A CLINICAL REVIEW OF LIPOMYELOMENINGOCELE IN CHILDREN :

A CASE REPORT
Prima Yanuar Ovari1,Chesny Stevani Ardento2, Grace Earny Pinta Madingin Sianturi3
1
General Surgery Resident, Surgery Department, A.W. Sjahranie Hospital, Samarinda, Indonesia
2
Intern Doctor, Neurosurgery Department, A.W. Sjahranie Hospital,Samarinda, Indonesia
3
Neurosurgeon, Neurosurgery Department, A.W. Sjahranie Hospital, Samarinda,Indonesia
Samarinda, East Borneo, Indonesia.

Abstract:
Objective : To report and discuss clinical of lipomyelomeningocele
in children

Background:
Lipomyelomeningocele (LMCC) is a type of congenital spinal
dysraphism, it represent a closed neural tube defects. Some LMCC
present from infancy throughtout childhood came to neurosurgeoun
because subcatenous lumbar mass, pain, bladder dysfunction, or leg
weakness associated with the mass. LMCC has been found 0,6 per
10.000 live births.

Methods:
A 2.7 years old girl came to our outpatient neurosurgery department
with lump on the lower back since 1 months ago, the lump was
Figure 1. Photograph demonstrating a lumbar mass
progressively increasing in size. And the mother complaint about her
daughter urinary and fecal incontinence.there were no complain of
back pain. The child development were normal for the age and no
deformity. A girl was born by spontaneous vaginal delivery with
midwife, preterm labor at 28 weeks gestation with weight <2000gr.
On physical examination the lump was 6x7cm, soft concistency, and
fixed. CT-scan shows defect at vertebrae lamina L4-L5 and arcus
posterior defect at S1-S5 with LMCC. Intraoperatively, the
periphery of the fatty subcatenous mass is exposed, then the lipoma
is trimmed as completely as possible. After surgery we do
histophatology for the tissue.

Results:
Histophatological mainly showed sheets of adipocytes.
Figure 2. The intra operatif imaging of excision cele due to
During a follow up 15 days after procedure the patient show
lipomyelomeningocele
improvement wound on the lower back with no CSF leakage. The
patient was control in the outpatient clinic with no complaint.

Conclusion:
Surgery are definitive treatment for LMCC because it release the
thetering cord and reduce the bulk of fatty mass.

Keyword: lipomyelomeningocele, children

Conflict of Interest: The author have no conflict of interest to
declare

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