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é ob Hscs/ri/we2 18-19 bee ¥ Ovee Hud 89 man Hea sinh a fang gu inh oxy da thie dn. Hu qua ting sin nhigt qué nh trong ki gilm ting hop ATP gust dung chat nay, ee hu g Tang ean béo phi B. Gidm edn nhigy 'C- Khong th ay déi gi vé trong lwong co thi fog doting nhige qué mic, dng hon li nguO dp cou ng 9 cy id (CN) ep, Chon et ding nhit d8 git Ah ay chi hy th gi thich tinh tne 1 bénh ahi nay: iam pon i ids Kt (ao accel CoA) qua cu thin acid ei, gun chub hs hp o bo 6 Doge rn gts ting duing phn yém kh (go acid acta) cone coarse Q Posi rhogtos|sease hang gu tn ony hb ng trong cho hp hy, ding John atin 8 cung chp ATP pha ng eng dmg pis yee tik oe ak cane cp thém ning iuong ATP (a i) Co dising phan hiéu kh} ido yém kh go acid lactic D.Do bénh shin tng thong ®. De diém eta Glycolipid: 14-mbt los lipid tap c6 nhém ngoaili polysaccharide Grong inn a ene sphingosine, acid béo, cic mor C. Trong think phin cfu tao ob chia nh D. Gm ee cht: cor Nhiing chit nio sau day lis 15i lan, gli go acetyl CoA gm to ning omg ATP, tng dtm ung edp thém ning Iuong ATP (dla it) khi phdi nén ting acid lactic. nosaccharide va acid sialic 16m phosphate. imide, sulfatide, va ganglioside lugt la omega 3, omega 6: ‘DHA, acid linoleic B. Acid oleic, acid linoleic C Acid inlenic, DHA « Dei oles ad el done ho ed bo o5 Sg ties tng Sic AS Acid bé0 bio da e6 céng thie: Chit, ,COOH B. Acid oleic c6 cong thirc: CHa, ; COOH OAcid linolenic 66 cong thie Chita, sCOOH D. Acid arachidonic e6 céng thirc CnHmn sCOOH osphatidy! cholin ts Mt log glycerophospholipid, din xudt cla acd phosphatidic, 6 nhidu ton B. Loai glycerophospholipid, dn xudtcda acid phosphatidic, C. Din xudt cia acid phosphatidic, cdn goi la cepeliy M64 loai sphingophospholipid, cén goi la lecithin, ‘6 tham gia dieu hda téng hgp cholesterol: @ Cholesterol thite an, estrogen, acid mat CAstrogen, progesteron, cholesterol thite in la lipoprotein cé: Hot A §. Ty trong rat thdp tirl,063-1,210 _B. Ty trong thap tir 1,019-1,063 LoL TY trong rat thp tir 1,006-1,019 TY trong rat thdp tir 0,93-1,006 vio. 8 tong 48 trimg cn goi licephalin techn £6 nhigu trong long d6 trimg. 6 nigu trong long dé tring B. Cholesterol thie in, testosteron, estrogen D, Estrogen, progesteron, acid mat ot scsi. NCO SONA VATA pee eee TEE £ 1Vai ota, A AMP vi Wine ag AT nee HBtnancy, coptontin sent B Adan: or il es 8 Gaur rch AP a 2. Nene ma en hy hn Ping edi nimiacabohgatiosuibdiaote Mo ich om Po A Dot nye aie te ope abt name ranting xkae ong hot enzyme PRPP phasporsae, FAP D tenzyme Hypoxsth TP rea 7 soutien te are ee or spilt Serie ain Hobie Sot fang gl ee ar) xe te boss S phosphate Kl mel sang amincwve tip Bi AN cea bani ine ee ose cia ang Snes are mas due ane wome SS { Ailoprio| ie hot o72 ride O ratat ee chyen x B Feb ing heat eZ Ceo eci iam do ha Prt an ay phon ph a in nan oagen laine cic a