HEM PHILIA

DOROTHY PEARL L. PALABRICA

 an inherited,
congenital
VIII, bleeding disorder
characterized by
IX, a lack of blood
clotting factors,
XI especially factors
Affects 1 in 5000 male live births

Occurs in approximately 1 in 20,000

people, accounting for 15% of
people with hemophilia
 1,200
Locally, there are only about
cases registered by Philippine
Hemophilia Foundation.
 LEVELS OF FACTOR VIII (8)
OR IX (9) IN THE BLOOD
SEVERITY

Normal (person who does 50% to 100%

not have hemophilia)

Mild hemophilia Greater than 5% but less

than 50%
Moderate hemophilia 1% to 5%

Severe hemophilia Less than 1%

Most commonly affected?
HMMMM.
Anatomy and Physiology
How bleeding stops
 How to
detect?
Family history
Symptoms (bruising,
bleeding with
circumcision, Muscle,
joint, or soft tissue
bleeding
Laboratory testing
 Diagnostics
Partial Thromboplastin
time
Prothrombin
consumption
Assays for clotting
factors VIII and IX
CT scan, MRI
General Nursing Interventions
Monitor for joint pain;
immobilize the affected
extremity if joint pain
occurs
Control joint bleeding by
immobilization, elevation,
and application of ice;
apply pressure (15
minutes) for superficial
bleeding.
 Medical Interventions
Administer replacement factors
DDAVP), a synthetic form of
vasopressin, increases plasma
factor VIII and may be
prescribed to treat mild
hemophilia
Antifibrinolytic/Antihemorrhagic
NURSING CARE PLANS