Tabet | {LLL i g oRIASE | HLYOSS Ad eobed NI) Lys gll&glt seagull byl call ‘AOU | HONE 04 dea tyay j A sO X¥8Hd ped Gysely 2014 ASiyatiudl dygul onc be: Fey 7 peg ioc asl ag 350 Cpagll ALI RS 34 3 | sansa OTs stall agle bala) 5 |] gues Ayily jalll p gall dns Ass yal a glell Aad any Maa ell 9b Kat) AY) Qual Gay | (2455) ds 1 oe 53 glabra) Judes SSS cLithy « palign J gail Alasaall 5 pl ghio @ed5 palall Qudls JA elit aot s Lb Alpes yphne age gs AS Abad) LudLall obe Guat gg lym ealaa dyad A Ua 6 yt spliley ely Ga DE Gyo Aska GLA obs Ugiags (O55 yl (000.5) sail at aye - Op shaall ol atlas Ij ype plaka) Gblisy pobll Gblis (gi A pata) peel) (Sat (603) Sagal natal pl (© 1,5) plane! Ghats s palall Ghis 8 Jynall pdvall St GS Gia - (BE 5) lS Ge eal (CO) OM aa S Ji Gall pect! gay EBL Spal ol) UL! G Fiees gle MAUAN c UG) ye A ypu Syditll MCLE gle Gy ys SI aS fF gala oh YW Sle cs gs. Gl yoat ish galaly ct Vall NADH” ATP iS fu Gahan spb coyote ce gy GL aS gine Glle tans 3:2 Ayal. 2k» AN eitsil 2 B53 oa ety Vad gd COst) Cail A NADH+HT Malo! 2 4S jal AS) ATP As GI 0) 88 A WA) co 15 | 10 NADH+H | 5 — OOo 1530 45 (60 75 sa Gap 15 30 45 60 75 Sac tr tb th tr t (0 1.5) Apadill De WH 8 9 52S aS gl gall 2G Stal 3 Ot ell 4G ATP ALS 0, JS 8 i hestates 34 (eay Gag — 2014 HLGasaMl Spell - Lys eagall qabgll glgall Aulysallaglall cllee dyyssllaglell dyer — erly Myall pyle » dla - A CRAY GF eH AOL pS sil Ge Gl etd! 5) eS) galal Oe 2M ABE SS dl 0 () SEEN glans 3 4a5 gl Gyo (I) DSc! 5 Baal 4 (SoS sual Atal Lael Adah GUS ys MMC pad US 3 92 9 1 (0 2).CO 2 QESY! cL ATP AS 5 ane YL Gpbreall GalE Laake AY) Clb DDE HW eLBS Oe Cry Spall d je a ald cuiasl Lape OLS: OSM) SUE Slants! oi ey 2 SII aS gl gala Gls SAYS A pal (Dla glans igi dantayy GL | : z = Cry Spall Lah pall CO And Gol pi ulld aes aes 9} Ut ys bal jhe [eco BAGS Oy 4 Gh) bad Adal 3 "| soo LS" Cee eS MI GE SS a | » (O15) on Si nSyl galas pet all 60 40 20 (QL) 402 585 Tt 20 30 «40 50 te SY) peal) OG! 8 IS A aap Lily y Lee > (phényleétonurie) 45 + heal naditll 5 dla cap atone Ob deal eh va pall ds os (Ad gindletall ALL Ot 4 ah A se gale Gadt Fil dye hey lb oy OLBY! ease gh O Y) Slo 2 488 31 Sisy ileal) adil) sic | galell adit! wie Alas) al gall 58 5 \ | Hise | 2 Gul a T . = 1000mé call 8 | 1000 a 3000 | 2alllue sls | me/1000m cal 1,8 0,3 oF 0 Leu : 200 cs!) 300 Gs 0 Osa gt mg/1000 mé phénylpurivique)RS 34 (Fay Gopal — 2014 aimsail aygall ~ iyplldyll sagall gall glsail | 4 q Tyilpaall aglell ellos Aysysaall gglell dyed — gioyVy Myallagle « Zale - i | J dad Phénylalanine mélanine (sis! Lad) all) tyrosine BE ail Ty ele Phénylalanine ————"_, acide phénylpyruvique (Usd! gi cub} piste vas) Ep asl wg ala) yoda Zya.8t) LLM By aS) wp) gi cull Jail 5S bie pI Ua GY TT da deta | 9 dag (0.75) clad) jedi sie ALenall itil pub 2 5 1 cuttsigll Gtubes Situ 1 Asiana Gatineall yx ADN cos le 5a 3 SB gM Sb ce all Wed iL gl) nll asta cys Adel) Sha yall Cus wegtlagll ja gil gael la ites 4 