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W.I.

W.I.S (23 May 2018)


• Common TOACS Slides
Case 1
• Diagnosis

• Associated dysmorphism / Abnormalities


Case 2
• Diagnosis

• Management

• Complications
Case 3
• A 2 year old boy with respiratory distress. He
had cough and coryza 8 days back. Now with
R/R-70br/min, heart rate – 186b/min. Heart
sounds muffled. Liver 4cm palpable below
costal margin.
• Diagnosis

• ECG Findings

• Management
Spot Diagnosis A
B
C
D
E
F
G
H
1
• Williams Syndrome

• Associated Features:

• Supravalvular aortic stenosis/ mental retardation/elfin facies (full


face/broad forehead/ flat nasal bridge/rounded cheeks),
hypercalcemia/hypersensivitiy to sound/hypoplastic nails/dental
anomalies/joint hypermobility/nephrocalcinosis/hypothyroidism/poor
weight gain)
2
• Neonatal Lupus

• Topical steroids for rash


• Pace maker for complete heart block

• Cytopenias
• Hepatitis
• Complete heart block
3
• Myocarditis

• Sinus tachycardia/Atria, Ventricular


arrhythmia/Low QRS voltages/non specific ST ,
T wave changes/Heart blocks

• A.B.C/Inotropes/Diuretics/IVIG/Steroids/Ventil
ation/ECMO/Heart transplant
• APericardial effusion (Water Bottle
Silhouette)
• BBoot Shaped Heart
• CKawasaki Disease
• DErythema Marginatum
• ETuberous Sclerosis (Cardiac
Rhabdomyoma)
• FTGA (Egg on string)
• GEbstein (Box shaped)
• HTAPVR (Snow man)
• THANK YOU

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