IV
ITEM 15. EXIITBITS AND FINANCIAL STATEMENT SCHEDULES ................................................................................ 128
ITEM 16. FORM 10-K SUMMARY ........................................................................................................................................ 133
SIGNATURES............................................................................................................................................................................. 134
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01
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012
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012
3456768:98 3456768
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012
23456579YW 2345657
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010
3456768987 3456768
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bM>faV&a(0cYaV0V&a0c"QQa&gf

012
2345657998 2345657
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011
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!iBg27'd1355

012
EXECUTIVE OFFICERS DIRECTORS

John M. Maraganore, Ph.D. Michael W. Bonney, Chair


Chief Executive Officer and Director Chief Executive Officer and Chair,
Kaleido Biosciences, Inc.
Barry E. Greene
President Dennis A. Ausiello, M.D.
Director, Center for Assessment Technology and
Yvonne L. Greenstreet, MBChB, MBA Continuous Health; Physician-in-Chief Emeritus,
Chief Operating Officer Massachusetts General Hospital
Akshay K. Vaishnaw, M.D., Ph.D. John K. Clarke
President, Research and Development Managing General Partner, Cardinal Partners
Manmeet S. Soni Marsha H. Fanucci
Chief Financial Officer Retired Senior Vice President and Chief Financial Officer,
Laurie B. Keating, J.D. Millennium Pharmaceuticals, Inc. (now a wholly-owned
Senior Vice President, subsidiary of Takeda Pharmaceutical Company Limited)
General Counsel and Secretary John M. Maraganore, Ph.D.
Michael P. Mason Chief Executive Officer, Alnylam Pharmaceuticals, Inc.
Vice President, Steven M. Paul, M.D.
Finance and Treasurer President, Chief Executive Officer and Director,
Voyager Therapeutics, Inc.

David E.I. Pyott


Retired Chief Executive Officer and Chair, Allergan, Inc.

Paul R. Schimmel, Ph.D.


Ernest and Jean Hahn Professor of Molecular Biology and
Chemistry, The Scripps Research Institute

Amy W. Schulman
Chief Executive Officer, Director and Co-Founder,
Lyndra, Inc.; Partner, Polaris Partners

Phillip A. Sharp, Ph.D.


Institute Professor, David H. Koch Institute for Integrative
Cancer Research, Massachusetts Institute of Technology
Stock Symbol: ALNY (NASDAQ) Corporate Counsel:
Goodwin Procter LLP
Transfer Agent: 100 Northern Avenue
First Class/Registered/Certified Mail: Boston, MA 02210
Corporate Headquarters:
Computershare Investor Services 617-570-1000
Alnylam Pharmaceuticals, Inc.
PO BOX 505000
300 Third Street Independent Auditors:
Louisville, KY 40233-5000
Cambridge, MA 02142 PricewaterhouseCoopers LLP
617-551-8200 Courier Services: 101 Seaport Boulevard, Suite 500
Computershare Investor Services Boston, MA 02210
www.alnylam.com 462 South 4th Street Suite 1600 617-530-5000
Follow @Alnylam on Twitter Louisville, KY 40202

Overnight Correspondence:
Computershare
211 Quality Circle, Suite 210
College Station, TX 77845
w
www.computershare.com/investor

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