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Date : 28/07/2022

Time : 10:15:27

HOSPITAL SULTANAH NUR ZAHIRAH


KUALA TERENGGANU

MEMO
Rujukan tuan Tarikh
Rujukan kami Tarikh 28/07/2022
Kepada Sesiapa Yang Berkenaan
Tajuk Memo Pengesahan Penyakit
Daripada Jabatan Pesakit Luar HSNZ
Salinan kepada Pusat Latihan Pengajar Dan Kemahiran Lanjutan (CIAST)
Klasifikasi

MUHAMMAD AMIN SYAKIR BIN AHMAD ZAIDI


020110-11-0285

20 years old Malay Male


.
Problem:
1) Beta Thalassemia Major
- dx at age of 3
- Tranfusion dependent
- on regular blood transfusion
- aim Hb pre-tx > 8
- infective screening on 12/01/2022 : NR
- latest serum ferritin 7201.3(22/08/2021) -→8433.8(12/01/2022) -→ 9264.5 (14/07/2022)
- done MRI T2* 11/07/2019
1. Mild liver and myocardial iron overload.
2. Hepatosplenomegaly
- echo 11/04/2021 : mild MR, Good LV Sytolic Function, ef 78%
- done MRI T2 on 29/11/2021
.
2) Spelonomegaly with cholelithiasis
- done splenectomy and cholecystectomy on 25/08/2021
.
Current meds:
T Ferriprox 1g TDS
Sc desferral 2.5 g od (5-7days/ week)
Vit c 100 mg od
Ca lactate 600mg od
T vit d ->pt buy from pharmacy
Oral maxolon 10mg tds/prn
Penicillin

This patient had regular 4-6 weeks follow up at paediatric daycare clinic adm 2-3 weeks follow up
on MOPD based on his iron overload.

DR. AUNI FARZANAH BINTI AWANG DAHAN (90061)


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