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DISTRESS
SYNDROME
MATRIX NO : PBPN 1020
COHORT
: COHORT 16 (1/2016)
COURSE
NURSING
1
LEARNING OBJECTIVES
AT THE END OF THE CASE STUDY I WILL ABLE TO:
1)
2)
3)
4)
5)
6)
7)
CONT..
5) EXPLAIN THE DISEASE CONDITION INCLUDING DEFINITION,
INCIDENCE, AETIOLOGY, PATHOPHYSIOLOGY, SIGN AND SYMPTOMS
6) DESCRIBE LABORATORY FINDING OF BABY FROM ADMISSION TILL
DISCHARGE.
7) DESCRIBE RADIOLOGY FINDING OF BABY FROM ADMISSION TILL
DISCHARGE.
8) EXPLAIN DRUG COMMENCE TO THE BABY DURING HOSPITALIZATION
INCLUDING NURSING RESPONSIBILITIES PRIOR TO THE
ADMINISTRATION.
9) DESCRIBE OTHER TREATMENT GIVEN TO THE BABY.
10) EXPLAIN APPROPRIATE NURSING CARE PLAN FOR THE PATIENT
DURING HOSPITALIZATION.
11) DESCRIBE DISCHARGE PLAN INCLUDING HEALTH EDUCATION GIVEN
TO FAMILY MEMBERS REGARDING CARE OF THE BABY IN HOME
AFTER DISCHARGE.
3
12) SUMMARIZE PATIENT FLOW OF HOSPITALIZATION TILL DISCHARGE.
MY
PATIE
NT
: 40XXXX
: 10 hours of Life
SEX : FEMALE
DATE OF BIRTH
IC NUMBER
RACE
: 75XXXX-XX-XXXX
: MALAY
RELIGION : MUSLIM
DATE OF ADMISSION
: 25 OCTOBER 2016
TIME OF ADMISSION
: 2345H
CONSULTANT
: DR.Q
DISTRESS5
CONT..
DATE OF DISCHARGED : 5 NOVEMBER 2016@1340H
FOLLOW UP : 14 NOVEMBER 2016@1200H
CHIEFT COMPLAINTS
have an episode of Grunting &
chest recession soon after
delivery and was intubated
after desaturated while on
head box oxygen
HISTORY OF PRESENTING
ILLNESS
PRETERM BABY DELIVER AT 4.49PM TRANSFERRED
FROM KPJ SELANGOR AFTER HAVING DIFFICULT LSCS
DUE TO PREVIOUS SCAR IN THE LABOR.(APGAR
SCORE 7 AT 1 MINUTE AND 9 AT 5 MINUTE)
DEVELOP GRUNTING WITH CHEST RESECTION SOON
AFTER DELIVERY. PUT ON HEAD BOX
AT 8.45 PM DESATURATED AND INTUBATED WITH SIZE
3 ETT AND ANCHORED AT 9CM
7
MISS Y WAS AMBUBAGGED OXYGEN, SATURATION WAS 90
-100 FROM KPJ SELANGOR LETTER.
CONT
ON ARRIVAL MISS Y WAS DUSKY AND CYANOSED, FLAT WITH
NO SPONTANEOUS MOVEMENT, SATURATION 17 20% IN 100
%O2.
PUT ON VENTILATOR , LEAK >30%, NO BETTER, CONT.
BAGGED, STILL NO BETTER, REINTUBATED WITH ETT SIZE
3.5, FIXED AT 9 AND GIVEN CUROSORF 100MG/KG.
UAC & UVC INSERTED, DOING CXR( SEVERE RDS, LARGE
HEART AND NO PNEUMOTHORAX)
PUT ON SIPPV WITH PIP 30, PEEP 8, RATE 50, FIO2 0.9
BLOOD GASES SHOWS(MIX RESPIRATORY & METABOLIC
ACIDOSIS)
CONT. CLOSE MONITORING IN NICU
PAST HISTORY
PAST MEDICAL HISOTRY : PROLONG DELIVERY
PAST SURGICAL HISTORY : NIL
ALLERGIC
: UNKNOWN
BLOOD GROUP
: B+
MEDICATIONS
:INTRAMUSCULAR VITAMIN K
WERE GIVEN IN KPJ SELANGOR.
