. HANDOUT . .

SUBJECT:- Adult Health Nursing

TOPIC:-SEMINAR ON Thalassemia.
GUIDED BY:- Mrs. Khomeshwari Yadu( Msc. Lecturer)
PRESENTED BY:- MS. Kalpana sahu Basic bsc(N) 3rd Sem)
CHAIR PERSON:- MS. Prachi patel ( Basic bsc(N) 3rd Sem) ..

 INTRODUCTION-  RISK FACTORS-

Thalassemia is an inherited blood 1. Family history of thalassemia
disorder in which the body 2. Iron overload
produce abnormal from of 3. Viral infection
himoglobin which result in
excessive destruction of red blood  ETIOLOGY-
cell and further lead to anemia
1. genetic
 DEFINITION
2. hemoglobin
According to Barbra k.timby
Talassemia is may be defiend as it is the 3. mutation in DNA
of inherited blood disorder 4. iron deficiency
characterized by abnormal formation.  PATHOPHYSIOLOGY-

 ANATOMY & PHYSIOLOGY- Due to etiology factor

Disturbance of ratio between

the alpha and beta globin chain
synthesis

Degrees production of one

haemoglobin struchure
 TYPES OF THALASSEMIA
A. ALPHA THALASSEMIA. Formation of abnormal
B. BETA THALASSEMIA. himoglobin struchure

 CLINICAL MANIFESTATION-
 Pele skin Enfective erythropoies
 fatigue
 Enlarge liver Hypochromia [an abnormal
  Bone abnormality
 Slow growth
 Shortness of breath
 DIAGNOSTIC EVALUATION-
1. History taking
2. Physical evaluation
3. Blood test
4. electrophoresis
5. bone marrow examination
 MANAGEMENT- Nursing management
1) Medical management
Blood transfusion
Iron chelation therapy
Folic acid supplement.
4) SURGICAL MANAGEMENT-
A. Bone marrow
transplantation
B. Splenectomy.
5) DIERTARY MANAGEMENT-
Iron rich diet.
Vitamin B diet.
 COMPLICATION-
 REHABILITION-
 CONCLUSION-
decrease in the haemoglobin
content of RBC
Exterme microcytosis [smaller
than normal RBC
Destruction of blood
elements[hemolysis]thalassemia
ACC TO ROY adaption thory
NURSING DIAGNOSIS- pain is related
to in effective tissue perfusion as
evidence by disturbed behaviour.
ACC TO FLORENCE NIGHTINGALE
THEORY-
Inefficient breathing pattern related
to insuffient oxygen supply to
muscles to skeletal muscle ewakness
and compromiswd respiratory state
ACC TO FLORENCE NIGHINGLE
THEORY-
Risk of infection related
compromised immune system as
evidence by raised body
temperature.
ACC TO ORANGE THEORY
Imbalance nutrition less than
requirement is related to inadequate
the tree intake as evidence by
weight loss and dry skin..
 Bone deformity
 Heart problem
 Late complication
 Slow growth
 Enlaege spleen
 Rehabilitation
 SUMMARY-

Thank you……