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National SVT
National SVT
4 ) :
al
hGH
+ :
hGH
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(
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iza D
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) (%
100
G6PD B
3
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G6PDB G6PDM
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iza D
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(
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A a
7).8
34
(2,5) .(.
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G6PD , 1/20
400
) 1(
-4
).( 0,5
. ATP
ATP
pH=7.5
.1
ATP O2
al
T
om ri
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iza D
r F
dfw
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4 ) :
Do
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w
02
( ATP
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1 ). 02 (.
2 ) . (.
ATP
-2
.....
4000
200
2000
1000
400
(LT/ul ) ul
(LB/ul ) ul
) ( mg/dl
)1(.
(1
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