1.

Hy
pogonadi
sm i
susual
lyencount
eredi
nthef
oll
owi
ngcondi
ti
ons,
except
A.Congeni
tal
adr
enal
hyper
plasi
a
B.NoonanSy
ndr
ome
C.Pr
ader
-Wi
l
liSy
ndr
ome
D.Bar
det
-Bi
edl
Syndr
ome

2.A6yearoldgi
rlwithshor tstat
ure,st
reakgonadsandmildmentalr
etar
dati
onhasarenal
ul
tr
asoundforafi
rsturinarytracti
nfect
ion.Arenalanomal
yisseenduri
ngtheexami
nati
on.
Whichi
sthemostlikelydiagnosis?
A.Uni
l
ater
alr
enal
agenesi
s
B.Mul
ti
cyst
icki
dney
C.Pol
ycy
sti
cki
dney
s
D.Hor
seshoeki
dney

3.Absol
utei
ndi
cat
ionsf
orsur
gical
expl
orat
ionwi
tha14y
earol
dchi
l
dwi
thr
enal
traumaar
eal
l
,
except
A.Expandi
ng,
pul
sat
il
eret
roper
it
oneal
haemat
omawi
thhaemody
nami
cinst
abi
l
ity
B.Penet
rat
ingt
raumawi
thpr
ogr
essi
vehy
pot
ensi
onandt
achy
car
dia
C.Coexi
sti
ngl
argebowel
inj
urywi
thanext
ensi
veuni
l
ater
alr
enal
inj
ury
D.Gr
ade4r
enal
inj
urycl
asi
fi
edt
heAmer
icanAssoci
ati
onofTr
aumaSur
ger
y

D
4.Ababyboypr
esent
swi
thar
ightsi
dedhy
dronephr
osi
sandanAPdi
amet
erof25mm.
MAG3scanr
eveal
ed48%di
ff
erent
ial
funct
ion.Thenextst
epi
s
A.I
VP
B.wat
chf
ulwai
ti
ng
C.VCUG
D.py
elopl
ast
y

B
5.I
na2y earol
dboywit
hunil
ater
alcr
ypt
orchi
dism l
aparoscopyi
sperfor
medr eveal
i
ngan
i
ntr
abdominalt
est
icl
eappr
ox.4cm abov
etheinter
nalingui
nalri
ng.Thebestt
reatmentopt
ion
i
s
A.t
wost
ageFowl
er-
Stephenspr
ocedur
e
B.onest
ageFowl
er-
Stephenspr
ecedur
e
C.i
ngui
nal
inci
sionandscr
otal
fixat
ion
D.or
chi
ect
omy

A
6.A3monthsoldboypr
esentswit
haunil
ater
alupperpol
ehydronephr
osi
sduetoauret
erocel
e.
MAG3scanreveal
edgoodfunct
ionoft
heupperpolebutobst
ruct
ed.Deobst
ruct
ingt
hesyst
em
i
sbestachi
evedwit
h
A.ur
eter
ocel
epunct
ure
B.per
cut
aneousnephr
ost
omy
C.openr
esect
ionandr
eimpl
ant
ati
on
D.st
ent
ing

A
7.A2y earol
dboyhasal eftt
esti
culartumor
.Serum Al
fafetopr
otei
niselevat
edandserum
humanchor i
oni
cgonadotrophi
nlevelisnor
mal.Computerizedtomographyscanshowsno
evi
denceofamet ast
ati
cdisease.
Thet umorismostli
kelytobea
A.gonadobl
ast
oma
B.y
olksact
umor
C.epi
der
moi
dcy
st
D.t
erat
oma

B
8.Themai
nsi
teofbi
car
bonat
ereabsor
pti
oni
s
A.pr
oxi
mal
tubul
e
B.col
l
ect
ingduct
C.di
stal
tubul
e
D.l
oopsofHenl
e

A
9.Ayoungadol
escentwast
reat
edforaki
dneyst
one.Ev
aluat
ionr
eveal
edamedul
l
arysponge
ki
dney.Themostcommonfindi
ngwil
lbe
A.hy
per
oxal
uri
a
B.hy
per
cit
rat
uri
a
C.hy
per
cal
cur
ia
D.hy
per
phosphat
aemi
a

