CONGENITAL EVENTRATION OF D
IRAGM
RESEMBLING DIAPHRAGMATIC HERNIA: A CASE REPORT
Jagadish Chandra Das*, Syeda Humaida Hasan2*, Nita Chowdhury3, Md. Akbar Husain Bhuiyan’,
Newton Ghosh3, Debashish Kumar Roy?
Professor & Head, Department of Neonatology, Chittagong Medical College Hospital (CMCH), Junior Consultant,
Department of Neonatology, CMCH, *Assistant Registrar, Department of Pediatrics, CCH, #Professor, Department of
Pediatric Surgery, CCH.
Introduction
Eventration of diaphragm isa rare anomaly where continuity
of diaphragm remain intact with abnormal elevation of its
musculature. The important aspect of the present case was
that the neonate was clinically diagnosed as diaphragmatic
hernia but eventually was confirmed as eventration of
diaphragm during operative procedure,
Objective
The case is presented here with a view to aware
pediatrician, neonatologist and pediatric surgeon regarding
diagnostic dilemma and management of eventration.
Case Report
7 days old full term female baby weighing 3000 ¢ was
referred to a tertiary care hospital with the complaints of
respiratory distress, cyanosis and feeding difficulties since
her 1st day of age. Mother's antenatal period was
Uneventful except polyhydramnios. On examination, she was
ddyspneic, cyanosed with poor tone and activities. Recorded
‘oxygen saturation (Sp02) was 78%. Her chest was bulged on
left side with mediastinal shifting to the right. Percussion
note was dull with decreased air entry on the left side, There
was no other congenital anomaly. Chest and abdominal
radiograph did not define left hemidiaphragm. The neonate
was initially diagnosed as left sided diaphragmatic hernia,
Supportive management was given
Fig: Patient ion artical ventilation
Fg 2: After weaning rom venlator and CPAP
Fig: Healing scar at nesion site
She underwent operative procedure on her 13th postnatal
day. Thin, intact left hemidiaphragm was found at the level
of 2nd intercostal space. Abdominal viscera were herniated
in the left thoracic cavity with compressed left lung.
Plication of the diaphragm was done with 1/0 prolene after
returning back the viscera. After operation, the patient was
fon intermittent positive pressure ventilation (IPPV) and
continuous positive airway pressure (CPAP) in neonatal
intensive care unit. Follow up xrays showed high up
diaphragm and gradual expansion of left lung field.
Preoperative and postoperative echocardiography was
normal. She was on oxygen support till 1 month of her age
with gradual weaning.
rr a
Incision site was healthy but she had suffered from sepsis with,
Staphylococcus aureas which was treated accordingly. The
infant was discharged from hospital on 42th postnatal day.
Figs Srl rertgenegrams rom ef tort
Svreoperatve Chest and abdominal xy fesemBlog hernia
B)ln immediate soxtopertve peri with hgh up daphrogm
] At the geo a day (ot 32th 200) wth expansion of Te ung
Discussion
Eventration occurs almost exclusively on the left side as seen
in this case though sex predilection does not match with
previous data. This patient presented with dyspnea in
neonatal period which is the principal symptom of both
diaphragmatic hernia and eventration. Imaging of the
ciaphragm, fluoroscopy, prenatal ultrasound may be used to
confirm the diagnosis. But in this case, only chest X-ray was
done. It showed loss of demarcation of left hemidiaphragm
‘and bowel loops in the let thoracie cavity mimicking hernia,
Even with the aid of MRi, sometimes it is difficult to
distinguish hernia from eventration. The management of
feventration depends upon the extent of cespiratory distress.
Surgical intervention was required inthis newborn as she had
severe respiratory distress with central cyanosis demanding
mechanical ventiation. Pst operative chest imaging showed
gradual expansion of ieft ung but long term outcome will
‘sepend on further pulmonary development.
Conclusion
Overall mortality of eventration of diaphragm is high even
after plication in neonatal period. The neonate is saved
probably due to absence of associated congenital anomaly,
timely referral, prompt operative decision and good
postoperative supportive care. Eventration of diaphragm
should be kept in mind as 2 differential diagnosis of
respiratory distress and cyanosis in neonate beside
diaphragmatic hernia,
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