sp woneptinceemtcn ea eg TSP G9 Pept di Ase rina aie, dnl asin ob 1h ing 5 ve pan gv ag vo Ninbyerinea in P GDP. GTP, GTP host ha vga ean dng tan ‘anti than Tdenosin deamina ib ure huyEt tw Sang agi cy cin mien ‘Alburiin sd wie is, hydro, Ko. nue, Ji vi base i vi acid 2. Phin img ‘ vei vita phan ing vol bas '5 Cho chin «mg Mol a: 7.86 isch slucose cho mau tim ‘inh trang huyét in. #6 hit nid cba glutathione in: gly glutamic, methionine jsltathione tr dang GP. 8 35. Mgt bénk nhén n@-20 tudi, nhép vign do gin day thdy tiéu nhidu, an nhiéu hon binh thu’mg, gay va mét mi. X6t nghifm o6 két qué nhu sau: ting glucose mau di, glucose nigu duong tinh (++), Mot tone exe coché din dén ting glucose méu & bénh nhan nay i A. Enzyme phosphoenol pyruvate carboxykinase (PEPCK) bj tre ché 22 tinghop glucose Enzyme hexokinase bj ire ché _thosi héa glucose C. Acetyl coenzyme A khéng di vio chu trinh Krebs D. Enzym glycogen phosphorylase bj fe ché tails glyonen 36. Mot nguti din 6ng 34 tui, khde manh cé néng dd glucose mau binh thutm Nhimg phan img néo sau giip duy tri glucose méu binh thug: Glycogen —> Glucose -1~P B. Acetyl CoA —> Palmitate C. Oxaloactetate —» Phosphoenolpyruvate D. Fructose 6 phosphate—> Fructose 1,6 bisphosphate . 37. Nhiing xét nghiém nao thuémg duge chi dinh dé ‘dan gid tinh trang thiéu oxy & mé: ‘A. Pyruvate va pyruvate dehydrogenase huyét thanh @® Lactate va lactate dehydrogenase huyét thanh . Pyruvate vit lactate dehydrogenase huyétthanh D ‘Lactate va pyruvate dehydrogenase huyét thanh ; 38. Mot bénh nhdn di kiém tra sit khée, bénh nhan duge ly mau va xét nghigm cing mét thai diém. 1 «qua x6t ghim cho thay: glucose méu d6i: 5,5 mmol, glucose nigu 500 mg/dl. Bgnh nbn nay c6 thé & nh nha bj dai thdo duég tiém fin B. Bénh nhiin bj cumg tuyén yén [Bénh nhin 6 nguong tdi hdp thu Gahan thép _D. Benh nhain sir dung corticoid kéo dai cose trong nub teu Si ngage la oe OSs Ko bidaito avira ‘inne her rig 4 Im) ig sau 12 gid nhin dei thto eb chin vitamin STAB. ViaminB, pantothenate 2 Sic dickens lin A phone 4.Enzym nil te phosshanes owzenne a C3 a vd chyna hh ANP hic pp na Phi hep CoQ yt rect Phige hop Il 1 CoQr cee He Locitate-sa toga; tog He; elope Co 6: Keloguaate—steciny COA males oleae Oo® inj Coa; succnate-vumarig alle sono Osorio ketosiuarate;«ketoghtarse-sucrinyi CoA men cc “4. Clean tn dn nian i hp So ee ees NES. ua. Thigu Fe 3. Thiu Aspanat 4.Ng6dbeCO 5, Thiéu Mgt Chon tip hop ding) 12,3 124 Caag Dias a 45. Thit ty céc chat chuyén héa trong thu trinh acid citric: A. Acetyl CoA + Citrate—oxaloacetate—cinate—isocitrate—v ketoputarte-scciny! (CoA—succinate—fumarate—malate Q Onaloacane + Acetyl CoA—itrate—rsocitiate—a ketoglitarate-ssucinyl yA—Succinate—fumarate—-malate C. Pyruvat— Acetyl CoA—Citrate—Isocitrate—a ketoglutarate—succiny GoASucinatefumarate—malate-ronaloaceate Acetyl CoA +oxaloncetatemalatefumarate-sucinte-»sicinyl