AAS DI ids All Ul AB, a GS ice 405 412 ACA ATA CCT CGG CCC TIC TCA GIT........ rrr rad | Bel itl gate Zaks CGU] GUU] AUU] CCU] UUU] ACU] UcUy UGG ccc| Guc} auc| ccc} vuc| acc} ucc sade | CGA] GUA] AUA| CCA ACA| UCA ee | | CGG|_GUG ccG ACG|_UCG | Arg | Val [We [Pro [ Phe] Thr | Ser | Tm | atoms] yas dey) Gola! lite bei ABD A Bad 53) 53) Ung ae Day 2 (00.25) 412 a! 405 ADE oe By aU Cleedll jadtll ie 412 4 405 48 (1) coe pall Vagd 3 sl) dhe) cline! See eta Hib) Gbbaeall US (ple 5 § scat an 3th ag al cca ll CUS | Ge Sade DSA gle paall Jal Oe II ype Ble gh Vy cele Ja ily dligh Gls Lata «gS GDL Ge Odd oe SI esl Aepety hey Ma gh Obie OS LS Ga UW Se Fy Dae yl jl Me cholo) ola dls 015) Magy ped ole OB SLE 4 F, all Ge ge dade 3 Hoaudy le jb, Smad Glee W110 - why 5 sha gly Ab sh Gly OS 106 28>} Jia Shy yaad Gly (21) Sls Ss cas sll cits a Gata ML (01.25) C31 5H ARs Laatee Ce ol jal ces slg al 5 bIB S59! gall oe da ped UW jaly eds L 2 Bll Ssh ce Gals (r IR jn osll ce yu dal Fy po WYN gl Ge Ay ueall GE gall y GLeall U pla Gye Ay pusall 45 y gall Jalal) pi mall ud gle Qu gallo gle Gye Ag pucall 25 5 gall g Bb y SVG Gye Ay yevall AB) gall Guy ALLotall AiLcall 31 yg) F Ge Ay gees sl : -8CMg ge Ghul (0,75) AEN Uy gall 03s Gye US ab go aad a! AS eal! Aula! Lil 55) Jail 6STs 34 Gap — 2OTE HAnaatl yall ~ Wyle maga ge gaat a Apslysdllaglell ellen Xysasaall gglell ayes — ayVy Mall agle + Mele — 5) Jolaals 25 38) canal sl Gls! Abas Goes Ge Lepli b yu Sel 8S) 2 yiell of Qenthll LLY! Ga pi oun Ci taal any che a pail iagy Aad gall olaally Aantal! clea! lea! Cagltl GY «Sb Ste ¢ by ball | Sblacall 3 oly US jb gly) 2002 Abe UE Gl phy date Gtilaus Gf Glos BDU G8 old) dass gilt 1 MLW Uae phe -T | cols A yall ulead 2 445 Syan lass Ate Suis Adie CN OHS Aly galyy sat wags = Bus laull olzall 62 55. | mgiL+PT | mg. «NH, | mg/l. = DBOS aud } | 2 14,1 39 (GH) JL gly 48 36,8 164 (EB) age gly C72 S07 195 GD) Gis gals | ; gill aghecsill :PT - gall Basa) Le jDU) Cyuaas gl Aas Bays all § DA Cues gS posh path nhl -DBOS - 20°C phy UY GB all 5 cd Lapel chpeantall Gib Gye Mi ghal) Sy yaa) ge’: NAY - [ = Su ee) or jas 3 jtlae basal the | [25 JS) 25 910 Ge| 1095cH | S53 cH 3nd DBOS(mg/L)_| [Boe sh | Bs ow | 2505 oH | 05 sO oe | OT gots Ta] (mg/L) nisl = [Be T3905 ow | 0,5 90.3 o8 | 0.3.30, ow | OL psy Tl | mg/l + AD pha | 2 Abs | (O15) 1 ARS 552518) BUD Gag Boledl Sage sae 2 AAS gl yas Glbes cle lobeiel fy (2.0.75) AG! ohs gl “bos Sat sas cy nd cl 19 Aid) Gbeall le Jaleo! a ae Oe A al Go Bate gl Ge Rd ct 5 gh al gl yao eal ll il TE gall ole (8 OU glall ods 1 (atlas Gen cals UL all Gila ls “( i 2) Agclinall Gaia 5 4S Chaat ye y eke 5g pweall jloall Sala ap. gi Abas Ph Cu Fe “ug/L pg/L ug.t0/L (pose i Ph Cu Fe ng/L pg/L pg.10/L MDGS YI peal sie 8 CB) S Gale uly Lenenal gid Ad poll baal! 4 ALS Gate 3:81 5 th -2 (0 1.25) Alas Xuall (2 1.5) AUSB Galeally 00a! CALS pill Cy i Gyo gall a yen CH costal ysisase pill Use Y) ues Jaa} -3} (+) | _t F