BIRTH HISTORY
BORN ON 24 OCTOBER 2016 @ 1649H IN HOSPITAL
KPJ SELANGOR, THROUGH LSCS PLUS VACUUM
FROM PREVIOUS SCAR IN LABOUR. IT TOOK ABOUT
20 MINUTE TO BRING HER OUT DUE TO ADHESION.
SHE IS PRETERM BABY AT 36 WEEKS OF
GESTATIONS WAS BORN WITH:
APGAR SCORE : 7 AT 1 MINUTE & 9 AT 5 MINUTE
BIRTH WEIGHT : 3.77 KG
HEAD CIRCUMFERENCE : 36 CM
BIRTH LENGTH : 56 CM
10
BIRTH HISTORY
ANTENATAL
11
IMMUNIZATIONS
FAMILY
HISTORY
13
FAMILY PEDIGREE
Mr. T
38 years old
Businessmen
NIL MEDICAL &
SURGICAL HISTORY
MISS A
3 Y/O
B.w:4.26
BORN AT 39 WEEK
HISTORY OF RDS
AFTERBIRTH
NIL SURGICAL HISTORY
Madam E
36 years old
Housewife
MEDICAL HISTORY :
GASTATIONAL DIABETIS
SURGICAL HISTORY OF LSCS
TIMES TWO
MASTER Z
2 Y/O
B.wt: 3.21
BORN AT 38 WEEK
NIL MEDICAL &
SURGICAL HISTORY
MISS Y 10 hour of
Life (patient)
BORN AT 36 WEEK
HISTORY OF
PROLONG LABOUR
FATHER:
BUSINESSM
EN
MOTHER
HOUSEW
IF
E
SOCIOECONOMIC
BACKGROUND
8000
per
month
Stay at
BANGLOW
15
PHYSICAL EXAMINATION
VITAL SIGN ON ADMISSION
TEMPERATURE : 37.4 C
PULSE
: 140BPM
BLOOD PRESSURE : 66/ 44
RESPIRATION RATE : 50BPM
SPO2 RATE
: 17% - 20%
16
10 hours of life
WEIGHT ON ADMISSION
3.77KG
HEIGHT
56 CM
HEAD CIRCUMFERENCE
36CM
CHEST CIRCUMFERENCE
34CM
NUTRITIONAL
MISS Y NIL BY MOUTH TILL 3 DAYS AND
STARTED TROPHIC FEEDING ON DAY 4
THROUGH NG TUBE FEEDING.
STARTED AMOUNT WAS 5 MLS OF EBM
(MOTHERS COLOSTRUM) FOR 3 HOURLY.
FEEDING TOLERATED WELL & ON DAY 5
FEEDING INCREASE TO10 MLS/3 HOURLY
DAY 6 INCREASE TO 30MLS/ 3 HOURLY
DAY 7 INCREASE TO 35 MLS/3 HOURLY AND
INCREASE 5 MLS FOR EVERY 2 CYCLE.
*MISS
ANATOMY
&
PHYSIOLO
GY
19
RESPIRATORY DISTRESS
SYNDROME (RDS)
IO
T
I
IN
F
E
D
N
RDS OF THE NEWBORN, ALSO KNOWN AS HYALINE
MEMBRANE DISEASE
IS A BREATHING DISORDER OF NEWBORN BABIES.
THE ALVEOLI (THE SMALL, AIR EXCHANGING SACS OF
THE LUNGS) ARE COATED BY SURFACTANT, WHICH IS A
SOAP-LIKE MATERIAL PRODUCED IN THE LUNGS AS THE
FETUS MATURES IN PREPARATION FOR BIRTH.
IF PREMATURE NEWBORNS HAVE NOT YET PRODUCED
ENOUGH SURFACTANT, THEY ARE UNABLE TO OPEN
THEIR LUNGS FULLY TO BREATHE.
G
O
L
IO
M
E
EPID Y
RESPIRATORY DISTRESS
SYNDROME
ic
t
i
s
t
St a
RESPIRATORY DISTRESS
SYNDROME
HOSPITAL
INCIDENCE
ic
t
i
s
t
St a
7
5
3
1
RESPIRATORY DISTRESS
SYNDROME
prematurity
A brother or
sister who had
RDS
maternal
diabetes.
RISK FACTORS
Multiple
pregnancy
Prolong
labor
Perinatal
asphyxia
O
L
RESPIRATORY DISTRESS
O
I
S
Y
H
P
SYNDROME
O
H
T
PA
GY
PREMATURITY & PRENATAL ASPHYXIA
REDUCED SURFACTANT SYNTHESIS, STORAGE, RELEASE
INCREASED ALVEOLAR SURFACE TENSION
PROGRESSIVE ATELECTASIS
HYPOVENTILATION
HYPOXEMIA CO2 RETENTION
RESPIRATORY ACIDOSIS
RESPIRATORY DISTRESS
n
tio
a
c
l
i
SYNDROME
p
com
1.Pneumothorax
2.pulmonary interstitial emphysema
3.persistent pulmonary hypertension
4.necrotising enterocolitis
5.intraventricular haemorrhage
6.patent ductus arteriosis
(Johnston et al, 2003)
* Miss Y develop no complication during hospitalization.