CoAa etoglutarate—isocitratecitate . nu & dng vat c6 vi, debit. mang yt chin mo protsin oi UCP Yay Ghemogenn (eh ie) Thernopenia chi gh hepsi, Ach chy girth cee eg ermogenin nay: : . Be vit est ba dye Klch ich boi tla Kn p gio en, nga sinh ai cho ob . [Noradrenalin duge gti ping trong th ian i anh, host hoa lipase hy phn wayne cho 2 bo ai bo ot ia herogein cane ip tans nang mee “Thermpogenin giim qua tinh ox héa, tng qué tinh phosphor Shai 5 eee tng hop acid béo thanh triglyceride dit tr do haat ha ATP thanh AMP se cf qul tn phosphor! ali gdm tit scopes uok pri wae rims téng hgp ATP. Bidu nay durgc bi tir bang s “thuBe gdm can gay cht ng) ‘ an = 7 a va phi Fc Ans 8a rm byob 5 6 itu gu Seta ‘ 3 wi 5. anh in phai IA cha mf bé ees yr 2 cali = PACES: J 16.Nam ims sham pi 1G Nam lh gg ang te ging dn. Ki ig eae can ning cna ce ene meet he ia eae ane ee vn dong i tng, Naz cay ttn i Af ng i. i i Oe pg phn Oe eye patie Kang lt ne een cect yn Mipntntuuane | @tyesse c.Penreae ,D.tan sang ret, anne vr ot dg om Che inh Vin ue ea hs 1 Mo ok ep myo cums ng tg cin a tn 2,3 DPG. Phin ti ny o6 vai to: ‘A: Tang ai lye oxy v6i hemos! .6n dinh trang thai R cia hemoglobin 18, Busimg cong phin ly O2- hemoglobin lech tdi Kh Tenet vating?,3DPG_ — @Tingpltvigiim 23.976 D.Tang H* va giim pCO: rich voi ‘8. Gidm sy phn ly oxy eda hemoglobin Gn din wang thi gin mop oS ai luc yaa we OD. Jobin CTang pCOr va ting 2,3 DPC 8 Jo, THis iu i nad gi wong ng decimate Cn dung de ob min A Pes Hem. Nong cit nh au dy tng ca Kine Oc = enzym wong qu tin GsPorphiilinogen 3. Uroporphyrinogen Il , Coproporphyrin It aminolevulinic acid oy levuli i : “Me Wn one fe uro Bilirubin toan phi mol. (Binh aie - ae ats bin tlm pe 38 wel iahtsing “VE prt) mowegmaen me eatin 9 Hh Gas in ng Cn dein ony om vi inet can GQ chp i DiwtchineRocr mcewavowms sense Xee nghigm mu 6 thoi didm nh vien: . Sitivchia -Blinbin tin phn: 67 pol (Binh ing: < 17,1 uo VL Bilirubin lan pry Sau thi kt hp ex neh co lim sing Big x ng nude tbs no sn dy ph hp 9 bea ah ny ‘Ac Bilidbin dong tinh By Madi nd deng nh E.Urcbilinogen bint rato Urtiiogen ing ema . A Cong hic charibose va deoxyribose Ke hau 6 C8 Clune bj oxi hd thin srbol Fruciow: nhém OH tin acetal gin vi C2 Phin tng Feng: th hig nh bj Kc don Gung tinh Kh 26. Dh diém ndo li ding di v6i disaccharide: "A. Savearose: igo bOI glucosefuranose Va fructopyranose _glucopyranose + fructofuranose ge chin dosn ving da do aps eg 7 kon a: B. Lactose: ign ké cia 2 don ding to bei 2 nim OH bin acetal 1 C. Maltose: go b4i 2 dom duémg khic hau gi6ng (glucose) Tin Kiet lactose do nhém OH bin acetal cia glucose quyét dink 27, Bc dil nio sau day la ding d6i v6i céc polysaccaride thubn: “A. Amylopectin phan nhinh nhieu hon so vi glycogen glycogen nhiéu hon B. Glycogen ign két a 1-6 glucostd mach thing. nhénh @ celsos: chia en kB 1-4 lucosd Dextran: in kéta 1-6 gucosid mach nhén thing 