Professional Documents
Culture Documents
A. Preoperative Preparation
1. Assess parents and child's level of understanding
2. Teaching based on developmental level
3. Involve parents and allow discussion
4. Gather baseline data
2. Pyloric stenosis
a. Congenital hypertrophy of pyloric sphincter
b. Clinical manifestations
1. Insidious vomiting occurring 2-3 weeks after birth, increasing in
intensity until forceful and projectile (no bile) by about 6 weeks of
age
2. Small olive-size mass in right upper quadrant
3. Weight loss, dehydration
4. Chronic hunger
c. Diagnosis
1. History and physical signs
2. Upper GI series
3. Barium swallow under fluoroscopy
d. Treatment
1. Correct dehydration, metabolic alkalosis
2. Pylorus resected
e. Nursing Interventions
1. Preoperative: NPO; daily weights; NG tube for gastric
decompression monitor intake, output and specific gravity;
monitor emesis
2. Postoperative: position on right side to prevent aspiration; begin
oral feedings 4-6 hours postoperatively after bowel sounds return;
maintain in upright position after feeding in infant seat; start with
small, frequent feeds of oral rehydration solution (Pedialyte);
monitor for emesis; advance feeding as tolerated.
3. Hirschsprung's disease (megacolon)
a. Congenital absence of parasympathetic ganglion in distal colon
b. Bowel proximal to a ganglionic section becomes enlarged
c. Characterized by
1. In newborn: failure to pass meconium within 24 hours after birth
2. In older child: recurrent abdominal distension; chronic
constipation with ribbon like stools; diarrhea; bile-stained emesis
d. Treatment
1. Cleansing enemas with antibiotics preoperatively
2. Temporary colostomy
3. Bowel resection to remove a ganglionic portion
e. Nursing Interventions
1. Colostomy care: same as adult client
1. Check stoma for color
2. Change dressings frequently (abdominal, perineal)
3. Monitor accurate intake and output
4. Avoid incision irritation (keep diapers low)
2. Parent and child instruction
1. Encourage independence of based on age of child
2. Discuss diet and hydration
1. Bronchial asthma
a. Also known as reactive airway disease (RAD)
b. Usually begins before 5 years of age
c. Pathology and etiology
1. Chronic condition with acute exacerbations
2. In response to allergen or trigger, acute hyperactive changes occur in
reactive (lower) airways
a. Spasm of smooth muscle
b. Edema of mucous membranes
c. Thick, tenacious mucous
d. Severe sudden dyspnea
3. Potential triggers
a. Foods
b. Inhalants (for example: secondhand smoke)
c. Infection
d. Vigorous activity
e. Stress, anxiety
f. Allergens (examples: pet dander, dust)
g. Cold air
d. Characterized by
1. Paroxysmal, hacking nonproductive cough
2. Prolonged expiratory phase with expiratory wheeze
3. Respiratory distress, anxiety
e. Complications
1. Pneumonia
2. Atelectasis
Treatment
1. Bronchodilators
a. Epinephrine (Adrenalin): subcutaneous
b. Aminophylline (Phyllocontin): IV drip
2. Steroids: IV
3. Inhalants: bronchodilators - albuterol (Proventil), metaproterenol
(Alupent)
4. Antibiotics: prophylactic
5. Hydration
6. Oxygen therapy
2. Scoliosis
a. Lateral curvature of the spine
b. Most common form is idiopathic seen (predominately) in adolescent females;
unknown etiology
c. Acquired scoliosis; associated with deformity resulting from other
neuromuscular disorders
d. DIAGNOSIS
1. Classic signs: truncal asymmetry; especially noted in hips and shoulders,
posture
2. Screening exam in school: child flexes at waist; one scapula more
prominent
3. Spinal x-ray
e. Treatment
1. Mild scoliosis (< 20° curvature): observation, encourage physical exercise
2. Moderate scoliosis (20°-40° curvature). Milwaukee brace (pelvis to neck),
Boston brace (body jacket/TLSO brace)
a. Goal is to prevent worsening of curve; not a cure
b. Nursing Interventions
1. Risk for noncompliance: difficult for adolescent due to
body image concerns; must wear 23 hours a day (one hour
off for hygiene care); wears T-shirt under brace
2. Body image disturbance: Boston brace better accepted
(can be completely hidden under clothing)
3. Severe scoliosis (> 40° curvature): surgery
a. Spinal fusion with instrumentation
b. Requires prolonged immobilization in cast, brace
or body jacket
c. Nursing Interventions
1. High risk for injury related to spinal
manipulation: log roll for the first 24 hours;
neurovascular checks; advance activity as
ordered; observe for paralytic ileus
2. Pain: adolescent good candidate for PCA
pump
a. Etiology
1. May be autoimmune response to environmental factors
2. Genetic component: inherit tendency, not disease
3. School-age child (5-7 years or at puberty)
b. Characteristics
1. Onset: rapid with progression to abrupt ketoacidosis
2. Hypertrophy and hyperplasia of islet cells occur early
3. Remission (honeymoon) phase
4. Insulin replacement (cannot use oral hypoglycemics)
5. Exercise lowers blood sugar
6. Management difficult due to
a. Immaturity of child
b. Lack of insight
c. Developmental needs
1. Preschool: biggest issues are the fear of injections and poor appetites of
preschoolers (difficult to maintain diet); "free diet"
2. School age: How will they maintain their regular activities (for example: birthday
parties, pizza after the soccer game)
3. Adolescent: Compliance is the problem. They are truly not interested in long-
term effects; they want to be like their peers.
