— Cee Aus
Urinary Bladder
Soa aT
.aooen (Ecronia Vesicnt)
B bxtcophy of bladder is complete ventral defect of Urogenital sinus arc the overlying skeletal system?
‘+ Defect in the infraumbilical part of anterior abdominal wall associated with incomplete development,apterior wall ofthe bladder®
Embryology
+ Basic defect is abnormal overdevelopment ofthe cloacal membrane snd its rupture.
‘+ Timing of this rupture ofthis defective cloacal membrane determines the variant othe extrophy-epispadias complex that results
Clinical Features
‘+ Posterior wall ofthe bladder protrudes through the defect with mucosal edges fused with skin and urine spurts onto the abdominal wl
from the ureteral orifes®
7 Rectus muscles which ae inserted on the pubic rami are also widely separated,
‘+"An umbilical heria® though usually small is present along with extrophie ladder,
‘+ Anus is dislocated anteriorly in both sexes and there may be reetal prolapse°.
Complication:
+ Consequeoss of unread Bladder exstrphy are total rinay incontinence? and an increased incience of bier cance, usually
coe
+ Many untreated extrophy of bladder ees ross derangement of muscularis cons and croncinfection lading tohydronephroi®
Treatment
G Eatercysaplsiy® isthe method of choice to augment ber cepa and si in revert function
Urinary diversion with estectomy/®is treatment of coke for enal, bro or inelni DadSer
+ Complete rconsratien is acored by