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UKK: Respiratory
Category: ePoster Presentation
Code: P - RES - 024

A 2-month-old baby girl with congenital cystic

adenomatoid malformation: a case report
David Anggara Putra(1) , Sacharissa Ardelia Larasati(2) , Ismiranti Andarini(2)

Department of Child Health, Medical Faculty of Sebelas Maret University/ Dr. Moewardi General Hospital,
Surakarta (1)
Department of Child Health, Medical Faculty of Sebelas Maret University/ Dr. Moewardi General Hospital,
Surakarta (2)

Background: Congenital cystic adenomatoid malformation (CCAM) is a rare congenital developmental

deformity of the lower respiratory tract. Its etiology remains unknown. The incidence of CCAM ranging
between 1:10,000 and 1:35,000 newborns. The pathological changes of CCAM patients include expansion of
pulmonary lobe or segment, single or multiple cystic shadows, ipsilateral pulmonary tissue compression
and pulmonary hypoplasia.

Objective: To describe the diagnosis and treatment of congenital cystic adenomatoid malformation.
Case: A baby girl admitted to Dr. Moewardi General Hospital with breathlessness and recurrent respiratory
tract infection since birth. In physical examination revealed tachypnea, nasal flare, subcostal retraction,
late li ed le -sided chest wall movement, bulging, widened intercostal space, hypersonor in percussion,
without vesicular sound. An X-ray demostrated giant bullae in the le lung with heart shadow was
displaced to the right. A chest CT scan revealed multiple air-filled vesicles in the le lung with di erent
sizes, with the diameter between 3 cm and 5 cm. Large cystic cavity compressed mediastinum, pulmonary
tissue, and trachea. An echocardiography showed dextroversion. She underwent a le thoracotomy and a
left lower bulectomy. Biopsy revealed type 1 congenital cystic adenomatoid malformation (CCAM).
Conclusion: Routine antenatal care with ultrasonography will help in detecting cystic lung lesions, which
allows for proper planning of peripartum and neonatal management. The diagnosis of congenital cystic
adenomatoid malformation (CCAM) is established based on clinical and pathological features, based on
Stocker’s classification. In the case of respiratory compromise, resection is indicated and is curative.
Keyword : congenital, cystic, adenomatoid, malformation, children