RESPIRATORY DISTRESS
N
SYNDROME
O
I
T
A
TIG
S
E
I NV
CHEST X- RAY
AN ARTERIAL BLOOD GAS
FULL BLOOD COUNT
SEPTIC SCREEN IS INDICATED IF INFECTION
IS SUSPECTED.
BUSE
y
a
r
X
t
s
e
Ch
ON ADMISSION:
25/10/16@ 0043H
POST REINTUBATED:
25/11/16@0820H
29
ay
r
X
t
s
e
h
C
ray
X
O
D
B
A
UAC REPOSITION
DATE:
25/10/16@1900HPOST UAC
ADJUSTMENT.
MARKING AT 12CM.
T
S
E
T
D
O
B LO
Date
ABG
Normal
range
25/10
27/10
0149
1408
PH
7.113
6.955
Mode: PTV
Pco2
69.6
114.3
Po2
60
19
Bic
22.3
25.4
BE
-7
-7
Glucose
10.4
7.3
Intepretation
met. acidosis
T
S
E
T
D
O
B LO
Date
ABG
Normal
range
25/10
26/10
1728
0829
PH
7.138
7.154
Mode: HFOV
Pco2
65.4
66.3
Po2
24
15
Bic
22.2
23.3
BE
-7
-5
Glucose
7.7
4.0
handling
Intepretation
T
S
E
T
D
O
B LO
Date
ABG
Normal
range
26/10
27/10
2245
0546
PH
7.518
7.386
Mode: HFOV
Pco2
22.5
32.5
Po2
192
85
Bic
18.3
19.5
BE
-5
-6
Glucose
7.4
6.5
handling
Intepretation
res. alkalosis
Normal
T
S
E
T
D
O
B LO
Date
Hb
PCV
White cells
Platelet
Neutrophils
Normal range
FBC
25/10
27/10
0240H
0806
10.0 13.1
18.5
16.5
35 45
5.3
5.5 15.5
5.2
150 509
36.4
17.1
15 55
23.3
26.3
T
S
E
T
D
O
B LO
Date
Normal
range
25/10
26/10
27/10
0240H
0903
0806
Sodium
139
139
145
Potassium
5.5
4.5
4.7
Urea
1.2
Chloride
CRP
115
0.35
17.80
2.48
TREATMENT
Treatment
1. IV drip
10%.
To
monitor
patient
responding
to
the
treatment
and
early
detection of detoriation
Related nursing
responsibilities
Maintain IV drip till
patient rehydrate and had
increased oral intake back
to normal.
Assess for the signs of
water toxicity
INTRAVENOUS FLUID
THERAPY
TO MAINTAIN PATIENTS HYDRATION STATUS
DR Q. ORDER IV DRIP DEXTROSE 10% FOR MISS Y STARTING
FROM 25/10/16 DAY 1: 60MLS/KG/DAY
DEXTROSE 10%@ 8MLS/ HOUR +INFUSION MORPHINE @1MLS /
HOUR +UAC FLUSHING 0.5MLS/HOUR.
DAY 2: 110/KG/DAY
DAY 3: 130/KG/DAY
38
TREATMENT
Treatment
Related nursing
responsibilities
Monitor O2 saturation,
Fio2, ETT marking,
Assess for the Sign or
hypoperfussion, perform
suction.strictly
Hand
hygiene and minimal
hamdling.
1. Ventilator
To assist patients
ventilation
- Give Oxygen and remove CO2 without
cause trauma to the lung
2. Feeding
Medication
Curousorf
Date On
Date Off
Dosage
Frequency
Route
25/10/2016
15/10/2016 400mg
stat
ET
25/10/2016
31/10/2016 400mg
BD
IV
26/10/2016
31/10/2016 60 mg
daily
IV
11/10/2016
16/10/2016
STAT
IV
Cafutaxime
25/10/2016
31/10/2016 200mg
BD
IV
Dobutamine
25/10/2016
27/10/2016
2mls/ho
Hourly
ur
IV
Dopamine
25/10/2016
28/10/2016
0.2mls/h
hourly
our
IV
morphine
25/10/2016
25/10/2016
1mls/ho
Hourly/ PRN IV
ur
ampicilin
Amikacin
Recurronium
1 mg
stat
40
y
d
t
u
s
Dr ug
RESPIRATORY DISTRESS
SYNDROME
Name of drug
Generic name
Action
Mode of action
Curosurf
Poractant alfa
Improve lung compliance
Absorb in the alveoli and reduce alveoli surface
tension.
