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EULAR Textbook on Systemic Sclerosis

List of chapters

No. Topic

Introduction

01 Systemic Sclerosis (diagnosis, differential diagnosis, evaluation of laboratory tests)

02 Localised scleroderma

03 Epidemiology

04 Activity

05 The natural history of systemic sclerosis and assessment of disease severity and damage

Pathogenesis

06 Synthesis: Early and late pathological events in scleroderma

07 Vascular disease in systemic sclerosis

08 Synthesis: Fibrosis in systemic sclerosis

09 Immunological changes in systemic sclerosis

10 Autoantibodies and autoimmunity in systemic sclerosis

11 The genetics of systemic sclerosis

Clinical manifestations: Skin, Peripheral Vascular

12 Skin involvement

13 Raynaud’s phenomenon

14 Nailfold capillaroscopy and other methods to assess microvasculopathy in systemic sclerosis

15 Microvascular and macrovascular disease in systemic sclerosis with refence to the digits

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EULAR | Education
Seestrasse 240 | 8802 Kilchberg | Switzerland
T: +41 44 716 30 30
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Heart involvement

16 Clinical consequences of functional and pathological changes in scleroderma cardiac


involvement

17 Diastolic dysfunction in systemic sclerosis

18 Arrhythmias and conduction in systemic sclerosis

19 Microvascular involvement in primary scleroderma myocardial disease

20 Pericarditis in systemic sclerosis

Pulmonary interstitial/vascular involvement

21 Interstitial lung disease associated with systemic sclerosis

22 Pulmonary arterial hypertension associated with scleroderma

Clinical manifestations: GI

23 The gastrointestinal tract in systemic sclerosis

24 Small intestinal involvement in systemic sclerosis

25 Colonic and anal involvement in systemic sclerosis

Scleroderma renal disease

26 Kidney involvement in systemic sclerosis: clinical characteristics and biopsy

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EULAR | Education
Seestrasse 240 | 8802 Kilchberg | Switzerland
T: +41 44 716 30 30
education@eular.org | esor.eular.org
Clinical manifestations: musculoskeletal disability

27 Joint involvement and synovitis in systemic sclerosis

28 Muscle involvement in systemic sclerosis and scleroderma-myositis overlap syndromes

29 Hand function in systemic sclerosis

30 Quality of life and functional disability in systemic sclerosis

31 Pain and fatigue in systemic sclerosis

32 Strategy in patient management

33 Patient education and lifestyle advice

34 Rehabilitation (including hands)

35 Management of systemic sclerosis with disease-modifying antirheumatic drugs

36 Vasodilators

37 Haematopoietic stem cell transplantation

Special conditions

38 Life-threating conditions: emergencies in scleroderma

39 Pregnancy and gynaecological problems in systemic sclerosis

40 Very early and early systemic sclerosis

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EULAR | Education
Seestrasse 240 | 8802 Kilchberg | Switzerland
T: +41 44 716 30 30
education@eular.org | esor.eular.org

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