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GambarTatalaksana Transposisi Arteri Besar
Keterangan : TAB = transposisi arteri besar; PAB = pulmonary artery bandirg; BTS=
BlalockTaussig Shunt: LVOTO = left ventricular outflow tract obstruction: PART= pulmonary
artery resistance index; F'GE= prostag!an"in F
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Kesimpulan
Kon"isi $ipo%se&ia 'ang ber!angs(ng !a&a &en'ebab%an ti&b(!n'a beberapa pen'(!it
pa"a P)B sianoti%* Beberapa pen'(!it it( a"a!a$ po!isite&ia "an sin"ro& $iper+is%ositas, stro%e,
abses, "iatesis $e&oragi%, ne-ropati,en"o%ar"itis, ane&ia "e-isiensi besi, $ipertensi p(!&ona! "an
gaga! .ant(ng 'ang a%an sangat &e&pengar($i per.a!anan $i"(p pen"erita P)B sianoti%* Pen'(!it
'ang ter.a"i a"a 'ang bersi-at re+ersibe! tetapi a"a .(ga 'ang &eningga!%an ge.a!a sisa 'ang
irre+ersibe!* /nt(% &en0ega$ ti&b(!n'a pen'(!it pa"a P)B sianoti% 'ait( "engan 0ara ti"a%
&en(n"a be"a$ %ore%si ata( pa!iati- bagi pen"erita P)B sianoti%* Se$ingga pengeta$(an tentang
in"i%asi "an 1a%t( opti&a! inter+ensi be"a$ pa"a !esi pira( %anan %e %iri P)B sangat "iper!(%an
(nt(% &en"apat prognosa pas%a be"a$ 'ang opti&a!
DaftarPustaka
* Par% 2K* Pe"iatri0 0ar"io!og' -or pra0titioners, e"isi %e34* P$i!a"e!p$ia: 2osb'; 2005*
2* 6inasKese$atanPro+insi)a1a Barat*Pro-i!%ese$atanpro+insi)a1a Barat* Ban"(ng:
6eparte&enKese$atanPro+insi)a1a Barat; 2007*
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2
8* Pa(! 6A, Karen L, Sara$ 9, )a&es E* B!oo" is t$i0%er t$an 1ater: T$e &anage&ent o-
$iper+is0osit' in a"(!ts 1it$ 0'anoti0 $eart "isease* 9ar"io! in Re+ 2005;4:;:837*
7* 6re'er <E, 2a$one' 6=, 209!ain KL, Pop!a0% 6G* =e&ato!ogi0 iss(es o- i&portan0e
-or t$e pe"iatri0 0ar"io!ogist* 6a!a&: Garson S, Bri0%er )T, Fis$er 6), >eis$ SR,
Pen'(nting* T$e s0ien0e an" pra0ti0e o- pe"iatri0 0ar"io!og'* Se0on" e"ition* Ba!ti&ore:
?i!!ia&s@?i!%insAAB:257234*
4* Fis$&an 2A, Par% )T* >e(ro!ogi0 0o&p!i0ations in 0$i!"ren 1it$ 0ongenita! $eart
"isease* 6a!a&: Garson S, Bri0%er )T, Fis$er 6), >eis$ SR, Pen'(nting* T$e s0ien0e an"
pra0ti0e o- pe"iatri0 0ar"io!og'* Se0on" e"ition* Ba!ti&ore:
?i!!ia&s@?i!%insAAB:250A38*
#* A&itai C, B!ie"en L, S$anto+, >e(-e!"* 9erebro+as0(!ar a00i"ents in in-ants an" 0$i!"ren
1it$ 0ongenita! 0'anoti0 $eart "isease* Dsr ) 2e" S0i AB7:7834*
5* Per!o-- )K, 2are!!i A), 2iner P6* Ris% o- stro%e in a"(!ts 1it$ 0'anoti0 0ongenita! $eart
"isease* 9ir0(!ation AA8;B5:A473A*
B* AtiE 2, A$&e" /S, A!!ana SS, 9$is$ti K>* 9!ini0a! -eat(res an" o(t0o&e o- 0erebra!
abs0ess in 0ongenita! $eart "isease* ) A'(b 2e" 9o!! Abbottaba" 200#;B:2;:237*
A* AtiE 2, A$&e" /S, A!!ana SS, 9$is$ti K>* Brain ab0ess in 0$i!"ren* Dn"ian ) Pe"iatr
200#;58:4;:7037*
0* =origo&e =, =ira&ats( C, S$igeta O, >agasa1a T, 2ats(i A* O+erpro"(0tion o- p!ate!et
&i0roparti0!es in 0'anoti0 0ongenita! $eart "isease 1it$ po!'0't$e&ia* ) A& 9o!!9ar"io!
2002;8A:05235*
* Dnato&i ), 2ats(o%o K, F(.i&ar( R, >a%aga1a A, Di.i&a K* 2e0$anis&s o- "e+e!op&ent
an" progression o- 0'anoti0 nep$ropat$'* ) Dnt Pe"iatri0 >ep$r Ass*200#
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2* <e!tser D, Tabb(tt S* 9riti0a! $eart "isease in t$e ne1born* 6a!a&Vetter VL, pen'(nting*
Pe"iatri0 0ar"io!og': t$e reE(isites in pe"iatri0s* P$i!a"e!p$ia: E!se+ier 2osb'; 200#* $*
8340*
8* Breitbart RE, F!'er 69* Tetra!og' o- -a!!ot* 6a!a&: Keane )F, Lo0% )E, F!'er 69,
pen'(nting* >A6ASF pe"iatri0 0ar"io!og'* E"isi %e32* P$i!a"e!p$ia: E!se+ier Sa(n"ers;
200#* $* 44A35A*
7* Si1i% ES, Erenberg FG, <a$%a KG, Go!"&(ntG E* Tetra!og' o- -a!!ot* 6a!a&: A!!en =6,
6ris0o!! 6), S$a""' RE, Fe!tes TF, pen'(nting* =eart "isease in in-ants, 0$i!"ren, an"
a"o!es0ents* E"isi %e35* P$i!a"e!p$ia: Lippin0ott ?i!!ia&s an" ?i!%ins; 200B* $* BBB3
A0*
4* Ci32ing ?eng C2, 9$ang C9, 9$i( TF* Tet spe!! in an a"(!tA&eri0an )o(rna! o-
E&ergen0' 2e"i0ine :200A; 25, 80*e8H80*e4
#* Ra$a'oe A/* Dn"i%asi"anpe&i!i$an1a%t( 'ang
tepat(nt(%inter+ensipen'a%it.ant(ngba1aan* 6a!a&: P(tra ST, A"+ani >, Ra$a'oe A/,
pen'(nting* 6asar3"asar "iagnosis "antata!a%sanapen'a%it.ant(ngpa"aana%* )a%arta:
For(& D!&ia$ Kar"io!ogi Ana%; AAB* $* #83B2*
5* Keane )F, F!'er 69* 6o(b!e o(t!et rig$t +entri0!e* 6a!a&: Keane )F, Lo0% )E, F!'er 69,
pen'(nting* >A6ASF pe"iatri0 0ar"io!og'* E"isi %e32* P$i!a"e!p$ia: E!se+ier Sa(n"ers;
200#* $* 58437*
B* F(!ton 6R, F!'er 69* 63transposition o- t$e great arteries* 6a!a&: Keane )F, Lo0% )E,
F!'er 69, pen'(nting* >A6ASF pe"iatri0 0ar"io!og'* E"isi %e32* P$i!a"e!p$ia: E!se+ier
Sa(n"ers; 200#* $* #743#*

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