Route
ETT
Dosage administered
Initial: 100mg/kg
Frequency: every 12 hour if needed
Rational for used
100- 200mg/kg
To replace surfactant deficiency and help lung in preventing
atelectatis .
No side effect
41
CONT..
Nursing
responsibilities in
serving the drug
42
y
d
t
u
s
Dr ug
RESPIRATORY DISTRESS
SYNDROME
Name of drug
Generic name
Action
Cafutaxime
Mode of action
Route
Dosage administered
Rational for used
CEFOTAXIME SODIUM
Broad spectrum cephalosporin antibiotic
43
CONT..
Nursing
responsibilities in
serving the drug
44
re
a
c
g
i
n
Nu rs
p la n
RESPIRATORY DISTRESS
SYNDROME
NURSING
DIAGNOSIS
NCP 1
Date: 25/10/2016 @ Time: 1800 pm
Nursing Diagnosis
Impaired gas exchange related to inadequate
surfactant levels
Supporting Data
-
Objective Data:
46
AND
DOCUMENT
HOURLY
FIO2
SIGNS
(TEMPERATURE,
HEART
MONITOR
LABORATORY
STUDIES
(ABGS,
GLUCOSE, ELECTROLYTES)
LAB STUDY IS ESSENTIAL MONITORING FOR
BODY SYSTEMS BALANCE
I:I TOOK ABG AND RESULT WAS MIX RESPIRATORY AND
METABOLIC ACIDOSIS.
CHILD
MUCOSA
MEMBRANE
OF
AIRWAY.
I: I ENSURE THE OXYGEN SUPPLY WAS
HUMIDIFIED AND TEMPERATURE MAINTAIN
POSITION
PATIENT
FOWLERS
TO
50
51
54
NCP 2
Date: 27/10/2016 @ Time: 2.00 pm
Nursing Diagnosis
Alteration in nutritional status less than body requirement
related respiratory distress and Nil By mouth status.
Supporting Data
Tacypnea > 60 breathe per min
Nil by mouth since birth 24/11/16 until 28nd October 2016
Orogastric feeding started on 28nd October 2016
55
56
2)
60
62
63
NCP 3
Date: 25/10/2016 @ Time: 1800 pm
Nursing Diagnosis
Ineffective thermoregulation (hypothermia) related to large body surface.
Supporting Data
-
Acrocyanosis
64
- ACROCYANOSIS
77
EVALUATIONS:
27TH OCTOBER 2016 @ 1400HOURS
CHILD EXHIBITS NO EVIDENCE OF NOSOCOMIAL
INFECTION AFTER NURSING INTERVENTION
GIVEN AND DURING HOSPITALIZATION.
RE- EVALUATION:
5 NOVEMBER 2016 @ 1200H
CHILD IS FREE FROM NOSOCOMIAL INFECTION
AFTER NURSING INTERVENTION GIVEN AND
BEFORE DISCHARGE.
81
82
84
85
88
Summary
24/10/16 @ Miss y transfer in from KPJ Selangor,
look very ill with central cyanosis, Spo2 <20%,
Intubated , Fix on ventilator leaking >30% ,OGT
tube inserted, after 30 min. still not pick up
spo2,Do CXR and Reintubated, put on PTV mode.
25/10/16@ early
morning Curousorf
400mg, Spo2 increase
to >95, turn to pinkish
in color, Sedated with
morphine infusion.
Started antibiotic.
Summary
25/10/16 @ afternoon- Desaturated, 40-60%, did
CXR, pull out ETT, increase Fio2 1.0%, MAP 4045mmhg, started infusion dobutamin, change
mode to HFOV, ABG show mix respiratory and
metabolic acidosis, ECHO done- normal
Summary
27/10/16@ morning- more
stable, fio2 0.4, spo2 >95 %
mainatain. Started BO, large
amount, CBD removed
fluid requirement110mls/kg/day.dobutamine
off. K+:3.5mmol/L+added
3.6 mls of KCL.
28/10/16morning,stable, have
eye opening. Start
trophic feeding, 5mls
for 3 hourly. Change
IPPV setting to PTV
mode, no spotanues
breathing- reduce
midazolam to 0.5
mls/hour..
Total fluid 120mls/kg/day
Summary
5/11/16@ SB
normal, -off
Photo, allow
discharge.
CONCLUSION
THE VAST MAJORITY OF BABIES WHO DEVELOP
RDS DO SO BECAUSE THEY ARE PREMATURE.
ATTEMPTS TO PREVENT EARLY DELIVERY ARE
THEREFORE A MAJOR CONSIDERATION. A NUMBER
OF STRATEGIES CAN BE USED.
95