Definition • Bronchiectasis is a chronic, irreversible dilation of the bronchi and the bronchioles.
• It is the abnormal, permanent dilatation of one or more
bronchi with destruction of bronchial wall proximal to the terminal bronchiole. • Bronchiectasis is defined as permanent, abnormal dilatation of one or more large bronchi. Classification/Types 1. Saccular or cystic 2. Cylindrical 3. Fusiform Etiology/Causes 1. Congenital • Cystic fibrosis (hereditary disease that affects the lungs and digestive system) • Ciliary dysfunction syndromes (genetic condition in which the microscopic organelles (cilia) in the respiratory system have defective function.) • Primary hypogammaglobulinaemia (problem with the immune system that prevents it from making enough antibodies called immunoglobulins) Etiology/Causes 1. Acquired-children • Pneumonia (complicating whooping cough or measles • Primary TB • Williams-Campbell syndrome (disease of the airways where cartilage in the bronchi is defective.) • Marfan’s syndrome (genetic disorder that affects the connective tissue. Those with the condition tend to be tall and thin, with long arms, legs, fingers, and toes.) • Primary immunodeficiencies • Inflammatory bowel disease, especially ulcerative colitis. • Childhood Acquired Immune Deficiency Syndrome (AIDS), • Inhaled foreign body Etiology/Causes 1. Acquired-Adult • Pneumonia • allergic bronchopulmonary aspergillosis (severe allergic reaction after being exposed to a type of fungus called Aspergillus) • Pulmonary TB • Infections caused by the staphylococcus, klebsiella • the causative agent of whooping cough • various allergies all appear to be linked to the development of Bronchiectasis • alcoholism, heroin (drug use), • Bronchial tumors • hernia can cause Bronchiectasis when the stomach acid that is aspirated into the lungs causes tissue damage. Clinical Features • The production of large quantities of purulent and often foul-smelling sputum. • The volume of sputum can be used for estimating the severity of the disease Mild < 10 mL Moderate 10~150 mL Severe >150 mL • Chronic cough Clinical Features • Hemoptysis: Frequent. Usually mild (blood streaking of purulent sputum), Massive hemoptysis is usually from dilated bronchial arteries • Recurrent pneumonia: same segment • Systemic manifestations: fever, weight loss • Chronic cough with foul smelling sputum production, Clinical Features • Some people with bronchiectasis may produce frequent green/yellow sputum (up to 240ml daily). • Pneumonia. • Frequent bronchial infections and breathlessness are two possible indicators. • Dyspnoea, • wheezing – • COPD: Sputum volume increase Investigation • Chest x-ray • Blood tests • Checking oxygen levels in the blood • Lung function tests • CT Scan • Sputum culture: Testing of the mucus to identify any bacteria present • Bronchoscopy: Obstruction – foreign body, tumor Complications • Haemoptysis, major pulmonary haemorrhage. • COPD, • Emphysema (the air sacs in the lungs (alveoli) are damaged) • Chronic respiratory insufficiency • Recurrent pneumonia • Lung abcess • Hemoptysis • Pulmonary hypertension • Hypoproteinemia • Generalized edema Nursing Diagnosis 1.Ineffective airway clearance R/t excessive secretions & weak cough. 2.Ineffective breathing pattern R/t tachypnea. Activity intolerance R/t decreased oxygen levels for metabolic demands. 3.Deficient fluid volume R/t fever, diaphoresis, & mouth breathing. 4.Imbalanced nutrition: less than body requirements R/t dyspnea. 5.Pain R/t frequent coughing. Intervention • Administer bronchodilators as prescribed. • Administer antibiotics as prescribed. • Inhalation is the preferred route • Educate regarding types of indoor and outdoor air pollution • Instruct and encourage patient in diaphragmatic breathing and effective coughing. • Adequately hydrate the patient. • Use of diaphragmatic breathing and coughing techniques. • Assist in administering nebulizer . • Avoid bronchial irritants such as cigarette smoke, • Teach early signs of infection : a. Increased sputum production b.Change in color of sputum c. Increased thickness of sputum d.Increased shortness of breath, tightness in chest, or fatigue e. Increased coughing f. Fever or chills • Administer antibiotics as prescribed. Common Surgery • Pneumonectomy (A pneumonectomy is a surgical procedure to remove a lung.) • Lobectomy (Lobectomy of the lung is a surgical operation where a lobe of the lung is removed) • Wedge resection (Wedge resection is a surgical procedure to remove a triangle-shaped slice of tissue) • Sleeve lobectomy (Surgery to remove a lung tumor in a lobe of the lung and a part of the main bronchus (airway). )