10.Thegeneassoci
atedwi
thVonHi
ppel
-Li
ndaudi
seasei
slocat
edonchr
omosome
A.3
B.9
C.11
D.16

A
11.Youareurgentl
ycall
edtotheneonat
ologydepar
tmentbecauseachi
ldisbor
nwithgeni
tal
ambiguit
y.Pr
enatalkar
yotypi
nghasshowna46XX.Whenexami ni
ngthechil
dyoucanobserv
e
aseverel
yvir
il
izedgeni
talandnogonadspalpabl
e.Whati
syournextst
ep?
A.r
epeatkar
yot
ype
B.HCGst
imul
ati
ont
est
C.ser
um el
ect
rol
ytes
D.hor
monal
scr
eeni
ng

12.A13yearsol
dboyi
sseenbecauseofi
nter
mit
tentt
ermi
nal
hemat
uri
a(spot
ti
ngof
under
wear)
Ur
inecul
tur
eisnegat
iveandul
tr
asoundoft
heur
inar
ytr
actr
eveal
snopat
hol
ogy
.
Whati
sthemostpr
obabl
edi
agnosi
s?
A.ur
ethr
alst
one
B.bul
barur
ethr
it
is
C.i
nfect
edsy
ringocoel
e
D.bal
ani
ti
s

B
13.Acoll
eaguer
efer
syouapat
ientwi
thacaecour
eter
ocel
e.Oni
nvest
igat
iony
ouwoul
dex
pect
tofi
nd:
A.aur
eter
ocel
ethatempt
iesi
ntot
hecol
on
B.agappi
ngopenur
eter
ocel
e
C.aur
eter
ocel
edescendi
ngi
nthesubmucosat
hrought
hebl
adderneck
D.aur
eter
ocel
ewi
thnour
eter
icor
if
ice

C
14.Theprobabi
l
ityofdi
sordersofsexual
dev
elopment(
DSD)i
naboywi
thpeni
l
ehy
pospadi
as
andpalpabl
eundescendedtesti
sis:
A.10%
B.30%
C.50%
D.70%

15.Pr
enatal
diagnosi
sofcongeni
tal
adrenal
hyper
plasi
a(CAH)i
ntheat
-r
iskf
etusi
smost
speci
fi
cal
l
ymadebyameasur ementofamniot
icf
lui
dfor:
A.17-
ket
ost
eroi
ds
B.17-
hydr
oxy
progest
eron
C.11-
deoxy
cor
ti
cost
eron
D.dehy
droepi
andr
ost
erone

B
16.TheX-
rayabov
eshows

A.post
eri
orur
ethr
alv
alv
es
B.ant
eri
orur
ethr
alv
alv
es
C.sy
ringocel
e
D.v
alv
eofGuer
in
D

17.Thei
nci
denceofr
efl
uxi
nof
fspr
ingi
s
A.10%
B.30%
C.66%
D.90%

18.I
nanewbornwi
thaseverefor
m ofaut
osomal
recessi
vepol
ycy
sti
cki
dneydi
sease,
whati
s
themostcommoncauseofneonat
aldeat
h?
A.Renal
insuf
fi
ciency
B.Li
veri
nsuf
fi
ciency
C.Por
tal
hyper
tensi
on
D.Respi
rat
oryi
nsuf
fi
ciency

19.Whatist
hepr
imar
ymechani
sm ofal
phabl
ocker
sint
het
reat
mentofchi
l
dren´
sbl
adder
dysf
unct
ion?
A.det
rusorr
elaxat
ion
B.bl
adderneckr
elaxat
ion
C.bl
adderneckcont
ract
ion
D.pel
vi
cfl
oorr
elaxat
ion
B

20.Whi
chi
sthemostcommonel
ect
rol
ytedi
stur
bancei
nagast
rocy
stopl
ast
y?
A.Hy
pochl
oraemi
cmet
abol
i
cal
kal
osi
s
B.Hy
per
chl
oraemi
cmet
abol
i
cal
kal
osi
s
C.Hy
pochl
oraemi
cmet
abol
i
caci
dosi
s
D.Hy
per
chl
oraemi
cmet
abol
i
caci
dosi
s