4. Hematological Disorders
A. Hemophilia
1. Characteristics
a. Impaired coagulation: deficiency of clotting factors
b. Sex-linked recessive trait more common in males
c. Factor VIII and IX are most common deficiencies
d. Hemarthrosis (bleeding into joint cavities), bruises
easily
2. Treatment
a. Cryoprecipitate (transfusion that replaces missing
clotting factor)
b. Supportive therapy
3. Nursing Interventions
a. Control bleeding
1. Immobilize joint
2. Provide ice packs
3. Administer cryoprecipitate
a. Prophylactic cryoprecipitate for
invasive procedures
b. Risk for AIDS, hepatitis is decreased
because of screening, but does still
exist
b. Safety directed toward developmental level to
prevent injury, bleeding
1. Avoid contact sports (difficult with
children)
2. Childproof environment
3. Avoid aspirin
c. Provide parental support
2. Treatment
a. Eliminate cause of crisis
b. Analgesics
c. Blood transfusions
d. Monitor complications
1. Anemia
2. Splenic sequestration
3. Cerebrovascular accidents
3. Nursing Interventions
a. Early recognition of crisis
1. Increasing irritability
2. Frequent infections
3. Pallor
4. Failure to thrive
b. Provide hydration
c. Administer analgesics, antibiotics as ordered
d. Oxygenation
e. Reduce stress of hospitalization
f. Provide parental support
5. Renal Disorders
1. Glomerulonephritis
2. Nephrotic syndrome
RENAL DISORDERS
6. Metabolic Disorders
a. Cystic fibrosis
b. Celiac disease
A. Leukemia
1. Characteristics
a. Most common childhood cancer
b. Peak incidence: 3-5 years of age
c. Etiology: unknown, may be related to environmental exposures (example:
radiation)
d. Characterized by proliferation of abnormal white blood cells
2. Pathology
a. Bone marrow failure secondary to invasion of cancer cells
1. Temperature and infection from decreased (normal) WBCs
2. Anemia, pallor and fatigue from decreased RBCs
3. Petechiae and epistaxis from decreased platelets
b. Leukemic infiltrate
1. Limb and joint pain
2. Lymphadenopathy
3. Central nervous system (CNS) involvement
4. Hepatosplenomegaly/bleeding tendencies
5. Treatments
a. Terminology
1. Induction, remission
2. CNS prophylaxis, consolidation
3. Maintenance
b. Chemotherapy
1. Purine antagonists: 6-mercaptopurine (Purinethol) (may affect
kidneys)
2. Alkylating agents: cyclophosphamide (Cytoxan) (causes chemical
cystitis)
3. Folic acid antagonists: methotrexate (Folex)
4. Plant alkaloid: vincristine sulfate (Oncovin) (neuro toxic)
5. Steroids: prednisone (Prelone)
6. Enzymes: L-asparaginase (EIspar)
c. Radiation therapy for CNS involvement
2. Pathology
a. Arises from embryonal tissue
b. Encapsulated (do not biopsy, will "seed" tumor further)
3. Diagnosis
a. Intravenous pyelogram
b. Computerized tomography
c. Bone marrow to rule out metastasis
4. Treatment
a. Nephrectomy and adrenalectomy
b. Radiation and chemotherapy determined by staging
5. Nursing Interventions
a. Preoperative care
1. Treatment begun quickly; support parents and keep explanations
simple
2. Monitor blood pressure due to excess renin production
3. Prevent rupture of encapsulated tumor
a. Post sign on bed: "DO NOT PALPATE ABDOMEN"
b. Bathe and handle gently
b. Postoperative care
1. Problems related to radiation, chemotherapy
2. Large surgical incision
a. Pain management
b. Gentle handling
c. Prepare parents
3. Protect remaining kidney
a. Monitor blood pressure
b. Dipstick urine for protein or blood
C. Neuroblastoma
1. Characteristics
a. Most frequently seen below 2 years of age
b. Frequently called "silent" tumor because by the time of diagnosis,
metastasis has occurred
c. Clinical signs include: abdominal mass, urinary retention and frequency,
lymphadenopathy, generalized weakness, malaise
d. Primary site is abdomen, most often in flank area
2. Diagnosis
a. Computerized tomography
b. Bone marrow to determine metastasis
c. Excessive catecholamine production
3. Treatment
a. Surgery to remove as much of the tumor as possible, determine staging
b. Chemotherapy and radiation determined by staging of tumor
D. Hodgkin's Lymphoma
1. Characteristics
a. Primarily affects adolescents and young adults
b. Clinical signs include: painless enlargement of
lymph nodes (cervical most common), metastasis
related manifestations (persistent cough,
abdominal pain), systemic problems (pruritus,
night sweats, fever)
2. Treatment
a. Radiation and chemotherapy determined by
clinical staging
b. Surgical laparotomy
c. Splenectomy
3. Nursing Interventions
a. Instruct family on long-term care following
splenectomy
1. Increased susceptibility to infection
2. Prophylactic long-term antibiotic therapy
is necessary (compliance issues)