28, Choiip hop ding cho duimg e6 chite aldose: Tythrose ribose ~ mannose glucose _B, Glucose ~ galactose ~ arabinose ~ ull D. Mannose ~ glucose ~ xylulose ~ galactose ©. Mannose — fructose ~ galactose ~ ribose oD pore Rs we bp, 063-1 210 15 tome tpt 1,019-1 063 Eye se ptr 1 006-1019 0 1 oe hth 095-1006 vee can bi i St sn iy tn vinta tone th, he te Sg enc pn fc, ean cn ng i chap mt ye a gage Fm? "Sie hf thu wt tan tong du eOAT Bee oa rae a Oe Sete pmmergotee Boheme Cheol, aid bso, acid phowphorie, Sines Oe aren piaaiattat ae Tree be yar Iepo na tn vere in 2 MR ean | Fe re a ly 1 pn mg Wi no mute On ONE EIS oe Do Cvs hydro Va Vpn Gn Kn me oe Ping vice yero in > ha oe Ba Gn i ei, pn emg ms phan ange Ue eS 65. Cog bens phi x0 5 ding ech Sin Sen gas yea 7 et orl tang cao din en 5 ing 6208 SIRES) © han mach Tamm tang trighyoerie ni sinh ng Brome wigye=ide mang ow tse to OSS) cn Ving dong cholesterol © thank Ging aa ecxerol vi CBE 19 do Sat ‘Acetyl CoA, ATP va) ‘Acetyl CoA, ATP va NADH ©. Ue chb enzym D. Ge ché enzyme Hi 67. Che gjai dogn chinh téng hop "A. Acety) CoA ~ isopenteny! pyroph 1 CoA — squalen — mevalonate ~ mevalonate —i — mevalonate — Pai heey re Hus mon Héa sin ng phin ly glee, thinh geet CoN ADE ohn nah Meee in be he lca eee ee ng dng pte tng to ace ee 1 Bing tao ‘slycerolqua ch ly chit ehuyén hoa lenyleyclase, glam hy yleyclase,gldm hoat enzy me protein kit c,d ay idm sr thi phinlipid do 46 ene mi bie oeh lous 0 med oe ‘hich uetng anion ee Thdeuequd age aes mss cl i ly ut gu ten nly 48g hop lines n qué trinh B oxy ha acd béo, shy a or ane bla, iting nme cn elm io acyl CoA, lam tb bap a Che 48 ting hop glucose nop Cholesterol eune hp skh xénghim bes cho la enzyme tham wia qué th, Cheah ter tow Pirie Nee eran ong acid be eud 2 tpi te 2 ii sega ne ‘cao va tir vong do bénh tim mech. Sean Neragnm cots jd na ot toan phn tng ceo * 2 Ebr sholeserol tng NStSteneral itm to binatbiceasronco agg es OE TT Hel tinge lot typ no? ‘ATypL Or, ula pit yp Gage phi 3 thang tuoi, Khd cho ain, kém pt iin vé thé Ie, Chiu cling 06 ve kém phiit trién ve ‘tinh than. Thm khém gan ach lon. Tay xuOng ‘xép, obra nid ‘sphingomyelin va ‘cholesterol (voi nhing, Ebi bop ab ng Pm iam tong Iveco tah ong nt 6 ren da (0%) Banh eM tage 4 tng 6h Seah bi ben Ty esau A i bin do tie enzyme PHENO AvB tceraid glucasidase AT Gaucher do whieu curve UST ee Niemann Pick A 60 60M sphingosaelinse Oe crigeler Naser dosh NE frgnyansfersie 72. peai trd chia AMP vong va! GTP trong din truyen ‘in higu ndi bdo: cA GDP, GDP How NER AE, means db go ANE vouBt ATE Ye teny)everase uve boat Noa fayén ADP thn AMP Yen ¢_ATP nam tcén pro me aden sei “AMP vong 190 th ace se Wich hot pts ase 73. Nguyen nha cba ben gout do y% Neca utenzme xa _ Do tang hoa! >P phospt jase fa pposphotiboast Transfers yo thieu hu 1D. Do ting hoat AGPRT)

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